{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,1]],"date-time":"2026-10-01T17:28:05Z","timestamp":1790875685636,"version":"4.1.0"},"reference-count":38,"publisher":"Elsevier BV","issue":"1","license":[{"start":{"date-parts":[[1998,8,1]],"date-time":"1998-08-01T00:00:00Z","timestamp":901929600000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.elsevier.com\/tdm\/userlicense\/1.0\/"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Experimental Cell Research"],"published-print":{"date-parts":[[1998,8]]},"DOI":"10.1006\/excr.1998.4147","type":"journal-article","created":{"date-parts":[[2002,9,16]],"date-time":"2002-09-16T15:46:56Z","timestamp":1032191216000},"page":"22-28","source":"Crossref","is-referenced-by-count":20,"title":["Complementation of Transformed Fibroblasts from Patients with Combined Xeroderma Pigmentosum\u2013Cockayne Syndrome"],"prefix":"10.1006","volume":"243","author":[{"given":"Aaron R.","family":"Ellison","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Thierry","family":"Nouspikel","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Nicolaas G.J.","family":"Jaspers","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Stuart G.","family":"Clarkson","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Dieter C.","family":"Gruenert","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"78","reference":[{"key":"10.1006\/excr.1998.4147_EX984147RF1","doi-asserted-by":"crossref","first-page":"135","DOI":"10.1146\/annurev.bi.65.070196.001031","article-title":"DNA repair in eukaryotes","volume":"65","author":"Wood","year":"1996","journal-title":"Annu. Rev. Biochem."},{"key":"10.1006\/excr.1998.4147_EX984147RF2","doi-asserted-by":"crossref","first-page":"652","DOI":"10.1038\/218652a0","article-title":"Defective repair replication of DNA in xeroderma pigmentosum","volume":"218","author":"Cleaver","year":"1968","journal-title":"Nature"},{"key":"10.1006\/excr.1998.4147_EX984147RF3","series-title":"The Metabolic and Molecular Basis of Inherited Disease","article-title":"Xeroderma pigmentosum and Cockayne syndrome","author":"Cleaver","year":"1995"},{"key":"10.1006\/excr.1998.4147_EX984147RF4","doi-asserted-by":"crossref","first-page":"43","DOI":"10.1146\/annurev.bi.65.070196.000355","article-title":"DNA excision repair","volume":"65","author":"Sancar","year":"1996","journal-title":"Annu. Rev. Biochem."},{"key":"10.1006\/excr.1998.4147_EX984147RF5","doi-asserted-by":"crossref","first-page":"68","DOI":"10.1002\/ajmg.1320420115","article-title":"Cockayne syndrome: Review of 140 cases","volume":"42","author":"Nance","year":"1992","journal-title":"Am. J. Med. Genet."},{"key":"10.1006\/excr.1998.4147_EX984147RF6","doi-asserted-by":"crossref","first-page":"4704","DOI":"10.1073\/pnas.87.12.4707","article-title":"The genetic defect in Cockayne's syndrome is associated with a defect in repair of UV-induced DNA damage in transcriptionally active DNA","volume":"87","author":"Venema","year":"1990","journal-title":"Proc. Natl. Acad. Sci. USA"},{"key":"10.1006\/excr.1998.4147_EX984147RF7","doi-asserted-by":"crossref","first-page":"5890","DOI":"10.1093\/nar\/21.25.5890","article-title":"Deficient repair of the transcribed strand of active genes in Cockayne's syndrome cells","volume":"21","author":"van Hoffen","year":"1993","journal-title":"Nucleic Acids Res."},{"key":"10.1006\/excr.1998.4147_EX984147RF8","doi-asserted-by":"crossref","first-page":"445","DOI":"10.1007\/BF01542989","article-title":"Genetic complementation groups in cockayne syndrome","volume":"7","author":"Tanaka","year":"1981","journal-title":"Som. Cell Genet."},{"key":"10.1006\/excr.1998.4147_EX984147RF9","doi-asserted-by":"crossref","first-page":"5806","DOI":"10.1128\/MCB.10.11.5806","article-title":"Molecular cloning of the human DNA excision repair gene ERCC-6","volume":"10","author":"Troelstra","year":"1990","journal-title":"Mol. Cell. Biol."},{"key":"10.1006\/excr.1998.4147_EX984147RF10","doi-asserted-by":"crossref","first-page":"555","DOI":"10.1016\/0092-8674(95)90028-4","article-title":"The Cockayne syndrome group A gene encodes a WD repeat protein that interacts with CSB protein and a subunit of RNA polymerase IIH","volume":"82","author":"Henning","year":"1995","journal-title":"Cell"},{"key":"10.1006\/excr.1998.4147_EX984147RF11","first-page":"185","article-title":"Xeroderma pigmentosum complementation group G associated with Cockayne syndrome","volume":"53","author":"Vermeulen","year":"1993","journal-title":"Am. J. Hum. Genet."},{"key":"10.1006\/excr.1998.4147_EX984147RF12","first-page":"191","article-title":"Clinical heterogeneity within xeroderma pigmentosum associated with mutations in the DNA repair and transcription gene ERCC3","volume":"54","author":"Vermeulen","year":"1994","journal-title":"Am. J. Hum. Genet."},{"key":"10.1006\/excr.1998.4147_EX984147RF13","first-page":"167","article-title":"Molecular and cellular analysis of the DNA repair defect in a patient in xeroderma pigmentosum complementation group D who has the clinical features of xeroderma pigmentosum and Cockayne syndrome","volume":"56","author":"Broughton","year":"1995","journal-title":"Am. J. Hum. Genet."},{"key":"10.1006\/excr.1998.4147_EX984147RF14","doi-asserted-by":"crossref","first-page":"607","DOI":"10.1136\/jmg.33.7.607","article-title":"Xeroderma pigmentosum\u2013Cockayne syndrome complex: A further case","volume":"33","author":"Hamel","year":"1996","journal-title":"J. Med. Genet."},{"key":"10.1006\/excr.1998.4147_EX984147RF15","doi-asserted-by":"crossref","first-page":"58","DOI":"10.1126\/science.8465201","article-title":"DNA repair helicase: A component of BTF2 (TFIIH) basic transcription factor","volume":"260","author":"Schaeffer","year":"1993","journal-title":"Science"},{"key":"10.1006\/excr.1998.4147_EX984147RF16","doi-asserted-by":"crossref","first-page":"2388","DOI":"10.1002\/j.1460-2075.1994.tb06522.x","article-title":"The ERCC2\/DNA repair protein is associated with the class II BTF2\/TFIIH transcription factor","volume":"13","author":"Schaeffer","year":"1994","journal-title":"EMBO"},{"key":"10.1006\/excr.1998.4147_EX984147RF17","doi-asserted-by":"crossref","first-page":"769","DOI":"10.1038\/368769a0","article-title":"Dual role of TFIIH in DNA excision repair and transcription by RNA polymerase II","volume":"368","author":"Drapkin","year":"1994","journal-title":"Nature"},{"key":"10.1006\/excr.1998.4147_EX984147RF18","doi-asserted-by":"crossref","first-page":"2415","DOI":"10.1074\/jbc.270.6.2415","article-title":"Reconstitution of human DNA repair excision nuclease in a highly defined system","volume":"270","author":"Mu","year":"1995","journal-title":"J. Biol. Chem."},{"key":"10.1006\/excr.1998.4147_EX984147RF19","doi-asserted-by":"crossref","first-page":"10718","DOI":"10.1073\/pnas.93.20.10718","article-title":"Transcription factor TFIIH and DNA endonuclease Rad2 constitute yeast nucleotide excision repair factor 3: Implications for nucleotide excision repair and Cockayne syndrome","volume":"93","author":"Habraken","year":"1996","journal-title":"Proc. Natl. Acad. Sci. USA"},{"key":"10.1006\/excr.1998.4147_EX984147RF20","doi-asserted-by":"crossref","first-page":"2157","DOI":"10.1021\/bi9524124","article-title":"Interactions involving the human RNA polymerase II transcription\/nucleotide excision repair factor TFIIH, the nucleotide excision repair protein XPG and Cockayne syndrome group B (CSB) protein","volume":"35","author":"Iyer","year":"1996","journal-title":"Biochemistry"},{"key":"10.1006\/excr.1998.4147_EX984147RF21","first-page":"L347","article-title":"Culture and transformation of human airway epithelial cells","volume":"268","author":"Gruenert","year":"1995","journal-title":"Am. J. Physiol."},{"key":"10.1006\/excr.1998.4147_EX984147RF22","doi-asserted-by":"crossref","first-page":"1493","DOI":"10.1093\/carcin\/15.8.1493","article-title":"Correction by the ERCC2 gene of UV sensitivity and repair deficiency phenotype in a subset of trichothiodystrophy cells","volume":"15","author":"Mezzina","year":"1994","journal-title":"Carcinogenesis"},{"key":"10.1006\/excr.1998.4147_EX984147RF23","doi-asserted-by":"crossref","first-page":"339","DOI":"10.1007\/BF00291378","article-title":"Clinical and biochemical studies in three patients with severe early infantile Cockayne syndrome","volume":"83","author":"Jaeken","year":"1989","journal-title":"Hum. Genet."},{"key":"10.1006\/excr.1998.4147_EX984147RF24","doi-asserted-by":"crossref","first-page":"3353","DOI":"10.1128\/MCB.7.9.3353","article-title":"Unique DNA repair properties of a xeroderma pigmentosum revertant","volume":"7","author":"Cleaver","year":"1987","journal-title":"Mol. Cell. Biol."},{"key":"10.1006\/excr.1998.4147_EX984147RF25","doi-asserted-by":"crossref","first-page":"990","DOI":"10.1126\/science.275.5302.990","article-title":"Defective transcription-coupled repair of oxidative base damage in Cockayne syndrome patients from XP group G","volume":"275","author":"Cooper","year":"1997","journal-title":"Science"},{"key":"10.1006\/excr.1998.4147_EX984147RF26","doi-asserted-by":"crossref","first-page":"3116","DOI":"10.1073\/pnas.94.7.3116","article-title":"A common mutational pattern in Cockayne syndrome patients from xeroderma pigmentosum group G: Implications for a second XPG function","volume":"94","author":"Nouspikel","year":"1997","journal-title":"Proc. Natl. Acad. Sci. USA"},{"key":"10.1006\/excr.1998.4147_EX984147RF27","doi-asserted-by":"crossref","first-page":"671","DOI":"10.1038\/296671a0","article-title":"Enhanced transformation of human fibroblasts by origin-defective simian virus 40","volume":"296","author":"Small","year":"1982","journal-title":"Nature"},{"key":"10.1006\/excr.1998.4147_EX984147RF28","doi-asserted-by":"crossref","first-page":"5951","DOI":"10.1073\/pnas.85.16.5951","article-title":"Characterization of human tracheal epithelial cells transformed by an origin-defective simian virus 40","volume":"85","author":"Gruenert","year":"1988","journal-title":"Proc. Natl. Acad. Sci. USA"},{"key":"10.1006\/excr.1998.4147_EX984147RF29","doi-asserted-by":"crossref","first-page":"182","DOI":"10.1038\/363182a0","article-title":"Complementation of the DNA repair defect in xeroderma pigmentosum group G cells by a human cDNA related to yeast RAD2","volume":"363","author":"Scherly","year":"1993","journal-title":"Nature"},{"key":"10.1006\/excr.1998.4147_EX984147RF30","doi-asserted-by":"crossref","first-page":"248","DOI":"10.1016\/0003-2697(76)90527-3","article-title":"A rapid and sensitive method for the quantification of microgram quantities of protein utalizing the principle of protein-dye binding","volume":"72","author":"Bradford","year":"1976","journal-title":"Anal. Biochem."},{"key":"10.1006\/excr.1998.4147_EX984147RF31","doi-asserted-by":"crossref","first-page":"293","DOI":"10.1101\/SQB.1980.044.01.033","article-title":"Origin-defective mutants of SV40","volume":"44","author":"Gluzman","year":"1980","journal-title":"Cold Spring Harbor Symp. Quant. Biol."},{"key":"10.1006\/excr.1998.4147_EX984147RF32","doi-asserted-by":"crossref","first-page":"69","DOI":"10.1002\/jcp.1030650110","article-title":"SV40-induced transformation and recovery of human diploid cells: crisis and recovery","volume":"65","author":"Girardi","year":"1965","journal-title":"J. Cell Comp. Physiol."},{"key":"10.1006\/excr.1998.4147_EX984147RF33","doi-asserted-by":"crossref","first-page":"522","DOI":"10.1165\/ajrcmb\/8.5.522","article-title":"An immortalized cystic fibrosis tracheal epithelial cell line homozygous for the dF508 CFTR mutation","volume":"8","author":"Kunzelmann","year":"1993","journal-title":"Am. J. Respir. Cell Mol. Biol."},{"key":"10.1006\/excr.1998.4147_EX984147RF34","doi-asserted-by":"crossref","first-page":"155","DOI":"10.1093\/mutage\/8.2.155","article-title":"A single-site mutation in the XPAC gene alters photoproduct recognition","volume":"8","author":"McDowell","year":"1993","journal-title":"Mutagenesis"},{"key":"10.1006\/excr.1998.4147_EX984147RF35","doi-asserted-by":"crossref","first-page":"2794","DOI":"10.1128\/MCB.7.8.2794","article-title":"Immortalization of human fibroblasts transformed by origin-defective simian virus 40","volume":"7","author":"Neufeld","year":"1987","journal-title":"Mol. Cell. Biol."},{"key":"10.1006\/excr.1998.4147_EX984147RF36","first-page":"59","article-title":"Establishment by SV40 transformation and characteristics of a cell line of xeroderma pigmentosum belonging to complementation group F","volume":"112","author":"Yagi","year":"1983","journal-title":"Mutat. Res."},{"key":"10.1006\/excr.1998.4147_EX984147RF37","doi-asserted-by":"crossref","first-page":"13","DOI":"10.1007\/BF01560723","article-title":"Immortalization of xeroderma pigmentosum cells by simian virus 40 DNA having a defective origin of DNA replication","volume":"12","author":"Canaani","year":"1986","journal-title":"Somatic Cell Mol. Genet."},{"key":"10.1006\/excr.1998.4147_EX984147RF38","doi-asserted-by":"crossref","first-page":"8368","DOI":"10.1073\/pnas.93.16.8368","article-title":"Ultraviolet-induced movement of the human DNA repair protein, Xeroderma pigmentosum type G, in the nucleus","volume":"93","author":"Park","year":"1996","journal-title":"Proc. Natl. Acad. Sci. USA"}],"container-title":["Experimental Cell Research"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0014482798941477?httpAccept=text\/xml","content-type":"text\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.elsevier.com\/content\/article\/PII:S0014482798941477?httpAccept=text\/plain","content-type":"text\/plain","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2019,12,16]],"date-time":"2019-12-16T04:12:48Z","timestamp":1576469568000},"score":1,"resource":{"primary":{"URL":"https:\/\/linkinghub.elsevier.com\/retrieve\/pii\/S0014482798941477"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[1998,8]]},"references-count":38,"journal-issue":{"issue":"1","published-print":{"date-parts":[[1998,8]]}},"alternative-id":["S0014482798941477"],"URL":"https:\/\/doi.org\/10.1006\/excr.1998.4147","relation":{},"ISSN":["0014-4827"],"issn-type":[{"value":"0014-4827","type":"print"}],"subject":[],"published":{"date-parts":[[1998,8]]}}}