{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,7,29]],"date-time":"2026-07-29T08:32:51Z","timestamp":1785313971027,"version":"3.55.0"},"reference-count":52,"publisher":"Springer Science and Business Media LLC","issue":"12","license":[{"start":{"date-parts":[[2017,9,22]],"date-time":"2017-09-22T00:00:00Z","timestamp":1506038400000},"content-version":"unspecified","delay-in-days":0,"URL":"http:\/\/www.springer.com\/tdm"}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["Pediatr Surg Int"],"published-print":{"date-parts":[[2017,12]]},"DOI":"10.1007\/s00383-017-4158-4","type":"journal-article","created":{"date-parts":[[2017,9,22]],"date-time":"2017-09-22T11:04:15Z","timestamp":1506078255000},"page":"1283-1287","update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":21,"title":["A review of long-term outcome and quality of life of patients after Kasai operation surviving with native livers"],"prefix":"10.1007","volume":"33","author":[{"given":"Kenneth K. Y.","family":"Wong","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Carol W. Y.","family":"Wong","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2017,9,22]]},"reference":[{"issue":"1","key":"4158_CR1","doi-asserted-by":"crossref","first-page":"4","DOI":"10.1097\/00005176-200307000-00003","volume":"37","author":"RJ Sokol","year":"2003","unstructured":"Sokol RJ et al (2003) Pathogenesis and outcome of biliary atresia: current concepts. J Pediatr Gastroenterol Nutr 37(1):4\u201321","journal-title":"J Pediatr Gastroenterol Nutr"},{"issue":"9197","key":"4158_CR2","doi-asserted-by":"crossref","first-page":"25","DOI":"10.1016\/S0140-6736(99)03492-3","volume":"355","author":"PJ McKiernan","year":"2000","unstructured":"McKiernan PJ, Baker AJ, Kelly DA (2000) The frequency and outcome of biliary atresia in the UK and Ireland. Lancet 355(9197):25 \u201329","journal-title":"Lancet"},{"key":"4158_CR3","doi-asserted-by":"crossref","unstructured":"Karrer FM et al (1990) Biliary atresia registry, 1976 to 1989. J Pediatr Surg 25","DOI":"10.1016\/0022-3468(90)90222-U"},{"key":"4158_CR4","doi-asserted-by":"crossref","first-page":"28","DOI":"10.1186\/1750-1172-1-28","volume":"1","author":"C Chardot","year":"2006","unstructured":"Chardot C (2006) Biliary atresia. Orphanet J Rare Dis 1:28","journal-title":"Orphanet J Rare Dis"},{"issue":"6","key":"4158_CR5","doi-asserted-by":"crossref","first-page":"F451-F455","DOI":"10.1136\/adc.2009.159780","volume":"94","author":"E Livesey","year":"2009","unstructured":"Livesey E et al (2009) Epidemiology of biliary atresia in England and Wales (1999\u20132006). Arch Dis Child Fetal Neonatal Ed 94(6):F451-F455","journal-title":"Arch Dis Child Fetal Neonatal Ed"},{"issue":"4","key":"4158_CR6","doi-asserted-by":"crossref","first-page":"1233","DOI":"10.1002\/hep.22182","volume":"47","author":"CH Hsiao","year":"2008","unstructured":"Hsiao CH et al (2008) Universal screening for biliary atresia using an infant stool color card in Taiwan. Hepatology 47(4):1233\u20131240","journal-title":"Hepatology"},{"issue":"7","key":"4158_CR7","doi-asserted-by":"crossref","first-page":"997","DOI":"10.1016\/S0022-3468(03)00178-7","volume":"38","author":"M Nio","year":"2003","unstructured":"Nio M et al (2003) Five- and 10-year survival rates after surgery for biliary atresia: a report from the Japanese Biliary Atresia Registry. J Pediatr Surg 38(7):997\u20131000","journal-title":"J Pediatr Surg"},{"issue":"6","key":"4158_CR8","doi-asserted-by":"crossref","first-page":"1285","DOI":"10.1016\/j.jhep.2013.07.021","volume":"59","author":"G Cheng","year":"2013","unstructured":"Cheng G et al (2013) Common genetic variants regulating ADD3 gene expression alter biliary atresia risk. J Hepatol 59(6):1285\u20131291","journal-title":"J Hepatol"},{"issue":"10","key":"4158_CR9","doi-asserted-by":"crossref","first-page":"1076","DOI":"10.1016\/0022-3468(90)90222-U","volume":"25","author":"FM Karrer","year":"1990","unstructured":"Karrer FM et al (1990) Biliary atresia registry, 1976 to 1989. J Pediatr Surg 25(10):1076\u20131080","journal-title":"J Pediatr Surg"},{"key":"4158_CR10","first-page":"733","volume":"13","author":"M Kasai","year":"1959","unstructured":"Kasai M, Suzuki S (1959) A new operation for non-correctable biliary atresia\u2014hepatic portoenterostomy. Shujutsu 13:733\u2013739","journal-title":"Shujutsu"},{"issue":"12","key":"4158_CR11","doi-asserted-by":"crossref","first-page":"1973","DOI":"10.1016\/j.jpedsurg.2006.08.019","volume":"41","author":"M Nio","year":"2006","unstructured":"Nio M et al (2006) Long-term outcome in type I biliary atresia. J Pediatr Surg 41(12):1973\u20131975","journal-title":"J Pediatr Surg"},{"issue":"4","key":"4158_CR12","doi-asserted-by":"crossref","first-page":"577","DOI":"10.1097\/SLA.0b013e3182300950","volume":"254","author":"R Superina","year":"2011","unstructured":"Superina R et al (2011) The anatomic pattern of biliary atresia identified at time of Kasai hepatoportoenterostomy and early postoperative clearance of jaundice are significant predictors of transplant-free survival. Ann Surg 254(4):577\u2013585","journal-title":"Ann Surg"},{"issue":"3","key":"4158_CR13","doi-asserted-by":"crossref","first-page":"606","DOI":"10.1002\/hep.510300330","volume":"30","author":"C Chardot","year":"1999","unstructured":"Chardot C et al (1999) Prognosis of biliary atresia in the era of liver transplantation: French national study from 1986 to 1996. Hepatology 30(3):606\u2013611","journal-title":"Hepatology"},{"issue":"6","key":"4158_CR14","doi-asserted-by":"crossref","first-page":"1682","DOI":"10.1002\/hep.510230652","volume":"23","author":"WF Balistreri","year":"1996","unstructured":"Balistreri WF et al (1996) Biliary atresia: current concepts and research directions. Summary of a symposium. Hepatology 23(6):1682\u20131692","journal-title":"Hepatology"},{"issue":"1 Pt 2","key":"4158_CR15","first-page":"41S","volume":"20","author":"JB Otte","year":"1994","unstructured":"Otte JB et al (1994) Sequential treatment of biliary atresia with Kasai portoenterostomy and liver transplantation: a review. Hepatology 20(1 Pt 2):41S\u201348S","journal-title":"Hepatology"},{"issue":"suppl 8","key":"4158_CR16","first-page":"viii23-viii28","volume":"22","author":"G Engelmann","year":"2007","unstructured":"Engelmann G et al (2007) Indications for pediatric liver transplantation. Data from the Heidelberg pediatric liver transplantation program. Nephrol Dial Transpl 22(suppl 8):viii23-viii28","journal-title":"Nephrol Dial Transpl"},{"issue":"4","key":"4158_CR17","doi-asserted-by":"crossref","first-page":"467","DOI":"10.1016\/j.jpeds.2005.12.054","volume":"148","author":"BL Shneider","year":"2006","unstructured":"Shneider BL et al (2006) A multicenter study of the outcome of biliary atresia in the United States, 1997 to 2000. J Pediatr 148(4):467\u2013474","journal-title":"J Pediatr"},{"issue":"11","key":"4158_CR18","doi-asserted-by":"crossref","first-page":"1482","DOI":"10.1002\/lt.21303","volume":"13","author":"BL Shneider","year":"2007","unstructured":"Shneider BL, Mazariegos GV (2007) Biliary atresia: a transplant perspective. Liver Transpl 13(11):1482\u20131495","journal-title":"Liver Transpl"},{"key":"4158_CR19","doi-asserted-by":"crossref","unstructured":"Bessho K (2015) Complications and quality of life in long-term survivors of biliary atresia with their native livers. J Pediatr","DOI":"10.1016\/j.jpeds.2015.08.041"},{"issue":"4","key":"4158_CR20","first-page":"170","volume":"71","author":"EJ Bijl","year":"2013","unstructured":"Bijl EJ et al (2013) The long-term outcome of the Kasai operation in patients with biliary atresia: a systematic review. Neth J Med 71(4):170\u2013173","journal-title":"Neth J Med"},{"issue":"6","key":"4158_CR21","doi-asserted-by":"crossref","first-page":"892","DOI":"10.1053\/jpsu.2001.23965","volume":"36","author":"ER Howard","year":"2001","unstructured":"Howard ER et al (2001) Survival patterns in biliary atresia and comparison of quality of life of long-term survivors in Japan and England. J Pediatr Surg 36(6):892\u2013897","journal-title":"J Pediatr Surg"},{"issue":"2","key":"4158_CR22","doi-asserted-by":"crossref","first-page":"312","DOI":"10.1016\/S0022-3468(99)90198-7","volume":"34","author":"T Okazaki","year":"1999","unstructured":"Okazaki T et al (1999) Long-term postsurgical outcome of biliary atresia. J Pediatr Surg 34(2):312\u2013315","journal-title":"J Pediatr Surg"},{"issue":"2","key":"4158_CR23","doi-asserted-by":"crossref","first-page":"366","DOI":"10.1002\/hep.20547","volume":"41","author":"P Lykavieris","year":"2005","unstructured":"Lykavieris P et al (2005) Outcome in adulthood of biliary atresia: a study of 63 patients who survived for over 20 years with their native liver. Hepatology 41(2):366\u2013371","journal-title":"Hepatology"},{"issue":"3","key":"4158_CR24","doi-asserted-by":"crossref","first-page":"348","DOI":"10.1097\/00000658-199709000-00014","volume":"226","author":"RP Altman","year":"1997","unstructured":"Altman RP et al (1997) A multivariable risk factor analysis of the portoenterostomy (Kasai) procedure for biliary atresia: twenty-five years of experience from two centers. Ann Surg 226(3):348\u2013353 (discussion 353\u2013355)","journal-title":"Ann Surg"},{"issue":"12","key":"4158_CR25","doi-asserted-by":"crossref","first-page":"1086","DOI":"10.1016\/j.cgh.2011.07.024","volume":"9","author":"W Vries de","year":"2011","unstructured":"de Vries W et al (2011) Twenty-year transplant-free survival rate among patients with biliary atresia. Clin Gastroenterol Hepatol 9(12):1086\u20131091","journal-title":"Clin Gastroenterol Hepatol"},{"issue":"1","key":"4158_CR26","doi-asserted-by":"crossref","first-page":"235","DOI":"10.1620\/tjem.181.235","volume":"181","author":"M Nio","year":"1997","unstructured":"Nio M et al (1997) The outcome of surgery for biliary atresia and the current status of long-term survivors. Tohoku J Exp Med 181(1):235\u2013244","journal-title":"Tohoku J Exp Med"},{"issue":"4","key":"4158_CR27","doi-asserted-by":"crossref","first-page":"443","DOI":"10.1097\/MPG.0b013e318189f2d5","volume":"48","author":"M Shinkai","year":"2009","unstructured":"Shinkai M et al (2009) Long-term outcome of children with biliary atresia who were not transplanted after the Kasai operation: >20-year experience at a children\u2019s hospital. J Pediatr Gastroenterol Nutr 48(4):443\u2013450","journal-title":"J Pediatr Gastroenterol Nutr"},{"issue":"3","key":"4158_CR28","doi-asserted-by":"crossref","first-page":"539","DOI":"10.1016\/j.jpeds.2014.05.038","volume":"165","author":"VL Ng","year":"2014","unstructured":"Ng VL et al (2014) Medical status of 219 children with biliary atresia surviving long-term with their native livers: results from a North American multicenter consortium. J Pediatr 165(3):539\u2013546 e2","journal-title":"J Pediatr"},{"issue":"3","key":"4158_CR29","doi-asserted-by":"crossref","first-page":"510","DOI":"10.1111\/j.1478-3231.2011.02668.x","volume":"32","author":"T Kumagi","year":"2012","unstructured":"Kumagi T et al (2012) Biliary atresia and survival into adulthood without transplantation: a collaborative multicentre clinic review. Liver Int 32(3):510\u2013518","journal-title":"Liver Int"},{"issue":"4","key":"4158_CR30","doi-asserted-by":"crossref","first-page":"590","DOI":"10.1053\/jpsu.2003.50128","volume":"38","author":"LN Bu","year":"2003","unstructured":"Bu LN et al (2003) Prophylactic oral antibiotics in prevention of recurrent cholangitis after the Kasai portoenterostomy. J Pediatr Surg 38(4):590\u2013593","journal-title":"J Pediatr Surg"},{"issue":"1","key":"4158_CR31","doi-asserted-by":"crossref","first-page":"14","DOI":"10.1007\/s12519-008-0003-0","volume":"4","author":"Y Luo","year":"2008","unstructured":"Luo Y, Zheng S (2008) Current concept about postoperative cholangitis in biliary atresia. World J Pediatr 4(1):14\u201319","journal-title":"World J Pediatr"},{"issue":"5","key":"4158_CR32","doi-asserted-by":"crossref","first-page":"654","DOI":"10.1097\/MPG.0000000000000676","volume":"60","author":"TH Lien","year":"2015","unstructured":"Lien TH et al (2015) Use of Lactobacillus casei rhamnosus to prevent cholangitis in biliary atresia after Kasai operation. J Pediatr Gastroenterol Nutr 60(5):654\u2013658","journal-title":"J Pediatr Gastroenterol Nutr"},{"issue":"5","key":"4158_CR33","doi-asserted-by":"crossref","first-page":"567","DOI":"10.1097\/MPG.0b013e31826eb0cf","volume":"55","author":"BL Shneider","year":"2012","unstructured":"Shneider BL et al (2012) Portal hypertension in children and young adults with biliary atresia. J Pediatr Gastroenterol Nutr 55(5):567\u2013573","journal-title":"J Pediatr Gastroenterol Nutr"},{"issue":"12","key":"4158_CR34","doi-asserted-by":"crossref","first-page":"1872","DOI":"10.1038\/ajg.2012.313","volume":"107","author":"L Amitrano","year":"2012","unstructured":"Amitrano L et al (2012) The effectiveness of current acute variceal bleed treatments in unselected cirrhotic patients: refining short-term prognosis and risk factors. Am J Gastroenterol 107(12):1872\u20131878","journal-title":"Am J Gastroenterol"},{"issue":"10","key":"4158_CR35","doi-asserted-by":"crossref","first-page":"1787","DOI":"10.1038\/ajg.2011.173","volume":"106","author":"S Augustin","year":"2011","unstructured":"Augustin S et al (2011) Effectiveness of combined pharmacologic and ligation therapy in high-risk patients with acute esophageal variceal bleeding. Am J Gastroenterol 106(10):1787\u20131795","journal-title":"Am J Gastroenterol"},{"issue":"3","key":"4158_CR36","doi-asserted-by":"crossref","first-page":"922","DOI":"10.1002\/hep.21907","volume":"46","author":"G Garcia-Tsao","year":"2007","unstructured":"Garcia-Tsao G et al (2007) Prevention and management of gastroesophageal varices and variceal hemorrhage in cirrhosis. Hepatology 46(3):922\u2013938","journal-title":"Hepatology"},{"issue":"2","key":"4158_CR37","doi-asserted-by":"crossref","first-page":"178","DOI":"10.1097\/MPG.0b013e318156ff07","volume":"46","author":"ED Fagundes","year":"2008","unstructured":"Fagundes ED et al (2008) Clinical and laboratory predictors of esophageal varices in children and adolescents with portal hypertension syndrome. J Pediatr Gastroenterol Nutr 46(2):178\u2013183","journal-title":"J Pediatr Gastroenterol Nutr"},{"issue":"6","key":"4158_CR38","doi-asserted-by":"crossref","first-page":"2009","DOI":"10.1053\/j.gastro.2011.08.049","volume":"141","author":"JC Gana","year":"2011","unstructured":"Gana JC et al (2011) A clinical prediction rule and platelet count predict esophageal varices in children. Gastroenterology 141(6):2009\u20132016","journal-title":"Gastroenterology"},{"issue":"13","key":"4158_CR39","doi-asserted-by":"crossref","first-page":"2053","DOI":"10.3748\/wjg.v19.i13.2053","volume":"19","author":"MR Adami","year":"2013","unstructured":"Adami MR et al (2013) Noninvasive methods for prediction of esophageal varices in pediatric patients with portal hypertension. World J Gastroenterol 19(13):2053\u20132059","journal-title":"World J Gastroenterol"},{"issue":"2","key":"4158_CR40","doi-asserted-by":"crossref","first-page":"136","DOI":"10.1034\/j.1399-3046.2002.01060.x","volume":"6","author":"GL Klein","year":"2002","unstructured":"Klein GL et al (2002) Hepatic osteodystrophy in chronic cholestasis: evidence for a multifactorial etiology. Pediatr Transpl 6(2):136\u2013140","journal-title":"Pediatr Transpl"},{"issue":"12","key":"4158_CR41","doi-asserted-by":"crossref","first-page":"2373","DOI":"10.1016\/j.jpedsurg.2013.08.009","volume":"48","author":"T Goda","year":"2013","unstructured":"Goda T et al (2013) The most reliable early predictors of outcome in patients with biliary atresia after Kasai\u2019s operation. J Pediatr Surg 48(12):2373\u20132377","journal-title":"J Pediatr Surg"},{"issue":"6","key":"4158_CR42","doi-asserted-by":"crossref","first-page":"1242","DOI":"10.1016\/j.jhep.2014.01.028","volume":"60","author":"H Tomita","year":"2014","unstructured":"Tomita H et al (2014) Long-term native liver fibrosis in biliary atresia: development of a novel scoring system using histology and standard liver tests. J Hepatol 60(6):1242\u20131248","journal-title":"J Hepatol"},{"issue":"2","key":"4158_CR43","doi-asserted-by":"crossref","first-page":"354","DOI":"10.1111\/j.1600-6143.2009.02822.x","volume":"10","author":"S Gupta","year":"2010","unstructured":"Gupta S et al (2010) Improved survival after liver transplantation in patients with hepatopulmonary syndrome. Am J Transpl 10(2):354\u2013363","journal-title":"Am J Transpl"},{"issue":"3","key":"4158_CR44","doi-asserted-by":"crossref","first-page":"441","DOI":"10.1007\/s00595-009-4219-y","volume":"41","author":"K Chen","year":"2011","unstructured":"Chen K, Li B (2011) Reversal of severe hepatopulmonary syndrome in chronic hepatic cirrhosis by living donor liver transplantation: report of two cases. Surg Today 41(3):441\u2013443","journal-title":"Surg Today"},{"issue":"2","key":"4158_CR45","doi-asserted-by":"crossref","first-page":"421","DOI":"10.1016\/j.cld.2014.01.004","volume":"18","author":"R Cartin-Ceba","year":"2014","unstructured":"Cartin-Ceba R, Krowka MJ (2014) Portopulmonary hypertension. Clin Liver Dis 18(2):421\u2013438","journal-title":"Clin Liver Dis"},{"issue":"2","key":"4158_CR46","doi-asserted-by":"crossref","first-page":"367","DOI":"10.1016\/j.jhep.2013.03.026","volume":"59","author":"MJ Krowka","year":"2013","unstructured":"Krowka MJ, Wiesner RH, Heimbach JK (2013) Pulmonary contraindications, indications and MELD exceptions for liver transplantation: a contemporary view and look forward. J Hepatol 59(2):367\u2013374","journal-title":"J Hepatol"},{"issue":"3","key":"4158_CR47","doi-asserted-by":"crossref","first-page":"331","DOI":"10.1097\/MOT.0b013e328346e138","volume":"16","author":"T Ayoub","year":"2011","unstructured":"Ayoub T (2011) Pulmonary hypertension in liver transplant. Curr Opin Organ Transpl 16(3):331\u2013337","journal-title":"Curr Opin Organ Transpl"},{"issue":"3","key":"4158_CR48","doi-asserted-by":"crossref","first-page":"336","DOI":"10.1097\/MPG.0b013e318233ff17","volume":"55","author":"A Vera","year":"2012","unstructured":"Vera A, Villaveces D, Lopez R (2012) Orthotopic liver transplantation for biliary atresia complicated by incidental cholangiocarcinoma. J Pediatr Gastroenterol Nutr 55(3):336\u2013337","journal-title":"J Pediatr Gastroenterol Nutr"},{"issue":"4","key":"4158_CR49","doi-asserted-by":"crossref","first-page":"617","DOI":"10.1016\/j.jpeds.2011.03.004","volume":"159","author":"N Hadzic","year":"2011","unstructured":"Hadzic N et al (2011) Hepatocellular carcinoma in biliary atresia: King\u2019s College Hospital experience. J Pediatr 159(4):617\u2013622 e1","journal-title":"J Pediatr"},{"issue":"4","key":"4158_CR50","doi-asserted-by":"crossref","first-page":"1052-7 e2","DOI":"10.1016\/j.jpeds.2013.04.037","volume":"163","author":"SS Sundaram","year":"2013","unstructured":"Sundaram SS et al (2013) Health related quality of life in patients with biliary atresia surviving with their native liver. J Pediatr 163(4):1052-7 e2","journal-title":"J Pediatr"},{"issue":"2","key":"4158_CR51","doi-asserted-by":"crossref","first-page":"61","DOI":"10.47102\/annals-acadmedsg.V45N2p61","volume":"45","author":"WS Lee","year":"2016","unstructured":"Lee WS, Ong SY (2016) Health-Related Quality of Life in Children with Biliary Atresia Living with Native Livers. Ann Acad Med Singapore 45(2):61\u201368","journal-title":"Ann Acad Med Singapore"},{"issue":"1","key":"4158_CR52","first-page":"60","volume":"25","author":"RC Lind","year":"2015","unstructured":"Lind RC et al (2015) Health status and quality of life in adult biliary atresia patients surviving with their native livers. Eur J Pediatr Surg 25(1):60\u201365","journal-title":"Eur J Pediatr Surg"}],"container-title":["Pediatric Surgery International"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/link.springer.com\/article\/10.1007\/s00383-017-4158-4\/fulltext.html","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1007\/s00383-017-4158-4.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1007\/s00383-017-4158-4.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2024,6,27]],"date-time":"2024-06-27T05:14:21Z","timestamp":1719465261000},"score":1,"resource":{"primary":{"URL":"http:\/\/link.springer.com\/10.1007\/s00383-017-4158-4"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2017,9,22]]},"references-count":52,"journal-issue":{"issue":"12","published-print":{"date-parts":[[2017,12]]}},"alternative-id":["4158"],"URL":"https:\/\/doi.org\/10.1007\/s00383-017-4158-4","relation":{},"ISSN":["0179-0358","1437-9813"],"issn-type":[{"value":"0179-0358","type":"print"},{"value":"1437-9813","type":"electronic"}],"subject":[],"published":{"date-parts":[[2017,9,22]]}}}