{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,13]],"date-time":"2026-10-13T01:47:45Z","timestamp":1791856065261,"version":"4.3.4"},"publisher-location":"Berlin, Heidelberg","reference-count":10,"publisher":"Springer Berlin Heidelberg","isbn-type":[{"value":"9783642249358","type":"print"},{"value":"9783642249365","type":"electronic"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2012]]},"DOI":"10.1007\/8904_2011_69","type":"book-chapter","created":{"date-parts":[[2011,9,21]],"date-time":"2011-09-21T12:04:01Z","timestamp":1316606641000},"page":"103-106","source":"Crossref","is-referenced-by-count":9,"title":["Cerebral Edema in Maple Syrup Urine Disease Despite Newborn Screening Diagnosis and Early Initiation of Treatment"],"prefix":"10.1007","author":[{"given":"Kenneth A.","family":"Myers","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Melanie","family":"Reeves","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Xing-Chang","family":"Wei","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Aneal","family":"Khan","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2011,9,22]]},"reference":[{"key":"69_CR1_69","first-page":"1219","volume":"11","author":"J Brismar","year":"1990","unstructured":"Brismar J, Aqeel A, Brismar G et al (1990) Maple syrup urine disease: findings on CT and MR scans of the brain in 10 infants. AJNR Am J Neuroradiol 11:1219\u20131228","journal-title":"AJNR Am J Neuroradiol"},{"key":"69_CR2_69","doi-asserted-by":"publisher","first-page":"499","DOI":"10.1007\/s00234-002-0771-5","volume":"44","author":"F Cavalleri","year":"2002","unstructured":"Cavalleri F, Berardi A, Burlina AB et al (2002) Diffusion-weighted MRI of maple syrup urine disease encephalopathy. Neuroradiology 44:499\u2013502","journal-title":"Neuroradiology"},{"key":"69_CR3_69","doi-asserted-by":"publisher","first-page":"719","DOI":"10.1590\/S0004-282X2009000400033","volume":"67","author":"JR Ferraz-Filho","year":"2009","unstructured":"Ferraz-Filho JR, Floriano VH, Quirici MB et al (2009) Contribution of the diffusion-weighted MRI in the diagnosis and follow-up of encephalopathy caused by maple syrup urine disease in a full-term newborn. Arq Neuropsiquiatr 67:719\u2013723","journal-title":"Arq Neuropsiquiatr"},{"key":"69_CR4_69","doi-asserted-by":"publisher","first-page":"393","DOI":"10.1007\/s00234-003-1035-8","volume":"45","author":"W Jan","year":"2003","unstructured":"Jan W, Zimmerman RA, Wang ZJ et al (2003) MR diffusion imaging and MR spectroscopy of maple syrup urine disease during acute metabolic decompensation. Neuroradiology 45:393\u2013399","journal-title":"Neuroradiology"},{"key":"69_CR5_69","doi-asserted-by":"publisher","first-page":"1793","DOI":"10.1111\/j.1471-4159.1973.tb00298.x","volume":"20","author":"MS Patel","year":"1973","unstructured":"Patel MS, Auerbach VH, Grover WD et al (1973) Effect of the branched-chain alpha-keto acids on pyruvate metabolism by homogenates of human brain. J Neurochem 20:1793\u20131796","journal-title":"J Neurochem"},{"key":"69_CR6_69","doi-asserted-by":"publisher","first-page":"524","DOI":"10.1097\/01.rct.0000164667.65648.72","volume":"29","author":"M Sakai","year":"2005","unstructured":"Sakai M, Inoue Y, Oba H et al (2005) Age dependence of diffusion-weighted magnetic resonance imaging findings in maple syrup urine disease encephalopathy. J Comput Assist Tomogr 29:524\u2013527","journal-title":"J Comput Assist Tomogr"},{"key":"69_CR7_69","doi-asserted-by":"publisher","first-page":"106","DOI":"10.1016\/j.compmedimag.2006.11.005","volume":"31","author":"RN Sener","year":"2007","unstructured":"Sener RN (2007) Maple syrup urine disease: diffusion MRI, and proton MR spectroscopy findings. Comput Med Imaging Graph 31:106\u2013110","journal-title":"Comput Med Imaging Graph"},{"key":"69_CR8_69","doi-asserted-by":"publisher","first-page":"232","DOI":"10.1016\/j.bbadis.2003.09.010","volume":"1639","author":"AM Sgaravatti","year":"2003","unstructured":"Sgaravatti AM, Rosa RB, Schuck PF et al (2003) Inhibition of brain energy metabolism by the alpha-keto acids accumulating in maple syrup urine disease. Biochim Biophys Acta 1639:232\u2013238","journal-title":"Biochim Biophys Acta"},{"key":"69_CR9_69","doi-asserted-by":"publisher","first-page":"333","DOI":"10.1016\/j.ymgme.2009.12.007","volume":"99","author":"KA Strauss","year":"2010","unstructured":"Strauss KA, Wardley B, Robinson D et al (2010) Classical maple syrup urine disease and brain development: principles of management and formula design. Mol Genet Metab 99:333\u2013345","journal-title":"Mol Genet Metab"},{"key":"69_CR10_69","doi-asserted-by":"publisher","first-page":"903","DOI":"10.1093\/brain\/awp024","volume":"132","author":"WJ Zinnanti","year":"2009","unstructured":"Zinnanti WJ, Lazovic J, Griffin K et al (2009) Dual mechanism of brain injury and novel treatment strategy in maple syrup urine disease. Brain 132:903\u2013918","journal-title":"Brain"}],"container-title":["JIMD Reports","JIMD Reports - Case and Research Reports, 2011\/3"],"original-title":[],"link":[{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1007\/8904_2011_69","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2019,5,10]],"date-time":"2019-05-10T14:58:01Z","timestamp":1557500281000},"score":1,"resource":{"primary":{"URL":"http:\/\/link.springer.com\/10.1007\/8904_2011_69"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2011,9,22]]},"ISBN":["9783642249358","9783642249365"],"references-count":10,"URL":"https:\/\/doi.org\/10.1007\/8904_2011_69","relation":{},"ISSN":["2192-8304","2192-8312"],"issn-type":[{"value":"2192-8304","type":"print"},{"value":"2192-8312","type":"electronic"}],"subject":[],"published":{"date-parts":[[2011,9,22]]}}}