{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,12]],"date-time":"2026-09-12T08:22:32Z","timestamp":1789201352813,"version":"build-2803163510"},"reference-count":25,"publisher":"Wiley","issue":"1","license":[{"start":{"date-parts":[[1991,7,5]],"date-time":"1991-07-05T00:00:00Z","timestamp":678672000000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["J of Inher Metab Disea"],"published-print":{"date-parts":[[1992,1]]},"abstract":"<jats:title>Summary<\/jats:title><jats:p>Two long\u2010haired Siamese cats are reported with clinical manifestations of human mucopolysaccharidosis VI (Maroteaux\u2010Lamy disease): facial dysmorphia, dysostosis multiplex, paralysis. Urine of the two affected animals contained a high concentration of glycosaminoglycans, as detected by the dimethylmethylene blue test. Qualitative analysis, performed by thin\u2010layer chromatography of the cetylpyridinium chloride\u2010precipitable material, showed dermatan sulphate. Excessive incorporation of [<jats:sup>35<\/jats:sup>S]sulphate in the intracellular mucopolysaccharide of cultured fibroblasts and deficiency of arylsulphatase B in such cells indicate that these cats are affected by Maroteaux\u2010Lamy disease. They should thus be considered the first European case of feline mucopolysaccharidosis VI.<\/jats:p>","DOI":"10.1007\/bf01800339","type":"journal-article","created":{"date-parts":[[2005,6,21]],"date-time":"2005-06-21T17:27:06Z","timestamp":1119374826000},"page":"17-24","source":"Crossref","is-referenced-by-count":9,"title":["Animal models for lysosomal storage diseases: A new case of feline mucopolysaccharidosis VI"],"prefix":"10.1002","volume":"15","author":[{"given":"P.","family":"Di Natale","sequence":"first","affiliation":[{"name":"Dipartimento di Biochimica e Biotecnologie Mediche, II Facolt\u00e0 di Medicina e Chirurgia Universit\u00e0 di Napoli \u201cFederico II\u201d  Naples Italy"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"T.","family":"Annella","sequence":"additional","affiliation":[{"name":"Dipartimento di Biochimica e Biotecnologie Mediche, II Facolt\u00e0 di Medicina e Chirurgia Universit\u00e0 di Napoli \u201cFederico II\u201d  Naples Italy"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"A.","family":"Daniele","sequence":"additional","affiliation":[{"name":"Dipartimento di Biochimica e Biotecnologie Mediche, II Facolt\u00e0 di Medicina e Chirurgia Universit\u00e0 di Napoli \u201cFederico II\u201d  Naples Italy"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"G.","family":"Spagnuolo","sequence":"additional","affiliation":[{"name":"Dipartimento di Biochimica e Biotecnologie Mediche, II Facolt\u00e0 di Medicina e Chirurgia Universit\u00e0 di Napoli \u201cFederico II\u201d  Naples Italy"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"R.","family":"Cerundolo","sequence":"additional","affiliation":[{"name":"Instituto di Clinica Medica, Facolt\u00e0 di Veterinaria Universit\u00e0 di Napoli \u201cFederico II\u201d  Naples Italy"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"D.","family":"de Caprariis","sequence":"additional","affiliation":[{"name":"Instituto di Clinica Medica, Facolt\u00e0 di Veterinaria Universit\u00e0 di Napoli \u201cFederico II\u201d  Naples Italy"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"A. E.","family":"Gravino","sequence":"additional","affiliation":[{"name":"Instituto di Clinica Medica, Facolt\u00e0 di Veterinaria Universit\u00e0 di Napoli \u201cFederico II\u201d  Naples Italy"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"311","published-online":{"date-parts":[[1991,7,5]]},"reference":[{"key":"e_1_2_1_2_1","first-page":"891","article-title":"A case of mucopolysaccharidosis VI in a cat","volume":"19","author":"Breton L.","year":"1983","journal-title":"J. Am. Anim. Hosp. Assoc."},{"key":"e_1_2_1_3_1","doi-asserted-by":"publisher","DOI":"10.1016\/0003-2697(67)90087-5"},{"key":"e_1_2_1_4_1","doi-asserted-by":"publisher","DOI":"10.3109\/03008208209160269"},{"key":"e_1_2_1_5_1","doi-asserted-by":"publisher","DOI":"10.1038\/312467a0"},{"key":"e_1_2_1_6_1","first-page":"439","volume-title":"Methods in Enzymology","author":"Hall C. 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