{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,8]],"date-time":"2026-10-08T22:15:37Z","timestamp":1791497737487,"version":"4.3.4"},"reference-count":16,"publisher":"Springer Science and Business Media LLC","issue":"2","license":[{"start":{"date-parts":[[2020,10,25]],"date-time":"2020-10-25T00:00:00Z","timestamp":1603584000000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0"},{"start":{"date-parts":[[2020,10,25]],"date-time":"2020-10-25T00:00:00Z","timestamp":1603584000000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0"}],"funder":[{"name":"University of Innsbruck and Medical University of Innsbruck"}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["Med Klin Intensivmed Notfmed"],"published-print":{"date-parts":[[2022,3]]},"abstract":"<jats:title>Zusammenfassung<\/jats:title><jats:p>Die Patientengruppe der Erwachsenen mit angeborenen Herzfehlern (EMAH) ist mittlerweile bereits gr\u00f6\u00dfer als die der Kinder mit angeborenen Herzfehlern. EMAH-Patienten weisen auch nach Reparaturoperationen oft komplexe pathophysiologische und anatomische Verh\u00e4ltnisse auf. Bei Komplikationen kann es sehr rasch zu Notfallsituationen auch bei ansonsten asymptomatischen oder nur wenig symptomatischen Patienten kommen. Gemessen an der Gesamtzahl der Patienten, die von Not\u00e4rzten und in den Notaufnahmen versorgt werden, sind EMAH-Notfallsituationen nach wie vor sehr selten. Diese \u00dcbersicht soll die Notfallbetreuung von EMAH-Patienten erleichtern. F\u00fcr ca. zwei Drittel aller Notf\u00e4lle sind Rhythmusst\u00f6rungen und akute Herzinsuffizienz verantwortlich. Rhythmusst\u00f6rungen m\u00fcssen in der Regel z\u00fcgig terminiert werden, weil sie unbehandelt rasch zur kardialen Dekompensation f\u00fchren k\u00f6nnen. Bei Scheitern der medikament\u00f6sen Therapie oder h\u00e4modynamischer Instabilit\u00e4t m\u00fcssen EMAH-Patienten mit tachykarden Rhythmusst\u00f6rungen rasch elektrisch kardiovertiert werden. Symptomatische Bradykardien k\u00f6nnen eine rasche Schrittmacherversorgung erforderlich machen. Aufgrund der komplexen Anatomie kann das Einschwemmen eines transven\u00f6sen Interim-Schrittmachers bei einzelnen Vitien unm\u00f6glich sein. Die akute kardiale Dekompensation bei EMAH ist oft durch ein akutes Rechtsherzversagen verursacht. Weitere relativ h\u00e4ufige Aufnahmegr\u00fcnde sind Infektionen, Synkopen, Thromboembolien und Aortendissektion. Der Herzpass der Patienten informiert \u00fcber das vorliegende Vitium. Die umgehende Kontaktaufnahme mit dem behandelnden EMAH-Zentrum wird dringend empfohlen.<\/jats:p>","DOI":"10.1007\/s00063-020-00752-6","type":"journal-article","created":{"date-parts":[[2020,10,25]],"date-time":"2020-10-25T23:02:26Z","timestamp":1603666946000},"page":"100-111","update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":1,"title":["Erwachsene mit angeborenen Herzfehlern im Notaufnahmedienst","Adults with congenital heart disease presenting to the emergency department"],"prefix":"10.1007","volume":"117","author":[{"given":"J.","family":"Mair","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"G.-P.","family":"Diller","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"H.","family":"Geiger","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"M.","family":"Greutmann","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"G.","family":"Hessling","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"D.","family":"Tobler","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2020,10,25]]},"reference":[{"key":"752_CR1","doi-asserted-by":"publisher","first-page":"194","DOI":"10.1007\/s00392-008-0639-8","volume":"97","author":"AA Schmaltz","year":"2008","unstructured":"Schmaltz\u00a0AA, Bauer\u00a0U, Baumgartner\u00a0H, Cesnjevar\u00a0R, de Haan\u00a0F, Franke\u00a0C et al (2008) Medizinische Leitlinie zur Behandlung von Erwachsenen mit angeborenen Herzfehlern (EMAH) der deutsch-\u00f6sterreichisch-schweizerischen kardiologischen Gesellschaften. 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J.\u00a0Mair erhielt Vortragshonorare von Abbott, \u00d6sterreich. G.-P.\u00a0Diller erhielt Honorare von Actelion und Daichii Sankyo au\u00dferhalb der vorliegenden Arbeit.","order":2,"name":"Ethics","group":{"name":"EthicsHeading","label":"Interessenkonflikt"}},{"value":"F\u00fcr diesen Beitrag wurden von den Autoren keine Studien an Menschen oder Tieren durchgef\u00fchrt.","order":3,"name":"Ethics","group":{"name":"EthicsHeading","label":"Interessenkonflikt"}}]}}