{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,31]],"date-time":"2026-10-31T01:44:40Z","timestamp":1793411080656,"version":"4.5.0"},"reference-count":9,"publisher":"Springer Science and Business Media LLC","issue":"5","license":[{"start":{"date-parts":[[2024,8,2]],"date-time":"2024-08-02T00:00:00Z","timestamp":1722556800000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0"},{"start":{"date-parts":[[2024,8,2]],"date-time":"2024-08-02T00:00:00Z","timestamp":1722556800000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0"}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["Skeletal Radiol"],"published-print":{"date-parts":[[2025,5]]},"abstract":"<jats:title>Abstract<\/jats:title>\n          <jats:p>Pseudoendocrine sarcoma is a rare, recently described intermediate grade sarcoma of uncertain phenotype\u00a0that most commonly affects the\u00a0paraspinal location in older patients with a distinctive endocrine\/paraganglioma-like morphology and unique <jats:italic>CTNNB1<\/jats:italic> point mutation. While these tumors appear as epithelial or even benign endocrine tumors, these lack markers for such and are highlighted by nuclear expression of beta-catenin. This case is the first among the previously reported only twenty-five cases of this entity,\u00a0including one original series and a few case reports, to correlate the radiologic imaging with the pathologic features. Furthermore, this case illustrates the oldest-to-date patient with this unique location as a palpable painful chest wall\/paraspinal location, with new morphologic observations and, finally, this is\u00a0only the second case to have\u00a0this\u00a0specific <jats:italic>CTNNB1<\/jats:italic> hotspot point mutation for this rare entity.<\/jats:p>","DOI":"10.1007\/s00256-024-04753-w","type":"journal-article","created":{"date-parts":[[2024,8,2]],"date-time":"2024-08-02T05:02:21Z","timestamp":1722574941000},"page":"1153-1158","update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":3,"title":["Pseudoendocrine sarcoma: a rare new entity with unique radiologic and pathologic\/molecular characteristics"],"prefix":"10.1007","volume":"54","author":[{"given":"Zachary","family":"Corey","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-5404-096X","authenticated-orcid":false,"given":"Julie C.","family":"Fanburg-Smith","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Cristy N.","family":"French","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Eric A.","family":"Walker","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Harry N.","family":"Kamerow","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Eric L.","family":"Cochran","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jessica D.","family":"Smith","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Donald J.","family":"Flemming","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mark D.","family":"Murphey","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2024,8,2]]},"reference":[{"issue":"1","key":"4753_CR1","doi-asserted-by":"publisher","first-page":"33","DOI":"10.1097\/PAS.0000000000001751","volume":"46","author":"DJ Papke Jr","year":"2022","unstructured":"Papke DJ Jr, Dickson BC, Sholl L, Fletcher CDM. Pseudoendocrine sarcoma: clinicopathologic analysis of 23 cases of a distinctive soft tissue neoplasm with metastatic potential, recurrent CTNNB1 mutations, and a predilection for truncal locations. Am J Surg Pathol. 2022;46(1):33\u201343. https:\/\/doi.org\/10.1097\/PAS.0000000000001751.","journal-title":"Am J Surg Pathol"},{"issue":"1","key":"4753_CR2","doi-asserted-by":"publisher","first-page":"54","DOI":"10.1111\/his.14460","volume":"80","author":"AL Folpe","year":"2022","unstructured":"Folpe AL. \u2018I Can\u2019t Keep Up!\u2019: an update on advances in soft tissue pathology occurring after the publication of the 2020 World Health Organization classification of soft tissue and bone tumours. 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