{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,1,7]],"date-time":"2026-01-07T23:35:32Z","timestamp":1767828932010,"version":"3.49.0"},"reference-count":43,"publisher":"Springer Science and Business Media LLC","issue":"7","license":[{"start":{"date-parts":[[2020,4,30]],"date-time":"2020-04-30T00:00:00Z","timestamp":1588204800000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.springer.com\/tdm"},{"start":{"date-parts":[[2020,4,30]],"date-time":"2020-04-30T00:00:00Z","timestamp":1588204800000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/www.springer.com\/tdm"}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["Rheumatol Int"],"published-print":{"date-parts":[[2020,7]]},"DOI":"10.1007\/s00296-020-04590-9","type":"journal-article","created":{"date-parts":[[2020,4,30]],"date-time":"2020-04-30T09:09:45Z","timestamp":1588237785000},"page":"1151-1162","update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":28,"title":["Macrophage activation syndrome in adult dermatomyositis: a case-based review"],"prefix":"10.1007","volume":"40","author":[{"ORCID":"https:\/\/orcid.org\/0000-0001-8309-7984","authenticated-orcid":false,"given":"Dai","family":"Kishida","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Noriko","family":"Sakaguchi","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ken-ichi","family":"Ueno","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Satoru","family":"Ushiyama","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-6570-5878","authenticated-orcid":false,"given":"Takanori","family":"Ichikawa","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-4323-0557","authenticated-orcid":false,"given":"Tsuneaki","family":"Yoshinaga","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-7100-1121","authenticated-orcid":false,"given":"Yasuhiro","family":"Shimojima","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-8132-2743","authenticated-orcid":false,"given":"Yoshiki","family":"Sekijima","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"297","published-online":{"date-parts":[[2020,4,30]]},"reference":[{"key":"4590_CR1","doi-asserted-by":"publisher","first-page":"135","DOI":"10.1016\/j.blre.2014.03.002","volume":"28","author":"GE Janka","year":"2014","unstructured":"Janka GE, Lehmberg K (2014) Hemophagocytic syndromes\u2014an update. Blood Rev 28:135\u2013142. https:\/\/doi.org\/10.1016\/j.blre.2014.03.002","journal-title":"Blood Rev"},{"key":"4590_CR2","first-page":"1414","volume":"16","author":"M Atteritano","year":"2012","unstructured":"Atteritano M, David A, Bagnato G, Beninati C, Frisina A, Iaria C, Bagnato G, Cascio A (2012) Haemophagocytic syndrome in rheumatic patients. A systematic review. Eur Rev Med Pharmacol Sci 16:1414\u20131424","journal-title":"Eur Rev Med Pharmacol Sci"},{"key":"4590_CR3","doi-asserted-by":"publisher","first-page":"119","DOI":"10.3389\/fimmu.2019.00119","volume":"10","author":"CB Crayne","year":"2019","unstructured":"Crayne CB, Albeituni S, Nichols KE, Cron RQ (2019) The immunology of macrophage activation syndrome. Front Immunol 10:119. https:\/\/doi.org\/10.3389\/fimmu.2019.00119","journal-title":"Front Immunol"},{"key":"4590_CR4","doi-asserted-by":"publisher","first-page":"e451","DOI":"10.1097\/MD.0000000000000451","volume":"94","author":"CB Bae","year":"2015","unstructured":"Bae CB, Jung JY, Kim HA, Suh CH (2015) Reactive hemophagocytic syndrome in adult-onset Still disease: clinical features, predictive factors, and prognosis in 21 patients. Medicine 94:e451. https:\/\/doi.org\/10.1097\/MD.0000000000000451","journal-title":"Medicine"},{"key":"4590_CR5","doi-asserted-by":"publisher","first-page":"109","DOI":"10.1159\/000312628","volume":"153","author":"S Deane","year":"2010","unstructured":"Deane S, Selmi C, Teuber SS, Gershwin ME (2010) Macrophage activation syndrome in autoimmune disease. Int Arch Allergy Immunol 153:109\u2013120. https:\/\/doi.org\/10.1159\/000312628","journal-title":"Int Arch Allergy Immunol"},{"key":"4590_CR6","doi-asserted-by":"publisher","DOI":"10.1007\/s40257-020-00502-6","author":"GA Cobos","year":"2020","unstructured":"Cobos GA, Femia A, Vleugels RA (2020) Dermatomyositis: an update on diagnosis and treatment. Am J Clin Dermatol. https:\/\/doi.org\/10.1007\/s40257-020-00502-6","journal-title":"Am J Clin Dermatol"},{"key":"4590_CR7","doi-asserted-by":"publisher","first-page":"8","DOI":"10.1111\/joim.12451","volume":"280","author":"Z Betteridge","year":"2016","unstructured":"Betteridge Z, McHugh N (2016) Myositis-specific autoantibodies: an important tool to support diagnosis of myositis. J Intern Med 280:8\u201323. https:\/\/doi.org\/10.1111\/joim.12451","journal-title":"J Intern Med"},{"key":"4590_CR8","doi-asserted-by":"publisher","first-page":"1503","DOI":"10.1016\/S0140-6736(13)61048-X","volume":"383","author":"M Ramos-Casals","year":"2014","unstructured":"Ramos-Casals M, Brito-Zeron P, Lopez-Guillermo A, Khamashta MA, Bosch X (2014) Adult haemophagocytic syndrome. Lancet 383:1503\u20131516. https:\/\/doi.org\/10.1016\/S0140-6736(13)61048-X","journal-title":"Lancet"},{"key":"4590_CR9","doi-asserted-by":"publisher","first-page":"695","DOI":"10.1007\/s00296-019-04442-1","volume":"40","author":"D Poddighe","year":"2019","unstructured":"Poddighe D, Dauyey K (2019) Macrophage activation syndrome in juvenile dermatomyositis: a systematic review. Rheumatol Int 40:695\u2013702. https:\/\/doi.org\/10.1007\/s00296-019-04442-1","journal-title":"Rheumatol Int"},{"key":"4590_CR10","doi-asserted-by":"publisher","first-page":"2297","DOI":"10.1002\/art.38672","volume":"66","author":"S Kumakura","year":"2014","unstructured":"Kumakura S, Murakawa Y (2014) Clinical characteristics and treatment outcomes of autoimmune-associated hemophagocytic syndrome in adults. Arthritis Rheumatol 66:2297\u20132307. https:\/\/doi.org\/10.1002\/art.38672","journal-title":"Arthritis Rheumatol"},{"key":"4590_CR11","doi-asserted-by":"publisher","first-page":"1357","DOI":"10.1093\/rheumatology\/37.12.1357","volume":"37","author":"S Yasuda","year":"1998","unstructured":"Yasuda S, Tsutsumi A, Nakabayashi T, Horita T, Ichikawa K, Ieko M, Koike T (1998) Haemophagocytic syndrome in a patient with dermatomyositis. Br J Rheumatol 37:1357\u20131358. https:\/\/doi.org\/10.1093\/rheumatology\/37.12.1357","journal-title":"Br J Rheumatol"},{"key":"4590_CR12","doi-asserted-by":"publisher","first-page":"1157","DOI":"10.1093\/rheumatology\/39.10.1157","volume":"39","author":"S Madaule","year":"2000","unstructured":"Madaule S, Porte L, Couret B, Arlet-Suau E (2000) Fatal haemophagocytic syndrome in the course of dermatomyositis with anti-Mi2 antibodies. Rheumatology 39:1157\u20131158. https:\/\/doi.org\/10.1093\/rheumatology\/39.10.1157","journal-title":"Rheumatology"},{"key":"4590_CR13","first-page":"1838","volume":"35","author":"N Yajima","year":"2008","unstructured":"Yajima N, Wakabayashi K, Odai T, Isozaki T, Matsunawa M, Miwa Y, Negishi M, Ide H, Kasama T (2008) Clinical features of hemophagocytic syndrome in patients with dermatomyositis. J Rheumatol 35:1838\u20131841","journal-title":"J Rheumatol"},{"key":"4590_CR14","first-page":"481","volume":"77","author":"A Thomas","year":"2013","unstructured":"Thomas A, Appiah J, Langsam J, Parker S, Christian C (2013) Hemophagocytic lymphohistiocytosis associated with dermatomyositis: a case report. Conn Med 77:481\u2013485","journal-title":"Conn Med"},{"key":"4590_CR15","doi-asserted-by":"publisher","first-page":"646","DOI":"10.3109\/14397595.2013.843753","volume":"25","author":"F Mizoguchi","year":"2015","unstructured":"Mizoguchi F, Takada K, Ishikawa K, Mizusawa H, Kohsaka H, Miyasaka N (2015) A case of dermatomyositis with rhabdomyolysis, rescued by intravenous immunoglobulin. Mod Rheumatol 25:646\u2013648. https:\/\/doi.org\/10.3109\/14397595.2013.843753","journal-title":"Mod Rheumatol"},{"key":"4590_CR16","doi-asserted-by":"publisher","first-page":"962","DOI":"10.3109\/14397595.2013.844402","volume":"25","author":"S Kaieda","year":"2015","unstructured":"Kaieda S, Yoshida N, Yamashita F, Okamoto M, Ida H, Hoshino T, Fukuda T (2015) Successful treatment of macrophage activation syndrome in a patient with dermatomyositis by combination with immunosuppressive therapy and plasmapheresis. Mod Rheumatol 25:962\u2013966. https:\/\/doi.org\/10.3109\/14397595.2013.844402","journal-title":"Mod Rheumatol"},{"key":"4590_CR17","doi-asserted-by":"publisher","first-page":"539","DOI":"10.1097\/DAD.0000000000000166","volume":"37","author":"K Kerl","year":"2015","unstructured":"Kerl K, Wolf IH, Cerroni L, Wolf P, French LE, Kerl H (2015) Hemophagocytosis in cutaneous autoimmune disease. Am J Dermatopathol 37:539\u2013543. https:\/\/doi.org\/10.1097\/DAD.0000000000000166","journal-title":"Am J Dermatopathol"},{"key":"4590_CR18","doi-asserted-by":"publisher","first-page":"2171","DOI":"10.1111\/1756-185X.12162","volume":"20","author":"S Bazan-Socha","year":"2017","unstructured":"Bazan-Socha S, Zolcinski M, Szostek M, Jurczyszyn A, Rucinska M, Demczuk S, Musial J (2017) A fatal case of acquired hemophagocytic lymphohistiocytosis (macrophage activation syndrome) in the initial course of dermatomyositis with anti-Jo-1 antibody. Int J Rheum Dis 20:2171\u20132174. https:\/\/doi.org\/10.1111\/1756-185X.12162","journal-title":"Int J Rheum Dis"},{"key":"4590_CR19","doi-asserted-by":"publisher","first-page":"3237","DOI":"10.2169\/internalmedicine.7966-16","volume":"56","author":"Y Komiya","year":"2017","unstructured":"Komiya Y, Saito T, Mizoguchi F, Kohsaka H (2017) Hemophagocytic syndrome complicated with dermatomyositis controlled successfully with infliximab and conventional therapies. Intern Med 56:3237\u20133241. https:\/\/doi.org\/10.2169\/internalmedicine.7966-16","journal-title":"Intern Med"},{"key":"4590_CR20","doi-asserted-by":"publisher","first-page":"1412","DOI":"10.4103\/0028-3886.217937","volume":"65","author":"BV Maramattom","year":"2017","unstructured":"Maramattom BV, Varghese R, Thomas J, Kachhare N (2017) Clinically amyopathic dermatomyositis associated with cerebral venous sinus thrombosis and macrophage activation syndrome. Neurol India 65:1412\u20131414. https:\/\/doi.org\/10.4103\/0028-3886.217937","journal-title":"Neurol India"},{"key":"4590_CR21","doi-asserted-by":"publisher","first-page":"3473","DOI":"10.2169\/internalmedicine.1121-18","volume":"57","author":"Y Fujita","year":"2018","unstructured":"Fujita Y, Fukui S, Suzuki T, Ishida M, Endo Y, Tsuji S et al (2018) Anti-MDA5 antibody-positive dermatomyositis complicated by autoimmune-associated hemophagocytic syndrome that was successfully treated with immunosuppressive therapy and plasmapheresis. Intern Med 57:3473\u20133478. https:\/\/doi.org\/10.2169\/internalmedicine.1121-18","journal-title":"Intern Med"},{"key":"4590_CR22","doi-asserted-by":"publisher","first-page":"62","DOI":"10.4274\/balkanmedj.2018.1339","volume":"36","author":"HT Liao","year":"2019","unstructured":"Liao HT, Yang CF, Tsai CY (2019) Hemophagocytic lymphohistiocytosis in dermatomyositis. Balkan Med J 36:62\u201363. https:\/\/doi.org\/10.4274\/balkanmedj.2018.1339","journal-title":"Balkan Med J"},{"key":"4590_CR23","doi-asserted-by":"publisher","first-page":"321","DOI":"10.1111\/1756-185X.12746","volume":"22","author":"Y Yoshimatsu","year":"2019","unstructured":"Yoshimatsu Y, Kotani T, Fujiki Y, Oda K, Kataoka T, Yamairi K, Hata K, Otani K, Kamimori T, Fujiwara H (2019) Successful treatment with intravenous high-dose immunoglobulin for cardiomyopathy in dermatomyositis complicated with rapid progressive interstitial pneumonia. Int J Rheum Dis 22:321\u2013324. https:\/\/doi.org\/10.1111\/1756-185X.12746","journal-title":"Int J Rheum Dis"},{"key":"4590_CR24","doi-asserted-by":"publisher","DOI":"10.1080\/03009742.2019.1653493","author":"M Honda","year":"2019","unstructured":"Honda M, Moriyama M, Kondo M, Kumakura S, Sumita Y, Murakawa Y (2019) Three cases of autoimmune-associated haemophagocytic syndrome in dermatomyositis with anti-MDA5 autoantibody. Scand J Rheumatol. https:\/\/doi.org\/10.1080\/03009742.2019.1653493","journal-title":"Scand J Rheumatol"},{"key":"4590_CR25","doi-asserted-by":"publisher","first-page":"743","DOI":"10.1016\/j.autrev.2017.05.010","volume":"16","author":"PE Gavand","year":"2017","unstructured":"Gavand PE, Serio I, Arnaud L, Costedoat-Chalumeau N, Carvelli J, Dossier A et al (2017) Clinical spectrum and therapeutic management of systemic lupus erythematosus-associated macrophage activation syndrome: a study of 103 episodes in 89 adult patients. Autoimmun Rev 16:743\u2013749. https:\/\/doi.org\/10.1016\/j.autrev.2017.05.010","journal-title":"Autoimmun Rev"},{"key":"4590_CR26","doi-asserted-by":"publisher","first-page":"124","DOI":"10.1002\/pbc.21039","volume":"48","author":"JI Henter","year":"2007","unstructured":"Henter JI, Horne A, Arico M, Egeler RM, Filipovich AH, Imashuku S, Ladisch S, McClain K, Webb D, Winiarski J, Janka G (2007) HLH-2004: diagnostic and therapeutic guidelines for hemophagocytic lymphohistiocytosis. Pediatr Blood Cancer 48:124\u2013131. https:\/\/doi.org\/10.1002\/pbc.21039","journal-title":"Pediatr Blood Cancer"},{"key":"4590_CR27","doi-asserted-by":"publisher","first-page":"855","DOI":"10.3109\/14397595.2013.874740","volume":"24","author":"MW So","year":"2014","unstructured":"So MW, Koo BS, Kim YJ, Kim YG, Lee CK, Yoo B (2014) Successful rituximab treatment of refractory hemophagocytic lymphohistiocytosis and autoimmune hemolytic anemia associated with systemic lupus erythematosus. Mod Rheumatol 24:855\u2013857. https:\/\/doi.org\/10.3109\/14397595.2013.874740","journal-title":"Mod Rheumatol"},{"key":"4590_CR28","doi-asserted-by":"publisher","first-page":"1544","DOI":"10.1177\/0961203313504634","volume":"22","author":"J Bakshi","year":"2013","unstructured":"Bakshi J, Hassan S, D'Cruz D, Chan A (2013) Rituximab therapy in refractory macrophage activation syndrome secondary to systemic lupus erythematosus. Lupus 22:1544\u20131546. https:\/\/doi.org\/10.1177\/0961203313504634","journal-title":"Lupus"},{"key":"4590_CR29","doi-asserted-by":"publisher","DOI":"10.1136\/bcr-2017-221347","author":"Z Junga","year":"2017","unstructured":"Junga Z, Stitt R, Tracy C, Keith M (2017) Novel use of rituximab in macrophage activation syndrome secondary to systemic lupus erythematosus. BMJ Case Rep. https:\/\/doi.org\/10.1136\/bcr-2017-221347","journal-title":"BMJ Case Rep"},{"key":"4590_CR30","doi-asserted-by":"publisher","first-page":"92","DOI":"10.3109\/s10165-010-0348-9","volume":"21","author":"M Kobayashi","year":"2011","unstructured":"Kobayashi M, Takahashi Y, Yamashita H, Kaneko H, Mimori A (2011) Benefit and a possible risk of tocilizumab therapy for adult-onset Still's disease accompanied by macrophage-activation syndrome. Mod Rheumatol 21:92\u201396. https:\/\/doi.org\/10.3109\/s10165-010-0348-9","journal-title":"Mod Rheumatol"},{"key":"4590_CR31","doi-asserted-by":"publisher","first-page":"141","DOI":"10.1007\/s10067-012-2105-2","volume":"32","author":"H de Boysson","year":"2013","unstructured":"de Boysson H, F\u00e9vrier J, Nicolle A, Auzary C, Geffray L (2013) Tocilizumab in the treatment of the adult-onset Still's disease: current clinical evidence. Clin Rheumatol 32:141\u2013147. https:\/\/doi.org\/10.1007\/s10067-012-2105-2","journal-title":"Clin Rheumatol"},{"key":"4590_CR32","doi-asserted-by":"publisher","first-page":"314","DOI":"10.1002\/art.37754","volume":"65","author":"CV Oddis","year":"2013","unstructured":"Oddis CV, Reed AM, Aggarwal R, Rider LG, Ascherman DP, Levesque MC et al (2013) Rituximab in the treatment of refractory adult and juvenile dermatomyositis and adult polymyositis: a randomized, placebo-phase trial. Arthritis Rheum 65:314\u2013324. https:\/\/doi.org\/10.1002\/art.37754","journal-title":"Arthritis Rheum"},{"key":"4590_CR33","doi-asserted-by":"publisher","first-page":"247","DOI":"10.1093\/rheumatology\/kew396","volume":"56","author":"R Aggarwal","year":"2017","unstructured":"Aggarwal R, Loganathan P, Koontz D, Qi Z, Reed AM, Oddis CV (2017) Cutaneous improvement in refractory adult and juvenile dermatomyositis after treatment with rituximab. Rheumatology (Oxford) 56:247\u2013254. https:\/\/doi.org\/10.1093\/rheumatology\/kew396","journal-title":"Rheumatology (Oxford)"},{"key":"4590_CR34","doi-asserted-by":"publisher","first-page":"5386797","DOI":"10.1155\/2017\/5386797","volume":"2017","author":"Y Ogawa","year":"2017","unstructured":"Ogawa Y, Kishida D, Shimojima Y, Hayashi K, Sekijima Y (2017) Effective administration of rituximab in anti-MDA5 antibody-positive dermatomyositis with rapidly progressive interstitial lung disease and refractory cutaneous involvement: a case report and literature review. Case Rep Rheumatol 2017:5386797. https:\/\/doi.org\/10.1155\/2017\/5386797","journal-title":"Case Rep Rheumatol"},{"key":"4590_CR35","doi-asserted-by":"publisher","first-page":"26","DOI":"10.1093\/rheumatology\/kew146","volume":"56","author":"S Fasano","year":"2017","unstructured":"Fasano S, Gordon P, Hajji R, Loyo E, Isenberg DA (2017) Rituximab in the treatment of inflammatory myopathies: a review. Rheumatology 56:26\u201336. https:\/\/doi.org\/10.1093\/rheumatology\/kew146","journal-title":"Rheumatology"},{"key":"4590_CR36","doi-asserted-by":"publisher","first-page":"127","DOI":"10.1124\/pr.109.002006","volume":"63","author":"P Engel","year":"2011","unstructured":"Engel P, Gomez-Puerta JA, Ramos-Casals M, Lozano F, Bosch X (2011) Therapeutic targeting of B cells for rheumatic autoimmune diseases. Pharmacol Rev 63:127\u2013156. https:\/\/doi.org\/10.1124\/pr.109.002006","journal-title":"Pharmacol Rev"},{"key":"4590_CR37","doi-asserted-by":"publisher","first-page":"2193","DOI":"10.1002\/art.24621","volume":"60","author":"S Sato","year":"2009","unstructured":"Sato S, Hoshino K, Satoh T, Fujita T, Kawakami Y, Fujita T, Kuwana M (2009) RNA helicase encoded by melanoma differentiation-associated gene 5 is a major autoantigen in patients with clinically amyopathic dermatomyositis: association with rapidly progressive interstitial lung disease. Arthritis Rheum 60:2193\u20132200. https:\/\/doi.org\/10.1002\/art.24621","journal-title":"Arthritis Rheum"},{"key":"4590_CR38","doi-asserted-by":"publisher","first-page":"1713","DOI":"10.1093\/rheumatology\/keq149","volume":"49","author":"T Gono","year":"2010","unstructured":"Gono T, Kawaguchi Y, Satoh T, Kuwana M, Katsumata Y, Takagi K, Masuda I, Tochimoto A, Baba S, Okamoto Y, Ota Y, Yamanaka H (2010) Clinical manifestation and prognostic factor in anti-melanoma differentiation-associated gene 5 antibody-associated interstitial lung disease as a complication of dermatomyositis. Rheumatology 49:1713\u20131719. https:\/\/doi.org\/10.1093\/rheumatology\/keq149","journal-title":"Rheumatology"},{"key":"4590_CR39","doi-asserted-by":"publisher","first-page":"46","DOI":"10.1111\/1346-8138.14092","volume":"45","author":"J Li","year":"2018","unstructured":"Li J, Liu Y, Li Y, Li F, Wang K, Pan W, Meng D (2018) Associations between anti-melanoma differentiation-associated gene 5 antibody and demographics, clinical characteristics and laboratory results of patients with dermatomyositis: a systematic meta-analysis. J Dermatol 45:46\u201352. https:\/\/doi.org\/10.1111\/1346-8138.14092","journal-title":"J Dermatol"},{"key":"4590_CR40","doi-asserted-by":"publisher","first-page":"901","DOI":"10.1007\/s00296-019-04255-2","volume":"39","author":"T Nagashima","year":"2019","unstructured":"Nagashima T, Kamata Y, Iwamoto M, Okazaki H, Fukushima N, Minota S (2019) Liver dysfunction in anti-melanoma differentiation-associated gene 5 antibody-positive patients with dermatomyositis. Rheumatol Int 39:901\u2013909. https:\/\/doi.org\/10.1007\/s00296-019-04255-2","journal-title":"Rheumatol Int"},{"key":"4590_CR41","doi-asserted-by":"publisher","first-page":"947","DOI":"10.3899\/jrheum.170997","volume":"45","author":"H Kawasumi","year":"2018","unstructured":"Kawasumi H, Katsumata Y, Nishino A, Hirahara S, Kawaguchi Y, Kuwana M, Yamanaka H (2018) Association of serum soluble CD163 with polymyositis and dermatomyositis, especially in anti-MDA5 antibody-positive cases. J Rheumatol 45:947\u2013955. https:\/\/doi.org\/10.3899\/jrheum.170997","journal-title":"J Rheumatol"},{"key":"4590_CR42","doi-asserted-by":"publisher","first-page":"10","DOI":"10.1016\/j.clim.2009.02.005","volume":"132","author":"A Coca","year":"2009","unstructured":"Coca A, Bundy KW, Marston B, Huggins J, Looney RJ (2009) Macrophage activation syndrome: serological markers and treatment with anti-thymocyte globulin. Clin Immunol 132:10\u201318. https:\/\/doi.org\/10.1016\/j.clim.2009.02.005","journal-title":"Clin Immunol"},{"key":"4590_CR43","doi-asserted-by":"publisher","first-page":"979","DOI":"10.3899\/jrheum.141307","volume":"42","author":"QL Peng","year":"2015","unstructured":"Peng QL, Zhang YL, Shu XM, Yang HB, Zhang L, Chen F, Lu X, Wang GC (2015) Elevated serum levels of soluble CD163 in polymyositis and dermatomyositis: associated with macrophage infiltration in muscle tissue. J Rheumatol 42:979\u2013987. https:\/\/doi.org\/10.3899\/jrheum.141307","journal-title":"J Rheumatol"}],"container-title":["Rheumatology International"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1007\/s00296-020-04590-9.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/link.springer.com\/article\/10.1007\/s00296-020-04590-9\/fulltext.html","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1007\/s00296-020-04590-9.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2022,7,29]],"date-time":"2022-07-29T16:41:09Z","timestamp":1659112869000},"score":1,"resource":{"primary":{"URL":"https:\/\/link.springer.com\/10.1007\/s00296-020-04590-9"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2020,4,30]]},"references-count":43,"journal-issue":{"issue":"7","published-print":{"date-parts":[[2020,7]]}},"alternative-id":["4590"],"URL":"https:\/\/doi.org\/10.1007\/s00296-020-04590-9","relation":{},"ISSN":["0172-8172","1437-160X"],"issn-type":[{"value":"0172-8172","type":"print"},{"value":"1437-160X","type":"electronic"}],"subject":[],"published":{"date-parts":[[2020,4,30]]},"assertion":[{"value":"27 February 2020","order":1,"name":"received","label":"Received","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"18 April 2020","order":2,"name":"accepted","label":"Accepted","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"30 April 2020","order":3,"name":"first_online","label":"First Online","group":{"name":"ArticleHistory","label":"Article History"}},{"order":1,"name":"Ethics","group":{"name":"EthicsHeading","label":"Compliance with ethical standards"}},{"value":"Dai Kishida, Noriko Sakaguchi, Ken-ichi Ueno, Satoru Ushiyama, Takanori Ichikawa, Tsuneaki Yoshinaga, Yasuhiro Shimojima, and Yoshiki Sekijima declare that they have no conflicts of interest.","order":2,"name":"Ethics","group":{"name":"EthicsHeading","label":"Conflicts of interest"}},{"value":"All procedures performed in studies involving human participants were in accordance with the ethical standards of the institutional and\/or national research committee and with the 1964 Helsinki declaration and its later amendments or comparable ethical standards.","order":3,"name":"Ethics","group":{"name":"EthicsHeading","label":"Ethics approval"}},{"value":"Informed consent was obtained from the patient.","order":4,"name":"Ethics","group":{"name":"EthicsHeading","label":"Consent to participate"}},{"value":"The participant has consented to the submission of the case report to the journal.","order":5,"name":"Ethics","group":{"name":"EthicsHeading","label":"Consent for publication"}}]}}