{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,11,7]],"date-time":"2026-11-07T19:36:21Z","timestamp":1794080181412,"version":"4.8.0"},"reference-count":62,"publisher":"Springer Science and Business Media LLC","issue":"1","license":[{"start":{"date-parts":[[2024,1,30]],"date-time":"2024-01-30T00:00:00Z","timestamp":1706572800000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.springernature.com\/gp\/researchers\/text-and-data-mining"},{"start":{"date-parts":[[2024,1,30]],"date-time":"2024-01-30T00:00:00Z","timestamp":1706572800000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/www.springernature.com\/gp\/researchers\/text-and-data-mining"}],"funder":[{"DOI":"10.13039\/501100019065","name":"Tianjin Science and Technology Program","doi-asserted-by":"crossref","award":["No.21ZXGWSY00070"],"award-info":[{"award-number":["No.21ZXGWSY00070"]}],"id":[{"id":"10.13039\/501100019065","id-type":"DOI","asserted-by":"crossref"}]},{"name":"Tianjin Applied Basic Research Project","award":["No.22JCZDJC00290"],"award-info":[{"award-number":["No.22JCZDJC00290"]}]}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["Pediatr Surg Int"],"DOI":"10.1007\/s00383-023-05627-3","type":"journal-article","created":{"date-parts":[[2024,1,30]],"date-time":"2024-01-30T08:02:59Z","timestamp":1706601779000},"update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":15,"title":["Biliary atresia: the development, pathological features, and classification of the bile duct"],"prefix":"10.1007","volume":"40","author":[{"given":"Shaowen","family":"Liu","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Tengfei","family":"Li","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Qianhui","family":"Yang","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Xingyuan","family":"Ke","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jianghua","family":"Zhan","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2024,1,30]]},"reference":[{"issue":"3","key":"5627_CR1","doi-asserted-by":"publisher","first-page":"1163","DOI":"10.1002\/hep.29905","volume":"68","author":"JA Bezerra","year":"2018","unstructured":"Bezerra JA, Wells RG, Mack CL et al (2018) Biliary atresia: clinical and research challenges for the twenty-first century. Hepatology 68(3):1163\u20131173. https:\/\/doi.org\/10.1002\/hep.29905","journal-title":"Hepatology"},{"issue":"3","key":"5627_CR2","doi-asserted-by":"publisher","first-page":"483","DOI":"10.1002\/lt.26339","volume":"28","author":"JM Boster","year":"2022","unstructured":"Boster JM, Feldman AG, Mack CL, Sokol RJ, Sundaram SS (2022) Malnutrition in biliary atresia: assessment, management, and outcomes. Liver Transpl 28(3):483\u2013492. https:\/\/doi.org\/10.1002\/lt.26339","journal-title":"Liver Transpl"},{"issue":"Suppl 2","key":"5627_CR3","doi-asserted-by":"publisher","first-page":"204","DOI":"10.1111\/ajt.16978","volume":"22","author":"AJ Kwong","year":"2022","unstructured":"Kwong AJ, Ebel NH, Kim WR et al (2022) OPTN\/SRTR 2020 Annual Data Report: Liver. Am J Transplant 22(Suppl 2):204\u2013309. https:\/\/doi.org\/10.1111\/ajt.16978","journal-title":"Am J Transplant"},{"key":"5627_CR4","doi-asserted-by":"publisher","DOI":"10.1111\/pin.13287","author":"H Tomita","year":"2022","unstructured":"Tomita H, Hara A (2022) Development of extrahepatic bile ducts and mechanisms of tumorigenesis: lessons from mouse models. Pathol Int. https:\/\/doi.org\/10.1111\/pin.13287","journal-title":"Pathol Int"},{"issue":"1","key":"5627_CR5","doi-asserted-by":"publisher","first-page":"62","DOI":"10.1053\/j.gastro.2009.03.035","volume":"137","author":"FP Lemaigre","year":"2009","unstructured":"Lemaigre FP (2009) Mechanisms of liver development: concepts for understanding liver disorders and design of novel therapies. Gastroenterology 137(1):62\u201379. https:\/\/doi.org\/10.1053\/j.gastro.2009.03.035","journal-title":"Gastroenterology"},{"issue":"6","key":"5627_CR6","doi-asserted-by":"publisher","first-page":"628","DOI":"10.1002\/ar.20710","volume":"291","author":"T Roskams","year":"2008","unstructured":"Roskams T, Desmet V (2008) Embryology of extra- and intrahepatic bile ducts, the ductal plate. Anat Rec (Hoboken) 291(6):628\u2013635. https:\/\/doi.org\/10.1002\/ar.20710","journal-title":"Anat Rec (Hoboken)"},{"issue":"8","key":"5627_CR7","doi-asserted-by":"publisher","first-page":"587","DOI":"10.1111\/j.1440-1827.1994.tb01719.x","volume":"44","author":"CE Tan","year":"1994","unstructured":"Tan CE, Moscoso GJ (1994) The developing human biliary system at the porta hepatis level between 29 days and 8 weeks of gestation: a way to understanding biliary atresia. Part 1. Pathol Int 44(8):587\u2013599. https:\/\/doi.org\/10.1111\/j.1440-1827.1994.tb01719.x","journal-title":"Pathol Int"},{"issue":"10","key":"5627_CR8","doi-asserted-by":"publisher","first-page":"832","DOI":"10.1002\/jemt.22406","volume":"77","author":"T Terada","year":"2014","unstructured":"Terada T (2014) Development of extrahepatic bile duct excluding gall bladder in human fetuses: histological, histochemical, and immunohistochemical analysis. Microsc Res Tech 77(10):832\u2013840. https:\/\/doi.org\/10.1002\/jemt.22406","journal-title":"Microsc Res Tech"},{"issue":"2","key":"5627_CR9","doi-asserted-by":"publisher","first-page":"355","DOI":"10.1016\/j.ydbio.2007.05.028","volume":"308","author":"MP Hunter","year":"2007","unstructured":"Hunter MP, Wilson CM, Jiang X et al (2007) The homeobox gene Hhex is essential for proper hepatoblast differentiation and bile duct morphogenesis. Dev Biol 308(2):355\u2013367. https:\/\/doi.org\/10.1016\/j.ydbio.2007.05.028","journal-title":"Dev Biol"},{"issue":"6","key":"5627_CR10","doi-asserted-by":"publisher","DOI":"10.1016\/j.sempedsurg.2022.151235","volume":"31","author":"A Muntean","year":"2022","unstructured":"Muntean A, Davenport M (2022) Biliary atresia & choledochal malformation\u2013Embryological and anatomical considerations. Semin Pediatr Surg 31(6):151235. https:\/\/doi.org\/10.1016\/j.sempedsurg.2022.151235","journal-title":"Semin Pediatr Surg"},{"issue":"1","key":"5627_CR11","doi-asserted-by":"publisher","first-page":"62","DOI":"10.1016\/j.devcel.2009.05.012","volume":"17","author":"JR Spence","year":"2009","unstructured":"Spence JR, Lange AW, Lin SCJ et al (2009) Sox17 regulates organ lineage segregation of ventral foregut progenitor cells. Dev Cell 17(1):62\u201374. https:\/\/doi.org\/10.1016\/j.devcel.2009.05.012","journal-title":"Dev Cell"},{"issue":"8","key":"5627_CR12","doi-asserted-by":"publisher","first-page":"1829","DOI":"10.1242\/dev.129.8.1829","volume":"129","author":"C Coffinier","year":"2002","unstructured":"Coffinier C, Gresh L, Fiette L et al (2002) Bile system morphogenesis defects and liver dysfunction upon targeted deletion of HNF1beta. Development 129(8):1829\u20131838. https:\/\/doi.org\/10.1242\/dev.129.8.1829","journal-title":"Development"},{"issue":"1","key":"5627_CR13","doi-asserted-by":"publisher","first-page":"83","DOI":"10.1038\/ng1273","volume":"36","author":"R Sumazaki","year":"2004","unstructured":"Sumazaki R, Shiojiri N, Isoyama S et al (2004) Conversion of biliary system to pancreatic tissue in Hes1-deficient mice. Nat Genet 36(1):83\u201387. https:\/\/doi.org\/10.1038\/ng1273","journal-title":"Nat Genet"},{"issue":"5","key":"5627_CR14","doi-asserted-by":"publisher","first-page":"1049","DOI":"10.1016\/j.jhep.2018.01.005","volume":"68","author":"EA Ober","year":"2018","unstructured":"Ober EA, Lemaigre FP (2018) Development of the liver: insights into organ and tissue morphogenesis. J Hepatol 68(5):1049\u20131062. https:\/\/doi.org\/10.1016\/j.jhep.2018.01.005","journal-title":"J Hepatol"},{"issue":"7","key":"5627_CR15","doi-asserted-by":"publisher","first-page":"2325","DOI":"10.1053\/j.gastro.2009.02.051","volume":"136","author":"A Antoniou","year":"2009","unstructured":"Antoniou A, Raynaud P, Cordi S et al (2009) Intrahepatic bile ducts develop according to a new mode of tubulogenesis regulated by the transcription factor SOX9. Gastroenterology 136(7):2325\u20132333. https:\/\/doi.org\/10.1053\/j.gastro.2009.02.051","journal-title":"Gastroenterology"},{"key":"5627_CR16","doi-asserted-by":"publisher","first-page":"1186882","DOI":"10.3389\/fgene.2023.1186882","volume":"14","author":"MR Bai","year":"2023","unstructured":"Bai MR, Pei HY, Zhou Y et al (2023) Association analysis and functional follow-up identified common variants of JAG1 accounting for risk to biliary atresia. Front Genet 14:1186882. https:\/\/doi.org\/10.3389\/fgene.2023.1186882","journal-title":"Front Genet"},{"issue":"4","key":"5627_CR17","doi-asserted-by":"publisher","first-page":"1331","DOI":"10.1002\/hep.30912","volume":"71","author":"JM Adams","year":"2020","unstructured":"Adams JM, Huppert KA, Castro EC et al (2020) Sox9 is a modifier of the liver disease severity in a mouse model of Alagille syndrome. Hepatology 71(4):1331\u20131349. https:\/\/doi.org\/10.1002\/hep.30912","journal-title":"Hepatology"},{"issue":"8","key":"5627_CR18","doi-asserted-by":"publisher","first-page":"5780","DOI":"10.1002\/jcp.26304","volume":"233","author":"W Wang","year":"2018","unstructured":"Wang W, Feng Y, Aimaiti Y, Jin X, Mao X, Li D (2018) TGF\u03b2 signaling controls intrahepatic bile duct development may through regulating the Jagged1-Notch-Sox9 signaling axis. J Cell Physiol 233(8):5780\u20135791. https:\/\/doi.org\/10.1002\/jcp.26304","journal-title":"J Cell Physiol"},{"issue":"7","key":"5627_CR19","doi-asserted-by":"publisher","first-page":"843","DOI":"10.1038\/labinvest.2017.29","volume":"97","author":"N Wu","year":"2017","unstructured":"Wu N, Nguyen Q, Wan Y et al (2017) The Hippo signaling functions through the Notch signaling to regulate intrahepatic bile duct development in mammals. Lab Investig 97(7):843\u2013853. https:\/\/doi.org\/10.1038\/labinvest.2017.29","journal-title":"Lab Investig"},{"issue":"8","key":"5627_CR20","doi-asserted-by":"publisher","first-page":"1819","DOI":"10.1242\/dev.129.8.1819","volume":"129","author":"F Clotman","year":"2002","unstructured":"Clotman F, Lannoy VJ, Reber M et al (2002) The onecut transcription factor HNF6 is required for normal development of the biliary tract. Development 129(8):1819\u20131828. https:\/\/doi.org\/10.1242\/dev.129.8.1819","journal-title":"Development"},{"issue":"1","key":"5627_CR21","doi-asserted-by":"publisher","first-page":"233","DOI":"10.1002\/hep.24631","volume":"55","author":"C Vanderpool","year":"2012","unstructured":"Vanderpool C, Sparks EE, Huppert KA, Gannon M, Means AL, Huppert SS (2012) Genetic interactions between hepatocyte nuclear factor-6 and Notch signaling regulate mouse intrahepatic bile duct development in vivo. Hepatology 55(1):233\u2013243. https:\/\/doi.org\/10.1002\/hep.24631","journal-title":"Hepatology"},{"issue":"1","key":"5627_CR22","doi-asserted-by":"publisher","first-page":"420","DOI":"10.1002\/hep.30150","volume":"69","author":"K Sato","year":"2019","unstructured":"Sato K, Marzioni M, Meng F, Francis H, Glaser S, Alpini G (2019) Ductular reaction in liver diseases: pathological mechanisms and translational significances. Hepatology 69(1):420. https:\/\/doi.org\/10.1002\/hep.30150","journal-title":"Hepatology"},{"issue":"3","key":"5627_CR23","doi-asserted-by":"publisher","first-page":"389","DOI":"10.1097\/MOP.0000000000000214","volume":"27","author":"JA Zagory","year":"2015","unstructured":"Zagory JA, Nguyen MV, Wang KS (2015) Recent advances in the pathogenesis and management of biliary atresia. Curr Opin Pediatr 27(3):389\u2013394. https:\/\/doi.org\/10.1097\/MOP.0000000000000214","journal-title":"Curr Opin Pediatr"},{"issue":"6","key":"5627_CR24","doi-asserted-by":"publisher","first-page":"4082","DOI":"10.1007\/s00330-022-09364-4","volume":"33","author":"BN Qi","year":"2023","unstructured":"Qi BN, Lv WJ, Jian JB et al (2023) Insight into microvascular adaptive alterations in the Glisson system of biliary atresia after Kasai portoenterostomy using X-ray phase-contrast CT. Eur Radiol 33(6):4082\u20134093. https:\/\/doi.org\/10.1007\/s00330-022-09364-4","journal-title":"Eur Radiol"},{"issue":"9","key":"5627_CR25","doi-asserted-by":"publisher","first-page":"759","DOI":"10.1097\/MEG.0b013e32832e9df0","volume":"23","author":"Y Dc","year":"2011","unstructured":"Dc Y, Fr P (2011) Morphometrical and immunohistochemical study of intrahepatic bile ducts in biliary atresia. Eur J Gastroenterol Hepatol 23(9):759\u2013765. https:\/\/doi.org\/10.1097\/MEG.0b013e32832e9df0","journal-title":"Eur J Gastroenterol Hepatol"},{"issue":"2","key":"5627_CR26","doi-asserted-by":"publisher","first-page":"G102","DOI":"10.1152\/ajpgi.00452.2016","volume":"313","author":"L Fabris","year":"2017","unstructured":"Fabris L, Spirli C, Cadamuro M, Fiorotto R, Strazzabosco M (2017) Emerging concepts in biliary repair and fibrosis. Am J Physiol Gastrointest Liver Physiol 313(2):G102\u2013G116. https:\/\/doi.org\/10.1152\/ajpgi.00452.2016","journal-title":"Am J Physiol Gastrointest Liver Physiol"},{"issue":"5","key":"5627_CR27","doi-asserted-by":"publisher","first-page":"269","DOI":"10.1038\/s41575-019-0125-y","volume":"16","author":"JM Banales","year":"2019","unstructured":"Banales JM, Huebert RC, Karlsen T, Strazzabosco M, LaRusso NF, Gores GJ (2019) Cholangiocyte pathobiology. Nat Rev Gastroenterol Hepatol 16(5):269\u2013281. https:\/\/doi.org\/10.1038\/s41575-019-0125-y","journal-title":"Nat Rev Gastroenterol Hepatol"},{"issue":"3","key":"5627_CR28","doi-asserted-by":"publisher","first-page":"568","DOI":"10.1002\/hep.510240318","volume":"24","author":"J Cocjin","year":"1996","unstructured":"Cocjin J, Rosenthal P, Buslon V et al (1996) Bile ductule formation in fetal, neonatal, and infant livers compared with extrahepatic biliary atresia. Hepatology 24(3):568\u2013574. https:\/\/doi.org\/10.1002\/hep.510240318","journal-title":"Hepatology"},{"issue":"3","key":"5627_CR29","doi-asserted-by":"publisher","first-page":"275","DOI":"10.1007\/s00383-010-2793-0","volume":"27","author":"R Arii","year":"2011","unstructured":"Arii R, Koga H, Arakawa A et al (2011) How valuable is ductal plate malformation as a predictor of clinical course in postoperative biliary atresia patients? Pediatr Surg Int 27(3):275\u2013277. https:\/\/doi.org\/10.1007\/s00383-010-2793-0","journal-title":"Pediatr Surg Int"},{"issue":"7","key":"5627_CR30","doi-asserted-by":"publisher","first-page":"1169","DOI":"10.1016\/j.jpedsurg.2021.03.039","volume":"56","author":"AHP Nguyen","year":"2021","unstructured":"Nguyen AHP, Pham YHT, Vu GH, Nguyen MH, Hoang TN, Holterman A (2021) Biliary atresia liver histopathological determinants of early post-Kasai outcome. J Pediatr Surg 56(7):1169\u20131173. https:\/\/doi.org\/10.1016\/j.jpedsurg.2021.03.039","journal-title":"J Pediatr Surg"},{"issue":"9","key":"5627_CR31","doi-asserted-by":"publisher","first-page":"837","DOI":"10.1007\/s00383-015-3728-6","volume":"31","author":"M Safwan","year":"2015","unstructured":"Safwan M, Ramachandran P, Vij M, Shanmugam N, Rela M (2015) Impact of ductal plate malformation on survival with native liver in children with biliary atresia. Pediatr Surg Int 31(9):837\u2013843. https:\/\/doi.org\/10.1007\/s00383-015-3728-6","journal-title":"Pediatr Surg Int"},{"issue":"1","key":"5627_CR32","doi-asserted-by":"publisher","first-page":"207","DOI":"10.1007\/s00383-023-05489-9","volume":"39","author":"S Chusilp","year":"2023","unstructured":"Chusilp S, Balsamo F, Li B, Vejchapipat P, Pierro A (2023) Development of liver inflammatory injury in biliary atresia: from basic to clinical research. Pediatr Surg Int 39(1):207. https:\/\/doi.org\/10.1007\/s00383-023-05489-9","journal-title":"Pediatr Surg Int"},{"issue":"4","key":"5627_CR33","doi-asserted-by":"publisher","first-page":"1069","DOI":"10.1002\/hep.1840160434","volume":"16","author":"VJ Desmet","year":"1992","unstructured":"Desmet VJ (1992) Congenital diseases of intrahepatic bile ducts: variations on the theme \u201cductal plate malformation.\u201d Hepatology 16(4):1069\u20131083. https:\/\/doi.org\/10.1002\/hep.1840160434","journal-title":"Hepatology"},{"issue":"2","key":"5627_CR34","doi-asserted-by":"publisher","first-page":"320","DOI":"10.1067\/mpd.2001.117003","volume":"139","author":"Y Low","year":"2001","unstructured":"Low Y, Vijayan V, Tan CE (2001) The prognostic value of ductal plate malformation and other histologic parameters in biliary atresia: an immunohistochemical study. J Pediatr 139(2):320\u2013322. https:\/\/doi.org\/10.1067\/mpd.2001.117003","journal-title":"J Pediatr"},{"issue":"12","key":"5627_CR35","doi-asserted-by":"publisher","first-page":"1601","DOI":"10.1097\/PAS.0000000000000755","volume":"40","author":"P Russo","year":"2016","unstructured":"Russo P, Magee JC, Anders RA et al (2016) Key histopathologic features of liver biopsies that distinguish biliary atresia from other causes of infantile cholestasis and their correlation with outcome: a multicenter study. Am J Surg Pathol 40(12):1601\u20131615. https:\/\/doi.org\/10.1097\/PAS.0000000000000755","journal-title":"Am J Surg Pathol"},{"issue":"9","key":"5627_CR36","doi-asserted-by":"publisher","first-page":"1167","DOI":"10.1007\/s00383-021-04932-z","volume":"37","author":"M Takeda","year":"2021","unstructured":"Takeda M, Sakamoto S, Uchida H et al (2021) The morphological and histopathological assessment of Alagille syndrome with extrahepatic bile duct obstruction: the importance of the differential diagnosis with subgroup \u201co\u201d biliary atresia. Pediatr Surg Int 37(9):1167\u20131174. https:\/\/doi.org\/10.1007\/s00383-021-04932-z","journal-title":"Pediatr Surg Int"},{"issue":"1","key":"5627_CR37","doi-asserted-by":"publisher","first-page":"89","DOI":"10.1002\/hep.32107","volume":"75","author":"SP Amarachintha","year":"2022","unstructured":"Amarachintha SP, Mourya R, Ayabe H et al (2022) Biliary organoids uncover delayed epithelial development and barrier function in biliary atresia. Hepatology 75(1):89\u2013103. https:\/\/doi.org\/10.1002\/hep.32107","journal-title":"Hepatology"},{"issue":"8","key":"5627_CR38","doi-asserted-by":"publisher","first-page":"664","DOI":"10.1111\/hepr.13060","volume":"48","author":"R Frassetto","year":"2018","unstructured":"Frassetto R, Parolini F, Marceddu S et al (2018) Intrahepatic bile duct primary cilia in biliary atresia. Hepatol Res 48(8):664\u2013674. https:\/\/doi.org\/10.1111\/hepr.13060","journal-title":"Hepatol Res"},{"key":"5627_CR39","doi-asserted-by":"publisher","DOI":"10.1016\/j.ebiom.2021.103530","volume":"71","author":"WY Lam","year":"2021","unstructured":"Lam WY, Tang CSM, So MT et al (2021) Identification of a wide spectrum of ciliary gene mutations in nonsyndromic biliary atresia patients implicates ciliary dysfunction as a novel disease mechanism. EBioMedicine 71:103530. https:\/\/doi.org\/10.1016\/j.ebiom.2021.103530","journal-title":"EBioMedicine"},{"issue":"2","key":"5627_CR40","doi-asserted-by":"publisher","first-page":"99","DOI":"10.1620\/tjem.115.99","volume":"115","author":"T Chiba","year":"1975","unstructured":"Chiba T, Kasai M, Sasano N (1975) Reconstruction of intrahepatic bile ducts in congenital biliary atresia. Tohoku J Exp Med 115(2):99\u2013110. https:\/\/doi.org\/10.1620\/tjem.115.99","journal-title":"Tohoku J Exp Med"},{"issue":"7","key":"5627_CR41","doi-asserted-by":"publisher","first-page":"997","DOI":"10.1016\/s0022-3468(03)00178-7","volume":"38","author":"M Nio","year":"2003","unstructured":"Nio M, Ohi R, Miyano T et al (2003) Five- and 10-year survival rates after surgery for biliary atresia: a report from the Japanese Biliary Atresia Registry. J Pediatr Surg 38(7):997\u20131000. https:\/\/doi.org\/10.1016\/s0022-3468(03)00178-7","journal-title":"J Pediatr Surg"},{"issue":"6","key":"5627_CR42","doi-asserted-by":"publisher","first-page":"429","DOI":"10.1016\/j.asjsur.2016.04.003","volume":"40","author":"J Zhan","year":"2017","unstructured":"Zhan J, Feng J, Chen Y, Liu J, Wang B (2017) Incidence of biliary atresia associated congenital malformations: a retrospective multicenter study in China. Asian J Surg 40(6):429\u2013433. https:\/\/doi.org\/10.1016\/j.asjsur.2016.04.003","journal-title":"Asian J Surg"},{"key":"5627_CR43","first-page":"327","volume":"12","author":"M Kasai","year":"1976","unstructured":"Kasai M, Sawaguchi M, Akiyama T et al (1976) A proposal for a new classification of biliary atresia. JJSPS 12:327\u2013331","journal-title":"JJSPS"},{"issue":"4","key":"5627_CR44","doi-asserted-by":"publisher","first-page":"577","DOI":"10.1097\/SLA.0b013e3182300950","volume":"254","author":"R Superina","year":"2011","unstructured":"Superina R, Magee JC, Brandt ML et al (2011) The anatomic pattern of biliary atresia identified at time of Kasai hepatoportoenterostomy and early postoperative clearance of jaundice are significant predictors of transplant-free survival. Ann Surg 254(4):577\u2013585. https:\/\/doi.org\/10.1097\/SLA.0b013e3182300950","journal-title":"Ann Surg"},{"issue":"11","key":"5627_CR45","doi-asserted-by":"publisher","first-page":"931","DOI":"10.1002\/jhbp.989","volume":"28","author":"H Sasaki","year":"2021","unstructured":"Sasaki H, Nio M, Ando H et al (2021) Anatomical patterns of biliary atresia including hepatic radicles at the porta hepatis influence short- and long-term prognoses. J Hepatobiliary Pancreat Sci 28(11):931\u2013941. https:\/\/doi.org\/10.1002\/jhbp.989","journal-title":"J Hepatobiliary Pancreat Sci"},{"issue":"11","key":"5627_CR46","doi-asserted-by":"publisher","first-page":"1411","DOI":"10.1016\/j.cgh.2006.07.005","volume":"4","author":"AM Muise","year":"2006","unstructured":"Muise AM, Turner D, Wine E, Kim P, Marcon M, Ling SC (2006) Biliary atresia with choledochal cyst: implications for classification. Clin Gastroenterol Hepatol 4(11):1411\u20131414. https:\/\/doi.org\/10.1016\/j.cgh.2006.07.005","journal-title":"Clin Gastroenterol Hepatol"},{"issue":"2","key":"5627_CR47","doi-asserted-by":"publisher","first-page":"217","DOI":"10.1007\/s00383-021-05030-w","volume":"38","author":"Z Qipeng","year":"2022","unstructured":"Qipeng Z, Fang Y, Yilin Z et al (2022) The favorable prognosis of cystic biliary atresia may be related to early surgery and mild liver pathological changes. Pediatr Surg Int 38(2):217\u2013224. https:\/\/doi.org\/10.1007\/s00383-021-05030-w","journal-title":"Pediatr Surg Int"},{"issue":"6","key":"5627_CR48","doi-asserted-by":"publisher","first-page":"1209","DOI":"10.1016\/j.jhep.2013.01.040","volume":"58","author":"C Chardot","year":"2013","unstructured":"Chardot C, Buet C, Serinet MO et al (2013) Improving outcomes of biliary atresia: French National Series 1986\u20132009. J Hepatol 58(6):1209\u20131217. https:\/\/doi.org\/10.1016\/j.jhep.2013.01.040","journal-title":"J Hepatol"},{"issue":"3","key":"5627_CR49","doi-asserted-by":"publisher","first-page":"175","DOI":"10.1053\/j.sempedsurg.2012.05.010","volume":"21","author":"M Davenport","year":"2012","unstructured":"Davenport M (2012) Biliary atresia: clinical aspects. Semin Pediatr Surg 21(3):175\u2013184. https:\/\/doi.org\/10.1053\/j.sempedsurg.2012.05.010","journal-title":"Semin Pediatr Surg"},{"issue":"9","key":"5627_CR50","doi-asserted-by":"publisher","first-page":"4841","DOI":"10.3390\/ijms23094841","volume":"23","author":"L He","year":"2022","unstructured":"He L, Chung PHY, Lui VCH, Tang CSM, Tam PKH (2022) Current understanding in the clinical characteristics and molecular mechanisms in different subtypes of biliary atresia. Int J Mol Sci 23(9):4841. https:\/\/doi.org\/10.3390\/ijms23094841","journal-title":"Int J Mol Sci"},{"issue":"3","key":"5627_CR51","doi-asserted-by":"publisher","first-page":"548","DOI":"10.1016\/j.surg.2017.04.013","volume":"162","author":"A Kerola","year":"2017","unstructured":"Kerola A, Lampela H, Lohi J et al (2017) Molecular signature of active fibrogenesis prevails in biliary atresia after successful portoenterostomy. Surgery 162(3):548\u2013556. https:\/\/doi.org\/10.1016\/j.surg.2017.04.013","journal-title":"Surgery"},{"issue":"1","key":"5627_CR52","doi-asserted-by":"publisher","first-page":"1","DOI":"10.1055\/s-0038-1668146","volume":"29","author":"ZH Wong","year":"2019","unstructured":"Wong ZH, Davenport M (2019) What happens after kasai for biliary atresia? A European Multicenter Survey. Eur J Pediatr Surg 29(1):1\u20136. https:\/\/doi.org\/10.1055\/s-0038-1668146","journal-title":"Eur J Pediatr Surg"},{"issue":"10","key":"5627_CR53","doi-asserted-by":"publisher","first-page":"1739","DOI":"10.1016\/j.jpedsurg.2015.03.001","volume":"50","author":"A Zani","year":"2015","unstructured":"Zani A, Quaglia A, Hadzi\u0107 N, Zuckerman M, Davenport M (2015) Cytomegalovirus-associated biliary atresia: an aetiological and prognostic subgroup. J Pediatr Surg 50(10):1739\u20131745. https:\/\/doi.org\/10.1016\/j.jpedsurg.2015.03.001","journal-title":"J Pediatr Surg"},{"key":"5627_CR54","doi-asserted-by":"publisher","DOI":"10.3389\/fped.2021.710450","volume":"9","author":"Y Zhao","year":"2021","unstructured":"Zhao Y, Xu X, Liu G, Yang F, Zhan J (2021) Prognosis of biliary atresia associated with cytomegalovirus: a meta-analysis. Front Pediatr 9:710450. https:\/\/doi.org\/10.3389\/fped.2021.710450","journal-title":"Front Pediatr"},{"issue":"9","key":"5627_CR55","doi-asserted-by":"publisher","first-page":"1941","DOI":"10.1016\/j.jpedsurg.2018.12.014","volume":"54","author":"F Parolini","year":"2019","unstructured":"Parolini F, Hadzic N, Davenport M (2019) Adjuvant therapy of cytomegalovirus IgM + ve associated biliary atresia: Prima facie evidence of effect. J Pediatr Surg 54(9):1941\u20131945. https:\/\/doi.org\/10.1016\/j.jpedsurg.2018.12.014","journal-title":"J Pediatr Surg"},{"issue":"8","key":"5627_CR56","doi-asserted-by":"publisher","first-page":"773","DOI":"10.1007\/s00383-007-1948-0","volume":"23","author":"R Lal","year":"2007","unstructured":"Lal R, Prasad DKV, Krishna P et al (2007) Biliary atresia with a \u201ccyst at porta\u201d: management and outcome as per the cholangiographic anatomy. Pediatr Surg Int 23(8):773\u2013778. https:\/\/doi.org\/10.1007\/s00383-007-1948-0","journal-title":"Pediatr Surg Int"},{"issue":"10","key":"5627_CR57","doi-asserted-by":"publisher","first-page":"931","DOI":"10.1007\/s00383-015-3771-3","volume":"31","author":"M Nio","year":"2015","unstructured":"Nio M, Wada M, Sasaki H, Tanaka H (2015) Does hepatic hilum morphology influence long-term prognosis in type I\/I cyst biliary atresia? Pediatr Surg Int 31(10):931\u2013936. https:\/\/doi.org\/10.1007\/s00383-015-3771-3","journal-title":"Pediatr Surg Int"},{"issue":"5","key":"5627_CR58","doi-asserted-by":"publisher","first-page":"751","DOI":"10.1038\/modpathol.2011.212","volume":"25","author":"AS Chu","year":"2012","unstructured":"Chu AS, Russo PA, Wells RG (2012) Cholangiocyte cilia are abnormal in syndromic and non-syndromic biliary atresia. Mod Pathol 25(5):751\u2013757. https:\/\/doi.org\/10.1038\/modpathol.2011.212","journal-title":"Mod Pathol"},{"issue":"3","key":"5627_CR59","doi-asserted-by":"publisher","DOI":"10.1136\/wjps-2021-000346","volume":"5","author":"X Xu","year":"2022","unstructured":"Xu X, Dou R, Zhao S et al (2022) Outcomes of biliary atresia splenic malformation (BASM) syndrome following Kasai operation: a systematic review and meta-analysis. World J Pediatr Surg 5(3):e000346. https:\/\/doi.org\/10.1136\/wjps-2021-000346","journal-title":"World J Pediatr Surg"},{"issue":"3","key":"5627_CR60","doi-asserted-by":"publisher","first-page":"899","DOI":"10.1002\/hep.30515","volume":"70","author":"JP Berauer","year":"2019","unstructured":"Berauer JP, Mezina AI, Okou DT et al (2019) Identification of polycystic kidney disease 1 like 1 gene variants in children with biliary atresia splenic malformation syndrome. Hepatology 70(3):899\u2013910. https:\/\/doi.org\/10.1002\/hep.30515","journal-title":"Hepatology"},{"issue":"1","key":"5627_CR61","doi-asserted-by":"publisher","first-page":"e24","DOI":"10.1097\/MPG.0000000000002531","volume":"70","author":"E Gonzales","year":"2020","unstructured":"Gonzales E, Davit-Spraul A, Jacquemin E (2020) A novel CFC1 mutation in a family with heterotaxy and biliary atresia splenic malformation syndromes. J Pediatr Gastroenterol Nutr 70(1):e24\u2013e25. https:\/\/doi.org\/10.1097\/MPG.0000000000002531","journal-title":"J Pediatr Gastroenterol Nutr"},{"issue":"1","key":"5627_CR62","doi-asserted-by":"publisher","first-page":"68","DOI":"10.1136\/archdischild-2020-319122","volume":"106","author":"B Aldeiri","year":"2021","unstructured":"Aldeiri B, Giamouris V, Pushparajah K, Miller O, Baker A, Davenport M (2021) Cardiac-associated biliary atresia (CABA): a prognostic subgroup. Arch Dis Child 106(1):68\u201372. https:\/\/doi.org\/10.1136\/archdischild-2020-319122","journal-title":"Arch Dis Child"}],"container-title":["Pediatric Surgery International"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1007\/s00383-023-05627-3.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/link.springer.com\/article\/10.1007\/s00383-023-05627-3\/fulltext.html","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1007\/s00383-023-05627-3.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2024,12,12]],"date-time":"2024-12-12T17:06:46Z","timestamp":1734023206000},"score":1,"resource":{"primary":{"URL":"https:\/\/link.springer.com\/10.1007\/s00383-023-05627-3"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2024,1,30]]},"references-count":62,"journal-issue":{"issue":"1","published-online":{"date-parts":[[2024,12]]}},"alternative-id":["5627"],"URL":"https:\/\/doi.org\/10.1007\/s00383-023-05627-3","relation":{},"ISSN":["1437-9813"],"issn-type":[{"value":"1437-9813","type":"electronic"}],"subject":[],"published":{"date-parts":[[2024,1,30]]},"assertion":[{"value":"26 December 2023","order":1,"name":"accepted","label":"Accepted","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"30 January 2024","order":2,"name":"first_online","label":"First Online","group":{"name":"ArticleHistory","label":"Article History"}},{"order":1,"name":"Ethics","group":{"name":"EthicsHeading","label":"Declarations"}},{"value":"The authors declare no competing interests.","order":2,"name":"Ethics","group":{"name":"EthicsHeading","label":"Conflict of interest"}},{"value":"Not applicable.","order":3,"name":"Ethics","group":{"name":"EthicsHeading","label":"Ethical approval"}},{"value":"Not applicable.","order":4,"name":"Ethics","group":{"name":"EthicsHeading","label":"Informed consent"}}],"article-number":"42"}}