{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,29]],"date-time":"2026-09-29T01:55:59Z","timestamp":1790646959800,"version":"4.1.0"},"reference-count":28,"publisher":"Springer Science and Business Media LLC","license":[{"start":{"date-parts":[[2026,9,28]],"date-time":"2026-09-28T00:00:00Z","timestamp":1790553600000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0\/deed.de"},{"start":{"date-parts":[[2026,9,28]],"date-time":"2026-09-28T00:00:00Z","timestamp":1790553600000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0\/deed.de"}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["Z Rheumatol"],"abstract":"<jats:title>Zusammenfassung<\/jats:title>\n                  <jats:sec>\n                    <jats:title>Hintergrund<\/jats:title>\n                    <jats:p>Fortschritte in Diagnostik, Molekulargenetik und zielgerichteten Therapien haben die Versorgung von Patient:innen mit autoinflammatorischen Erkrankungen (AID) optimiert. Dadurch erreichen mehr Kinder und Jugendliche mit AID das Erwachsenenalter, wodurch die Transition in die internistische Rheumatologie an Bedeutung gewinnt.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Ziel der Arbeit<\/jats:title>\n                    <jats:p>Darstellung der Besonderheiten der Transition von Jugendlichen mit AID von der p\u00e4diatrischen in die internistische Rheumatologie sowie Zusammenfassung aktueller Empfehlungen.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Material und Methoden<\/jats:title>\n                    <jats:p>Narrative \u00dcbersichtsarbeit auf Basis publizierter Daten (Leitlinien, Konsensuspapiere, Register\u2011, Kohortenstudien und Surveys).<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Ergebnisse<\/jats:title>\n                    <jats:p>Die Transition von Jugendlichen mit AID erfordert einen fr\u00fchzeitigen, strukturierten und multidisziplin\u00e4ren Prozess, der medizinische, psychosoziale und edukative Aspekte ber\u00fccksichtigt, Selbstmanagement und Eigenverantwortung f\u00f6rdert sowie die professionelle Therapiekontinuit\u00e4t sichert. Empfehlungen f\u00fcr chronisch-entz\u00fcndlich rheumatische Erkrankungen sind grunds\u00e4tzlich auf AID \u00fcbertragbar. AID weisen jedoch Besonderheiten wie genetische Ursachen, relevante Komorbidit\u00e4ten und h\u00e4ufig lebenslange, teils Off-label-Therapien auf, die spezifische Anforderungen an den Transitionsprozess stellen. AID-spezifische Empfehlungen und Daten zur Wirksamkeit strukturierter Transitionsprogramme sind bislang begrenzt.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Diskussion<\/jats:title>\n                    <jats:p>Die Transition von Patient:innen mit AID ist anspruchsvoll. Eine enge Zusammenarbeit zwischen p\u00e4diatrischer und internistischer Rheumatologie sowie patientenzentrierte Transitionskonzepte sind entscheidend, um Krankheitskontrolle, Lebensqualit\u00e4t und gesellschaftliche Teilhabe zu sichern.<\/jats:p>\n                  <\/jats:sec>","DOI":"10.1007\/s00393-026-01871-9","type":"journal-article","created":{"date-parts":[[2026,9,28]],"date-time":"2026-09-28T12:22:20Z","timestamp":1790598140000},"update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":0,"title":["Junge Erwachsene mit Autoinflammation \u2013 was kommt auf Rheumatolog:innen zu?","Young adults with autoinflammation\u2014What can rheumatologists expect?"],"prefix":"10.1007","author":[{"ORCID":"https:\/\/orcid.org\/0000-0001-9641-3691","authenticated-orcid":false,"given":"Marc-Alexander","family":"Oestreich","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jessica","family":"Pauz","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mary-Louise","family":"Daly","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Martin","family":"Krusche","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Tatjana","family":"Welzel","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2026,9,28]]},"reference":[{"key":"1871_CR1","doi-asserted-by":"publisher","first-page":"177","DOI":"10.4081\/reumatismo.2019.1192","volume":"71","author":"T Borges","year":"2020","unstructured":"Borges\u00a0T, Barbosa\u00a0A, Silva\u00a0S (2020) Adult-onset systemic autoinflammatory disorders: a clinical approach. 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