{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,2,18]],"date-time":"2026-02-18T11:10:01Z","timestamp":1771413001286,"version":"3.50.1"},"publisher-location":"New York, NY","reference-count":84,"publisher":"Springer US","isbn-type":[{"value":"9781461406525","type":"print"},{"value":"9781461406532","type":"electronic"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2012]]},"DOI":"10.1007\/978-1-4614-0653-2_23","type":"book-chapter","created":{"date-parts":[[2012,3,12]],"date-time":"2012-03-12T08:35:13Z","timestamp":1331541313000},"page":"300-316","source":"Crossref","is-referenced-by-count":13,"title":["Pick\u2019s Disease"],"prefix":"10.1007","author":[{"given":"Naoya","family":"Takeda","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Yuki","family":"Kishimoto","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Osamu","family":"Yokota","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"297","reference":[{"key":"23_CR1","first-page":"165","volume":"17","author":"A Pick","year":"1892","unstructured":"Pick A. Ueber die Beziehungen der senilen Hirnatrophie zur Aphasie. Prag Med Wochenschr 1892; 17: 165\u2013167.","journal-title":"Prag Med Wochenschr"},{"key":"23_CR2","doi-asserted-by":"publisher","first-page":"356","DOI":"10.1007\/BF02866241","volume":"4","author":"A Alzheimer","year":"1911","unstructured":"Alzheimer A. \u00dcber eigenartige Krankheitf\u00e4lle des sp\u00e4tern Alters. Z Ges Neurol Psychiatr 1911; 4: 356\u2013385.","journal-title":"Z Ges Neurol Psychiatr"},{"key":"23_CR3","doi-asserted-by":"publisher","first-page":"470","DOI":"10.1007\/BF02878348","volume":"101","author":"K Onari","year":"1926","unstructured":"Onari K, Spatz H. Anatomische Beitr\u00e4ge zur Lehre von pickschen umschriebenen Gr\u00f6\u00dfhirnrinden Atrophie (Picksche Krankheit). Z Ges Neurol Psychiatr 1926; 101:470\u2013511.","journal-title":"Z Ges Neurol Psychiatr"},{"key":"23_CR4","doi-asserted-by":"crossref","first-page":"1415","DOI":"10.1212\/WNL.31.11.1415","volume":"31","author":"JL Cummings","year":"1981","unstructured":"Cummings JL, Duchen LW. Kl\u00fcver-Bucy syndrome in Pick disease: clinical and pathologic correlations. Neurology 1981; 31:1415\u20131422.","journal-title":"Neurology"},{"key":"23_CR5","doi-asserted-by":"publisher","first-page":"416","DOI":"10.1136\/jnnp.57.4.416","volume":"57","author":"The Lund and Manchester Groups","year":"1994","unstructured":"The Lund and Manchester Groups. Clinical and neuropathological criteria for frontotemporal dementia. J Neurol Neurosurg Psychiatry 1994; 57:416\u2013418.","journal-title":"J Neurol Neurosurg Psychiatry"},{"key":"23_CR6","doi-asserted-by":"crossref","first-page":"1546","DOI":"10.1212\/WNL.51.6.1546","volume":"51","author":"D Neary","year":"1998","unstructured":"Neary D, Snowden JS, Gustafson L et al. Frontotemporal lobar degeneration: a consensus on clinical diagnostic criteria. Neurology 1998; 51:1546\u20131554.","journal-title":"Neurology"},{"key":"23_CR7","doi-asserted-by":"publisher","first-page":"1171","DOI":"10.1093\/brain\/112.5.1171","volume":"112","author":"WR Gibb","year":"1989","unstructured":"Gibb WR, Luthert PJ, Marsden CD. Corticobasal degeneration. Brain 1989; 112:1171\u20131192.","journal-title":"Brain"},{"key":"23_CR8","doi-asserted-by":"publisher","first-page":"333","DOI":"10.1001\/archneur.1964.00460160003001","volume":"10","author":"JC Steele","year":"1964","unstructured":"Steele JC, Richardson JC, Olszewski J. Progressive supranuclear palsy. A heterogeneous degeneration involving the brain stem, basal ganglia and cerebellum with vertical gaze and pseudobulbar palsy, nuchal dystonia and dementia. Arch Neurol 1964; 10:333\u2013359.","journal-title":"Arch Neurol"},{"key":"23_CR9","doi-asserted-by":"publisher","first-page":"124","DOI":"10.1016\/0304-3940(87)90204-7","volume":"76","author":"H Braak","year":"1987","unstructured":"Braak H, Braak E. Argyrophilic grains: characteristic pathology of cerebral cortex in cases of adult onset dementia without Alzheimer changes. Neurosci Lett 1987; 76:124\u2013127.","journal-title":"Neurosci Lett"},{"key":"23_CR10","doi-asserted-by":"publisher","first-page":"467","DOI":"10.1002\/ana.410160408","volume":"16","author":"D Munoz-Garcia","year":"1984","unstructured":"Munoz-Garcia D, Ludwin SK. Classic and generalized variants of Pick\u2019s disease: a clinicopathological, ultrastructural and immunocytochemical comparative study. Ann Neurol 1984; 16:467\u2013480.","journal-title":"Ann Neurol"},{"key":"23_CR11","doi-asserted-by":"publisher","first-page":"177","DOI":"10.1016\/S0304-3940(03)00100-9","volume":"341","author":"NJ Cairns","year":"2003","unstructured":"Cairns NJ, Perry RH, Jaros E et al. Patients with a novel neurofilamentopathy: dementia with neurofilament inclusions. Neurosci Lett 2003; 341:177\u2013180.","journal-title":"Neurosci Lett"},{"key":"23_CR12","doi-asserted-by":"publisher","first-page":"2291","DOI":"10.1093\/brain\/awg231","volume":"126","author":"KA Josephs","year":"2003","unstructured":"Josephs KA, Holton JL, Rossor MN et al. Neurofilament inclusion body disease: a new proteinopathy. Brain 2003; 126:2291\u20132303.","journal-title":"Brain"},{"key":"23_CR13","doi-asserted-by":"publisher","first-page":"602","DOI":"10.1016\/j.bbrc.2006.10.093","volume":"351","author":"T Arai","year":"2006","unstructured":"Arai T, Hasegawa M, Akiyama H et al. TDP-43 is a component of ubiquitin-positive tau-negative inclusions in frontotemporal lobar degeneration and amyotrophic lateral sclerosis. Biochem Biophys Res Commun 2006; 351:602\u2013611.","journal-title":"Biochem Biophys Res Commun"},{"key":"23_CR14","doi-asserted-by":"publisher","first-page":"130","DOI":"10.1126\/science.1134108","volume":"314","author":"M Neumann","year":"2006","unstructured":"Neumann M, Sampathu DM, Kwong LK et al. Ubiquitinated TDP-43 in frontotemporal lobar degeneration and amyotrophic lateral sclerosis. Science 2006; 314:130\u2013133.","journal-title":"Science"},{"key":"23_CR15","doi-asserted-by":"publisher","first-page":"339","DOI":"10.1006\/neur.1996.0046","volume":"5","author":"M Jackson","year":"1996","unstructured":"Jackson M, Lennox G, Lowe J. Motor neuron disease-inclusion dementia. Neurodegeneration 1996; 5:339\u2013350.","journal-title":"Neurodegeneration"},{"key":"23_CR16","doi-asserted-by":"publisher","first-page":"5","DOI":"10.1007\/s00401-007-0237-2","volume":"114","author":"NJ Cairns","year":"2007","unstructured":"Cairns NJ, Bigio EH, Mackenzie IR et al. Neuropathologic diagnostic and nosologic criteria for frontotemporal lobar degeneration: consensus of the consortium for frontotemporal lobar degeneration. Acta Neuropathol 2007; 114:5\u201322.","journal-title":"Acta Neuropathol"},{"key":"23_CR17","doi-asserted-by":"publisher","first-page":"15","DOI":"10.1007\/s00401-008-0460-5","volume":"117","author":"IR Mackenzie","year":"2009","unstructured":"Mackenzie IR, Neumann M, Bigio EH et al. Nomenclature for neuropathologic subtypes of frontotemporal lobar degeneration: consensus recommendations. Acta Neuropathol 2009; 117:15\u201318.","journal-title":"Acta Neuropathol"},{"key":"23_CR18","doi-asserted-by":"crossref","first-page":"1376","DOI":"10.1212\/01.WNL.0000139809.16817.DD","volume":"63","author":"NJ Cairns","year":"2004","unstructured":"Cairns NJ, Grossman M, Arnold SE et al. Clinical and neuropathologic variation in neuronal intermediate filament inclusion disease. Neurology 2004; 63:1376\u20131384.","journal-title":"Neurology"},{"key":"23_CR19","doi-asserted-by":"publisher","first-page":"617","DOI":"10.1007\/s00401-009-0598-9","volume":"118","author":"DG Munoz","year":"2009","unstructured":"Munoz DG, Neumann M, Kusaka H et al. FUS pathology in basophilic inclusion body disease. Acta Neuropathol 2009; 118:617\u2013627.","journal-title":"Acta Neuropathol"},{"key":"23_CR20","doi-asserted-by":"publisher","first-page":"605","DOI":"10.1007\/s00401-009-0581-5","volume":"118","author":"M Neumann","year":"2009","unstructured":"Neumann M, Roeber S, Kretzschmar HA et al. Abundant FUS-immunoreactive pathology in neuronal intermediate filament inclusion disease. Acta Neuropathol 2009; 118:605\u2013616.","journal-title":"Acta Neuropathol"},{"key":"23_CR21","doi-asserted-by":"crossref","first-page":"251","DOI":"10.1212\/WNL.40.2.251","volume":"40","author":"DS Knopman","year":"1990","unstructured":"Knopman DS, Mastri AR, Frey WH 2nd et al. Dementia lacking distinctive histologic features: a common non-Alzheimer degenerative dementia. Neurology 1990; 40:251\u2013256.","journal-title":"Neurology"},{"key":"23_CR22","doi-asserted-by":"publisher","first-page":"551","DOI":"10.1007\/s00401-006-0123-3","volume":"112","author":"IR Mackenzie","year":"2006","unstructured":"Mackenzie IR, Shi J, Shaw CL et al. Dementia lacking distinctive histology (DLDH) revisited. Acta Neuropathol 2006; 112:551\u2013559.","journal-title":"Acta Neuropathol"},{"key":"23_CR23","doi-asserted-by":"crossref","first-page":"s24","DOI":"10.1002\/ana.10571","volume":"54","author":"DG Munoz","year":"2003","unstructured":"Munoz DG, Dickson DW, Bergeron C et al. The neuropathology and biochemistry of frontotemporal dementia. Ann Neurol 2003; 54 Suppl 5:s24\u2013s28.","journal-title":"Ann Neurol"},{"key":"23_CR24","doi-asserted-by":"publisher","first-page":"369","DOI":"10.1111\/j.1365-2990.2003.00545.x","volume":"30","author":"KA Josephs","year":"2004","unstructured":"Josephs KA, Holton JL, Rossor MN et al. Frontotemporal lobar degeneration and ubiquitin immunohistochemistry. Neuropathol Appl Neurobiol 2004; 30:369\u2013373.","journal-title":"Neuropathol Appl Neurobiol"},{"key":"23_CR25","doi-asserted-by":"publisher","first-page":"952","DOI":"10.1002\/ana.20873","volume":"59","author":"MS Forman","year":"2006","unstructured":"Forman MS, Farmer J, Johnson JK et al. Frontotemporal dementia: clinicopathological correlations. Ann Neurol 2006; 59:952\u2013962.","journal-title":"Ann Neurol"},{"key":"23_CR26","doi-asserted-by":"publisher","first-page":"76","DOI":"10.1046\/j.1440-1789.2000.00270.x","volume":"20","author":"K Ikeda","year":"2000","unstructured":"Ikeda K. Neuropathological discrepancy between Japanese Pick\u2019s disease without Pick bodies and frontal lobe degeneration type of frontotemporal dementia proposed by Lund and Manchester Group. Neuropathology 2000; 20:76\u201382.","journal-title":"Neuropathology"},{"key":"23_CR27","doi-asserted-by":"publisher","first-page":"1","DOI":"10.1007\/s00401-009-0612-2","volume":"119","author":"IR Mackenzie","year":"2010","unstructured":"Mackenzie IR, Neumann M, Bigio EH et al. Nomenclature and nosology for neuropathologic subtypes of frontotemporal lobar degeneration: an update. Acta Neuropathol 2010; 119:1\u20134.","journal-title":"Acta Neuropathol"},{"key":"23_CR28","doi-asserted-by":"publisher","first-page":"1282","DOI":"10.1093\/brain\/awn061","volume":"131","author":"IR Mackenzie","year":"2008","unstructured":"Mackenzie IR, Foti D, Woulfe J et al. Atypical frontotemporal lobar degeneration with ubiquitin-positive, TDP-43-negative neuronal inclusions. Brain 2008; 131:1282\u20131293.","journal-title":"Brain"},{"key":"23_CR29","doi-asserted-by":"publisher","first-page":"2922","DOI":"10.1093\/brain\/awp214","volume":"132","author":"M Neumann","year":"2009","unstructured":"Neumann M, Rademakers R, Roeber S et al. A new subtype of frontotemporal lobar degeneration with FUS pathology. Brain 2009; 132:2922\u20132931.","journal-title":"Brain"},{"key":"23_CR30","doi-asserted-by":"publisher","first-page":"629","DOI":"10.1007\/s00401-009-0602-4","volume":"118","author":"S Frank","year":"2009","unstructured":"Frank S, Tolnay M. Frontotemporal lobar degeneration: toward the end of confusion. Acta Neuropathol 2009; 118:629.","journal-title":"Acta Neuropathol"},{"key":"23_CR31","doi-asserted-by":"publisher","first-page":"435","DOI":"10.1002\/ana.21154","volume":"61","author":"C Azmador-Ortiz","year":"2007","unstructured":"Azmador-Ortiz C, Lin WL, Ahmed Z et al. TDP-43 immunoreactivity in hippocampal sclerosis and Alzheimer\u2019s disease. Ann Neurol 2007; 61:435\u2013445.","journal-title":"Ann Neurol"},{"key":"23_CR32","doi-asserted-by":"publisher","first-page":"125","DOI":"10.1007\/s00401-008-0480-1","volume":"117","author":"T Arai","year":"2009","unstructured":"Arai T, Mackenzie IR, Hasegawa M et al. Phosphorylated TDP-43 in Alzheimer\u2019s disease and dementia with Lewy bodies. Acta Neuropathol 2009; 117:125\u2013136.","journal-title":"Acta Neuropathol"},{"key":"23_CR33","doi-asserted-by":"publisher","first-page":"284","DOI":"10.1016\/j.brainres.2007.09.048","volume":"1184","author":"S Higashi","year":"2007","unstructured":"Higashi S, Iseki E, Yamamoto R et al. Concurrence of TDP-43, tau and alpha-synuclein pathology in brains of Alzheimer\u2019s disease and dementia with Lewy bodies. Brain Res 2007; 1184:284\u2013294.","journal-title":"Brain Res"},{"key":"23_CR34","doi-asserted-by":"publisher","first-page":"221","DOI":"10.1007\/s00401-007-0261-2","volume":"114","author":"H Nakashima-Yasuda","year":"2007","unstructured":"Nakashima-Yasuda H, Uryu K et al. Co-morbidity of TDP-43 proteinopathy in Lewy body related diseases. Acta Neuropathol 2007; 114:221\u2013229.","journal-title":"Acta Neuropathol"},{"key":"23_CR35","doi-asserted-by":"crossref","unstructured":"Yokota O, Davidson Y, Arai T et al. Effect of topographical distribution of alpha-synuclein pathology on TDP-43 accumulation in Lewy body disease. Acta Neuropathol 2010, in press.","DOI":"10.1007\/s00401-010-0731-9"},{"key":"23_CR36","doi-asserted-by":"publisher","first-page":"555","DOI":"10.1097\/NEN.0b013e31817713b5","volume":"67","author":"K Uryu","year":"2008","unstructured":"Uryu K, Nakashima-Yasuda H, Forman MS et al. Concomitant TAR-DNA-binding protein 43 pathology is present in Alzheimer disease and corticobasal degeneration but not in other tauopathies. J Neuropathol Exp Neurol 2008; 67:555\u2013564.","journal-title":"J Neuropathol Exp Neurol"},{"key":"23_CR37","doi-asserted-by":"publisher","first-page":"1386","DOI":"10.1093\/brain\/awm065","volume":"130","author":"M Hasegawa","year":"2007","unstructured":"Hasegawa M, Arai T, Akiyama H et al. TDP-43 is deposited in the Guam parkinsonism-dementia complex brains. Brain 2007; 130:1386\u20131394.","journal-title":"Brain"},{"issue":"1","key":"23_CR38","doi-asserted-by":"publisher","first-page":"133","DOI":"10.1007\/s00401-007-0257-y","volume":"115","author":"F Geser","year":"2008","unstructured":"Geser F, Winton MJ, Kwong LK et al. Pathological TDP-43 in parkinsonism-dementia complex and amyotrophic lateral sclerosis of Guam. Acta Neuropathol 2008; 115(1):133\u2013145.","journal-title":"Acta Neuropathol"},{"key":"23_CR39","doi-asserted-by":"publisher","first-page":"151","DOI":"10.1007\/s00401-008-0463-2","volume":"117","author":"H Fujishiro","year":"2009","unstructured":"Fujishiro H, Uchikado H, Arai T et al. Accumulation of phosphorylated TDP-43 in brains of patients with argyrophilic grain disease. Acta Neuropathol 2009; 117:151\u2013158.","journal-title":"Acta Neuropathol"},{"key":"23_CR40","doi-asserted-by":"publisher","first-page":"55","DOI":"10.1007\/s00401-010-0702-1","volume":"120","author":"O Yokota","year":"2010","unstructured":"Yokota O, Davidson Y, Bigio EH et al. Phosphorylated TDP-43 pathology and hippocampal sclerosis in progressive supranuclear palsy. Acta Neuropathol 2010; 120:55\u201366.","journal-title":"Acta Neuropathol"},{"issue":"8","key":"23_CR41","doi-asserted-by":"publisher","first-page":"1205","DOI":"10.1007\/s00415-009-5069-7","volume":"256","author":"F Geser","year":"2009","unstructured":"Geser F, Martinez-Lage M, Kwong LK et al. Amyotrophic lateral sclerosis, frontotemporal dementia and beyond: the TDP-43 diseases. J Neurol 2009; 256(8):1205\u20131214.","journal-title":"J Neurol"},{"issue":"4","key":"23_CR42","doi-asserted-by":"publisher","first-page":"211","DOI":"10.1038\/nrneurol.2010.18","volume":"6","author":"AS Chen-Plotkin","year":"2010","unstructured":"Chen-Plotkin AS, Lee VM, Trojanowski JQ. TAR DNA-binding protein 43 in neurodegenerative disease. Nat Rev Neurol 2010; 6(4):211\u2013220.","journal-title":"Nat Rev Neurol"},{"key":"23_CR43","doi-asserted-by":"publisher","first-page":"1850","DOI":"10.1212\/01.wnl.0000304041.09418.b1","volume":"70","author":"KA Josephs","year":"2008","unstructured":"Josephs KA, Whitwell JL, Knopman DS et al. Abnormal TDP-43 immunoreactivity in AD modifies clinicopathologic and radiologic phenotype. Neurology 2008; 70:1850\u20131857.","journal-title":"Neurology"},{"key":"23_CR44","doi-asserted-by":"publisher","first-page":"265","DOI":"10.1159\/000077151","volume":"17","author":"M Ikeda","year":"2004","unstructured":"Ikeda M, Ishikawa T, Tanabe H. Epidemiology of frontotemporal lobar degeneration. Dement Geriatr Cogn Disord 2004; 17:265\u2013268.","journal-title":"Dement Geriatr Cogn Disord"},{"key":"23_CR45","doi-asserted-by":"publisher","first-page":"782","DOI":"10.1111\/j.1468-1331.2005.01072.x","volume":"12","author":"O Yokota","year":"2005","unstructured":"Yokota O, Sasaki K, Fujisawa Y et al. Frequency of early and late-onset dementias in a Japanese memory disorders clinic. Eur J Neurol 2005; 12:782\u2013790.","journal-title":"Eur J Neurol"},{"key":"23_CR46","doi-asserted-by":"publisher","first-page":"399","DOI":"10.1002\/ana.20203","volume":"56","author":"JR Hodges","year":"2004","unstructured":"Hodges JR, Davies RR, Xuereb JH et al. Clinicopathological correlates in frontotemporal dementia. Ann Neurol 2004; 56:399\u2013406.","journal-title":"Ann Neurol"},{"key":"23_CR47","doi-asserted-by":"publisher","first-page":"379","DOI":"10.1007\/s00401-004-0900-9","volume":"108","author":"AM Lipton","year":"2004","unstructured":"Lipton AM, White CL 3rd, Bigio EH. Frontotemporal lobar degeneration with motor neuron disease-type inclusions predominates in 76 cases of frontotemporal degeneration. Acta Neuropathol 2004; 108:379\u2013385.","journal-title":"Acta Neuropathol"},{"key":"23_CR48","doi-asserted-by":"publisher","first-page":"1996","DOI":"10.1093\/brain\/awh598","volume":"128","author":"A Kertesz","year":"2005","unstructured":"Kertesz A, McMonagle P, Blair M et al. The evolution and pathology of frontotemporal dementia. Brain 2005; 128:1996\u20132005.","journal-title":"Brain"},{"key":"23_CR49","doi-asserted-by":"publisher","first-page":"501","DOI":"10.1007\/s00401-005-1079-4","volume":"110","author":"J Shi","year":"2005","unstructured":"Shi J, Shaw CL, Du Plessis D et al. Histopathological changes underlying frontotemporal lobar degeneration with clinicopathological correlation. Acta Neuropathol 2005; 110:501\u2013512.","journal-title":"Acta Neuropathol"},{"key":"23_CR50","doi-asserted-by":"publisher","first-page":"429","DOI":"10.1007\/s00401-009-0493-4","volume":"117","author":"O Yokota","year":"2009","unstructured":"Yokota O, Tsuchiya K, Arai T et al. Clinicopathological characterization of Pick\u2019s disease versus frontotemporal lobar degeneration with ubiquitin\/TDP-43-positive inclusions. Acta Neuropathol 2009; 117: 429\u2013444.","journal-title":"Acta Neuropathol"},{"key":"23_CR51","doi-asserted-by":"publisher","first-page":"3091","DOI":"10.1093\/brain\/awl267","volume":"129","author":"JS Snowden","year":"2006","unstructured":"Snowden JS, Pickering-Brown SM, Mackenzie IR et al. Progranulin gene mutations associated with frontotemporal dementia and progressive nonfluent aphasia. Brain 2006; 129:3091\u20133102.","journal-title":"Brain"},{"issue":"4","key":"23_CR52","doi-asserted-by":"publisher","first-page":"1481","DOI":"10.1016\/S0002-9440(10)64099-0","volume":"158","author":"ME King","year":"2001","unstructured":"King ME, Ghoshal N, Wall JS et al. Structural analysis of Pick\u2019s disease-derived and in vitro-assembled tau filaments. Am J Pathol 2001; 158(4):1481\u20131490.","journal-title":"Am J Pathol"},{"key":"23_CR53","doi-asserted-by":"publisher","first-page":"19","DOI":"10.1159\/000066674","volume":"15","author":"T Odawara","year":"2003","unstructured":"Odawara T, Iseki E, Kanai A et al. Clinicopathological study of two subtypes of Pick\u2019s disease in Japan. Dement Geriatr Cogn Disord 2003; 15:19\u201325.","journal-title":"Dement Geriatr Cogn Disord"},{"key":"23_CR54","doi-asserted-by":"publisher","first-page":"1984","DOI":"10.1093\/brain\/awh582","volume":"128","author":"RR Davies","year":"2005","unstructured":"Davies RR, Hodges JR, Kril JJ et al. The pathological basis of semantic dementia. Brain 2005; 128: 1984\u20131995.","journal-title":"Brain"},{"key":"23_CR55","doi-asserted-by":"publisher","first-page":"1097","DOI":"10.1001\/archneur.62.7.1097","volume":"62","author":"AK Godbolt","year":"2005","unstructured":"Godbolt AK, Josephs KA, Revesz T et al. Sporadic and familial dementia with ubiquitin-positive tau-negative inclusions: clinical features of one histopathological abnormality underlying frontotemporal lobar degeneration. Arch Neurol 2005; 62:1097\u20131101.","journal-title":"Arch Neurol"},{"key":"23_CR56","doi-asserted-by":"publisher","first-page":"674","DOI":"10.1002\/1531-8257(199907)14:4<674::AID-MDS1019>3.0.CO;2-X","volume":"14","author":"DA Grimes","year":"1999","unstructured":"Grimes DA, Bergeron CB, Lang AE. Motor neuron disease-inclusion dementia presenting as cortical-basal ganglionic degeneration. Mov Disord 1999; 14:674\u2013780.","journal-title":"Mov Disord"},{"key":"23_CR57","doi-asserted-by":"publisher","first-page":"2441","DOI":"10.1093\/brain\/awh265","volume":"127","author":"DC Paviour","year":"2004","unstructured":"Paviour DC, Lees AJ, Josephs KA et al. Frontotemporal lobar degeneration with ubiquitin-onlyimmunoreactive neuronal changes: broadening the clinical picture to include progressive supranuclear palsy. Brain 2004; 127:2441\u20132451.","journal-title":"Brain"},{"key":"23_CR58","doi-asserted-by":"publisher","first-page":"597","DOI":"10.1093\/brain\/awh348","volume":"128","author":"A Graham","year":"2005","unstructured":"Graham A, Davies R, Xuereb J et al. Pathologically proven frontotemporal dementia presenting with severe amnesia. Brain 2005; 128:597\u2013605.","journal-title":"Brain"},{"issue":"3","key":"23_CR59","doi-asserted-by":"publisher","first-page":"157","DOI":"10.1097\/WNN.0b013e3181864a09","volume":"21","author":"DO Claassen","year":"2008","unstructured":"Claassen DO, Parisi JE, Giannini C et al. Frontotemporal dementia mimicking dementia with Lewy bodies. Cogn Behav Neurol 2008; 21(3):157\u2013163.","journal-title":"Cogn Behav Neurol"},{"key":"23_CR60","doi-asserted-by":"publisher","first-page":"142","DOI":"10.1097\/nen.0b013e31803020cf","volume":"66","author":"KA Josephs","year":"2007","unstructured":"Josephs KA, Ahmed Z, Katsuse O et al. Neuropathologic features of frontotemporal lobar degeneration with ubiquitin-positive inclusions with progranulin gene (PGRN) mutations. J Neuropathol Exp Neurol 2007; 66:142\u2013151.","journal-title":"J Neuropathol Exp Neurol"},{"key":"23_CR61","doi-asserted-by":"publisher","first-page":"721","DOI":"10.1093\/brain\/awm331","volume":"131","author":"SM Pickering-Brown","year":"2008","unstructured":"Pickering-Brown SM, Rollinson S, Du Plessis D et al. Frequency and clinical characteristics of progranulin mutation carriers in the Manchester frontotemporal lobar degeneration cohort: comparison with patients with MAPT and no known mutations. Brain 2008; 131:721\u2013731.","journal-title":"Brain"},{"key":"23_CR62","doi-asserted-by":"publisher","first-page":"732","DOI":"10.1093\/brain\/awn012","volume":"131","author":"I Ber Le","year":"2008","unstructured":"Le Ber I, Camuzat A, Hannequin D et al. Phenotype variability in progranulin mutation carriers: a clinical, neuropsychological, imaging and genetic study. Brain 2008; 131:732\u2013746.","journal-title":"Brain"},{"key":"23_CR63","doi-asserted-by":"crossref","first-page":"467","DOI":"10.1212\/WNL.47.2.467","volume":"47","author":"T Fukui","year":"1996","unstructured":"Fukui T, Sugita K, Kawamura M et al. Primary progressive apraxia in Pick\u2019s disease: a clinicopathologic study. Neurology 1996; 47:467\u2013473.","journal-title":"Neurology"},{"key":"23_CR64","doi-asserted-by":"publisher","first-page":"249","DOI":"10.1046\/j.1440-1789.1999.00235.x","volume":"19","author":"M Kawamura","year":"1999","unstructured":"Kawamura M, Mochizuki S. Primary progressive apraxia. Neuropathology 1999; 19:249\u2013258.","journal-title":"Neuropathology"},{"key":"23_CR65","doi-asserted-by":"publisher","first-page":"416","DOI":"10.1007\/s004010050728","volume":"94","author":"K Tsuchiya","year":"1997","unstructured":"Tsuchiya K, Ikeda K, Uchihara T et al. Distribution of cerebral cortical lesions in corticobasal degeneration: a clinicopathological study of five autopsy cases in Japan. Acta Neuropathol 1997; 94:416\u2013424.","journal-title":"Acta Neuropathol"},{"key":"23_CR66","doi-asserted-by":"crossref","first-page":"1969","DOI":"10.1212\/WNL.53.9.1969","volume":"53","author":"DA Grimes","year":"1999","unstructured":"Grimes DA, Lang AE, Bergeron CB. Dementia as the most common presentation of cortical-basal ganglionic degeneration. Neurology 1999; 53:1969\u20131974.","journal-title":"Neurology"},{"key":"23_CR67","doi-asserted-by":"publisher","first-page":"41","DOI":"10.1212\/01.wnl.0000191307.69661.c3","volume":"66","author":"KA Joseph","year":"2006","unstructured":"Joseph KA, Petersen RC, Knopman DS et al. Clinicopathological analysis of frontotemporal and corticobasal degenerations and PSP. Neurology 2006; 66:41\u201348.","journal-title":"Neurology"},{"key":"23_CR68","doi-asserted-by":"publisher","first-page":"688","DOI":"10.1097\/WCO.0b013e3283168ddd","volume":"21","author":"KA Josephs","year":"2008","unstructured":"Josephs KA, Duffy JR. Apraxia of speech and nonfluent aphasia: a new clinical marker for corticobasal degeneration and progressive supranuclear palsy. Current Opinion in Neurology 2008; 21:688\u2013692.","journal-title":"Current Opinion in Neurology"},{"key":"23_CR69","doi-asserted-by":"publisher","first-page":"534","DOI":"10.1007\/s004010050558","volume":"92","author":"K Ikeda","year":"1996","unstructured":"Ikeda K, Akiyama H, Iritani S et al. Corticobasal degeneration with primary progressive aphasia and accentuated cortical lesion in superior temporal gyrus: case report and review. Acta Neuropathol 1996; 92:534\u2013539.","journal-title":"Acta Neuropathol"},{"key":"23_CR70","doi-asserted-by":"publisher","first-page":"353","DOI":"10.1007\/s00401-004-0966-4","volume":"109","author":"K Tsuchiya","year":"2005","unstructured":"Tsuchiya K, Murayama S, Mitani K et al. Constant and severe involvement of Betz cells in corticobasal degeneration is not consistent with pyramidal signs: a clinicopathological study of ten autopsy cases. Acta Neuropathol 2005; 109:353\u2013366.","journal-title":"Acta Neuropathol"},{"key":"23_CR71","doi-asserted-by":"crossref","first-page":"795","DOI":"10.1212\/WNL.53.4.795","volume":"53","author":"BF Boeve","year":"1999","unstructured":"Boeve BF, Maraganore DM, Parisi JE et al. Pathologic heterogeneity in clinically diagnosed corticobasal degeneration. Neurology 1999; 53:795\u2013800.","journal-title":"Neurology"},{"key":"23_CR72","doi-asserted-by":"publisher","first-page":"561","DOI":"10.1007\/s00401-007-0329-z","volume":"115","author":"O Yokota","year":"2008","unstructured":"Yokota O, Tsuchiya K, Terada S et al. Basophilic inclusion body disease and neuronal intermediate filament inclusion disease: a comparative clinicopathological study. Acta Neuropathol 2008; 115:561\u2013575.","journal-title":"Acta Neuropathol"},{"key":"23_CR73","doi-asserted-by":"publisher","first-page":"270","DOI":"10.1016\/S1474-4422(09)70042-0","volume":"8","author":"DR Williams","year":"2009","unstructured":"Williams DR, Lees AJ. Progressive supranuclear palsy: clinicopathological concepts and diagnostic challenges. Lancet Neurol 2009; 8:270\u2013279.","journal-title":"Lancet Neurol"},{"key":"23_CR74","doi-asserted-by":"publisher","first-page":"660","DOI":"10.1007\/BF00307636","volume":"80","author":"H Kusaka","year":"1990","unstructured":"Kusaka H, Matsumoto S, Imai T. An adult-onset case of sporadic motor neuron disease with basophilic inclusions. Acta Neuropathol 1990; 80:660\u2013665.","journal-title":"Acta Neuropathol"},{"key":"23_CR75","first-page":"215","volume":"12","author":"H Kusaka","year":"1993","unstructured":"Kusaka H, Matsumoto S, Imai T. Adult-onset motor neuron disease with basophilic intraneuronal inclusion bodies. Clin Neuropathol 1993; 12:215\u2013218.","journal-title":"Clin Neuropathol"},{"key":"23_CR76","doi-asserted-by":"publisher","first-page":"447","DOI":"10.1111\/j.1440-1789.2006.00717.x","volume":"26","author":"K Ishihara","year":"2006","unstructured":"Ishihara K, Araki S, Ihori N et al. An autopsy case of frontotemporal dementia with severe dysarthria and motor neuron disease showing numerous basophilic inclusions. Neuropathology 2006; 26: 447\u2013454.","journal-title":"Neuropathology"},{"issue":"6","key":"23_CR77","doi-asserted-by":"crossref","first-page":"547","DOI":"10.1093\/jnen\/61.6.547","volume":"61","author":"T Togo","year":"2002","unstructured":"Togo T, Sahara N, Yen SH et al. Argyrophilic grain disease is a sporadic 4-repeat tauopathy. J Neuropathol Exp Neurol 2002; 61(6):547\u2013556.","journal-title":"J Neuropathol Exp Neurol"},{"key":"23_CR78","doi-asserted-by":"publisher","first-page":"45","DOI":"10.1111\/j.1750-3639.2002.tb00421.x","volume":"12","author":"T Togo","year":"2002","unstructured":"Togo T, Cookson N, Dickson DW. Argyrophilic grain disease: neuropathology, frequency in a dementia brain bank and lack of relationship with apolipoprotein E. Brain Pathol 2002; 12:45\u201352.","journal-title":"Brain Pathol"},{"key":"23_CR79","doi-asserted-by":"crossref","first-page":"911","DOI":"10.1093\/jnen\/63.9.911","volume":"63","author":"Y Saito","year":"2004","unstructured":"Saito Y, Ruberu NN, Sawabe M et al. Staging of argyrophilic grains: an age-associated tauopathy. J Neuropathol Exp Neurol 2004; 63:911\u2013918.","journal-title":"J Neuropathol Exp Neurol"},{"key":"23_CR80","doi-asserted-by":"crossref","first-page":"195","DOI":"10.1007\/s004010100406","volume":"102","author":"K Tsuchiya","year":"2001","unstructured":"Tsuchiya K, Mitani K, Arai T et al. Argyrophilic grain disease mimicking temporal Pick\u2019s disease: a clinical, radiological and pathological study of an autopsy case with a clinical course of 15 years. Acta Neuropathol 2001; 102:195\u2013199.","journal-title":"Acta Neuropathol"},{"key":"23_CR81","doi-asserted-by":"publisher","first-page":"165","DOI":"10.1111\/j.1440-1789.2005.00598.x","volume":"25","author":"K Ishihara","year":"2005","unstructured":"Ishihara K, Araki S, Ihori N et al. Argyrophilic grain disease presenting with frontotemporal dementia: a neuropsychological and pathological study of an autopsied case with presenile onset. Neuropathology 2005; 25:165\u2013170.","journal-title":"Neuropathology"},{"key":"23_CR82","first-page":"278","volume":"19","author":"K Ikeda","year":"2000","unstructured":"Ikeda K, Akiyama H, Arai T et al. Clinical aspects of argyrophilic grain disease. Clin Neuropathol 2000; 19:278\u2013284.","journal-title":"Clin Neuropathol"},{"key":"23_CR83","doi-asserted-by":"crossref","first-page":"1083","DOI":"10.1097\/00019442-200512000-00008","volume":"13","author":"T Togo","year":"2005","unstructured":"Togo T, Isojima D, Akatsu H et al. Clinical features of argyrophilic grain disease: a retrospective survey of cases with neuropsychiatric symptoms. Am J Geriatr Psychiatry 2005; 13:1083\u20131091.","journal-title":"Am J Geriatr Psychiatry"},{"key":"23_CR84","first-page":"785","volume":"56","author":"H Uchikado","year":"2004","unstructured":"Uchikado H, Tsuchiya K, Tominaga I et al. Argyrophilic grain disease clinically mimicking Parkinson\u2019s disease with dementia: report of an autopsy case. Brain and Nerve 2004; 56:785\u2013788 (in Japanese with English abstract).","journal-title":"Brain and Nerve"}],"container-title":["Advances in Experimental Medicine and Biology","Neurodegenerative Diseases"],"original-title":[],"link":[{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1007\/978-1-4614-0653-2_23.pdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2021,5,1]],"date-time":"2021-05-01T04:41:30Z","timestamp":1619844090000},"score":1,"resource":{"primary":{"URL":"http:\/\/link.springer.com\/10.1007\/978-1-4614-0653-2_23"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2012]]},"ISBN":["9781461406525","9781461406532"],"references-count":84,"URL":"https:\/\/doi.org\/10.1007\/978-1-4614-0653-2_23","relation":{},"ISSN":["0065-2598"],"issn-type":[{"value":"0065-2598","type":"print"}],"subject":[],"published":{"date-parts":[[2012]]}}}