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Phenotypically, this rare hereditary syndrome is characterized by microphthalmia\/anophthalmia and other eye disorders; mental disability; dental, ear, and digital abnormalities; and variable malformations affecting the heart, skeleton (limbs and\/or spine), and genitourinary tract. In this paper, a case of a young adult with LMS affected additionally by immuno-hematological disturbances was treated with decompressive craniectomy after domestic accidental fall. Case description and a brief review of the current literature about this rare condition are presented here.<\/jats:p>","DOI":"10.1007\/s00381-020-05035-1","type":"journal-article","created":{"date-parts":[[2021,1,25]],"date-time":"2021-01-25T03:03:25Z","timestamp":1611543805000},"page":"2713-2718","update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":5,"title":["Lenz microphthalmia syndrome in neurosurgical practice: a case report and review of the literature"],"prefix":"10.1007","volume":"37","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-3738-5106","authenticated-orcid":false,"given":"Matteo","family":"Monticelli","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Raffaele","family":"De Marco","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Diego","family":"Garbossa","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2021,1,25]]},"reference":[{"issue":"4","key":"5035_CR1","doi-asserted-by":"publisher","first-page":"384","DOI":"10.1007\/BF00437927","volume":"77","author":"W Lenz","year":"1955","unstructured":"Lenz W (1955) Recessiv-geschlechtsgebundene Mikrophthalmie mit multiplen Mi\u00dfbildungen. 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