{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,28]],"date-time":"2026-08-28T20:10:16Z","timestamp":1787947816876,"version":"build-2784847793"},"reference-count":38,"publisher":"Springer Science and Business Media LLC","issue":"1","license":[{"start":{"date-parts":[[2019,9,14]],"date-time":"2019-09-14T00:00:00Z","timestamp":1568419200000},"content-version":"tdm","delay-in-days":0,"URL":"http:\/\/www.springer.com\/tdm"},{"start":{"date-parts":[[2019,9,14]],"date-time":"2019-09-14T00:00:00Z","timestamp":1568419200000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/www.springer.com\/tdm"}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["Rheumatol Int"],"published-print":{"date-parts":[[2020,1]]},"DOI":"10.1007\/s00296-019-04443-0","type":"journal-article","created":{"date-parts":[[2019,9,14]],"date-time":"2019-09-14T07:02:46Z","timestamp":1568444566000},"page":"29-40","update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":30,"title":["Familial mediterranean fever: assessment of clinical manifestations, pregnancy, genetic mutational analyses, and disease severity in a national cohort"],"prefix":"10.1007","volume":"40","author":[{"given":"Hatice","family":"Bodur","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-8630-9233","authenticated-orcid":false,"given":"Fatma G\u00fcl","family":"Yurdakul","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Hasan Fatih","family":"\u00c7ay","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"\u00dclk\u00fc","family":"U\u00e7ar","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ya\u015far","family":"Keskin","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Bet\u00fcl","family":"Sarg\u0131n","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"G\u00fclcan","family":"G\u00fcrer","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ozan Volkan","family":"Yurdakul","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mustafa","family":"\u00c7al\u0131\u015f","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"H\u00fclya","family":"Deveci","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Y\u0131ld\u0131ray","family":"Ayd\u0131n","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Sami","family":"Hizmetli","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Remzi","family":"\u00c7evik","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ali Yavuz","family":"Karahan","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"\u0130smihan","family":"Sunar","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mehmet Tuncay","family":"Duru\u00f6z","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Hilal","family":"Ecesoy","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Zafer","family":"G\u00fcnendi","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Murat","family":"Toprak","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Nesrin","family":"\u015een","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Duygu","family":"Alt\u0131nta\u015f","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ahmet K\u0131van\u00e7","family":"Cengiz","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"G\u00f6khan","family":"\u00c7a\u011flayan","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ali Nail","family":"Demir","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"H\u00fcseyin","family":"Kaplan","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Serta\u00e7","family":"Ketenci","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Meltem Alkan","family":"Meliko\u011flu","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mehmet","family":"Nayimo\u011flu","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Kemal","family":"Nas","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ay\u015fe Banu","family":"Sar\u0131fak\u0131o\u011flu","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"\u0130lhan","family":"Sezer","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2019,9,14]]},"reference":[{"key":"4443_CR1","doi-asserted-by":"publisher","first-page":"667","DOI":"10.1007\/s12041-016-0682-6","volume":"95","author":"M Beheshtian","year":"2016","unstructured":"Beheshtian M, Izadi N, Kriegshauser G, Kahrizi K, Mehr EP, Rostami M, Hosseini M, Azad M, Montajabiniat M, Kariminejad A, Nemeth S, Oberkanins C, Najmabadi H (2016) Prevalence of common MEFV mutations and carrier frequencies in a large cohort of Iranian populations. J Genet 95:667\u2013674","journal-title":"J Genet"},{"key":"4443_CR2","doi-asserted-by":"publisher","first-page":"254","DOI":"10.1016\/j.berh.2018.09.003","volume":"32","author":"S \u00d6zen","year":"2018","unstructured":"\u00d6zen S (2018) Update\u00a0on the epidemiology and disease outcome of Familial Mediterranean fever. Best Pract Res Clin Rheumatol 32:254\u2013260. \nhttps:\/\/doi.org\/10.1016\/j.berh.2018.09.003","journal-title":"Best Pract Res Clin Rheumatol"},{"key":"4443_CR3","first-page":"1","volume":"10","author":"SA Ar\u0131c\u0131","year":"2017","unstructured":"Ar\u0131c\u0131 SA, Bilginer Y, \u00d6zen S (2017) Familial mediterranean fever: epidemyology and genetics. J Rheumatol-Special 10:1\u20137 (Turkiye Klinikleri)","journal-title":"J Rheumatol-Special"},{"key":"4443_CR4","doi-asserted-by":"publisher","DOI":"10.1016\/j.lpm.2018.08.014","author":"H Ozdogan","year":"2019","unstructured":"Ozdogan H, Ugurlu S (2019) Familial mediterranean fever. Presse Med. \nhttps:\/\/doi.org\/10.1016\/j.lpm.2018.08.014","journal-title":"Presse Med"},{"key":"4443_CR5","doi-asserted-by":"publisher","first-page":"1902791","DOI":"10.1155\/2018\/1902791","volume":"2018","author":"L Shahbaznejad","year":"2018","unstructured":"Shahbaznejad L, Raeeskarami SR, Assari R, Shakoori A, Azhideh H, Aghighi Y, Tahghighi F, Ziaee V (2018) Familial mediterranean gene (MEFV) mutation in parents of children with familial mediterranean fever: what are the exceptions? Int J Inflam 2018:1902791. \nhttps:\/\/doi.org\/10.1155\/2018\/1902791","journal-title":"Int J Inflam"},{"key":"4443_CR6","first-page":"13","volume":"10","author":"K \u00dcreten","year":"2017","unstructured":"\u00dcreten K (2017) Familial Mediterranean Fever: Clinical Manifestations. J Rheumatol-Special 10:13\u201318 (Turkiye Klinikleri)","journal-title":"J Rheumatol-Special"},{"key":"4443_CR7","doi-asserted-by":"publisher","first-page":"343","DOI":"10.1093\/rheumatology\/kev315","volume":"55","author":"S Akar","year":"2016","unstructured":"Akar S, Solmaz D, Kasifoglu T, Bilge SY, Sari I, Gumus ZZ, Tunca M (2016) Different disease subtypes with distinct clinical expression in familial Mediterranean fever: results of a cluster analysis. Rheumatology (Oxford) 55:343\u2013346","journal-title":"Rheumatology (Oxford)"},{"key":"4443_CR8","doi-asserted-by":"publisher","first-page":"118","DOI":"10.5152\/eurjrheum.2016.16012","volume":"3","author":"S G\u00fcncan","year":"2016","unstructured":"G\u00fcncan S, Bilge N\u015e, Cansu D\u00dc, Ka\u015fifo\u011flu T, Korkmaz C (2016) The role of MEFV mutations in the concurrent\u00a0disorders\u00a0observed in patients with\u00a0familial Mediterranean\u00a0fever. Eur J Rheumatol 3:118\u2013121","journal-title":"Eur J Rheumatol"},{"key":"4443_CR9","doi-asserted-by":"publisher","first-page":"356","DOI":"10.1016\/j.rbr.2014.03.022","volume":"54","author":"GY Cetin","year":"2014","unstructured":"Cetin GY, Balkarli A, \u00d6ks\u00fcz AN, Kimyon G, Pehlivan Y, Orhan O, Kisacik B, Cobankara V, Sayarlioglu H, Onat AM, Sayarlioglu M (2014) Evaluation of frequency and the attacks features of patients with colchicine resistance in FMF. Rev Bras Reumatol. 54:356\u2013359","journal-title":"Rev Bras Reumatol."},{"key":"4443_CR10","doi-asserted-by":"publisher","first-page":"257","DOI":"10.1186\/s13075-018-1738-1","volume":"20","author":"Y Endo","year":"2018","unstructured":"Endo Y, Koga T, Ishida M, Fujita Y, Tsuji S, Takatani A (2018) Musculoskeletal manifestations occur predominantly in patients with later-onset familial Mediterranean fever: data from a multicenter, prospective national cohort study in Japan. Arthritis Res Ther 20:257. \nhttps:\/\/doi.org\/10.1186\/s13075-018-1738-1","journal-title":"Arthritis Res Ther"},{"key":"4443_CR11","first-page":"46","volume":"10","author":"F Ayd\u0131n","year":"2017","unstructured":"Ayd\u0131n F, \u00d6z\u00e7akar ZB, Yal\u00e7\u0131nkaya F (2017) Familial Mediterranean Fever Diagnosis and Treatment. J Rheumatol-Special 10:46\u201354 (Turkiye Klinikleri)","journal-title":"J Rheumatol-Special"},{"key":"4443_CR12","doi-asserted-by":"publisher","first-page":"89","DOI":"10.5152\/jarem.2015.642","volume":"5","author":"S \u00dcstebay","year":"2015","unstructured":"\u00dcstebay S, \u00dcstebay D\u00dc, Y\u0131lmaz Y (2015) Familial Mediterranean fever. JAREM 5:89\u201393","journal-title":"JAREM"},{"key":"4443_CR13","doi-asserted-by":"publisher","first-page":"1879","DOI":"10.1002\/art.1780401023","volume":"40","author":"A Livneh","year":"1997","unstructured":"Livneh A, Langevitz P, Zemer D, Zaks N, Kees S, Lidar T, Migdal A, Padeh S, Pras M (1997) Criteria for the diagnosis of familial Mediterranean fever. Arthritis Rheum 40:1879\u20131885","journal-title":"Arthritis Rheum"},{"key":"4443_CR14","doi-asserted-by":"publisher","first-page":"1198","DOI":"10.3906\/sag-1402-1","volume":"45","author":"E Y\u0131lmaz","year":"2015","unstructured":"Y\u0131lmaz E, Din\u00e7el N, S\u00f6zeri B, \u00d6zdemir K, Bulut \u0130, Berdel\u0131 A, Mir M (2015) Familial Mediterranean fever in children from the Aegean region of Turkey: gene mutation frequencies and phenotype-genotype correlation. Turk J Med Sci 45:1198\u20131206","journal-title":"Turk J Med Sci"},{"issue":"75","key":"4443_CR15","doi-asserted-by":"publisher","first-page":"216","DOI":"10.1002\/(SICI)1096-8628(19980113)75:2<216::AID-AJMG20>3.0.CO;2-R","volume":"13","author":"E Pras","year":"1998","unstructured":"Pras E, Livneh A, Balow JE Jr, Pras E, Kastner DL, Pras M, Langevitz P (1998) Clinical differences between North African and Iraqi Jews with familial Mediterranean fever. Am J Med Genet 13(75):216\u2013219","journal-title":"Am J Med Genet"},{"key":"4443_CR16","first-page":"97","volume":"34","author":"O Soylemezoglu","year":"2016","unstructured":"Soylemezoglu O, Kandur Y, Gonen S, D\u00fczova A, \u00d6z\u00e7akar ZB, Fidan K, Yalcinkaya F (2016) Familial Mediterranean fever gene mutation frequencies in a sample Turkish population. Clin Exp Rheumatol 34:97\u2013100","journal-title":"Clin Exp Rheumatol"},{"key":"4443_CR17","doi-asserted-by":"publisher","first-page":"629","DOI":"10.1007\/s12041-015-0568-z","volume":"94","author":"S Co\u015fkun","year":"2015","unstructured":"Co\u015fkun S, Kurtg\u00f6z S, Keskin E, S\u00f6nmez F, Bozkurt G (2015) Frequency of mutations in Mediterranean fever gene, with gender and genotype-phenotype correlations in a Turkish population. J Genet 94:629\u2013635","journal-title":"J Genet"},{"key":"4443_CR18","doi-asserted-by":"publisher","first-page":"1447","DOI":"10.1002\/art.24458","volume":"61","author":"E Ben-Chetrit","year":"2009","unstructured":"Ben-Chetrit E, Touitou I (2009) Familial mediterranean Fever in the world. Arthritis Rheum 61:1447\u20131453","journal-title":"Arthritis Rheum"},{"key":"4443_CR19","doi-asserted-by":"publisher","first-page":"58","DOI":"10.4274\/haseki.68077","volume":"56","author":"S Yavuz","year":"2018","unstructured":"Yavuz S, Sel\u00e7uk Duru N, Elevli M (2018) Ailevi Akdeniz Ate\u015fi hastalar\u0131nda klinik, laboratuar Bulgular\u0131, Hastal\u0131k a\u011f\u0131rl\u0131k skorlar\u0131 ve Gen Mutasyonlar\u0131 Aras\u0131ndaki \u0130li\u015fki. Med Bull Haseki 56:58\u201364","journal-title":"Med Bull Haseki"},{"key":"4443_CR20","first-page":"86","volume":"4","author":"V \u00c7obankara","year":"2011","unstructured":"\u00c7obankara V, Balkarl\u0131 A (2011) Familial Mediterranean Fever. Pam T\u0131p Derg 4:86\u201398","journal-title":"Pam T\u0131p Derg"},{"key":"4443_CR21","doi-asserted-by":"publisher","first-page":"282","DOI":"10.5606\/ArchRheumatol.2018.6488","volume":"33","author":"RM Ki\u015fla Ekinci","year":"2017","unstructured":"Ki\u015fla Ekinci RM, Balci S, Ufuk Altinta\u015f D, Yilmaz M (2017) The influence of concomitant disorders on disease severity of familial mediterranean fever in children. Arch Rheumatol 33:282\u2013287","journal-title":"Arch Rheumatol"},{"key":"4443_CR22","doi-asserted-by":"publisher","DOI":"10.1186\/ar4154","author":"S Akar","year":"2013","unstructured":"Akar S, Soysal O, Balci A, Solmaz D, Gerdan V, Onen F, Tunca M, Akkoc N (2013) High\u00a0prevalence\u00a0of\u00a0spondyloarthritis\u00a0and\u00a0ankylosing\u00a0spondylitis\u00a0among\u00a0familial\u00a0Mediterraneanfever\u00a0patients\u00a0and their first-degree\u00a0relatives: further\u00a0evidence\u00a0for the\u00a0connection. Arthritis Res Ther. \nhttps:\/\/doi.org\/10.1186\/ar4154","journal-title":"Arthritis Res Ther"},{"issue":"1054\u20135","key":"4443_CR23","first-page":"5","volume":"65","author":"F Onen","year":"2013","unstructured":"Onen F, Solmaz D, Cetin P, Balci A, Akar S, Akkoc N (2013) Prevelance of inflammatory back pain and axial spondyloarthritis among university employees In Izmir, Turkey. Arthritis Rheum 65(1054\u20135):5","journal-title":"Arthritis Rheum"},{"key":"4443_CR24","doi-asserted-by":"publisher","first-page":"916","DOI":"10.1136\/ard.62.10.916","volume":"62","author":"E Ben-Chetrit","year":"2003","unstructured":"Ben-Chetrit E, Levy M (2003) Reproductive system in familial Mediterranean fever: an overview. Ann Rheum Dis 62:916\u2013919","journal-title":"Ann Rheum Dis"},{"key":"4443_CR25","doi-asserted-by":"publisher","first-page":"143","DOI":"10.1002\/acr.20061","volume":"62","author":"E Ben-Chetrit","year":"2010","unstructured":"Ben-Chetrit E, Ben-Chetrit A, Berkun Y, Ben-Chetrit E (2010) Pregnancy outcomes in women with familial Mediterranean fever receiving colchicine: is amniocentesis justified? Arthritis Care Res 62:143\u2013148","journal-title":"Arthritis Care Res"},{"key":"4443_CR26","unstructured":"Ben-Chetrit E (2018) Management of familial Mediterranean fever. \nhttps:\/\/www.uptodate.com\/contents\/management-of-familial-mediterranean-fever\n\n. Accessed 4 Nov 2018"},{"key":"4443_CR27","doi-asserted-by":"publisher","first-page":"382","DOI":"10.1093\/rheumatology\/kex353","volume":"57","author":"L Praveen","year":"2018","unstructured":"Praveen L, Sohaib I, Divya V, Gurram Richard O (2018) Day use of colchicine in pregnancy: a systematic review and meta- analysis. Rheumatology 57:382\u2013387","journal-title":"Rheumatology"},{"key":"4443_CR28","doi-asserted-by":"publisher","first-page":"94","DOI":"10.5606\/ArchRheumatol.2014.3707","volume":"29","author":"A Yaz\u0131c\u0131o\u011flu","year":"2014","unstructured":"Yaz\u0131c\u0131o\u011flu A, Turgal M, Y\u00fccel \u00d6S, \u00d6zy\u00fcnc\u00fc \u00d6, Beksa\u00e7 MS (2014) Pregnancy outcome in women with familial Mediterranean fever: a retrospective analysis of 50 cases with a 10-year experience. Arch Rheumatol 29:94\u201398","journal-title":"Arch Rheumatol"},{"key":"4443_CR29","doi-asserted-by":"publisher","DOI":"10.3390\/jcm7050105","author":"E G\u00fcm\u00fc\u015f","year":"2018","unstructured":"G\u00fcm\u00fc\u015f E (2018) The frequency of MEFV gene mutations and genotypes in Sanliurfa Province, South-Eastern Region of Turkey, after the Syrian Civil War by using next generation sequencing and report of a Novel Exon 4 Mutation (I423T). J Clin Med. \nhttps:\/\/doi.org\/10.3390\/jcm7050105","journal-title":"J Clin Med"},{"key":"4443_CR30","doi-asserted-by":"publisher","first-page":"49","DOI":"10.1080\/13506120701815456","volume":"15","author":"S Pasa","year":"2008","unstructured":"Pasa S, Alt\u0131ntas A, Devecioglu B, Cil T, Dan\u0131\u015f R, Is\u0131 H, Bayan K, Tuzun Y, Ecer S, Batun S, Ayy\u0131ld\u0131z O (2008) Familial Mediterranean fever gene mutations in the Southeastern region of Turkey and their phenotypical features. Amyloid 15:49\u201353","journal-title":"Amyloid"},{"key":"4443_CR31","doi-asserted-by":"publisher","first-page":"131","DOI":"10.1159\/000077375","volume":"96","author":"MP Atagunduza","year":"2004","unstructured":"Atagunduza MP, Tuglularb S, Kantarcic G, Akoglub E, Direskenelia H (2004) Association of FMF-related (MEFV) point mutations with secondary and FMF amyloidosis. Nephron Clin Pract 96:131\u2013135","journal-title":"Nephron Clin Pract"},{"key":"4443_CR32","doi-asserted-by":"publisher","first-page":"911","DOI":"10.1007\/s00296-009-1073-6","volume":"30","author":"K \u00dcreten","year":"2010","unstructured":"\u00dcreten K, G\u00f6n\u00fclalan G, Akbal E, G\u00fcneo F, Aky\u00fcrek \u00d6, \u00d6zbek M, \u00d6zt\u00fcrk MA (2010) Demographic, clinical and mutational characteristics of Turkish familial Mediterranean fever patients: results of a single center in Central Anatolia. Rheumatol Int 30:911\u2013915","journal-title":"Rheumatol Int"},{"key":"4443_CR33","doi-asserted-by":"publisher","first-page":"971","DOI":"10.1007\/s00431-010-1158-y","volume":"169","author":"V Akse-\u00d6nal","year":"2010","unstructured":"Akse-\u00d6nal V, Sa\u011f E, Ozen S, Bakkaloglu A, Cakar N, Besbas N, Gucer S (2010) Decrease in the rate of secondary amyloidosis in Turkish children with FMF: are we doing better? Eur J Pediatr 169:971\u2013974","journal-title":"Eur J Pediatr"},{"key":"4443_CR34","doi-asserted-by":"publisher","first-page":"750","DOI":"10.1136\/ard.2004.026963","volume":"64","author":"R Topaloglu","year":"2005","unstructured":"Topaloglu R, Ozaltin F, Yilmaz E, Ozen S, Balci B, Besbas N, Bakkaloglu A (2005) E148Q is a disease-causing MEFV mutation: a phenotypic evaluation in patients with familial Mediterranean fever. Ann Rheum Dis 64:750\u2013752","journal-title":"Ann Rheum Dis"},{"key":"4443_CR35","doi-asserted-by":"publisher","first-page":"2372","DOI":"10.3899\/jrheum.090250","volume":"36","author":"D Marek-Yagel","year":"2009","unstructured":"Marek-Yagel D, Bar-Joseph I, Pras E, Berkun Y (2009) Is E148Q a benign polymorphism or a disease-causing mutation? J Rheumatol 36:2372\u20132373","journal-title":"J Rheumatol"},{"key":"4443_CR36","doi-asserted-by":"publisher","first-page":"3854","DOI":"10.12659\/MSM.914343","volume":"24","author":"A Bakan","year":"2019","unstructured":"Bakan A, Oral A, Al\u0131\u015f\u0131r Ecder S, \u015ea\u015fak Kuzgun G, El\u00e7io\u011flu \u00d6C, Demirci R, Ayd\u0131n Bahat K, Odabas AR (2019) Assessment of mean platelet volume in patients with AA\u00a0amyloidosis\u00a0and AA\u00a0amyloidosis secondary to familial Mediterranean fever: a retrospective chart: review study. Med Sci Monit 24:3854\u20133859","journal-title":"Med Sci Monit"},{"key":"4443_CR37","first-page":"50","volume":"3","author":"H Nobakht","year":"2011","unstructured":"Nobakht H, Zamani F, Ajdarkosh H, Mohamadzadeh Z, Fereshtehnejad S, Nassaji M (2011) Adult- onset familial Mediterranean fever in Northwestern Iran; clinical feature and treatment outcome. Middle East J Dig Dis 3:50\u201355","journal-title":"Middle East J Dig Dis"},{"key":"4443_CR38","first-page":"202","volume":"59","author":"M Sayaliolu","year":"2005","unstructured":"Sayaliolu M, Cefle A, \u0130nan\u00e7 M, Kamali S, Dalk\u0131l\u0131\u00e7 E, Gul A, Ocal L, Aral O, Konice M (2005) Characteristics of patients with adult-onset familial Mediterranean fever in Turkey: analysis of 401 cases. Int J Clin Pract 59:202\u2013205","journal-title":"Int J Clin Pract"}],"container-title":["Rheumatology International"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1007\/s00296-019-04443-0.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/link.springer.com\/article\/10.1007\/s00296-019-04443-0\/fulltext.html","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1007\/s00296-019-04443-0.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2020,9,12]],"date-time":"2020-09-12T23:10:22Z","timestamp":1599952222000},"score":1,"resource":{"primary":{"URL":"http:\/\/link.springer.com\/10.1007\/s00296-019-04443-0"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2019,9,14]]},"references-count":38,"journal-issue":{"issue":"1","published-print":{"date-parts":[[2020,1]]}},"alternative-id":["4443"],"URL":"https:\/\/doi.org\/10.1007\/s00296-019-04443-0","relation":{},"ISSN":["0172-8172","1437-160X"],"issn-type":[{"value":"0172-8172","type":"print"},{"value":"1437-160X","type":"electronic"}],"subject":[],"published":{"date-parts":[[2019,9,14]]},"assertion":[{"value":"9 July 2019","order":1,"name":"received","label":"Received","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"5 September 2019","order":2,"name":"accepted","label":"Accepted","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"14 September 2019","order":3,"name":"first_online","label":"First Online","group":{"name":"ArticleHistory","label":"Article History"}},{"order":1,"name":"Ethics","group":{"name":"EthicsHeading","label":"Compliance with ethical standards"}},{"value":"Author Hatice Bodur, Fatma G\u00fcl Yurdakul Hasan Fatih \u00c7ay \u00dclk\u00fc U\u00e7ar Ya\u015far Keskin Bet\u00fcl Sarg\u0131nn G\u00fclcan G\u00fcrer Ozan Volkan Yurdakul Mustafa \u00c7al\u0131\u015f H\u00fclya Deveci Y\u0131ld\u0131ray Ayd\u0131n Sami Hizmetli Remzi \u00c7evik Ali Yavuz Karahan \u0130smihan Sunar Mehmet Tuncay Duru\u00f6z Hilal Ecesoy Zafer G\u00fcnendi Murat Toprak Nesrin \u015een Duygu Alt\u0131nta\u015f Ahmet K\u0131van\u00e7 Cengiz G\u00f6khan \u00c7a\u011flayan Ali Nail Demir H\u00fcseyin Kaplan Serta\u00e7 Ketenci Meltem Alkan Meliko\u011flu Mehmet Nayimo\u011flu Kemal Nas Ay\u015fe Banu Sar\u0131fak\u0131o\u011flu and \u0130lhan Sezer declare that they have no conflict of interest.","order":2,"name":"Ethics","group":{"name":"EthicsHeading","label":"Conflict of interest"}},{"value":"All procedures performed in studies involving human participants were in accordance with the ethical standards of the institutional and\/or national research committee and with the 1964 Helsinki declaration and its later amendments or comparable ethical standards (ethic committee approval date\/no:22.11.2107\/E-17-1626).","order":3,"name":"Ethics","group":{"name":"EthicsHeading","label":"Ethical approval"}},{"value":"Informed consent was obtained from all individual participants included in the study.","order":4,"name":"Ethics","group":{"name":"EthicsHeading","label":"Informed consent"}}]}}