{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2024,9,7]],"date-time":"2024-09-07T13:00:37Z","timestamp":1725714037944},"publisher-location":"Berlin, Heidelberg","reference-count":59,"publisher":"Springer Berlin Heidelberg","isbn-type":[{"type":"print","value":"9783642057564"},{"type":"electronic","value":"9783662084410"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2004]]},"DOI":"10.1007\/978-3-662-08441-0_7","type":"book-chapter","created":{"date-parts":[[2013,1,23]],"date-time":"2013-01-23T12:39:48Z","timestamp":1358944788000},"page":"161-191","source":"Crossref","is-referenced-by-count":1,"title":["The Epidemiology of Variant Creutzfeldt-Jakob Disease"],"prefix":"10.1007","author":[{"given":"P. G.","family":"Smith","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"S. N.","family":"Cousens","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"J. N. Huillard","family":"d\u2019Aignaux","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"H. J. T.","family":"Ward","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"R. G.","family":"Will","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"297","reference":[{"key":"7_CR1","doi-asserted-by":"publisher","first-page":"437","DOI":"10.1038\/38876","volume":"389","author":"J Almond","year":"1997","unstructured":"Almond J, Pattison J. Human BSE. Nature 1997; 389: 437\u2013438","journal-title":"Nature"},{"key":"7_CR2","doi-asserted-by":"publisher","first-page":"33","DOI":"10.1016\/S1631-0691(02)01410-5","volume":"325","author":"A Alperovitch","year":"2002","unstructured":"Alperovitch A, Will RG. Predicting the size of the vCJD epidemic in France. C.R.Acad. Sci III Biologies 2002; 325: 33\u201336","journal-title":"Sci III Biologies"},{"key":"7_CR3","doi-asserted-by":"publisher","first-page":"1673","DOI":"10.1016\/S0140-6736(99)01342-2","volume":"353","author":"A Alperovitch","year":"1999","unstructured":"Alperovitch A, Zerr I, Pocchiari M, Mitrova E, de Pedro Cuesta J, Hegyi I et al. Codon 129 prion protein genotype and sporadic Creutzfeldt-Jakob disease. Lancet 1999; 353: 1673\u20131674","journal-title":"Lancet"},{"key":"7_CR4","doi-asserted-by":"publisher","first-page":"779","DOI":"10.1038\/382779a0","volume":"382","author":"RM Anderson","year":"1996","unstructured":"Anderson RM, Donnelly CA, Ferguson NM, Woolhouse MEJ, Watt CI, Udy HJ et al. Transmission dynamics and epidemiology of BSE in British cattle. Nature 1996; 382: 779\u2013788","journal-title":"Nature"},{"key":"7_CR5","doi-asserted-by":"publisher","first-page":"481","DOI":"10.1016\/S0140-6736(00)02559-9","volume":"356","author":"NJ Andrews","year":"2000","unstructured":"Andrews NJ, Farrington CP, Cousens SN, Smith PG, Ward HJT, Knight RS et al. Inci- dence of variant Creutzfeldt-Jakob disease in the UK. Lancet 2000; 356: 481\u2013482","journal-title":"Lancet"},{"issue":"75","key":"7_CR6","first-page":"2003","volume":"361","author":"NJ Andrews","year":"1752","unstructured":"Andrews NJ, Farrington CP, Ward HIT, Cousens SN, Smith PG, Molesworth AM et al. Deaths from variant Creutzfeldt-Jakob disease in the UK. Lancet 2003; 361: 75 1752","journal-title":"Lancet"},{"key":"7_CR7","doi-asserted-by":"publisher","first-page":"6358","DOI":"10.1093\/emboj\/cdf653","volume":"21","author":"EA Asante","year":"2002","unstructured":"Asante EA, Linehan JM, Desbruslais M, Joiner S, Gowland I, Wood AL et al. BSE prions propagate as either variant CJD-like or sporadic CJD-like prion strains in transgenic mice expressing human prion protein. EMBO J 2002; 21: 6358\u20136366","journal-title":"EMBO J"},{"key":"7_CR8","doi-asserted-by":"publisher","first-page":"1155","DOI":"10.1016\/S0140-6736(95)91828-0","volume":"346","author":"D Bateman","year":"1995","unstructured":"Bateman D, Hilton D, Love S, Zeidler M, Beck J, Collinge J. Sporadic CreutzfeldtJakob disease in a 18-year-old in the UK. Lancet 1995; 346: 1155\u20131156","journal-title":"Lancet"},{"key":"7_CR9","doi-asserted-by":"publisher","first-page":"1155","DOI":"10.1016\/S0140-6736(95)91827-2","volume":"346","author":"TC Britton","year":"1995","unstructured":"Britton TC, al-Sarraj S, Shaw C, Campbell T, Collinge J. Sporadic Creutzfeldt-Jakob disease in a 16-year-old in the UK. Lancet 1995; 346: 1155","journal-title":"Lancet"},{"key":"7_CR10","doi-asserted-by":"publisher","first-page":"1075","DOI":"10.1212\/WNL.55.8.1075","volume":"55","author":"P Brown","year":"2000","unstructured":"Brown P, Preece M, Brandel JP, Sato T, McShane L, Zerr I et al. Iatrogenic Creutzfeldt-Jakob disease at the millennium. Neurology 2000; 55: 1075\u20131081","journal-title":"Neurology"},{"key":"7_CR11","doi-asserted-by":"publisher","first-page":"498","DOI":"10.1038\/39057","volume":"389","author":"ME Bruce","year":"1997","unstructured":"Bruce ME, Will RG, Ironside JW, McConnell I, Drummond D, Suttie A et al. Transmissions to mice indicate that `new variant\u2019 CJD is caused by the BSE agent. Nature 1997; 389: 498\u2013501","journal-title":"Nature"},{"key":"7_CR12","volume-title":"doc","author":"G Bryant","year":"2001","unstructured":"Bryant G, Monk PN. Final report of the investigation into the North Leicestershire cluster of variant Creutzfeldt-Jakob., http:\/\/www.leics-ha.org.uk\/Publics\/vcjd_rep. doc, 2001"},{"key":"7_CR13","doi-asserted-by":"publisher","first-page":"59","DOI":"10.1080\/147666502321082728","volume":"7","author":"JD Cooper","year":"2002","unstructured":"Cooper JD, Bird SM. UK dietary exposure to BSE in beef mechanically recovered meat: by birth cohort and gender. J Cancer Epidemiol Prevent 2002; 7: 59\u201370","journal-title":"J Cancer Epidemiol Prevent"},{"key":"7_CR14","doi-asserted-by":"publisher","first-page":"1002","DOI":"10.1016\/S0140-6736(00)04236-7","volume":"357","author":"S Cousens","year":"2001","unstructured":"Cousens S, Smith PG, Ward H, Everington D, Knight RSG, Zeidler M et al. Geographical distribution of variant Creutzfeldt-Jakob disease in Great Britain, 1994\u20132000. Lancet 2001; 357: 1002\u20131007","journal-title":"Lancet"},{"key":"7_CR15","doi-asserted-by":"publisher","first-page":"18","DOI":"10.1016\/S0140-6736(98)08062-3","volume":"353","author":"SN Cousens","year":"1999","unstructured":"Cousens SN, Linsell L, Smith PG, Chandrakumar M, Wilesmith JW, Knight RSG et al. Geographical distribution of variant CJD in the UK (excluding Northern Ireland). Lancet 1999; 353: 18\u201321","journal-title":"Lancet"},{"key":"7_CR16","doi-asserted-by":"publisher","first-page":"197","DOI":"10.1038\/385197a0","volume":"385","author":"SN Cousens","year":"1997","unstructured":"Cousens SN, Vynnycky E, Zeidler M, Will RG, Smith PG. Predicting the CJD epidemic. Nature 1997a; 385: 197\u2013198","journal-title":"Nature"},{"key":"7_CR17","doi-asserted-by":"publisher","first-page":"389","DOI":"10.1136\/bmj.315.7105.389","volume":"315","author":"SN Cousens","year":"1997","unstructured":"Cousens SN, Zeidler M, Esmonde TF, DeSilva R, Wilesmith JW, Smith PG et al. Sporadic Creutzfeldt-Jakob disease in the United Kingdom: analysis of epidemiological surveillance data for 1970\u201396. Br Med J 1997b; 315: 389\u2013395","journal-title":"Br Med J"},{"key":"7_CR18","doi-asserted-by":"publisher","first-page":"1197","DOI":"10.1212\/WNL.53.6.1197","volume":"53","author":"JH d\u2019Aignaux","year":"1999","unstructured":"d\u2019Aignaux JH, Costagliola D, Maccario J, de Villemeur TB, Brandel JP, Deslys JP et al. Incubation period of Creutzfeldt-Jakob disease in human growth hormone recipients in France. American Academy of Neurology 1999; 53: 1197\u20131201","journal-title":"American Academy of Neurology"},{"key":"7_CR19","doi-asserted-by":"publisher","first-page":"86","DOI":"10.1108\/00070709910261891","volume":"101","author":"NM Ferguson","year":"1999","unstructured":"Ferguson NM, Donnelly CA, Ghani AC, Anderson RM. Predicting the size of the epidemic of new variant Creutzfeldt-Jakob disease. Br Food J 1999; 101: 86\u201398.","journal-title":"Br Food J"},{"key":"7_CR20","first-page":"1","volume":"709","author":"NM Ferguson","year":"2002","unstructured":"Ferguson NM, Ghani AC, Donnelly AC, Hagenaars TJ, Anderson RM. Estimating the human health risk from possible BSE infection of the British sheep flock. Nature 2002; 709: 1\u20135","journal-title":"Nature"},{"key":"7_CR21","doi-asserted-by":"publisher","first-page":"900","DOI":"10.1093\/jnci\/80.12.900","volume":"80","author":"MH Gail","year":"1988","unstructured":"Gail MH, Brookmeyer R. Methods for projecting course of acquired immunodeficiency syndrome epidemic. J Natl Cancer Inst 1988; 80: 900\u2013911","journal-title":"J Natl Cancer Inst"},{"key":"7_CR22","doi-asserted-by":"publisher","first-page":"1353","DOI":"10.1016\/S0140-6736(05)60744-1","volume":"352","author":"AC Ghani","year":"1998","unstructured":"Ghani AC, Ferguson NM, Donnelly CA, Hagenaars TJ, Anderson RM. Estimation of the number of people incubating variant CJD. Lancet 1998; 352: 1353\u20131354","journal-title":"Lancet"},{"key":"7_CR23","doi-asserted-by":"publisher","first-page":"4","DOI":"10.1186\/1471-2334-3-4","volume":"3","author":"AC Ghani","year":"2003","unstructured":"Ghani AC, Donnelly CA, Ferguson NM, Anderson RM. Updated projections of future vCJD deaths in the UK. BMC Infect Dis. 2003 3: 4","journal-title":"BMC Infect Dis"},{"key":"7_CR24","unstructured":"Glatzel M, Rogivue C, Ghani A, Streffer JR, Amsler L, Aguzzi A. Sharply increased"},{"key":"7_CR25","doi-asserted-by":"crossref","first-page":"139","DOI":"10.1016\/S0140-6736(02)09384-4","volume":"360","author":"Creutzfeldt-Jakob disease mortality in Switzerland","year":"2002","unstructured":"Creutzfeldt-Jakob disease mortality in Switzerland. Lancet 2002; 360:139\u2013141 Gore SM. Commentary: Age related exposure of patients to the agent of BSE should not be downplayed. Br Med 1 1997; 315: 395\u2013396","journal-title":"Lancet"},{"key":"7_CR26","doi-asserted-by":"publisher","first-page":"1416","DOI":"10.1136\/bmj.311.7017.1416a","volume":"311","author":"SM Gore","year":"1995","unstructured":"Gore SM. More than happenstance: Creutzfeldt-Jakob disease in farmers and young adults. Br Med J 1995; 311: 1416\u20131418","journal-title":"Br Med J"},{"key":"7_CR27","doi-asserted-by":"publisher","first-page":"1113","DOI":"10.1136\/jnnp.51.9.1113","volume":"51","author":"R Harris-Jones","year":"1988","unstructured":"Harris-Jones R, Knight R, Will RG, Cousens S, Smith PG, Matthews WB. CreutzfeldtJakob disease in England and Wales 1980\u201384: a case-control study of potential risk factors. J Neurol, Neurosurg Psychiatr 1988; 51: 1113\u20131119","journal-title":"Neurosurg Psychiatr"},{"key":"7_CR28","doi-asserted-by":"publisher","first-page":"183","DOI":"10.1016\/S0140-6736(98)12075-5","volume":"353","author":"AF Hill","year":"1999","unstructured":"Hill AF, Butterworth RI, Joiner S, Jackson G, Rossor MN, Thomas DK et al. Investigation of variant Creutzfeldt-Jakob disease and other human prion diseases with tonsil biopsy samples. Lancet 1999; 353: 183\u2013189","journal-title":"Lancet"},{"key":"7_CR29","doi-asserted-by":"publisher","first-page":"448","DOI":"10.1038\/38925","volume":"389","author":"AF Hill","year":"1997","unstructured":"Hill AF, Desbruslais M, Joiner S, Sidle KCL, Gowland I, Collinge J. The same prion strain causes vCJD and BSE. Nature 1997; 389: 448\u2013450","journal-title":"Nature"},{"key":"7_CR30","doi-asserted-by":"publisher","first-page":"703","DOI":"10.1016\/S0140-6736(98)24035-9","volume":"352","author":"DA Hilton","year":"1998","unstructured":"Hilton DA, Fathers E, Edwards P, Ironside JW, Zajicek J. Prion immunoreactivity in appendix before clinical onset of variant Creutzfeldt-Jakob disease. Lancet 1998; 352: 703\u2013704","journal-title":"Lancet"},{"key":"7_CR31","doi-asserted-by":"publisher","first-page":"633","DOI":"10.1136\/bmj.325.7365.633","volume":"325","author":"DA Hilton","year":"2002","unstructured":"Hilton DA, Ghani AC, Conyers L, Edwards P, McCardle L, Penney M et al. Accumulation of prion protein in tonsil and appendix: review of tissue samples. Br Med J 2002; 325: 633\u2013634","journal-title":"Br Med J"},{"key":"7_CR32","unstructured":"Horn G, Bobrow M, Bruce M, Goedert M, McLean A, Webster J. Review of the Origin of BSE: Report to UK Government. 2001 www.defra.gov.uk\/animalh\/bse\/bseorigin. pdf"},{"key":"7_CR33","doi-asserted-by":"publisher","first-page":"999","DOI":"10.1016\/S0140-6736(00)02719-7","volume":"356","author":"F Houston","year":"2000","unstructured":"Houston F, Foster JD, Chong A, Hunter N, Bostock CJ. Transmission of BSE by blood transfusion in sheep. Lancet 2000; 356: 999\u20131000","journal-title":"Lancet"},{"key":"7_CR34","doi-asserted-by":"publisher","first-page":"1197","DOI":"10.1212\/WNL.53.6.1197","volume":"53","author":"J Huillard d\u2019Aignaux","year":"1999","unstructured":"Huillard d\u2019Aignaux J, Costagliola D, Maccario J, Billette de Villemeur T, Brandel JP, Deslys JP et al. Incubation period of Creutzfeldt-Jakob disease in human growth hormone recipients in France. Neurology 1999; 53: 1197\u20131201","journal-title":"Neurology"},{"key":"7_CR35","doi-asserted-by":"publisher","first-page":"402","DOI":"10.1097\/00001648-200207000-00007","volume":"13","author":"JN Huillard d\u2019Aignaux","year":"2002","unstructured":"Huillard d\u2019Aignaux JN, Cousens SN, Maccario J, Costagliola D, Alpers MP, Smith PG et al. The incubation period of kuru. Epidemiology 2002; 13: 402\u2013408","journal-title":"Epidemiology"},{"key":"7_CR36","unstructured":"Huillard d\u2019Aignaux JN, Cousens SN, Smith PG. Predictability of the UK variant"},{"key":"7_CR37","doi-asserted-by":"crossref","unstructured":"Creutzfeldt-Jakob disease epidemic. Science 2001; 294: 1729\u20131731","DOI":"10.1126\/science.1064748"},{"key":"7_CR38","doi-asserted-by":"crossref","first-page":"2897","DOI":"10.1099\/0022-1317-83-11-2897","volume":"83","author":"N Hunter","year":"2002","unstructured":"Hunter N, Foster JD, Chong A, McCutcheon S, Parnham DW, Eaton S et al. Transmission of prion diseases by blood transfusion. J Gen Virol 2002; 83: 2897\u20132905","journal-title":"J Gen Virol"},{"key":"7_CR39","doi-asserted-by":"publisher","first-page":"269","DOI":"10.1038\/35104694","volume":"414","author":"GS Jackson","year":"2001","unstructured":"Jackson GS, Beck JA, Navarrete C, Brown J, Sutton PM, Contreras M et al. HLA-DQ7 antigen and resistance to variant CJD. Nature 2001; 414: 269\u2013270","journal-title":"Nature"},{"key":"7_CR40","doi-asserted-by":"publisher","first-page":"332","DOI":"10.1126\/science.1067475","volume":"295","author":"RR Kao","year":"2002","unstructured":"Kao RR, Gravenor MB, Baylis M, Bostock CJ, Chihota CM, Evans JC et al. The potential size and duration of an epidemic of bovine spongiform encephalopathy in British sheep. Science 2002; 295: 332\u2013335","journal-title":"Science"},{"key":"7_CR41","doi-asserted-by":"publisher","first-page":"531","DOI":"10.1016\/S0140-6736(03)12480-4","volume":"361","author":"JL Laplanche","year":"2003","unstructured":"Laplanche JL, Lepage V, Peoc\u2019h K, Delasnerie-Laupretre N, Charron D. HLA in French patients with variant Creutzfeldt-Jakob disease. Lancet 2003; 361: 531\u2013532","journal-title":"Lancet"},{"key":"7_CR42","doi-asserted-by":"publisher","first-page":"192","DOI":"10.1086\/317935","volume":"183","author":"HS Lee","year":"2001","unstructured":"Lee HS, Brown P, Cervenakova L, Garruto RM, Alpers MP, Gajdusek DC et al. Increased susceptibility to Kuru of carriers of the PRNP 129 methionine\/methionine genotype. J Infect Dis 2001; 183: 192\u2013196","journal-title":"J Infect Dis"},{"key":"7_CR43","doi-asserted-by":"publisher","first-page":"555","DOI":"10.1111\/j.1750-3639.1997.tb01073.x","volume":"7","author":"PP Liberski","year":"1997","unstructured":"Liberski PP, Gajdusek DC. Kuru: forty years later, a historical note. Brain Pathol 1997; 7: 555\u2013560","journal-title":"Brain Pathol"},{"key":"7_CR44","doi-asserted-by":"publisher","first-page":"6279","DOI":"10.1073\/pnas.101130398","volume":"98","author":"SE Lloyd","year":"2001","unstructured":"Lloyd SE, Onwuazor ON, Beck JA, Mallinson G, Farrall M, Targonski P et al. Identification of multiple quantitative trait loci linked to prion disease incubation period in mice. Proc Natl Acad Sci USA 2001; 98: 6279\u20136283","journal-title":"Proc Natl Acad Sci USA"},{"key":"7_CR45","doi-asserted-by":"publisher","first-page":"1011","DOI":"10.1136\/bmj.320.7240.1011","volume":"320","author":"J Lowe","year":"2000","unstructured":"Lowe J. Evidence of a CJD epidemic may still be missed. Br Med J 2000; 320: 1011","journal-title":"Br Med J"},{"key":"7_CR46","doi-asserted-by":"publisher","first-page":"1043","DOI":"10.1098\/rstb.2000.0641","volume":"355","author":"AR Mclean","year":"2000","unstructured":"McLean AR, Bostock CJ. Scrapie infections initiated at varying doses: an analysis of 117 titration experiments. Philos Trans R Soc Lond B Biol Sci 2000; 355: 1043\u20131050","journal-title":"Philos Trans R Soc Lond B Biol Sci"},{"key":"7_CR47","doi-asserted-by":"crossref","unstructured":"Minor PD, Will RG, Salisbury D. Vaccines and variant CJD. Vaccine 2000; 19:409\u2013410 National CJD Surveillance Unit. Creutzfeldt-Jakob disease surveillance in the UK, http:\/\/www.cjd.ed.ac.uk\/rep2001.html 2002","DOI":"10.1016\/S0264-410X(00)00136-5"},{"key":"7_CR48","volume-title":"Scrapie disease in sheep: historical, clinical, epidemiological and practical aspects of the natural disease","author":"HB Parry","year":"1983","unstructured":"Parry HB. Scrapie disease in sheep: historical, clinical, epidemiological and practical aspects of the natural disease. London, Academic Press, 1983"},{"key":"7_CR49","doi-asserted-by":"publisher","first-page":"487","DOI":"10.1016\/S0140-6736(03)12455-5","volume":"361","author":"MB Pepys","year":"2003","unstructured":"Pepys MB, Bybee A, Booth DR, Bishop MT, Will RG, Little A-M et al. MHC typing in variant Creutzfeldt-Jakob disease. Lancet 2003; 361: 487\u2013489","journal-title":"Lancet"},{"key":"7_CR50","doi-asserted-by":"publisher","first-page":"1","DOI":"10.1002\/ana.410120102","volume":"12","author":"SB Prusiner","year":"1982","unstructured":"Prusiner SB, Gajdusek DC, Alpers MP. Kuru with Incubation Periods Exceeding Two Decades. Am Neurolog 1982; 12: 1\u20139","journal-title":"Am Neurolog"},{"key":"7_CR51","first-page":"310","volume":"51","author":"PE Sartwell","year":"1950","unstructured":"Sartwell PE. The distribution of incubation periods of infectious disease. Am J Hyg 1950; 51: 310\u2013318","journal-title":"Am J Hyg"},{"key":"7_CR52","doi-asserted-by":"publisher","first-page":"1726","DOI":"10.1126\/science.1066838","volume":"294","author":"A-J Valleron","year":"2001","unstructured":"Valleron A-J, Boelle P-Y, Will R, Cesbron J-Y. Estimation of epidemic size and incubation time based on age characteristics of vCJD in the United Kingdom. Science 2001; 294: 1726\u20131728","journal-title":"Science"},{"key":"7_CR53","doi-asserted-by":"publisher","first-page":"1081","DOI":"10.1016\/S0140-6736(97)09468-3","volume":"351","author":"CM Duijn","year":"1998","unstructured":"van Duijn CM, Delasnerie-Laupetre N, Masullo C, Zerr I, de Silva R, Wientjens DPWM et al. Case-control study of risk factors of Creutzfeldt-Jakob disease in Europe during 1993\u201395. Lancet 1998; 351: 1081\u20131085","journal-title":"Lancet"},{"key":"7_CR54","doi-asserted-by":"publisher","first-page":"1224","DOI":"10.1016\/S0140-6736(00)02785-9","volume":"356","author":"CM Verity","year":"2000","unstructured":"Verity CM, Nicoll A, Will RG, Devereux G, Stellitano L. Variant Creutzfeldt-Jakob dis- ease in UK children: a national surveillance study. Lancet 2000; 356: 1224\u20131227","journal-title":"Lancet"},{"key":"7_CR55","doi-asserted-by":"publisher","first-page":"1287","DOI":"10.1212\/WNL.46.5.1287","volume":"46","author":"DPWM Wientjens","year":"1996","unstructured":"Wientjens DPWM, Davanipour Z, Hofman A, Kondo K, Matthews WB, Will RG et al. Risk factors for Creutzfeldt-Jakob disease: a reanalysis of case-control studies. Neurology 1996; 46: 1287\u20131291","journal-title":"Neurology"},{"key":"7_CR56","doi-asserted-by":"publisher","first-page":"90","DOI":"10.1136\/vr.130.5.90","volume":"130","author":"JW Wilesmith","year":"1992","unstructured":"Wilesmith JW, Ryan JBM, Hueston WD, Hoinville LJ. Bovine spongiform encephalopathy: epidemiological features 1985\u20131990. Veterinary Record 1992; 130: 90\u201394","journal-title":"Veterinary Record"},{"key":"7_CR57","doi-asserted-by":"publisher","first-page":"921","DOI":"10.1016\/S0140-6736(96)91412-9","volume":"347","author":"RG Will","year":"1996","unstructured":"Will RG, Ironside JW, Zeidler M, Cousens SN, Estibeiro K, Alperovitch A et al. A new variant of Creutzfeldt-Jakob disease in the UK. Lancet 1996; 347: 921\u2013925","journal-title":"Lancet"},{"key":"7_CR58","doi-asserted-by":"publisher","first-page":"749","DOI":"10.1136\/jnnp.49.7.749","volume":"49","author":"RG Will","year":"1986","unstructured":"Will RG, Matthews WB, Smith PG, Hudson C. A retrospective study of CreutzfeldtJakob Disease in England and Wales 1970\u20131979 II: epidemiology. J Neurol, Neurosurg Psychiatr 1986; 49: 749\u2013755","journal-title":"Neurosurg Psychiatr"},{"key":"7_CR59","unstructured":"Working Party on Bovine Spongiform Encephalopathy. Report of the Working Party on Bovine Spongiform Encephalopathy (Southwood Report). London, UK, Dept of Health and Ministry of Agriculture, Food and Fisheries, 1989"}],"container-title":["Current Topics in Microbiology and Immunology","Mad Cow Disease and Related Spongiform Encephalopathies"],"original-title":[],"link":[{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1007\/978-3-662-08441-0_7","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2019,5,10]],"date-time":"2019-05-10T17:11:07Z","timestamp":1557508267000},"score":1,"resource":{"primary":{"URL":"http:\/\/link.springer.com\/10.1007\/978-3-662-08441-0_7"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2004]]},"ISBN":["9783642057564","9783662084410"],"references-count":59,"URL":"https:\/\/doi.org\/10.1007\/978-3-662-08441-0_7","relation":{},"ISSN":["0070-217X"],"issn-type":[{"type":"print","value":"0070-217X"}],"subject":[],"published":{"date-parts":[[2004]]}}}