{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,1,6]],"date-time":"2026-01-06T05:27:45Z","timestamp":1767677265820},"reference-count":11,"publisher":"Springer Science and Business Media LLC","issue":"2","license":[{"start":{"date-parts":[[2022,5,16]],"date-time":"2022-05-16T00:00:00Z","timestamp":1652659200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0"},{"start":{"date-parts":[[2022,5,16]],"date-time":"2022-05-16T00:00:00Z","timestamp":1652659200000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0"}],"funder":[{"name":"Universit\u00e4tsklinikum Bonn"}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["Z Rheumatol"],"published-print":{"date-parts":[[2024,3]]},"abstract":"<jats:title>Zusammenfassung<\/jats:title><jats:p>Die eosinophile Fasziitis (EF, auch Shulman-Syndrom) ist eine seltene Erkrankung des Bindegewebes mit entz\u00fcndlicher Verdickung der Faszien sowie Schwellung und Verh\u00e4rtung der Haut. Betroffen sind v.\u00a0a. die distalen Extremit\u00e4ten. Typische klinische Befunde stellen eine lokalisierte Schwellung und Verh\u00e4rtung der Haut sowie das Groove-Sign (deutsch: Rillenzeichen\/negatives Venenzeichen\/Matratzenph\u00e4nomen) dar. Der Goldstandard f\u00fcr die Diagnosesicherung ist bisher der bioptische Nachweis entz\u00fcndlich verdickter Faszien. In der Literatur wird alternativ die Diagnosesicherung durch MRT-Bildgebung diskutiert. Wir berichten \u00fcber einen Fall von asymmetrischer EF bei einem 54\u00a0Jahre alten, m\u00e4nnlichen Deutschen. Die Vorstellung erfolgte mit schmerzhafter Verh\u00e4rtung im Bereich des rechten Unterarms sowie charakteristischem Groove-Sign und einer Bewegungseinschr\u00e4nkung der rechten Hand. Im Blutbild zeigte sich eine Eosinophilie mit 0,57\u202fG\/l bzw. 9,6\u202f% (norm. 0,05\u20130,5\u202fG\/l und 0,5\u20135,5\u202f%), ANAs und ENAs waren negativ. Die Diagnosesicherung erfolgte histologisch, zus\u00e4tzlich konnten wir verdickte Faszien sowohl im MRT als auch in der Sonographie nachweisen. Im Verlauf manifestierte sich die EF auch am linken Malleolus lateralis. Die Therapie erfolgte mit Prednisolon und Methotrexat.<\/jats:p>","DOI":"10.1007\/s00393-022-01207-3","type":"journal-article","created":{"date-parts":[[2022,5,16]],"date-time":"2022-05-16T12:03:01Z","timestamp":1652702581000},"page":"134-138","update-policy":"http:\/\/dx.doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":2,"title":["Darstellung der eosinophilen Fasziitis in Ultraschall und MRT (Magnetresonanztomographie): ein Fallbericht","Imaging of eosinophilic fasciitis in ultrasound and MRI (magnetic resonance imaging): a\u00a0case report"],"prefix":"10.1007","volume":"83","author":[{"given":"Nicolas","family":"Gerritzen","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Jana","family":"Ziob","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Peter","family":"Brossart","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Valentin S.","family":"Sch\u00e4fer","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"297","published-online":{"date-parts":[[2022,5,16]]},"reference":[{"key":"1207_CR1","doi-asserted-by":"publisher","first-page":"e1","DOI":"10.1111\/ddg.130_12724","volume":"14","author":"A Kreuter","year":"2016","unstructured":"Kreuter\u00a0A, Krieg\u00a0T, Worm\u00a0M et\u00a0al (2016) Deutsche Leitlinie zur Diagnostik und Therapie der zirkumskripten Sklerodermie. 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F\u00fcr die aufgef\u00fchrten Studien gelten die jeweils dort angegebenen ethischen Richtlinien. F\u00fcr Bildmaterial oder anderweitige Angaben innerhalb des Manuskripts, \u00fcber die Patienten zu identifizieren sind, liegt von ihnen und\/oder ihren gesetzlichen Vertretern eine schriftliche Einwilligung vor.","order":3,"name":"Ethics","group":{"name":"EthicsHeading","label":"Interessenkonflikt"}}]}}