{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,27]],"date-time":"2026-09-27T01:36:15Z","timestamp":1790472975044,"version":"4.1.0"},"reference-count":7,"publisher":"Wiley","issue":"2","license":[{"start":{"date-parts":[[1993,3,1]],"date-time":"1993-03-01T00:00:00Z","timestamp":730944000000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["J of Inher Metab Disea"],"published-print":{"date-parts":[[1993,3]]},"DOI":"10.1007\/bf00710269","type":"journal-article","created":{"date-parts":[[2004,12,1]],"date-time":"2004-12-01T12:15:16Z","timestamp":1101903316000},"page":"296-298","source":"Crossref","is-referenced-by-count":10,"title":["Molecular basis of lysosomal accumulation of subunit c of mitochondrial ATP synthase in neuronal ceroid\u2010lipofuscinosis"],"prefix":"10.1002","volume":"16","author":[{"given":"J.","family":"Ezaki","sequence":"first","affiliation":[{"name":"Department of Biochemistry Juntendo University School of Medicine  Hongo 2\u20101\u20101, Bunkyo\u2010ku Tokyo 113 Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"L. S.","family":"Wolfe","sequence":"additional","affiliation":[{"name":"Montreal Neurological Institute and Hospital McGill University  3801 University Street Montreal Quebec H3A\u20102B4 Canada"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"E.","family":"Kominami","sequence":"additional","affiliation":[{"name":"Department of Biochemistry Juntendo University School of Medicine  Hongo 2\u20101\u20101, Bunkyo\u2010ku Tokyo 113 Japan"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"311","published-online":{"date-parts":[[1993,3]]},"reference":[{"key":"e_1_2_1_2_1","doi-asserted-by":"publisher","DOI":"10.1042\/bj2680751"},{"key":"e_1_2_1_3_1","doi-asserted-by":"publisher","DOI":"10.1042\/bj2750269"},{"key":"e_1_2_1_4_1","doi-asserted-by":"publisher","DOI":"10.1016\/0888-7543(91)90235-7"},{"key":"e_1_2_1_5_1","doi-asserted-by":"publisher","DOI":"10.1016\/S0021-9258(18)32377-9"},{"key":"e_1_2_1_6_1","doi-asserted-by":"publisher","DOI":"10.1093\/oxfordjournals.jbchem.a123749"},{"key":"e_1_2_1_7_1","doi-asserted-by":"publisher","DOI":"10.1016\/S0021-9258(18)83610-9"},{"key":"e_1_2_1_8_1","doi-asserted-by":"publisher","DOI":"10.1007\/978-1-4899-5339-1_15"}],"container-title":["Journal of Inherited Metabolic Disease"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1007\/BF00710269","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,9,15]],"date-time":"2023-09-15T16:29:14Z","timestamp":1694795354000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1007\/BF00710269"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[1993,3]]},"references-count":7,"journal-issue":{"issue":"2","published-print":{"date-parts":[[1993,3]]}},"alternative-id":["10.1007\/BF00710269"],"URL":"https:\/\/doi.org\/10.1007\/bf00710269","archive":["Portico"],"relation":{},"ISSN":["0141-8955","1573-2665"],"issn-type":[{"value":"0141-8955","type":"print"},{"value":"1573-2665","type":"electronic"}],"subject":[],"published":{"date-parts":[[1993,3]]}}}