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Wir berichten von einem 3\u2011j\u00e4hrigen Kind, bei dem ein derartiges Sweet-Syndrom zur Erstdiagnose einer Takayasu-Arteriitis f\u00fchrte. Die postinflammatorische Elastolyse mit erworbener Cutis laxa stellt beim kindlichen Sweet-Syndrom einen klinisch relevanten kutanen Indikator f\u00fcr lebensbedrohliche kardiale Gef\u00e4\u00dfkomplikationen wie Aortitis, Aortenaneurysma, Koronararterienstenose und Herzversagen dar. Da das Cutis-laxa-artig abheilende Sweet-Syndrom den kardialen Komplikationen zumeist zeitlich vorausgeht oder wie in unserem Fall simultan auftritt, sollten die betroffenen Patienten umgehend kardiologisch und rheumatologisch untersucht werden, um bei vaskul\u00e4rer Beteiligung einen komplikativen Verlauf durch fr\u00fche antiinflammatorische und immunmodulierende Systemtherapie zu verhindern.<\/jats:p>","DOI":"10.1007\/s00105-022-04999-2","type":"journal-article","created":{"date-parts":[[2022,7,15]],"date-time":"2022-07-15T11:05:32Z","timestamp":1657883132000},"page":"884-890","update-policy":"http:\/\/dx.doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":2,"title":["Sweet-Syndrom des Kindesalters mit erworbener Cutis laxa (Marshall-Syndrom) als Erstmanifestation einer Takayasu-Arteriitis"],"prefix":"10.1007","volume":"73","author":[{"given":"Christiane","family":"Michl","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Regina","family":"H\u00fchn","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Cord","family":"Sunderk\u00f6tter","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"297","published-online":{"date-parts":[[2022,7,15]]},"reference":[{"key":"4999_CR1","doi-asserted-by":"publisher","first-page":"842","DOI":"10.1111\/j.1365-4632.2008.03689.x","volume":"47","author":"XL Bi","year":"2008","unstructured":"Bi\u00a0XL, Gu\u00a0J, Yan\u00a0M et\u00a0al (2008) A case of Sweet\u2019s syndrome with slack skin and pathergy phenomenon. 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F\u00fcr die aufgef\u00fchrten Studien gelten die jeweils dort angegebenen ethischen Richtlinien. F\u00fcr Bildmaterial oder anderweitige Angaben innerhalb des Manuskripts, \u00fcber die Patienten zu identifizieren sind, liegt von ihnen und\/oder ihren gesetzlichen Vertretern eine schriftliche Einwilligung vor.","order":3,"name":"Ethics","group":{"name":"EthicsHeading","label":"Interessenkonflikt"}}]}}