{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,12,31]],"date-time":"2025-12-31T00:12:01Z","timestamp":1767139921084,"version":"build-2238731810"},"reference-count":9,"publisher":"Springer Science and Business Media LLC","issue":"4","license":[{"start":{"date-parts":[[2020,12,8]],"date-time":"2020-12-08T00:00:00Z","timestamp":1607385600000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0"},{"start":{"date-parts":[[2020,12,8]],"date-time":"2020-12-08T00:00:00Z","timestamp":1607385600000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0"}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["Anaesthesist"],"published-print":{"date-parts":[[2021,4]]},"abstract":"<jats:title>Zusammenfassung<\/jats:title>\n                  <jats:p>Die Dopa-responsive Dystonie (Segawa-Syndrom) ist eine sehr seltene neurologische Erkrankung. Bei korrekter Diagnosestellung und ad\u00e4quater Therapie sind gravierende Organfunktionsst\u00f6rungen kaum zu erwarten. Dennoch sind Kenntnisse \u00fcber das Krankheitsbild und die m\u00f6glichen An\u00e4sthesieverfahren bei der Versorgung dieser Patienten von Bedeutung. Anhand zweier Kasuistiken werden die wesentlichen Fakten zur perioperativen Betreuung dieser Patientengruppe dargestellt.<\/jats:p>","DOI":"10.1007\/s00101-020-00898-0","type":"journal-article","created":{"date-parts":[[2020,12,8]],"date-time":"2020-12-08T13:12:31Z","timestamp":1607433151000},"page":"316-319","update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":0,"title":["An\u00e4sthesief\u00fchrung bei Patienten mit Dopa-responsiver Dystonie (Segawa-Syndrom)","Anesthesia in patients with dopa-responsive dystonia (Segawa syndrome)"],"prefix":"10.1007","volume":"70","author":[{"given":"K.","family":"Gro\u00df","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"S.","family":"Kleinschmidt","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"297","published-online":{"date-parts":[[2020,12,8]]},"reference":[{"key":"898_CR1","doi-asserted-by":"publisher","first-page":"350","DOI":"10.1016\/j.jclinane.2016.08.023","volume":"35","author":"N Howze","year":"2016","unstructured":"Howze\u00a0N, Will\u00a0ND, Klassen\u00a0BT, Sprung\u00a0J, Weingarten\u00a0T (2016) Anesthetic implications for patients with Segawa syndrome. 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Anaesth Intensivmed. https:\/\/doi.org\/10.19224\/ai2018.s450","journal-title":"Anaesth Intensivmed"},{"key":"898_CR9","doi-asserted-by":"publisher","first-page":"889","DOI":"10.1097\/EJA.000000000000035","volume":"32","author":"T Warnecke","year":"2015","unstructured":"Warnecke\u00a0T, Fiedler\u00a0F (2015) A septuagenarian patient with Segawa\u2019s dystonia. 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F\u00fcr die aufgef\u00fchrten Studien gelten die jeweils dort angegebenen ethischen Richtlinien. F\u00fcr Bildmaterial oder anderweitige Angaben innerhalb des Manuskripts, \u00fcber die Patienten zu identifizieren sind, liegt von ihnen und\/oder ihren gesetzlichen Vertretern eine schriftliche Einwilligung vor.","order":3,"name":"Ethics","group":{"name":"EthicsHeading","label":"Interessenkonflikt"}}]}}