{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,6,15]],"date-time":"2026-06-15T19:48:48Z","timestamp":1781552928898,"version":"3.54.5"},"reference-count":18,"publisher":"Springer Science and Business Media LLC","issue":"1","license":[{"start":{"date-parts":[[2023,7,28]],"date-time":"2023-07-28T00:00:00Z","timestamp":1690502400000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0"},{"start":{"date-parts":[[2023,7,28]],"date-time":"2023-07-28T00:00:00Z","timestamp":1690502400000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0"}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["Pediatr Surg Int"],"abstract":"<jats:title>Abstract<\/jats:title><jats:sec>\n                <jats:title>Purpose<\/jats:title>\n                <jats:p>To assess the number, characteristics, and functional short-, and midterm outcomes of patients with rectal atresia (RA) and stenosis (RS) in the ARM-Net registry.<\/jats:p>\n              <\/jats:sec><jats:sec>\n                <jats:title>Methods<\/jats:title>\n                <jats:p>Patients with RA\/RS were retrieved from the ARM-Net registry. Patient characteristics, associated anomalies, surgical approach, and functional bowel outcomes at 1 and 5-year follow-up were assessed.<\/jats:p>\n              <\/jats:sec><jats:sec>\n                <jats:title>Results<\/jats:title>\n                <jats:p>The ARM-Net registry included 2619 patients, of whom 36 (1.3%) had RA\/RS. Median age at follow-up was 7.0\u00a0years (IQR 2.3\u20139.0). Twenty-three patients (63.9%, RA n\u2009=\u200913, RS n\u2009=\u200910) had additional anomalies. PSARP was the most performed reconstructive surgery for both RA (n\u2009=\u20099) and RS (n\u2009=\u20096) patients. At 1-year follow-up, 11\/24 patients with known data (45.8%, RA n\u2009=\u20095, RS n\u2009=\u20096) were constipated, of whom 9 required stool softeners and\/or laxatives. At 5-year follow-up, 8\/9 patients with known data (88.9%, RA n\u2009=\u20094, RS n\u2009=\u20094) were constipated, all requiring laxatives and\/or enema.<\/jats:p>\n              <\/jats:sec><jats:sec>\n                <jats:title>Conclusion<\/jats:title>\n                <jats:p>RA and RS are rare types of ARM, representing 1.3% of patients in the ARM-Net registry. Additional anomalies were present in majority of patients. Different surgical approaches were performed as reconstructive treatment, with constipation occurring in 46% and 89% of the patients at 1 and 5-year follow-up. However, accurate evaluation of long-term functional outcomes remains challenging.<\/jats:p>\n              <\/jats:sec>","DOI":"10.1007\/s00383-023-05518-7","type":"journal-article","created":{"date-parts":[[2023,7,28]],"date-time":"2023-07-28T17:01:49Z","timestamp":1690563709000},"update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":7,"title":["Rectal atresia and rectal stenosis: the ARM-Net Consortium experience"],"prefix":"10.1007","volume":"39","author":[{"given":"Cunera M. 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