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The management of PAIS poses both diagnostic and therapeutic challenges. It presents with nonspecific symptoms and is often misdiagnosed as pulmonary embolism. While surgical resection is the primary treatment modality, the role of adjuvant chemotherapy and radiotherapy remains uncertain. However, given the high recurrence rate, adjuvant chemotherapy and\/or radiotherapy have been utilized in a\u00a0limited number of case reports. We present the case of a\u00a046-year-old woman who was diagnosed with PAIS and underwent surgical resection followed by adjuvant chemotherapy (ChT) and radiotherapy (RT), demonstrating good tolerance to this multimodal treatment approach.<\/jats:p>","DOI":"10.1007\/s00066-024-02250-6","type":"journal-article","created":{"date-parts":[[2024,6,12]],"date-time":"2024-06-12T16:01:56Z","timestamp":1718208116000},"page":"725-729","update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":10,"title":["Pulmonary artery intimal sarcoma: Case report of a\u00a0patient managed with multimodality treatment and a\u00a0comprehensive literature review"],"prefix":"10.1007","volume":"200","author":[{"given":"C.","family":"Atahan","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Z.","family":"G\u00fcral","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"S.","family":"Y\u00fccel","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-4868-9543","authenticated-orcid":false,"given":"F.","family":"A\u011fao\u011flu","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2024,6,12]]},"reference":[{"issue":"4","key":"2250_CR1","doi-asserted-by":"publisher","first-page":"787","DOI":"10.1093\/EJCTS\/EZS387","volume":"43","author":"S Mussot","year":"2013","unstructured":"Mussot\u00a0S et\u00a0al (2013) Retrospective institutional study of 31\u00a0patients treated for pulmonary artery sarcoma. 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