{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2023,10,23]],"date-time":"2023-10-23T00:54:20Z","timestamp":1698022460129},"reference-count":8,"publisher":"Wiley","issue":"1","license":[{"start":{"date-parts":[[1980,12,1]],"date-time":"1980-12-01T00:00:00Z","timestamp":344476800000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["J of Inher Metab Disea"],"published-print":{"date-parts":[[1980,12]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>Cobalamin metabolism has been investigated in a new case of transcobalamin II (TC II) deficiency. Using the chromatobioautographic technique, an abnormal distribution of cobalamins was detected in the child's erythrocytes and reduced synthesis of adenosylcobalamin but not of methylcobalamin in cultured fibroblasts. These results suggest that there may be a close link between TC II\u2010mediated cobalamin transport and intracellular synthesis of adenosylcobalamin (Ado\u2010Cbl).<\/jats:p>","DOI":"10.1007\/bf02312538","type":"journal-article","created":{"date-parts":[[2006,2,15]],"date-time":"2006-02-15T06:26:55Z","timestamp":1139984815000},"page":"95-96","source":"Crossref","is-referenced-by-count":9,"title":["Defective adenosylcobalamin synthesis in a case of transcobalamin II deficiency"],"prefix":"10.1002","volume":"3","author":[{"given":"J. C.","family":"Linnell","sequence":"first","affiliation":[{"name":"Department of Experimental Chemical Pathology Vincent Square Laboratories of Westminster Hospital  124 Vauxhall Bridge Road London SW1V 2RH"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"E. V.","family":"Quadros","sequence":"additional","affiliation":[{"name":"Department of Experimental Chemical Pathology Vincent Square Laboratories of Westminster Hospital  124 Vauxhall Bridge Road London SW1V 2RH"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"P. G.","family":"Elliott","sequence":"additional","affiliation":[{"name":"Department of Physics Westminster Hospital  London SW1P 2AP"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"P.","family":"Malleson","sequence":"additional","affiliation":[{"name":"Hospital for Sick Children  Great Ormond Street London WC1N 1EH"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[1980,12]]},"reference":[{"key":"e_1_2_1_2_1","doi-asserted-by":"publisher","DOI":"10.1111\/j.1365-2141.1979.tb03716.x"},{"key":"e_1_2_1_3_1","doi-asserted-by":"publisher","DOI":"10.1515\/9783111510828-091"},{"key":"e_1_2_1_4_1","doi-asserted-by":"publisher","DOI":"10.1056\/NEJM197111182852103"},{"key":"e_1_2_1_5_1","doi-asserted-by":"publisher","DOI":"10.1172\/JCI109580"},{"key":"e_1_2_1_6_1","doi-asserted-by":"publisher","DOI":"10.1016\/S0022-3476(74)80503-2"},{"key":"e_1_2_1_7_1","first-page":"163","article-title":"Tissue distribution of coenzyme and other forms of vitamin B12 in control subjects and patients with pernicious anaemia","volume":"46","author":"Linnell J. C.","year":"1974","journal-title":"Clin. Sci. Mol. Med."},{"key":"e_1_2_1_8_1","doi-asserted-by":"publisher","DOI":"10.1203\/00006450-197603000-00007"},{"key":"e_1_2_1_9_1","doi-asserted-by":"publisher","DOI":"10.1136\/jcp.20.5.683"}],"container-title":["Journal of Inherited Metabolic Disease"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1007\/BF02312538","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1007\/BF02312538","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,9,17]],"date-time":"2023-09-17T03:52:03Z","timestamp":1694922723000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1007\/BF02312538"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[1980,12]]},"references-count":8,"journal-issue":{"issue":"1","published-print":{"date-parts":[[1980,12]]}},"alternative-id":["10.1007\/BF02312538"],"URL":"https:\/\/doi.org\/10.1007\/bf02312538","archive":["Portico"],"relation":{},"ISSN":["0141-8955","1573-2665"],"issn-type":[{"value":"0141-8955","type":"print"},{"value":"1573-2665","type":"electronic"}],"subject":[],"published":{"date-parts":[[1980,12]]}}}