{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,7,15]],"date-time":"2026-07-15T18:56:20Z","timestamp":1784141780563,"version":"3.55.0"},"reference-count":38,"publisher":"Springer Science and Business Media LLC","issue":"6","license":[{"start":{"date-parts":[[2024,7,20]],"date-time":"2024-07-20T00:00:00Z","timestamp":1721433600000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.springernature.com\/gp\/researchers\/text-and-data-mining"},{"start":{"date-parts":[[2024,7,20]],"date-time":"2024-07-20T00:00:00Z","timestamp":1721433600000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/www.springernature.com\/gp\/researchers\/text-and-data-mining"}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["Pediatr Cardiol"],"published-print":{"date-parts":[[2025,8]]},"DOI":"10.1007\/s00246-024-03585-8","type":"journal-article","created":{"date-parts":[[2024,7,20]],"date-time":"2024-07-20T16:08:31Z","timestamp":1721491711000},"page":"1676-1683","update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":2,"title":["Assessing Left Ventricular Pathology in Patients with Ebstein Anomaly Using Cardiovascular Magnetic Resonance: Looking Past the Right Heart"],"prefix":"10.1007","volume":"46","author":[{"given":"Aditi","family":"Gupta","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Luciana","family":"Da Silva","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Li","family":"Wang","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Carlos E.","family":"Diaz-Castrillon","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Craig P.","family":"Dobson","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jose","family":"Da Silva","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Laura J.","family":"Olivieri","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Tarek","family":"Alsaied","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Adam","family":"Christopher","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2024,7,20]]},"reference":[{"issue":"19\u201320","key":"3585_CR1","first-page":"269","volume":"135","author":"CH Attenhofer Jost","year":"2005","unstructured":"Attenhofer Jost CH, Connolly HM, Edwards WD, Hayes D, Warnes CA, Danielson GK (2005) Ebstein\u2019s anomaly\u2014review of a multifaceted congenital cardiac condition. Swiss Med Wkly 135(19\u201320):269\u2013281","journal-title":"Swiss Med Wkly"},{"issue":"10","key":"3585_CR2","doi-asserted-by":"publisher","first-page":"1101","DOI":"10.1586\/14779072.2015.1087849","volume":"13","author":"JA Dearani","year":"2015","unstructured":"Dearani JA, Mora BN, Nelson TJ, Haile DT, O\u2019Leary PW (2015) Ebstein anomaly review: what\u2019s now, what\u2019s next? Expert Rev Cardiovasc Ther 13(10):1101\u20131109","journal-title":"Expert Rev Cardiovasc Ther"},{"issue":"3","key":"3585_CR3","doi-asserted-by":"publisher","first-page":"704","DOI":"10.1016\/j.ijcard.2012.03.062","volume":"167","author":"CM Lee","year":"2013","unstructured":"Lee CM, Sheehan FH, Bouzas B, Chen SS, Gatzoulis MA, Kilner PJ (2013) The shape and function of the right ventricle in Ebstein\u2019s anomaly. Int J Cardiol 167(3):704\u2013710","journal-title":"Int J Cardiol"},{"issue":"1","key":"3585_CR4","doi-asserted-by":"publisher","first-page":"146","DOI":"10.1016\/j.ijcard.2011.08.004","volume":"165","author":"D Tobler","year":"2013","unstructured":"Tobler D, Yalonetsky S, Crean AM, Granton JT, Burchill L, Silversides CK et al (2013) Right heart characteristics and exercise parameters in adults with Ebstein anomaly: new perspectives from cardiac magnetic resonance imaging studies. Int J Cardiol 165(1):146\u2013150","journal-title":"Int J Cardiol"},{"key":"3585_CR5","unstructured":"lv geomety and function in adults wuth ebstein of TV-1987, UCLA.pdf"},{"key":"3585_CR6","doi-asserted-by":"publisher","DOI":"10.1186\/1532-429X-18-S1-P159","author":"D Yang","year":"2016","unstructured":"Yang D, Sun J, Wan K, Luo Y, Liu H, Cheng W et al (2016) LV geometric and substrate remodelling in patient with Ebstein anomaly\u2014a deep insight from MRI T1 mapping fibrosis imaging. J Cardiovasc Magn Reson. https:\/\/doi.org\/10.1186\/1532-429X-18-S1-P159","journal-title":"J Cardiovasc Magn Reson"},{"issue":"3","key":"3585_CR7","doi-asserted-by":"publisher","first-page":"404","DOI":"10.1016\/j.ijcard.2013.12.037","volume":"171","author":"PJ Goleski","year":"2014","unstructured":"Goleski PJ, Sheehan FH, Chen SS, Kilner PJ, Gatzoulis MA (2014) The shape and function of the left ventricle in Ebstein\u2019s anomaly. Int J Cardiol 171(3):404\u2013412","journal-title":"Int J Cardiol"},{"issue":"3","key":"3585_CR8","doi-asserted-by":"publisher","first-page":"361","DOI":"10.4065\/80.3.361","volume":"80","author":"CH Attenhofer Jost","year":"2005","unstructured":"Attenhofer Jost CH, Connolly HM, O\u2019Leary PW, Warnes CA, Tajik AJ, Seward JB (2005) Left heart lesions in patients with Ebstein anomaly. Mayo Clin Proc 80(3):361\u2013368","journal-title":"Mayo Clin Proc"},{"issue":"2","key":"3585_CR9","doi-asserted-by":"publisher","first-page":"353","DOI":"10.1161\/01.CIR.75.2.353","volume":"75","author":"LN Benson","year":"1987","unstructured":"Benson LN, Child JS, Schwaiger M, Perloff JK, Schelbert HR (1987) Left ventricular geometry and function in adults with Ebstein\u2019s anomaly of the tricuspid valve. Circulation 75(2):353\u2013359","journal-title":"Circulation"},{"issue":"12","key":"3585_CR10","doi-asserted-by":"publisher","first-page":"1724","DOI":"10.1016\/j.amjcard.2008.08.018","volume":"102","author":"ML Brown","year":"2008","unstructured":"Brown ML, Dearani JA, Danielson GK, Cetta F, Connolly HM, Warnes CA et al (2008) Effect of operation for Ebstein anomaly on left ventricular function. Am J Cardiol 102(12):1724\u20131727","journal-title":"Am J Cardiol"},{"key":"3585_CR11","doi-asserted-by":"publisher","first-page":"131","DOI":"10.1016\/j.ijcard.2016.01.032","volume":"206","author":"X Li","year":"2016","unstructured":"Li X, Wang SM, Schreiber C, Cheng W, Lin K, Sun JY et al (2016) More than valve repair: effect of cone reconstruction on right ventricular geometry and function in patients with Ebstein anomaly. Int J Cardiol 206:131\u2013137","journal-title":"Int J Cardiol"},{"issue":"2","key":"3585_CR12","doi-asserted-by":"publisher","first-page":"316","DOI":"10.1093\/ejcts\/ezu472","volume":"48","author":"R Lange","year":"2015","unstructured":"Lange R, Burri M, Eschenbach LK, Badiu CC, da Silva JP, Nagdyman N et al (2015) Da Silva\u2019s cone repair for Ebstein\u2019s anomaly: effect on right ventricular size and function. Eur J Cardiothorac Surg 48(2):316\u2013320","journal-title":"Eur J Cardiothorac Surg"},{"issue":"6","key":"3585_CR13","doi-asserted-by":"publisher","first-page":"460","DOI":"10.1016\/j.jacc.2008.03.064","volume":"52","author":"ML Brown","year":"2008","unstructured":"Brown ML, Dearani JA, Danielson GK, Cetta F, Connolly HM, Warnes CA et al (2008) Functional status after operation for Ebstein anomaly: the Mayo Clinic experience. J Am Coll Cardiol 52(6):460\u2013466","journal-title":"J Am Coll Cardiol"},{"issue":"3","key":"3585_CR14","doi-asserted-by":"publisher","first-page":"1097","DOI":"10.1016\/j.jtcvs.2020.10.124","volume":"161","author":"RML Neijenhuis","year":"2021","unstructured":"Neijenhuis RML, Tsang VT, Marek J, Issitt R, Bonello B, Von Klemperer K et al (2021) Cone reconstruction for Ebstein anomaly: late biventricular function and possible remodeling. J Thorac Cardiovasc Surg 161(3):1097\u20131108","journal-title":"J Thorac Cardiovasc Surg"},{"issue":"1","key":"3585_CR15","doi-asserted-by":"publisher","first-page":"32","DOI":"10.1186\/s12968-018-0452-0","volume":"20","author":"RS Beroukhim","year":"2018","unstructured":"Beroukhim RS, Jing L, Harrild DM, Fornwalt BK, Mejia-Spiegeler A, Rhodes J et al (2018) Impact of the cone operation on left ventricular size, function, and dyssynchrony in Ebstein anomaly: a cardiovascular magnetic resonance study. J Cardiovasc Magn Reson 20(1):32","journal-title":"J Cardiovasc Magn Reson"},{"issue":"1","key":"3585_CR16","doi-asserted-by":"publisher","first-page":"51","DOI":"10.1186\/1532-429X-15-51","volume":"15","author":"S Fratz","year":"2013","unstructured":"Fratz S, Chung T, Greil GF, Samyn MM, Taylor AM, Valsangiacomo Buechel ER et al (2013) Guidelines and protocols for cardiovascular magnetic resonance in children and adults with congenital heart disease: SCMR expert consensus group on congenital heart disease. J Cardiovasc Magn Reson 15(1):51","journal-title":"J Cardiovasc Magn Reson"},{"issue":"1","key":"3585_CR17","doi-asserted-by":"publisher","first-page":"154","DOI":"10.1016\/0735-1097(88)90182-9","volume":"11","author":"MP Leung","year":"1988","unstructured":"Leung MP, Baker EJ, Anderson RH, Zuberbuhler JR (1988) Cineangiographic spectrum of Ebstein\u2019s malformation: its relevance to clinical presentation and outcome. J Am Coll Cardiol 11(1):154\u2013161","journal-title":"J Am Coll Cardiol"},{"key":"3585_CR18","doi-asserted-by":"publisher","DOI":"10.1016\/j.ijcchd.2022.100342","author":"T Alsaied","year":"2022","unstructured":"Alsaied T, Castrillon CD, Christopher A, Da Silva J, Morell VO, Lanford L et al (2022) Cardiac MRI predictors of right ventricular dysfunction after the Da Silva cone operation for Ebstein\u2019s anomaly. Int J Cardiol Cong Heart Dis. https:\/\/doi.org\/10.1016\/j.ijcchd.2022.100342","journal-title":"Int J Cardiol Cong Heart Dis"},{"issue":"1","key":"3585_CR19","doi-asserted-by":"publisher","first-page":"101","DOI":"10.1016\/j.jacc.2005.03.045","volume":"46","author":"SE Petersen","year":"2005","unstructured":"Petersen SE, Selvanayagam JB, Wiesmann F, Robson MD, Francis JM, Anderson RH et al (2005) Left ventricular non-compaction: insights from cardiovascular magnetic resonance imaging. J Am Coll Cardiol 46(1):101\u2013105","journal-title":"J Am Coll Cardiol"},{"issue":"12","key":"3585_CR20","doi-asserted-by":"publisher","first-page":"2699","DOI":"10.1007\/s00330-012-2554-7","volume":"22","author":"M Grothoff","year":"2012","unstructured":"Grothoff M, Pachowsky M, Hoffmann J, Posch M, Klaassen S, Lehmkuhl L et al (2012) Value of cardiovascular MR in diagnosing left ventricular non-compaction cardiomyopathy and in discriminating between other cardiomyopathies. Eur Radiol 22(12):2699\u20132709","journal-title":"Eur Radiol"},{"issue":"2","key":"3585_CR21","doi-asserted-by":"publisher","first-page":"139","DOI":"10.1161\/CIRCIMAGING.110.960229","volume":"4","author":"DK Dawson","year":"2011","unstructured":"Dawson DK, Maceira AM, Raj VJ, Graham C, Pennell DJ, Kilner PJ (2011) Regional thicknesses and thickening of compacted and trabeculated myocardial layers of the normal left ventricle studied by cardiovascular magnetic resonance. Circ Cardiovasc Imaging 4(2):139\u2013146","journal-title":"Circ Cardiovasc Imaging"},{"issue":"1","key":"3585_CR22","doi-asserted-by":"publisher","first-page":"258","DOI":"10.1016\/j.ijcard.2011.12.081","volume":"167","author":"S Fratz","year":"2013","unstructured":"Fratz S, Janello C, Muller D, Seligmann M, Meierhofer C, Schuster T et al (2013) The functional right ventricle and tricuspid regurgitation in Ebstein\u2019s anomaly. Int J Cardiol 167(1):258\u2013261","journal-title":"Int J Cardiol"},{"issue":"8","key":"3585_CR23","doi-asserted-by":"publisher","first-page":"1051","DOI":"10.1016\/S0002-9149(97)00602-4","volume":"80","author":"L Daliento","year":"1997","unstructured":"Daliento L, Angelini A, Ho SY, Frescura C, Turrini P, Baratella MC et al (1997) Angiographic and morphologic features of the left ventricle in Ebstein\u2019s malformation. Am J Cardiol 80(8):1051\u20131059","journal-title":"Am J Cardiol"},{"issue":"9","key":"3585_CR24","doi-asserted-by":"publisher","first-page":"716","DOI":"10.1016\/0002-9149(94)90945-8","volume":"73","author":"RA Hurwitz","year":"1994","unstructured":"Hurwitz RA (1994) Left ventricular function in infants and children with symptomatic Ebstein\u2019s anomaly. Am J Cardiol 73(9):716\u2013718","journal-title":"Am J Cardiol"},{"issue":"4","key":"3585_CR25","doi-asserted-by":"publisher","first-page":"525","DOI":"10.1016\/S1010-7940(02)00836-9","volume":"23","author":"S Chauvaud","year":"2003","unstructured":"Chauvaud S, Berrebi A, D\u2019Attellis N, Mousseaux E, Hernigou A, Carpentier A (2003) Ebstein\u2019s anomaly: repair based on functional analysis. Eur J Cardiothorac Surg 23(4):525\u2013531","journal-title":"Eur J Cardiothorac Surg"},{"issue":"4","key":"3585_CR26","doi-asserted-by":"publisher","first-page":"819","DOI":"10.1161\/01.CIR.92.4.819","volume":"92","author":"EK Louie","year":"1995","unstructured":"Louie EK, Lin SS, Reynertson SI, Brundage BH, Levitsky S, Rich S (1995) Pressure and volume loading of the right ventricle have opposite effects on left ventricular ejection fraction. Circulation 92(4):819\u2013824","journal-title":"Circulation"},{"issue":"6","key":"3585_CR27","doi-asserted-by":"publisher","first-page":"1315","DOI":"10.1161\/01.CIR.63.6.1315","volume":"63","author":"RO Bonow","year":"1981","unstructured":"Bonow RO, Borer JS, Rosing DR, Bacharach SL, Green MV, Kent KM (1981) Left ventricular functional reserve in adult patients with atrial septal defect: pre- and postoperative studies. Circulation 63(6):1315\u20131322","journal-title":"Circulation"},{"issue":"3","key":"3585_CR28","doi-asserted-by":"publisher","first-page":"403","DOI":"10.1161\/01.CIR.44.3.403","volume":"44","author":"DT Kelly","year":"1971","unstructured":"Kelly DT, Spotnitz HM, Beiser GD, Pierce JE, Epstein SE (1971) Effects of chronic right ventricular volume and pressure loading on left ventricular performance. Circulation 44(3):403\u2013412","journal-title":"Circulation"},{"issue":"4","key":"3585_CR29","first-page":"115","volume":"9","author":"SK Thareja","year":"2022","unstructured":"Thareja SK, Frommelt MA, Lincoln J, Lough JW, Mitchell ME, Tomita-Mitchell A (2022) A systematic review of Ebstein\u2019s anomaly with left ventricular noncompaction. J Cardiovasc Dev Dis 9(4):115","journal-title":"J Cardiovasc Dev Dis"},{"issue":"3","key":"3585_CR30","doi-asserted-by":"publisher","first-page":"178","DOI":"10.1002\/ajmg.c.31365","volume":"163C","author":"AM Vermeer","year":"2013","unstructured":"Vermeer AM, van Engelen K, Postma AV, Baars MJ, Christiaans I, De Haij S et al (2013) Ebstein anomaly associated with left ventricular noncompaction: an autosomal dominant condition that can be caused by mutations in MYH7. Am J Med Genet C Semin Med Genet 163C(3):178\u2013184","journal-title":"Am J Med Genet C Semin Med Genet"},{"issue":"22","key":"3585_CR31","doi-asserted-by":"publisher","first-page":"2893","DOI":"10.1161\/CIRCULATIONAHA.107.746164","volume":"117","author":"S Klaassen","year":"2008","unstructured":"Klaassen S, Probst S, Oechslin E, Gerull B, Krings G, Schuler P et al (2008) Mutations in sarcomere protein genes in left ventricular noncompaction. Circulation 117(22):2893\u20132901","journal-title":"Circulation"},{"issue":"3","key":"3585_CR32","doi-asserted-by":"publisher","first-page":"113","DOI":"10.1007\/s12471-011-0141-1","volume":"21","author":"K van Engelen","year":"2013","unstructured":"van Engelen K, Postma AV, van de Meerakker JB, Roos-Hesselink JW, van den Helderman ATE, Vliegen HW et al (2013) Ebstein\u2019s anomaly may be caused by mutations in the sarcomere protein gene MYH7. Neth Heart J 21(3):113\u2013117","journal-title":"Neth Heart J"},{"issue":"2","key":"3585_CR33","doi-asserted-by":"publisher","first-page":"207","DOI":"10.1016\/j.jcmg.2013.05.021","volume":"7","author":"RH Pignatelli","year":"2014","unstructured":"Pignatelli RH, Texter KM, Denfield SW, Grenier MA, Altman CA, Ayres NA et al (2014) LV noncompaction in Ebstein\u2019s anomaly in infants and outcomes. JACC Cardiovasc Imaging 7(2):207\u2013209","journal-title":"JACC Cardiovasc Imaging"},{"issue":"5","key":"3585_CR34","doi-asserted-by":"publisher","first-page":"484","DOI":"10.1016\/j.jjcc.2017.11.012","volume":"71","author":"M Kumor","year":"2018","unstructured":"Kumor M, Lipczynska M, Biernacka EK, Klisiewicz A, Wojcik A, Konka M et al (2018) Cardiac arrest and ventricular arrhythmia in adults with Ebstein anomaly and left ventricular non-compaction. J Cardiol 71(5):484\u2013487","journal-title":"J Cardiol"},{"key":"3585_CR35","doi-asserted-by":"publisher","DOI":"10.1186\/1532-429X-18-S1-O31","author":"D Yang","year":"2016","unstructured":"Yang D, Sun J, Luo Y, Liu H, Wan K, Zhang T et al (2016) Feature tracking (FT) and extracelluar volume (ECV) by cardiac magnetic resonance segmentally analyze change of LV in Ebstein: a novel perspective in myocardial remodeling. J Cardiovasc Magn Reson. https:\/\/doi.org\/10.1186\/1532-429X-18-S1-O31","journal-title":"J Cardiovasc Magn Reson"},{"issue":"15","key":"3585_CR36","doi-asserted-by":"publisher","first-page":"1196","DOI":"10.1093\/eurheartj\/ehv529","volume":"37","author":"OA Smiseth","year":"2016","unstructured":"Smiseth OA, Torp H, Opdahl A, Haugaa KH, Urheim S (2016) Myocardial strain imaging: how useful is it in clinical decision making? Eur Heart J 37(15):1196\u20131207","journal-title":"Eur Heart J"},{"issue":"4","key":"3585_CR37","doi-asserted-by":"publisher","first-page":"425","DOI":"10.1161\/CIRCIMAGING.110.958751","volume":"4","author":"AH Aletras","year":"2011","unstructured":"Aletras AH, Tilak GS, Hsu LY, Arai AE (2011) Heterogeneity of intramural function in hypertrophic cardiomyopathy: mechanistic insights from MRI late gadolinium enhancement and high-resolution displacement encoding with stimulated echoes strain maps. Circ Cardiovasc Imaging 4(4):425\u2013434","journal-title":"Circ Cardiovasc Imaging"},{"issue":"9","key":"3585_CR38","doi-asserted-by":"publisher","first-page":"1601","DOI":"10.1016\/j.ejrad.2016.06.012","volume":"85","author":"X Liu","year":"2016","unstructured":"Liu X, Zhang Q, Yang ZG, Guo YK, Shi K, Xu HY et al (2016) Morphologic and functional abnormalities in patients with Ebstein\u2019s anomaly with cardiac magnetic resonance imaging: correlation with tricuspid regurgitation. Eur J Radiol 85(9):1601\u20131606","journal-title":"Eur J Radiol"}],"container-title":["Pediatric Cardiology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1007\/s00246-024-03585-8.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/link.springer.com\/article\/10.1007\/s00246-024-03585-8\/fulltext.html","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1007\/s00246-024-03585-8.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2025,9,5]],"date-time":"2025-09-05T20:58:57Z","timestamp":1757105937000},"score":1,"resource":{"primary":{"URL":"https:\/\/link.springer.com\/10.1007\/s00246-024-03585-8"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2024,7,20]]},"references-count":38,"journal-issue":{"issue":"6","published-print":{"date-parts":[[2025,8]]}},"alternative-id":["3585"],"URL":"https:\/\/doi.org\/10.1007\/s00246-024-03585-8","relation":{"has-preprint":[{"id-type":"doi","id":"10.21203\/rs.3.rs-4219470\/v1","asserted-by":"object"}]},"ISSN":["0172-0643","1432-1971"],"issn-type":[{"value":"0172-0643","type":"print"},{"value":"1432-1971","type":"electronic"}],"subject":[],"published":{"date-parts":[[2024,7,20]]},"assertion":[{"value":"4 April 2024","order":1,"name":"received","label":"Received","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"8 July 2024","order":2,"name":"accepted","label":"Accepted","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"20 July 2024","order":3,"name":"first_online","label":"First Online","group":{"name":"ArticleHistory","label":"Article History"}},{"order":1,"name":"Ethics","group":{"name":"EthicsHeading","label":"Declarations"}},{"value":"The authors declare that they have no competing interests.","order":2,"name":"Ethics","group":{"name":"EthicsHeading","label":"Competing Interests"}}]}}