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We present histopathological proof of the extremely rare bilateral occurrence of intracochlear schwannomas with negative blood genetic testing for neurofibromatosis type\u00a02 (NF2). Bilateral schwannomas are typically associated with the condition NF2 and this case is presumed to have either mosaicism for NF2 or sporadic development of bilateral tumours. For progressive bilateral tumour growth and associated profound hearing loss, surgical intervention via partial cochleoectomy, tumour removal, preservation of the modiolus, and simultaneous cochlear implantation with lateral wall electrode carrier with basal double electrode contacts was performed. The right side was operated on first with a\u00a014-month gap between each side. The hearing in aided speech recognition for consonant-nucleus-consonant (CNC) phonemes in quiet improved from 57% to 83% 12\u00a0months after bilateral cochlear implantation (CI). Bilateral intracochlear schwannomas in non-NF2 patients are extremely rare but should be considered in cases of progressive bilateral hearing loss. Successful tumour removal and cochlear implantation utilizing a\u00a0lateral wall electrode is possible and can achieve good hearing outcomes.<\/jats:p>","DOI":"10.1007\/s00106-023-01379-7","type":"journal-article","created":{"date-parts":[[2023,10,30]],"date-time":"2023-10-30T17:01:39Z","timestamp":1698685299000},"page":"802-808","update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":6,"title":["Bilateral intracochlear schwannomas: histopathological confirmation and outcomes following tumour removal and cochlear implantation with lateral wall electrodes","Bilaterale intracochle\u00e4re Schwannome: histopathologische Best\u00e4tigung und Ergebnisse nach Tumorentfernung und Cochleaimplantation mit \u201elateral wall\u201c-Elektroden"],"prefix":"10.1007","volume":"71","author":[{"given":"Mark E.","family":"Quick","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Shannon","family":"Withers","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Stefan K.","family":"Plontke","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ronel","family":"Chester-Browne","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Jafri","family":"Kuthubutheen","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"297","published-online":{"date-parts":[[2023,10,30]]},"reference":[{"issue":"2","key":"1379_CR1","doi-asserted-by":"publisher","first-page":"223","DOI":"10.1007\/s11060-015-1827-9","volume":"124","author":"VR Kshettry","year":"2015","unstructured":"Kshettry\u00a0VR, Hsieh\u00a0JK, Ostrom\u00a0QT, Kruchko\u00a0C, Barnholtz-Sloan\u00a0JS (2015) Incidence of vestibular schwannomas in the United States. 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All studies mentioned were in accordance with the ethical standards indicated in each case. For images or other information within the manuscript which identify patients, consent was obtained from them and\/or their legal guardians.","order":3,"name":"Ethics","group":{"name":"EthicsHeading","label":"Conflict of interest"}}]}}