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Eine pulmonale Beteiligung ist eine h\u00e4ufige und klinisch bedeutsame Manifestation von CTD, wobei die interstitielle Lungenerkrankung (ILD) einen wesentlichen Beitrag zur Morbidit\u00e4t und Mortalit\u00e4t leistet. Daher ist die fr\u00fchzeitige Erkennung von CTD-ILD von entscheidender Bedeutung, und ein multidisziplin\u00e4rer Ansatz ist sowohl f\u00fcr die Diagnose als auch f\u00fcr das Patientenmanagement von gr\u00f6\u00dfter Wichtigkeit. In diesem Zusammenhang spielt die hochaufl\u00f6sende Computertomographie (HRCT) eine zentrale Rolle\u00a0\u2013 nicht nur bei der Identifizierung charakteristischer ILD-Muster, sondern auch bei der Verlaufskontrolle und der therapeutischen Entscheidungsfindung. Obwohl das h\u00e4ufigste bildgebende Muster bei CTD-ILD die nichtspezifische interstitielle Pneumonie (NSIP) ist, zeigt sich das Spektrum pulmonaler Manifestationen komplex und heterogen. Weitere Muster wie die gew\u00f6hnliche interstitielle Pneumonie (UIP), die organisierende Pneumonie (OP), die lymphozytische interstitielle Pneumonie (LIP) und die diffuse alveol\u00e4re Sch\u00e4digung (DAD) k\u00f6nnen ebenfalls auftreten und zeigen jeweils spezifische Assoziationen mit bestimmten CTD. Dar\u00fcber hinaus sind \u00dcberlappungen und \u00dcberg\u00e4nge zwischen den Mustern nicht selten, was die Diagnosestellung zus\u00e4tzlich erschwert. Diese \u00dcbersichtsarbeit zielt darauf ab, einen umfassenden \u00dcberblick \u00fcber die wichtigsten pulmonalen Manifestationen von CTD, insbesondere der ILD, zu geben\u00a0\u2013 mit Schwerpunkt auf der HRCT-basierten Mustererkennung, um die diagnostische Sicherheit und das Musterverst\u00e4ndnis der Radiologinnen zu verbessern.<\/jats:p>","DOI":"10.1007\/s00117-025-01492-4","type":"journal-article","created":{"date-parts":[[2025,8,22]],"date-time":"2025-08-22T04:46:10Z","timestamp":1755837970000},"page":"734-747","update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":0,"title":["Interstitielle Lungenerkrankungen bei Kollagenosen","Connective tissue disease-associated interstitial lung diseases"],"prefix":"10.1007","volume":"65","author":[{"given":"Rebecca","family":"Mura","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Daria","family":"Kifjak","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Kastriot","family":"Kastrati","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Nino","family":"Bogveradze","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Lucian","family":"Beer","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Helmut","family":"Prosch","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"297","published-online":{"date-parts":[[2025,8,22]]},"reference":[{"issue":"1","key":"1492_CR1","doi-asserted-by":"publisher","first-page":"108","DOI":"10.1186\/s13244-022-01243-2","volume":"13","author":"S Palmucci","year":"2022","unstructured":"Palmucci\u00a0S, Galioto\u00a0F, Fazio\u00a0G, Ferlito\u00a0A, Cancemi\u00a0G, Di Mari\u00a0A, Sambataro\u00a0G, Sambataro\u00a0D, Zanframundo\u00a0G, Mauro\u00a0LA, Foti\u00a0PV, Vancheri\u00a0C, Basile\u00a0A (2022) Clinical and Radiological Features of Lung Disorders Related to Connective-Tissue Diseases: A\u00a0Pictorial Essay. 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