{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,7,30]],"date-time":"2026-07-30T13:02:12Z","timestamp":1785416532213,"version":"3.56.0"},"reference-count":3,"publisher":"Springer Science and Business Media LLC","license":[{"start":{"date-parts":[[2026,7,30]],"date-time":"2026-07-30T00:00:00Z","timestamp":1785369600000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0\/deed.de"},{"start":{"date-parts":[[2026,7,30]],"date-time":"2026-07-30T00:00:00Z","timestamp":1785369600000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0\/deed.de"}],"funder":[{"DOI":"10.13039\/501100018936","name":"Universit\u00e4tsklinikum Heidelberg","doi-asserted-by":"crossref","id":[{"id":"10.13039\/501100018936","id-type":"DOI","asserted-by":"crossref"}]}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["HNO"],"abstract":"<jats:title>Zusammenfassung<\/jats:title>\n                  <jats:p>Das Cogan-I-Syndrom ist eine seltene Systemerkrankung, die sich durch das Auftreten audiovestibul\u00e4rer und okul\u00e4rer Symptome auszeichnet. Wir pr\u00e4sentieren den Fall einer 62-j\u00e4hrigen Patientin, die nach einseitiger Ertaubung ein Cochleaimplantat erhielt. Trotz regelrechter Implantation kam es zu einem protrahierten Verlauf mit chronischer Zephalgie, wiederkehrender Otitis, schwankenden intracochle\u00e4ren Impedanzen sowie langsam progredientem H\u00f6rverlust der Gegenseite. In interdisziplin\u00e4rer Zusammenarbeit wurde die Diagnose des Cogan-I-Syndroms gestellt und eine Biologikatherapie eingeleitet.<\/jats:p>","DOI":"10.1007\/s00106-026-01791-9","type":"journal-article","created":{"date-parts":[[2026,7,30]],"date-time":"2026-07-30T12:12:39Z","timestamp":1785413559000},"update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":0,"title":["Das Cogan-I-Syndrom als seltene Ertaubungsursache","Cogan syndrome as a\u00a0rare cause of deafness"],"prefix":"10.1007","author":[{"given":"Lena","family":"Kappert","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Vera","family":"Lohnherr","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Sara","family":"Euteneuer","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ute","family":"Geiger","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Patrick J.","family":"Schuler","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Miray-Su","family":"Y\u0131lmaz Top\u00e7uo\u011flu","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2026,7,30]]},"reference":[{"key":"1791_CR1","doi-asserted-by":"publisher","first-page":"1","DOI":"10.2147\/JMDH.S150940","volume":"11","author":"V D\u2019Aguanno","year":"2018","unstructured":"D\u2019Aguanno\u00a0V, Ralli\u00a0M, De Vincentiis\u00a0M et\u00a0al (2018) Optimal management of Cogan\u2019s syndrome: a multidisciplinary approach. J\u00a0Multidiscip Healthc 11:1\u201311","journal-title":"J Multidiscip Healthc"},{"key":"1791_CR2","doi-asserted-by":"publisher","DOI":"10.1007\/s11882-020-00945-1","volume":"20","author":"GM Espinoza","year":"2020","unstructured":"Espinoza\u00a0GM, Wheeler\u00a0J, Temprano\u00a0KK et\u00a0al (2020) Cogan\u2019s Syndrome: Clinical Presentations and Update on Treatment. Curr Allergy Asthma Rep 20:46","journal-title":"Curr Allergy Asthma Rep"},{"key":"1791_CR3","doi-asserted-by":"publisher","first-page":"275","DOI":"10.1159\/000318870","volume":"72","author":"G Kontorinis","year":"2010","unstructured":"Kontorinis\u00a0G, Giourgas\u00a0A, Neuburger\u00a0J et\u00a0al (2010) Long-term evaluation of Cochlear implantation in Cogan syndrome. ORL J Otorhinolaryngol Relat Spec 72:275\u2013279","journal-title":"ORL J Otorhinolaryngol Relat Spec"}],"container-title":["HNO"],"original-title":[],"language":"de","link":[{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1007\/s00106-026-01791-9.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/link.springer.com\/article\/10.1007\/s00106-026-01791-9","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1007\/s00106-026-01791-9.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,7,30]],"date-time":"2026-07-30T12:12:40Z","timestamp":1785413560000},"score":1,"resource":{"primary":{"URL":"https:\/\/link.springer.com\/10.1007\/s00106-026-01791-9"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2026,7,30]]},"references-count":3,"alternative-id":["1791"],"URL":"https:\/\/doi.org\/10.1007\/s00106-026-01791-9","relation":{},"ISSN":["0017-6192","1433-0458"],"issn-type":[{"value":"0017-6192","type":"print"},{"value":"1433-0458","type":"electronic"}],"subject":[],"published":{"date-parts":[[2026,7,30]]},"assertion":[{"value":"12 April 2026","order":1,"name":"received","label":"Received","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"9 June 2026","order":2,"name":"accepted","label":"Accepted","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"30 July 2026","order":3,"name":"first_online","label":"First Online","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"L.\u00a0Kappert, V.\u00a0Lohnherr, S.\u00a0Euteneuer, U.\u00a0Geiger und M.-S.\u00a0Y\u0131lmaz Top\u00e7uo\u011flu f\u00fchren klinische Studien mit MED-EL und Cochlear durch. L.\u00a0Kappert, S.\u00a0Euteneuer und U.\u00a0Geiger erhielten Kongressunterst\u00fctzung von MED-EL. L.\u00a0Kappert, V.\u00a0Lohnherr, U.\u00a0Geiger und M.-S.\u00a0Y\u0131lmaz Top\u00e7uo\u011flu erhielten finanzielle Unterst\u00fctzung durch die Firmen MED-EL und Cochlear f\u00fcr die Teilnahme an otologischen Fortbildungen. P.J.\u00a0Schuler gibt an, dass kein Interessenkonflikt besteht. Weitere finanzielle oder nichtfinanzielle Interessenkonflikte bestehen nicht. F\u00fcr diese Arbeit gab es keine externe oder interne finanzielle Unterst\u00fctzung.","order":1,"name":"Ethics","label":"Interessenkonflikt","group":{"name":"EthicsHeading","label":"Einhaltung ethischer Richtlinien"}},{"value":"Dieser Beitrag beinhaltet keine Studien an Menschen oder Tieren. Der Ver\u00f6ffentlichung des Fallbeispiels stimmte die Ethikkommission der Universit\u00e4tsklinik Heidelberg zu unter dem Zeichen S\u2011427\/2025. Die Deklaration von Helsinki in ihrer aktuellen Fassung wurde beachtet. Die schriftliche Einwilligung der Patientin zur Ver\u00f6ffentlichung des Falls liegt vor.","order":2,"name":"Ethics","group":{"name":"EthicsHeading","label":"Einhaltung ethischer Richtlinien"}}]}}