{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,9,2]],"date-time":"2025-09-02T10:37:42Z","timestamp":1756809462451},"reference-count":23,"publisher":"Wiley","issue":"6","license":[{"start":{"date-parts":[[1991,3,21]],"date-time":"1991-03-21T00:00:00Z","timestamp":669513600000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["J of Inher Metab Disea"],"published-print":{"date-parts":[[1991,11]]},"abstract":"<jats:title>Summary<\/jats:title><jats:p>The progress of nine maple syrup urine disease patients (eight classical, one possible variant) was reviewed to look for similarities in developmental patterns. A consistent developmental profile of stronger Verbal than Performance IQ and lower than familially expected IQ was seen. Younger age at diagnosis was associated with a milder neonatal course. Those who were asymptomatic or suffered mild complications in the newborn period have higher IQs than children experiencing moderate or severe complications. Children with asymptomatic or mild neonatal course also required less special education services. Overall, a picture of ubiquitous motor, visual\u2010analytic and learning deficits is seen.<\/jats:p>","DOI":"10.1007\/bf01800467","type":"journal-article","created":{"date-parts":[[2005,6,21]],"date-time":"2005-06-21T17:04:17Z","timestamp":1119373457000},"page":"881-889","source":"Crossref","is-referenced-by-count":23,"title":["Developmental profile of patients with maple syrup urine disease"],"prefix":"10.1002","volume":"14","author":[{"given":"A.","family":"Nord","sequence":"first","affiliation":[{"name":"Department of Pediatrics The Children's Hospital\/University of Colorado Health Sciences Center  Box 153 1056 East 19th Ave Denver Colorado 80218 USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"W. J.","family":"van Doorninck","sequence":"additional","affiliation":[{"name":"Department of Pediatrics The Children's Hospital\/University of Colorado Health Sciences Center  Box 153 1056 East 19th Ave Denver Colorado 80218 USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"C.","family":"Greene","sequence":"additional","affiliation":[{"name":"Department of Pediatrics The Children's Hospital\/University of Colorado Health Sciences Center  Box 153 1056 East 19th Ave Denver Colorado 80218 USA"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[1991,3,21]]},"reference":[{"key":"e_1_2_1_2_1","doi-asserted-by":"crossref","first-page":"856","DOI":"10.1542\/peds.68.6.856","article-title":"Outcome of early and long\u2010term management of classical maple syrup urine disease","volume":"68","author":"Clow C. 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