{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,17]],"date-time":"2026-09-17T01:21:18Z","timestamp":1789608078603,"version":"build-2803163510"},"reference-count":25,"publisher":"Springer Science and Business Media LLC","issue":"4","license":[{"start":{"date-parts":[[2020,9,18]],"date-time":"2020-09-18T00:00:00Z","timestamp":1600387200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.springer.com\/tdm"},{"start":{"date-parts":[[2020,9,18]],"date-time":"2020-09-18T00:00:00Z","timestamp":1600387200000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/www.springer.com\/tdm"}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["Skeletal Radiol"],"published-print":{"date-parts":[[2021,4]]},"DOI":"10.1007\/s00256-020-03610-w","type":"journal-article","created":{"date-parts":[[2020,9,17]],"date-time":"2020-09-17T23:09:29Z","timestamp":1600384169000},"page":"821-825","update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":7,"title":["Fibroma-like perivascular epithelioid cell tumor: a rare case in a long bone"],"prefix":"10.1007","volume":"50","author":[{"given":"Sara","family":"Ramezanpour","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Andrew E.","family":"Horvai","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Melissa","family":"Zimel","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Matthew","family":"Bucknor","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Thomas M.","family":"Link","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2020,9,18]]},"reference":[{"issue":"5","key":"3610_CR1","doi-asserted-by":"publisher","first-page":"359","DOI":"10.1016\/j.anndiagpath.2015.06.003","volume":"19","author":"K Thway","year":"2015","unstructured":"Thway K, Fisher C. PEComa: morphology and genetics of a complex tumor family. Ann Diagn Pathol. 2015;19(5):359\u201368.","journal-title":"Ann Diagn Pathol"},{"issue":"12","key":"3610_CR2","doi-asserted-by":"publisher","first-page":"1558","DOI":"10.1097\/01.pas.0000173232.22117.37","volume":"29","author":"AL Folpe","year":"2005","unstructured":"Folpe AL, Mentzel T, Lehr HA, Fisher C, Balzer BL, Weiss SW. Perivascular epithelioid cell neoplasms of soft tissue and gynecologic origin: a clinicopathologic study of 26 cases and review of the literature. Am J Surg Pathol. 2005;29(12):1558\u201375.","journal-title":"Am J Surg Pathol"},{"issue":"2","key":"3610_CR3","doi-asserted-by":"publisher","first-page":"304","DOI":"10.1097\/PAS.0b013e3181854929","volume":"33","author":"WR Sukov","year":"2009","unstructured":"Sukov WR, Cheville JC, Amin MB, Gupta R, Folpe AL. Perivascular epithelioid cell tumor (PEComa) of the urinary bladder: report of 3 cases and review of the literature. Am J Surg Pathol. 2009;33(2):304\u20138.","journal-title":"Am J Surg Pathol"},{"issue":"12","key":"3610_CR4","doi-asserted-by":"publisher","first-page":"1769","DOI":"10.1097\/PAS.0b013e31829caab3","volume":"37","author":"LA Doyle","year":"2013","unstructured":"Doyle LA, Hornick JL, Fletcher CD. PEComa of the gastrointestinal tract: clinicopathologic study of 35 cases with evaluation of prognostic parameters. Am J Surg Pathol. 2013;37(12):1769\u201382.","journal-title":"Am J Surg Pathol"},{"issue":"11","key":"3610_CR5","doi-asserted-by":"publisher","first-page":"1622","DOI":"10.1097\/PAS.0b013e3181f5974f","volume":"34","author":"K Yamashita","year":"2010","unstructured":"Yamashita K, Fletcher CD. PEComa presenting in bone: clinicopathologic analysis of 6 cases and literature review. Am J Surg Pathol. 2010;34(11):1622\u20139.","journal-title":"Am J Surg Pathol"},{"issue":"4","key":"3610_CR6","doi-asserted-by":"publisher","first-page":"608","DOI":"10.1097\/PAS.0b013e31815604ab","volume":"32","author":"B Liegl","year":"2008","unstructured":"Liegl B, Hornick JL, Fletcher CD. Primary cutaneous PEComa: distinctive clear cell lesions of skin. Am J Surg Pathol. 2008;32(4):608\u201314.","journal-title":"Am J Surg Pathol"},{"issue":"11","key":"3610_CR7","doi-asserted-by":"publisher","first-page":"1469","DOI":"10.1007\/s00256-012-1479-1","volume":"41","author":"NM Desy","year":"2012","unstructured":"Desy NM, Bernstein M, Nahal A, Aziz M, Kenan S, Turcotte RE, et al. Primary perivascular epithelioid cell neoplasm (PEComa) of bone: report of two cases and review of the literature. Skelet Radiol. 2012;41(11):1469\u201374.","journal-title":"Skelet Radiol"},{"issue":"10","key":"3610_CR8","doi-asserted-by":"publisher","first-page":"1127","DOI":"10.1136\/jcp.2008.060137","volume":"61","author":"DW Lian","year":"2008","unstructured":"Lian DW, Chuah KL, Cheng MH, Yap WM. Malignant perivascular epithelioid cell tumour of the fibula: a report and a short review of bone perivascular epithelioid cell tumour. J Clin Pathol. 2008;61(10):1127\u20139.","journal-title":"J Clin Pathol"},{"issue":"1","key":"3610_CR9","doi-asserted-by":"publisher","first-page":"1","DOI":"10.1016\/j.humpath.2009.05.011","volume":"41","author":"AL Folpe","year":"2010","unstructured":"Folpe AL, Kwiatkowski DJ. Perivascular epithelioid cell neoplasms: pathology and pathogenesis. Hum Pathol. 2010;41(1):1\u201315.","journal-title":"Hum Pathol"},{"issue":"13","key":"3610_CR10","doi-asserted-by":"publisher","first-page":"1345","DOI":"10.1056\/NEJMra055323","volume":"355","author":"PB Crino","year":"2006","unstructured":"Crino PB, Nathanson KL, Henske EP. The tuberous sclerosis complex. N Engl J Med. 2006;355(13):1345\u201356.","journal-title":"N Engl J Med"},{"key":"3610_CR11","doi-asserted-by":"publisher","first-page":"16035","DOI":"10.1038\/nrdp.2016.35","volume":"2","author":"EP Henske","year":"2016","unstructured":"Henske EP, Jozwiak S, Kingswood JC, Sampson JR, Thiele EA. Tuberous sclerosis complex. Nat Rev Dis Primers. 2016;2:16035.","journal-title":"Nat Rev Dis Primers"},{"issue":"3","key":"3610_CR12","doi-asserted-by":"publisher","first-page":"387","DOI":"10.1002\/path.2289","volume":"214","author":"CC Pan","year":"2008","unstructured":"Pan CC, Chung MY, Ng KF, Liu CY, Wang JS, Chai CY, et al. Constant allelic alteration on chromosome 16p (TSC2 gene) in perivascular epithelioid cell tumour (PEComa): genetic evidence for the relationship of PEComa with angiomyolipoma. J Pathol. 2008;214(3):387\u201393.","journal-title":"J Pathol"},{"issue":"10","key":"3610_CR13","doi-asserted-by":"publisher","first-page":"1395","DOI":"10.1097\/PAS.0b013e3181f17ac0","volume":"34","author":"P Argani","year":"2010","unstructured":"Argani P, Aulmann S, Illei PB, Netto GJ, Ro J, Cho HY, et al. A distinctive subset of PEComas harbors TFE3 gene fusions. Am J Surg Pathol. 2010;34(10):1395\u2013406.","journal-title":"Am J Surg Pathol"},{"key":"3610_CR14","doi-asserted-by":"crossref","unstructured":"Odono EIG, Tan KB, Tay SY, Lee VKM. Cutaneous \u2018fibroma-like\u2019 perivascular epithelioid cell tumor: a case report and review of literature. J Cutan Pathol. 2020.","DOI":"10.1111\/cup.13647"},{"issue":"4","key":"3610_CR15","doi-asserted-by":"publisher","first-page":"500","DOI":"10.1097\/PAS.0000000000001024","volume":"42","author":"AB Larque","year":"2018","unstructured":"Larque AB, Kradin RL, Chebib I, Nielsen GP, Selig MK, Thiele EA, et al. Fibroma-like PEComa: a tuberous sclerosis complex-related lesion. Am J Surg Pathol. 2018;42(4):500\u20135.","journal-title":"Am J Surg Pathol"},{"issue":"6","key":"3610_CR16","doi-asserted-by":"publisher","first-page":"965","DOI":"10.1007\/s00256-018-3065-7","volume":"48","author":"JP Harvey","year":"2019","unstructured":"Harvey JP, Suster DI, Raskin KA, Nielsen GP, Bredella MA. Intra-articular fibroma-like perivascular epithelioid tumor (PEComa) mimicking tenosynovial giant cell tumor, diffuse type. Skelet Radiol. 2019;48(6):965\u20139.","journal-title":"Skelet Radiol"},{"issue":"4","key":"3610_CR17","doi-asserted-by":"publisher","first-page":"493","DOI":"10.1097\/PAS.0b013e318161dc34","volume":"32","author":"JL Hornick","year":"2008","unstructured":"Hornick JL, Fletcher CD. Sclerosing PEComa: clinicopathologic analysis of a distinctive variant with a predilection for the retroperitoneum. Am J Surg Pathol. 2008;32(4):493\u2013501.","journal-title":"Am J Surg Pathol"},{"issue":"3","key":"3610_CR18","doi-asserted-by":"publisher","first-page":"286","DOI":"10.1046\/j.1365-2559.2002.01356.x","volume":"40","author":"L Insabato","year":"2002","unstructured":"Insabato L, De Rosa G, Terracciano LM, Fazioli F, Di Santo F, Rosai J. Primary monotypic epithelioid angiomyolipoma of bone. Histopathology. 2002;40(3):286\u201390.","journal-title":"Histopathology."},{"issue":"6","key":"3610_CR19","doi-asserted-by":"publisher","first-page":"697","DOI":"10.1007\/s00428-008-0612-y","volume":"452","author":"I Torii","year":"2008","unstructured":"Torii I, Kondo N, Takuwa T, Matsumoto S, Okumura Y, Sato A, et al. Perivascular epithelioid cell tumor of the rib. Virchows Arch. 2008;452(6):697\u2013702.","journal-title":"Virchows Arch"},{"key":"3610_CR20","doi-asserted-by":"publisher","first-page":"16","DOI":"10.1177\/1066896907309733","volume":"16","author":"A Righi","year":"2008","unstructured":"Righi A, Dimosthenous K, Rosai J. PEComa: another member of the MiT tumor family? Int J Surg Pathol. 2008;16:16\u201320.","journal-title":"Int J Surg Pathol"},{"issue":"11","key":"3610_CR21","doi-asserted-by":"publisher","first-page":"1465","DOI":"10.1007\/s00256-012-1411-8","volume":"41","author":"D Kazzaz","year":"2012","unstructured":"Kazzaz D, Khalifa M, Alorjan M, Shaw M, Rezajooi K, Saifuddin A. Malignant PEComa of the lumbar vertebra: a rare bone tumour. Skelet Radiol. 2012;41(11):1465\u20138.","journal-title":"Skelet Radiol"},{"key":"3610_CR22","doi-asserted-by":"publisher","first-page":"54","DOI":"10.1186\/s13000-015-0292-2","volume":"10","author":"IW Lao","year":"2015","unstructured":"Lao IW, Yu L, Wang J. Malignant perivascular epithelioid cell tumor (PEComa) of the femur: a case report and literature review. Diagn Pathol. 2015;10:54.","journal-title":"Diagn Pathol"},{"key":"3610_CR23","unstructured":"Yu H, Zhu X, Sheng H, Gao H, Xiao W, Wang C. Primary perivascular epithelioid cell neoplasm of thigh bone: a case report and literature review. 2016;9:2487\u201391."},{"issue":"3","key":"3610_CR24","first-page":"2946","volume":"15","author":"S Sadigh","year":"2018","unstructured":"Sadigh S, Shah P, Weber K, Sebro R, Zhang PJ. Primary malignant perivascular epithelioid cell neoplasm (PEComa) of the bone mimicking granular cell tumor in core biopsy: a case report and literature review. Oncol Lett. 2018;15(3):2946\u201352.","journal-title":"Oncol Lett"},{"issue":"5","key":"3610_CR25","doi-asserted-by":"publisher","first-page":"257","DOI":"10.5732\/cjc.011.10402","volume":"31","author":"J Yang","year":"2012","unstructured":"Yang J, Tian W, Zhu X, Wang J. Chondroblastoma in the long bone diaphysis: a report of two cases with literature review. Chin J Cancer. 2012;31(5):257\u201364.","journal-title":"Chin J Cancer"}],"container-title":["Skeletal Radiology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1007\/s00256-020-03610-w.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/link.springer.com\/article\/10.1007\/s00256-020-03610-w\/fulltext.html","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1007\/s00256-020-03610-w.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2021,9,18]],"date-time":"2021-09-18T00:07:47Z","timestamp":1631923667000},"score":1,"resource":{"primary":{"URL":"https:\/\/link.springer.com\/10.1007\/s00256-020-03610-w"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2020,9,18]]},"references-count":25,"journal-issue":{"issue":"4","published-print":{"date-parts":[[2021,4]]}},"alternative-id":["3610"],"URL":"https:\/\/doi.org\/10.1007\/s00256-020-03610-w","relation":{},"ISSN":["0364-2348","1432-2161"],"issn-type":[{"value":"0364-2348","type":"print"},{"value":"1432-2161","type":"electronic"}],"subject":[],"published":{"date-parts":[[2020,9,18]]},"assertion":[{"value":"21 July 2020","order":1,"name":"received","label":"Received","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"2 September 2020","order":2,"name":"revised","label":"Revised","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"10 September 2020","order":3,"name":"accepted","label":"Accepted","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"18 September 2020","order":4,"name":"first_online","label":"First Online","group":{"name":"ArticleHistory","label":"Article History"}},{"order":1,"name":"Ethics","group":{"name":"EthicsHeading","label":"Compliance with ethical standards"}},{"value":"The authors declare that they have no conflicts of interest.","order":2,"name":"Ethics","group":{"name":"EthicsHeading","label":"Conflict of interest"}},{"value":"Informed consent was obtained from the mother of the patient due to mild cognitive delay of the patient.","order":3,"name":"Ethics","group":{"name":"EthicsHeading","label":"Consent"}}]}}