{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,9,4]],"date-time":"2025-09-04T14:19:02Z","timestamp":1756995542029},"reference-count":36,"publisher":"Springer Science and Business Media LLC","issue":"16","license":[{"start":{"date-parts":[[1963,8,1]],"date-time":"1963-08-01T00:00:00Z","timestamp":-202608000000},"content-version":"tdm","delay-in-days":0,"URL":"http:\/\/www.springer.com\/tdm"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Klin Wochenschr"],"published-print":{"date-parts":[[1963,8]]},"DOI":"10.1007\/bf01789076","type":"journal-article","created":{"date-parts":[[2005,6,20]],"date-time":"2005-06-20T03:29:05Z","timestamp":1119238145000},"page":"818-825","source":"Crossref","is-referenced-by-count":23,"title":["Glykogenose der Leber mit Aminoacidurie und Glucosurie"],"prefix":"10.1007","volume":"41","author":[{"given":"H. W.","family":"Rotthauwe","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"H.","family":"Fichsel","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"H. W.","family":"Heldt","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"E.","family":"Kirsten","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"M.","family":"Reim","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"E.","family":"Schmidt","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"F. W.","family":"Schmidt","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"W.","family":"Wesemann","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"297","reference":[{"key":"BF01789076_CR1","doi-asserted-by":"crossref","first-page":"1193","DOI":"10.1021\/ac60128a025","volume":"29","author":"W. L. Bencze","year":"1957","unstructured":"Bencze, W. L., andK. Schmid: Determination of tyrosine and tryptophane in proteins. Analyt. Chem.29, 1193 (1957).","journal-title":"Analyt. Chem."},{"key":"BF01789076_CR2","unstructured":"Bickel, H., u.F. Souchon: Die Papierchromatographie in der Kinderheilkunde. Arch. Kinderheilk.31, Beiheft (1955)."},{"key":"BF01789076_CR3","doi-asserted-by":"crossref","first-page":"256","DOI":"10.1016\/0006-3002(62)91119-8","volume":"57","author":"P. Borst","year":"1962","unstructured":"Borst, P.: The pathway of glutamate oxidation by mitochondria isolated from different tissues. Biochim. biophys. Acta (Amst.)57, 256 (1962).","journal-title":"Biochim. biophys. Acta"},{"key":"BF01789076_CR4","doi-asserted-by":"crossref","first-page":"264","DOI":"10.1016\/0002-9343(59)90316-X","volume":"26","author":"G. F. Cahill","year":"1959","unstructured":"Cahill, G. F., J. Ashmore, A. E. Renold andA. B. Hastings: Blood glucose and the liver. Amer. J. Med.26, 264 (1959).","journal-title":"Amer. J. Med."},{"key":"BF01789076_CR5","doi-asserted-by":"crossref","first-page":"583","DOI":"10.1016\/S0021-9258(18)65284-6","volume":"222","author":"N. W. Carrol","year":"1956","unstructured":"Carrol, N. W., R. W. Longley andJ. H. Roe: The determination of glycogen in liver and muscle by the use of anthrone reagent. J. biol. Chem.222, 583 (1956).","journal-title":"J. biol. Chem."},{"key":"BF01789076_CR6","first-page":"145","volume":"48","author":"G. T. Cori","year":"1953","unstructured":"Cori, G. T.: Glycogen structure and enzyme deficiencies in glycogen storage disease. Harvey Lect.48, 145 (1953).","journal-title":"Harvey Lect."},{"key":"BF01789076_CR7","first-page":"269","volume":"3","author":"R. Debere","year":"1958","unstructured":"Debere, R., J. C. Dreyfus, F. Schapira etG. Schapira: Les aldolases et transaminases s\u00e9riques au cours des polycories glycog\u00e9niques. Rev. fran\u00e7. Etud. clin. biol.3, 269 (1958).","journal-title":"Rev. fran\u00e7. Etud. clin. biol."},{"key":"BF01789076_CR8","first-page":"359","volume":"4","author":"G. Fanconi","year":"1949","unstructured":"Fanconi, G., u.H. Bickel: Die chronische Aminoacidurie (Aminos\u00e4urediabetes oder nephrotisch-glukosurischer Zwergwuchs) bei der Glykogenose und der Cystinkrankheit. Helv. paediat. Acta4, 359 (1949).","journal-title":"Helv. paediat. Acta"},{"key":"BF01789076_CR9","unstructured":"Hagge, W., u.H. W. Rotthauwe: Unver\u00f6ffentlicht."},{"key":"BF01789076_CR10","unstructured":"Heldt, H. W.: Phosphathaltige Metabolite in Anionenaustauschchromatogrammen s\u00e4urel\u00f6slicher Extrakte aus Rattenleber im Nanobereich. Biochem. Z. (im Druck)."},{"key":"BF01789076_CR11","first-page":"35","volume":"9","author":"H. G. Hers","year":"1959","unstructured":"Hers, H. G.: Etudes enzymatiques sur fragments h\u00e9patiques. Rev. int. H\u00e9pat.9, 35 (1959).","journal-title":"Rev. int. H\u00e9pat."},{"key":"BF01789076_CR12","first-page":"203","volume":"4","author":"H. G. Hers","year":"1959","unstructured":"Hers, H. G., etH. Malbrain: Etude biochimique d'un cas de maladie glycog\u00e9nique. Mod. Probl. P\u00e4diat.4, 203 (1959).","journal-title":"Mod. Probl. P\u00e4diat."},{"key":"BF01789076_CR13","first-page":"437","volume":"57","author":"H. G. Hers","year":"1961","unstructured":"Hers, H. G.: Recent development in the biochemistry of glycogen storage disease and of fructose intolerance. Chem. Weekbl.57, 437 (1961).","journal-title":"Chem. Weekbl."},{"key":"BF01789076_CR14","unstructured":"Hers, H. G.: Pers\u00f6nliche Mitteilung."},{"key":"BF01789076_CR15","first-page":"18","volume":"332","author":"H. J. Hohorst","year":"1959","unstructured":"Hohorst, H. J., F. H. Kreutz u.Th. B\u00fccher: \u00dcber Metabolitgehalte und Metabolitkonzentrationen in der Leber der Ratte. Biochem. Z.332, 18 (1959).","journal-title":"Biochem. Z."},{"key":"BF01789076_CR16","doi-asserted-by":"crossref","first-page":"159","DOI":"10.1016\/0006-291X(61)90262-5","volume":"4","author":"H. J. Hohorst","year":"1961","unstructured":"Hohorst, H. J., F. H. Kreutz andM. Reim: Steady state equilibria of some DPN-linked reactions and the oxidation\/reduction state of the DPN\/DPNH system in the cytoplasmatic compartment of liver cells in vitro. Biochem. biophys. Res. Commun.4, 159 (1961).","journal-title":"Biochem. biophys. Res. Commun."},{"key":"BF01789076_CR17","doi-asserted-by":"crossref","first-page":"163","DOI":"10.1016\/0006-291X(61)90263-7","volume":"4","author":"H. J. Hohorst","year":"1961","unstructured":"Hohorst, H. J., F. H. Kreutz, M. Reim andH. J. H\u00fcbener: The oxidation\/reduction state of the extramitochondrial DPN\/DPNH system in rat liver and the normal control of substrate levels in vivo. Biochem. biophys. Res. Commun.4, 163 (1961).","journal-title":"Biochem. biophys. Res. Commun."},{"key":"BF01789076_CR18","volume-title":"Methoden der enzymatischen Analyse","author":"H. J. Hohorst","year":"1962","unstructured":"Hohorst, H. J.: In: Methoden der enzymatischen Analyse, Hrsg.H. U. Bergmeyer. Darmstadt: Verlag Chemie 1962."},{"key":"BF01789076_CR19","unstructured":"Hohorst, H. J.: Pers\u00f6nliche Mitteilung."},{"key":"BF01789076_CR20","doi-asserted-by":"crossref","first-page":"553","DOI":"10.1542\/peds.29.4.553","volume":"29","author":"R. R. Howell","year":"1962","unstructured":"Howell, R. R., D. M. Ashton andJ. B. Wyngaarden: Glucose-6-phosphatase deficiency glycogen storage disease. Studies on the interrelationship of carbohydrate, lipid, and purin abnormalities. Pediatrics29, 553 (1962).","journal-title":"Pediatrics"},{"key":"BF01789076_CR21","doi-asserted-by":"crossref","first-page":"653","DOI":"10.1016\/S0021-9258(18)38503-X","volume":"199","author":"B. Illingworth","year":"1952","unstructured":"Illingworth, B., andG. T. Cori: Structure of glycogens and amylopectins. III. Normal and abnormal human glycogen. J. biol. Chem.199, 653 (1952).","journal-title":"J. biol. Chem."},{"key":"BF01789076_CR22","doi-asserted-by":"crossref","first-page":"169","DOI":"10.1016\/0006-291X(61)90264-9","volume":"4","author":"E. Kirsten","year":"1961","unstructured":"Kirsten, E., R. Kirsten, H. J. Hohorst andTh. B\u00fccher: Free amino acids in alloxan diabetic rat livers. Biochem. biophys. Res. Commun.4, 169 (1961).","journal-title":"Biochem. biophys. Res. Commun."},{"key":"BF01789076_CR23","doi-asserted-by":"crossref","first-page":"523","DOI":"10.1042\/bj0750523","volume":"75","author":"H. A. Krebs","year":"1960","unstructured":"Krebs, H. A., andD. Bellamy: The interconversion of glutamic acid and aspartic acid in respiring tissues. Biochem. J.75, 523 (1960).","journal-title":"Biochem. J."},{"key":"BF01789076_CR24","first-page":"14","volume":"17","author":"M. Lamy","year":"1960","unstructured":"Lamy, M., R. Dubois, A. Rossier, J. Frezal, H. Loeb etG. Blancher: La glyc\u00e9nose par d\u00e9ficience en phosphorylase h\u00e9patique. Arch. fran\u00e7. P\u00e9diat.17, 14 (1960).","journal-title":"Arch. fran\u00e7. P\u00e9diat."},{"key":"BF01789076_CR25","first-page":"422","volume":"67","author":"F. Linneweh","year":"1936","unstructured":"Linneweh, F.: Zur Differentialdiagnose kindlicher Lebertumoren. Mschr. Kinderheilk.67, 422 (1936).","journal-title":"Mschr. Kinderheilk."},{"key":"BF01789076_CR26","first-page":"147","volume-title":"Erbliche Stoffwechselkrankheiten","author":"F. Linneweh","year":"1962","unstructured":"Linneweh, F.: Erbliche Stoffwechselkrankheiten, Hrsg.F. Linneweh, S. 147. M\u00fcnchen: Urban & Schwarzenberg 1962."},{"key":"BF01789076_CR27","doi-asserted-by":"crossref","first-page":"893","DOI":"10.1016\/S0021-9258(18)71177-0","volume":"211","author":"St. Moore","year":"1954","unstructured":"Moore, St., andW. H. Stein: Procedures for the chromatographic determination of amino acids on four per cent crosslinkes sulfonated polystrene resins. J. biol. Chem.211, 893 (1954).","journal-title":"J. biol. Chem."},{"key":"BF01789076_CR28","doi-asserted-by":"crossref","first-page":"739","DOI":"10.1007\/BF01479875","volume":"39","author":"K. Papenberg","year":"1961","unstructured":"Papenberg, K.: Zum Nachweis und zur klinischen Bedeutung der freien Nucleotide in menschlichen Organextrakten. I. Folge: Gehaltsbestimmungen in der normalen menschlichen Leber. Klin. Wschr.39, 739 (1961).","journal-title":"Klin. Wschr."},{"key":"BF01789076_CR29","doi-asserted-by":"crossref","unstructured":"Rauen, H. M. (Hrsg.): Biochemisches Taschenbuch, S. 828. Springer 1956.","DOI":"10.1007\/978-3-642-53240-5"},{"key":"BF01789076_CR30","unstructured":"Reim, M., u.H. J. Hohorst: Unver\u00f6ffentlicht."},{"key":"BF01789076_CR31","doi-asserted-by":"crossref","first-page":"227","DOI":"10.1007\/BF01480164","volume":"36","author":"E. Schmidt","year":"1958","unstructured":"Schmidt, E., F. W. Schmidt u.E. Wildhirt: Aktivit\u00e4tsbestimmungen von Enzymen des energieliefernden Stoffwechsels in der menschlichen Leber bei der akuten Hepatitis und ihren Ausheilungszust\u00e4nden. Klin. Wschr.36, 227 (1958).","journal-title":"Klin. Wschr."},{"key":"BF01789076_CR32","doi-asserted-by":"crossref","first-page":"1221","DOI":"10.1007\/BF01486383","volume":"37","author":"E. Schmidt","year":"1959","unstructured":"Schmidt, E., F. W. Schmidt u.E. Wildhirt: Ergebnisse der Untersuchung weiterer Enzyme des energieliefernden Stoffwechsels in der normalen und pathologisch ver\u00e4nderten menschlichen Leber. Untersuchungen \u00fcber den Eiwei\u00df- und Blutgehalt in Leberpunktaten. Klin. Wschr.37, 1221 (1959).","journal-title":"Klin. Wschr."},{"key":"BF01789076_CR33","doi-asserted-by":"crossref","first-page":"103","DOI":"10.1542\/peds.27.1.103","volume":"27","author":"J. B. Sidbury Jr.","year":"1961","unstructured":"Sidbury jr., J. B., M. Cornblath, J. Fisher andE. House: Glycogen in erythrocytes of patients with glycogen storage disease. Pediatrics27, 103 (1961).","journal-title":"Pediatrics"},{"key":"BF01789076_CR34","doi-asserted-by":"crossref","first-page":"183","DOI":"10.1007\/978-3-642-86337-0_22","volume-title":"Die physiologische Entwicklung des Kindes","author":"U. Stave","year":"1959","unstructured":"Stave, U.: Die Leberfunktionsteste und Serumenzymaktivit\u00e4ten. In: Die physiologische Entwicklung des Kindes, ed.F. Linneweh, S. 183. Berlin-G\u00f6ttingen-Heidelberg: Springer 1959."},{"key":"BF01789076_CR35","first-page":"508","volume":"329","author":"B. E. Wahler","year":"1959","unstructured":"Wahler, B. E., u.A. Wollenberger: Zur Bestimmung des Orthophosphat neben s\u00e4urelabilen molybdatlabilen Phosphors\u00e4ureverbindungen. Biochem. Z.329, 508 (1959).","journal-title":"Biochem. Z."},{"key":"BF01789076_CR36","first-page":"880","volume":"9","author":"G. Weber","year":"1960","unstructured":"Weber, G., andE. R. Harpur: Liver enzymes in glycogen storage disease. Metabolism9, 880 (1960).","journal-title":"Metabolism"}],"container-title":["Klinische Wochenschrift"],"original-title":[],"language":"de","link":[{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1007\/BF01789076.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/link.springer.com\/article\/10.1007\/BF01789076\/fulltext.html","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1007\/BF01789076","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2024,1,27]],"date-time":"2024-01-27T01:17:58Z","timestamp":1706318278000},"score":1,"resource":{"primary":{"URL":"http:\/\/link.springer.com\/10.1007\/BF01789076"}},"subtitle":["Klinische und biochemische Untersuchungen"],"short-title":[],"issued":{"date-parts":[[1963,8]]},"references-count":36,"journal-issue":{"issue":"16","published-print":{"date-parts":[[1963,8]]}},"alternative-id":["BF01789076"],"URL":"https:\/\/doi.org\/10.1007\/bf01789076","relation":{},"ISSN":["0023-2173","1432-1440"],"issn-type":[{"value":"0023-2173","type":"print"},{"value":"1432-1440","type":"electronic"}],"subject":[],"published":{"date-parts":[[1963,8]]}}}