{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2023,10,29]],"date-time":"2023-10-29T07:34:38Z","timestamp":1698564878565},"reference-count":9,"publisher":"Wiley","issue":"2","license":[{"start":{"date-parts":[[1993,3,1]],"date-time":"1993-03-01T00:00:00Z","timestamp":730944000000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["J of Inher Metab Disea"],"published-print":{"date-parts":[[1993,3]]},"DOI":"10.1007\/bf00710272","type":"journal-article","created":{"date-parts":[[2004,12,1]],"date-time":"2004-12-01T12:15:16Z","timestamp":1101903316000},"page":"308-311","source":"Crossref","is-referenced-by-count":10,"title":["Juvenile neuronal ceroid\u2010lipofuscinosis: Characterization of the dyslipoproteinaemia and demonstration of membrane phospholipid and phospholipid\u2010dependent signal transduction abnormalities in cultured skin fibroblasts"],"prefix":"10.1002","volume":"16","author":[{"given":"M. J.","family":"Bennett","sequence":"first","affiliation":[{"name":"Department of Pediatrics The Children's Hospital of Philadelphia  Pennsylvania USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"S. F.","family":"Poirier","sequence":"additional","affiliation":[{"name":"Department of Pediatrics The Children's Hospital of Philadelphia  Pennsylvania USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"L.","family":"Chern","sequence":"additional","affiliation":[{"name":"Department of Pediatrics The Children's Hospital of Philadelphia  Pennsylvania USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"A. R.","family":"Gayton","sequence":"additional","affiliation":[{"name":"The Ryegate Children's Centre  Sheffield UK"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"G. P.","family":"Hosking","sequence":"additional","affiliation":[{"name":"The Ryegate Children's Centre  Sheffield UK"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"N. \u2010A.","family":"Le","sequence":"additional","affiliation":[{"name":"Department of Medicine Emory University  Georgia USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"S.","family":"Majumdar","sequence":"additional","affiliation":[{"name":"Department of Pediatrics The Children's Hospital of Philadelphia  Pennsylvania USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"H. M.","family":"Korchak","sequence":"additional","affiliation":[{"name":"Department of Pediatrics The Children's Hospital of Philadelphia  Pennsylvania USA"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[1993,3]]},"reference":[{"key":"e_1_2_1_2_1","doi-asserted-by":"publisher","DOI":"10.1055\/s-2008-1071496"},{"key":"e_1_2_1_3_1","doi-asserted-by":"publisher","DOI":"10.1016\/0009-8981(92)90028-O"},{"key":"e_1_2_1_4_1","doi-asserted-by":"publisher","DOI":"10.1172\/JCI115081"},{"key":"e_1_2_1_5_1","first-page":"195","article-title":"Direct measurement of apolipoprotein B synthesis in human very low density lipoprotein using stable isotopes and mass spectrometry","volume":"28","author":"Cryer DR","year":"1986","journal-title":"J Lipid Res"},{"key":"e_1_2_1_6_1","doi-asserted-by":"publisher","DOI":"10.1016\/0888-7543(90)90297-8"},{"key":"e_1_2_1_7_1","doi-asserted-by":"publisher","DOI":"10.1007\/BF01811442"},{"key":"e_1_2_1_8_1","doi-asserted-by":"publisher","DOI":"10.1159\/000112183"},{"key":"e_1_2_1_9_1","doi-asserted-by":"publisher","DOI":"10.1007\/978-1-4899-5339-1_15"},{"key":"e_1_2_1_10_1","doi-asserted-by":"publisher","DOI":"10.1002\/ajmg.1320420428"}],"container-title":["Journal of Inherited Metabolic Disease"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1007\/BF00710272","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1007\/BF00710272","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,9,15]],"date-time":"2023-09-15T16:30:24Z","timestamp":1694795424000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1007\/BF00710272"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[1993,3]]},"references-count":9,"journal-issue":{"issue":"2","published-print":{"date-parts":[[1993,3]]}},"alternative-id":["10.1007\/BF00710272"],"URL":"https:\/\/doi.org\/10.1007\/bf00710272","archive":["Portico"],"relation":{},"ISSN":["0141-8955","1573-2665"],"issn-type":[{"value":"0141-8955","type":"print"},{"value":"1573-2665","type":"electronic"}],"subject":[],"published":{"date-parts":[[1993,3]]}}}