{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,24]],"date-time":"2026-10-24T07:16:27Z","timestamp":1792826187076,"version":"4.5.0"},"reference-count":52,"publisher":"Springer Science and Business Media LLC","issue":"1","license":[{"start":{"date-parts":[[2007,6,14]],"date-time":"2007-06-14T00:00:00Z","timestamp":1181779200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.springer.com\/tdm"},{"start":{"date-parts":[[2007,6,14]],"date-time":"2007-06-14T00:00:00Z","timestamp":1181779200000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/www.springer.com\/tdm"}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["Acta Neuropathol"],"published-print":{"date-parts":[[2007,7]]},"DOI":"10.1007\/s00401-007-0236-3","type":"journal-article","created":{"date-parts":[[2007,6,14]],"date-time":"2007-06-14T06:27:31Z","timestamp":1181802451000},"page":"31-38","update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":251,"title":["Frontotemporal lobar degeneration: clinical and pathological relationships"],"prefix":"10.1007","volume":"114","author":[{"given":"Julie","family":"Snowden","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"David","family":"Neary","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"David","family":"Mann","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2007,6,14]]},"reference":[{"key":"236_CR1","doi-asserted-by":"publisher","first-page":"602","DOI":"10.1016\/j.bbrc.2006.10.093","volume":"351","author":"T Arai","year":"2006","unstructured":"Arai T, Hasegawa M, Akiyama H, Ikeda K, Nonaka T, Mori H, Mann D, Tsuchiya K, Yoshida M, Hashizume Y, T Oda (2006) TDP-43 is a component of ubiquitin-positive tau-negative inclusions in frontotemporal lobar degeneration and amyotrophic lateral sclerosis. Biochem Biophys Res Commun 351:602\u2013611","journal-title":"Biochem Biophys Res Commun"},{"key":"236_CR2","doi-asserted-by":"publisher","first-page":"916","DOI":"10.1038\/nature05016","volume":"442","author":"M Baker","year":"2006","unstructured":"Baker M, Mackenzie IR, Pickering-Brown SM, Gass J, Rademakers R, Lindholm C, Snowden J, Adamson J, Sadovnick AD, Rollinson S, Cannon A, Dwosh E, Neary D, Melquist S, Richardson A, Dickson D, Berger Z, Eriksen J, Robinson T, Zehr C, Dickey CA, Crook R, McGowan E, Mann D, Boeve B, Feldman H, Hutton M (2006) Mutations in Progranulin cause tau-negative frontotemporal dementia linked to chromosome 17. Nature 442:916\u2013919","journal-title":"Nature"},{"key":"236_CR3","doi-asserted-by":"crossref","first-page":"539","DOI":"10.1001\/archneur.1997.00550170021010","volume":"54","author":"H Basun","year":"1997","unstructured":"Basun H, Almkvist O, Axelman K, Brun A, Campbell TA, Collinge J, Forsell C, Froelich S, Wahlund LO, Wetterberg L, Lannfelt L (1997) Clinical characteristics of a chromosome 17-linked rapidly progressive familial frontotemporal dementia. Arch Neurol 54:539\u2013544","journal-title":"Arch Neurol"},{"key":"236_CR4","doi-asserted-by":"crossref","unstructured":"Cairns NJ, Bigio EH, Mackenzie IRA, Hatanpaa KJ, White CL, Schneider JA, Morris JC, Lee VM-Y, Trojanowski JQ, Mann DMA (2007) Neuropathological diagnostic criteria and nosology of the frontotemporal lobar degenerations: consensus criteria of the Consortium for frontotemporal lobar degeneration. Acta Neuropathol (this issue)","DOI":"10.1007\/s00401-007-0237-2"},{"key":"236_CR5","doi-asserted-by":"publisher","first-page":"200","DOI":"10.1002\/ana.410330210","volume":"33","author":"RJ Caselli","year":"1993","unstructured":"Caselli RJ, Windebank AJ, Petersen RC, Komori T, Parisi JE, Okazaki H, Kokmen E, Iverson R, Dinapoli RP, Graff-Radford NR (1993) Rapidly progressive aphasic dementia and motor neuron disease. Ann Neurol 33:200\u2013207","journal-title":"Ann Neurol"},{"key":"236_CR6","doi-asserted-by":"publisher","first-page":"21","DOI":"10.1159\/000074139","volume":"17","author":"M Catani","year":"2004","unstructured":"Catani M, Piccirilli M, Geloso MC, Cherubino A, Finali G, Pelliccioli G, Senin U, Mecocci P (2004) Rapidly progressive aphasic dementia with motor neuron disease: a distinctive clinical entity. Dement Geriatr Cogn Disord 17:21\u201328","journal-title":"Dement Geriatr Cogn Disord"},{"key":"236_CR7","doi-asserted-by":"publisher","first-page":"521","DOI":"10.1007\/s00401-006-0189-y","volume":"113","author":"Y Davidson","year":"2007","unstructured":"Davidson Y, Kelley T, Mackenzie IRA, Pickering-Brown S, Du Plessis D, Neary D, Snowden JS, Mann DMA (2007) Ubiquitinated pathological lesions in frontotemporal lobar degeneration contain the TAR DNA-binding protein, TDP-43. Acta Neuropathol (Berl) 113:521\u2013533","journal-title":"Acta Neuropathol (Berl)"},{"key":"236_CR8","doi-asserted-by":"crossref","first-page":"171","DOI":"10.1016\/S0010-9452(86)80041-7","volume":"22","author":"E De Renzi","year":"1986","unstructured":"De Renzi E (1986) Slowly progressive visual agnosia or apraxia without dementia. Cortex 22:171\u2013180","journal-title":"Cortex"},{"key":"236_CR9","first-page":"101","volume":"2","author":"J Dick","year":"1989","unstructured":"Dick J, Snowden JS, Goulding PJ, Northen B, Neary D (1989) Slowly progressive apraxia. Behav Neurol 2:101\u2013114","journal-title":"Behav Neurol"},{"key":"236_CR10","doi-asserted-by":"publisher","first-page":"419","DOI":"10.1007\/s00401-003-0756-4","volume":"106","author":"I Ferrer","year":"2003","unstructured":"Ferrer I, Hernandez I, Boada M, Llorente A, Rey MJ, Cardozo A, Ezquerra M, Puig B (2003) Primary progressive aphasia as the initial manifestation of corticobasal degeneration and unusual tauopathies. Acta Neuropathol (Berl) 106:419\u2013435","journal-title":"Acta Neuropathol (Berl)"},{"key":"236_CR11","doi-asserted-by":"publisher","first-page":"952","DOI":"10.1002\/ana.20873","volume":"59","author":"MS Forman","year":"2006","unstructured":"Forman MS, Farmer J, Johnson JK, Clark CM, Arnold SE, Coslett HB, Chatterjee A, Hurtig HI, Karlawish JH, Rosen HJ, VanDeerlin V, Lee VM, Miller BL, Trojanowski JQ, Grossman M (2006) Frontotemporal dementia: clinicopathological correlations. Ann Neurol 59:952\u2013962","journal-title":"Ann Neurol"},{"key":"236_CR12","doi-asserted-by":"crossref","first-page":"467","DOI":"10.1212\/WNL.47.2.467","volume":"47","author":"T Fukui","year":"1996","unstructured":"Fukui T, Sugita K, Kawamura M, Shiota J, Nakano I (1996) Primary progressive apraxia in Pick\u2019s disease: a clinicopathologic study. Neurology 47:467\u2013473","journal-title":"Neurology"},{"key":"236_CR13","doi-asserted-by":"publisher","first-page":"484","DOI":"10.1093\/brain\/123.3.484","volume":"123","author":"CJ Galton","year":"2000","unstructured":"Galton CJ, Patterson K, Xuereb JH, Hodges JR (2000) Atypical and typical presentations of Alzheimer\u2019s disease: a clinical, neuropsychological, neuroimaging and pathological study of 13 cases. Brain 123: 484\u2013498","journal-title":"Brain"},{"key":"236_CR14","doi-asserted-by":"publisher","first-page":"1783","DOI":"10.1093\/brain\/115.6.1783","volume":"115","author":"JR Hodges","year":"1992","unstructured":"Hodges JR, Patterson K, Oxbury S, Funnell E (1992) Semantic dementia. progressive fluent aphasia with temporal lobe atrophy. Brain 115:1783\u20131806","journal-title":"Brain"},{"key":"236_CR15","doi-asserted-by":"publisher","first-page":"399","DOI":"10.1002\/ana.20203","volume":"56","author":"JR Hodges","year":"2004","unstructured":"Hodges JR, Davies RR, Xuereb JH, Casey B, Broe M, Bak TH, Kril JJ, Halliday GM (2004) Clinicopathological correlates in frontotemporal dementia. Ann Neurol 56:399\u2013406","journal-title":"Ann Neurol"},{"key":"236_CR16","doi-asserted-by":"publisher","first-page":"441","DOI":"10.1016\/0028-3932(94)00127-B","volume":"33","author":"JR Hodges","year":"1995","unstructured":"Hodges JR, Patterson K (1995) Is semantic memory consistently impaired early in the course of Alzheimer\u2019s disease? Neuroanatomical and diagnostic implications. Neuropsychologia 33:441\u2013459","journal-title":"Neuropsychologia"},{"key":"236_CR17","doi-asserted-by":"publisher","first-page":"702","DOI":"10.1038\/31508","volume":"393","author":"M Hutton","year":"1998","unstructured":"Hutton M, Lendon CL, Rizzu P, Baker M, Froelich S, Houlden H, Pickering-Brown S, Chakraverty S, Isaacs A, Grover A, Hackett J, Adamson J, Lincoln S, Dickson D, Davies P, Petersen RC, Stevens M, de Graaff E, Wauters E, van Baren J, Hillebrand M, Joosse M, Kwon JM, Nowotny P, Che LK, Norton J, Morris JC, Reed JC, Trojanowski J, Basun H, Lannfelt L, Neystat M, Fahn S, Dark F, Tannenberg T, Dodd PR, Hayward N, Kwok JB, Schofield PR, Andreadis A, Snowden J, Craufurd D, Neary D, Owen F, Oostra BA, Hardy J, Goate A, van Swieten J, Mann D, Lynch T, Heutink P (1998) Association of missense and 5\u2019 splice site mutations in tau with the inherited dementia FTDP-17. Nature 393:702\u2013705","journal-title":"Nature"},{"key":"236_CR18","first-page":"135","volume":"20","author":"P Ioannides","year":"2005","unstructured":"Ioannides P, Karacostas D, Hatzipantazi M (2005) Primary progressive aphasia as the initial manifestation of corticobasal degeneration. A \u201cthree-in-one\u201d syndrome? Funct Neurol 20:135\u2013137","journal-title":"Funct Neurol"},{"key":"236_CR19","doi-asserted-by":"publisher","first-page":"369","DOI":"10.1111\/j.1365-2990.2003.00545.x","volume":"30","author":"KA Josephs","year":"2004","unstructured":"Josephs KA, Holton JL, Rossor MN, Godbolt AK, Ozawa T, Strand K, Khan N, Al-Sarraj S, Revesz T (2004) Frontotemporal lobar degeneration and ubiquitin immunohistochemistry. Neuropath Appl Neurobiol 30:369\u2013373","journal-title":"Neuropath Appl Neurobiol"},{"key":"236_CR20","doi-asserted-by":"publisher","first-page":"142","DOI":"10.1097\/nen.0b013e31803020cf","volume":"66","author":"KA Josephs","year":"2007","unstructured":"Josephs KA, Ahmed Z, Katsuse O, Parisi JF, Boeve BF, Knopman DS, Petersen RC, Davies P, Duara R, Graff-Radford NR, Uitti RJ, Rademakers R, Adamson J, Baker M, Hutton ML, Dickson DW (2007) Neuropathologic features of frontotemporal lobar degeneration with ubiquitin-positive inclusions with progranulin gene (PGRN) mutations. J Neuropathol Exp Neurol 66:142\u2013151","journal-title":"J Neuropathol Exp Neurol"},{"key":"236_CR21","doi-asserted-by":"publisher","first-page":"1385","DOI":"10.1093\/brain\/awl078","volume":"129","author":"KA Josephs","year":"2006","unstructured":"Josephs KA, Duffy JR, Strand EA, Whitwell JL, Layton KF, Parisi JE, Hauser MF, Witte RJ, Boeve BF, Knopman DS, Dickson DW, Jack CR, Petersen RC (2006) Clinicopathological and imaging correlates of progressive aphasia and apraxia of speech. Brain 129:1385\u20131398","journal-title":"Brain"},{"key":"236_CR22","doi-asserted-by":"publisher","first-page":"311","DOI":"10.1097\/01.nrl.0000094943.84390.cf","volume":"9","author":"A Kertesz","year":"2003","unstructured":"Kertesz A (2003) Pick complex: an integrative approach to frontotemporal dementia: primary progressive aphasia, corticobasal degeneration and progressive supranuclear palsy. Neurologist 9:311\u2013317","journal-title":"Neurologist"},{"key":"236_CR23","doi-asserted-by":"publisher","first-page":"156","DOI":"10.1002\/ana.20700","volume":"59","author":"JA Knibb","year":"2006","unstructured":"Knibb JA, Xuereb JH, Patterson K, Hodges JR (2006) Clinical and pathological characterization of progressive aphasia. Ann Neurol 59:156\u2013165","journal-title":"Ann Neurol"},{"key":"236_CR24","doi-asserted-by":"publisher","first-page":"480","DOI":"10.1002\/ana.20425","volume":"57","author":"DS Knopman","year":"2005","unstructured":"Knopman DS, Boeve BF, Parisi JE, Dickson DW, Smith GE, Ivnik RJ, Josephs KA, Petersen RC (2005) Antemortem diagnosis of frontotemporal lobar degeneration. Ann Neurol 57:480\u2013488","journal-title":"Ann Neurol"},{"key":"236_CR25","doi-asserted-by":"crossref","first-page":"742","DOI":"10.1212\/01.WNL.0000113729.77161.C9","volume":"62","author":"W Liu","year":"2004","unstructured":"Liu W, Miller BL, Kramer, Rankin K, Wyss-Coray C, Gearhart R, Phengrasamy L, Weiner M, Rosen HJ (2004) Behavioral disorders in the frontal and temporal variants of frontotemporal dementia. Neurology 62:742\u2013748","journal-title":"Neurology"},{"key":"236_CR26","doi-asserted-by":"publisher","first-page":"379","DOI":"10.1007\/s00401-004-0900-9","volume":"108","author":"AM Lipton","year":"2004","unstructured":"Lipton AM, White CL, Bigio EH (2004) Frontotemporal lobar degeneration with motor neuron disease-type inclusions predominates in 76 cases of frontotemporal degeneration. Acta Neuropath 108:379\u2013385","journal-title":"Acta Neuropath"},{"key":"236_CR27","doi-asserted-by":"crossref","first-page":"416","DOI":"10.1136\/jnnp.57.4.416","volume":"57","author":"Lund","year":"1994","unstructured":"Lund, Manchester groups (1994) Consensus statement. Clinical and neuropathological criteria for frontotemporal dementia. J Neurol Neurosurg Psychiatry 57:416\u2013418","journal-title":"J Neurol Neurosurg Psychiatry"},{"key":"236_CR28","doi-asserted-by":"publisher","first-page":"539","DOI":"10.1007\/s00401-006-0138-9","volume":"112","author":"IRA Mackenzie","year":"2006","unstructured":"Mackenzie IRA, Baborie A, Pickering-Brown S, Du Plessis D, Jaros E, Perry RH, Neary D, Snowden JS, Mann DM (2006) Heterogeneity of ubiquitin pathology in frontotemporal lobar degeneration: classification and relation to clinical phenotype. Acta Neuropathol (Berl) 112:539\u2013549","journal-title":"Acta Neuropathol (Berl)"},{"key":"236_CR29","doi-asserted-by":"publisher","first-page":"3081","DOI":"10.1093\/brain\/awl271","volume":"129","author":"IRA Mackenzie","year":"2006","unstructured":"Mackenzie IRA, Baker M, Pickering-Brown S, Hsiung G-Y R, Lindholm C, Dwosh E, Gass J, Cannon A, Rademakers R, Hutton M, Feldman H (2006) The neuropathology of frontotemporal lobar degeneration caused by mutations in the progranulin gene. Brain 129:3081\u20133090","journal-title":"Brain"},{"key":"236_CR30","doi-asserted-by":"crossref","unstructured":"Mackenzie IR (2007) The neuropathology and clinical phenotype of FTD with progranulin mutations. Acta Neuropath (Berl) (this issue)","DOI":"10.1007\/s00401-007-0223-8"},{"key":"236_CR31","doi-asserted-by":"publisher","first-page":"1803","DOI":"10.1001\/archneur.58.11.1803","volume":"58","author":"GM McKhann","year":"2001","unstructured":"McKhann GM, Albert MS, Grossman M, Miller B, Dickson D, Trojanowski JQ (2001) Clinical and pathological diagnosis of frontotemporal dementia. Report of the Work Group on frontotemporal dementia and Pick\u2019s disease. Arch Neurol 58:1803\u20131809","journal-title":"Arch Neurol"},{"key":"236_CR32","doi-asserted-by":"publisher","first-page":"592","DOI":"10.1002\/ana.410110607","volume":"11","author":"M-M Mesulam","year":"1982","unstructured":"Mesulam M-M (1982) Slowly progressive aphasia without generalized dementia. Ann Neurol 11:592\u2013598","journal-title":"Ann Neurol"},{"key":"236_CR33","doi-asserted-by":"publisher","first-page":"425","DOI":"10.1002\/ana.91","volume":"49","author":"M-M Mesulam","year":"2001","unstructured":"Mesulam M-M (2001) Primary progressive aphasia. Ann Neurol 49:425\u2013432","journal-title":"Ann Neurol"},{"key":"236_CR34","doi-asserted-by":"publisher","first-page":"43","DOI":"10.1001\/archneur.64.1.43","volume":"64","author":"M Mesulam","year":"2007","unstructured":"Mesulam M, Johnson N, Krefft TA, Gass JM, Cannon AD, Adamson JL, Bigio EH, Weintraub S, Dickson DW, Hutton ML, Graff-Radford NR (2007) Progranulin mutations in primary progressive aphasia: the PPA1 and PPA3 families. Arch Neurol 64:43\u201347","journal-title":"Arch Neurol"},{"key":"236_CR35","doi-asserted-by":"crossref","first-page":"937","DOI":"10.1212\/WNL.48.4.937","volume":"48","author":"BL Miller","year":"1997","unstructured":"Miller BL, Ikonte BS, Ponton M, Levy M, Boone K, Darby A, Berman N, Mena I, Cummings J (1997) A study of the Lund-Manchester research criteria for frontotemporal dementia: clinical and single photon emission CT correlations. Neurology 48:937\u2013942","journal-title":"Neurology"},{"key":"236_CR36","doi-asserted-by":"crossref","first-page":"1546","DOI":"10.1212\/WNL.51.6.1546","volume":"51","author":"D Neary","year":"1998","unstructured":"Neary D, Snowden JS, Gustafson L, Passant U, Stuss D, Black S, Freedman M, Kertesz A, Robert PH, Albert M, Boone K, Miller BL, Cummings J, Benson DF (1998) Frontotemporal lobar degeneration. A consensus on clinical diagnostic criteria. Neurology 51:1546\u20131554","journal-title":"Neurology"},{"key":"236_CR37","doi-asserted-by":"publisher","first-page":"1122","DOI":"10.1136\/jnnp.56.10.1122","volume":"56","author":"D Neary","year":"1993","unstructured":"Neary D, Snowden JS, Mann DMA (1993) Familial progressive aphasia: its relationship to other forms of lobar atrophy. J Neurol Neurosurg Psychiatry 56:1122\u20131125","journal-title":"J Neurol Neurosurg Psychiatry"},{"key":"236_CR38","doi-asserted-by":"crossref","first-page":"23","DOI":"10.1136\/jnnp.53.1.23","volume":"53","author":"D Neary","year":"1990","unstructured":"Neary D, Snowden JS, Mann DMA, Northen B, Goulding, Mcdermott N (1990) Frontal lobe dementia and motor neurone disease. J Neurol Neurosurg Psychiatry 53:23\u201332","journal-title":"J Neurol Neurosurg Psychiatry"},{"key":"236_CR39","doi-asserted-by":"publisher","first-page":"130","DOI":"10.1126\/science.1134108","volume":"314","author":"M Neumann","year":"2006","unstructured":"Neumann M, Sampathu DM, Kwong LK, Truax AC, Micsenyi MC, Chou TT, Bruce J, Schuck T, Grossman M, Clark CM, McCluskey LF, Miller BL, Masliah E, Mackenzie IR, Feldman H, Feiden W, Kretzchmar HA, Trojanowski JQ, Lee VM (2006) Ubiquitinated TDP-43 in frontotemporal lobar degeneration and amyotrophic lateral sclerosis. Science 314:130\u2013133","journal-title":"Science"},{"key":"236_CR40","doi-asserted-by":"publisher","first-page":"2441","DOI":"10.1093\/brain\/awh265","volume":"127","author":"DC Paviour","year":"2004","unstructured":"Paviour DC, Lees AJ, Josephs KA, Ozawa T, Ganguly M, Strand C, Godbolt A, Howard RS, Revesz T, Holton JL (2004) Frontotemporal lobar degeneration with ubiquitin-only-immunoreactive neuronal changes: broadening the clinical picture to include progressive supranuclear palsy. Brain 127:2441\u20132451","journal-title":"Brain"},{"key":"236_CR41","doi-asserted-by":"crossref","first-page":"2277","DOI":"10.1212\/WNL.54.12.2277","volume":"54","author":"RJ Perry","year":"2000","unstructured":"Perry RJ, Hodges JR (2000) Differentiating frontal and temporal variant frontotemporal dementia from Alzheimer\u2019s disease. Neurology 54:2277\u20132284","journal-title":"Neurology"},{"key":"236_CR42","doi-asserted-by":"publisher","first-page":"732","DOI":"10.1093\/brain\/awf069","volume":"125","author":"SM Pickering-Brown","year":"2002","unstructured":"Pickering-Brown SM, Richardson AMT, Snowden JS, McDonagh AM, Burns A, Braude W, Baker M, Liu W-K, Yen S-H, Hardy J, Hutton M, Davies Y, Allsop D, Craufurd D, Neary D, Mann DMA (2002) Inherited frontotemporal dementia in nine British families associated with intronic mutations in the tau gene. Brain 125:732\u2013751","journal-title":"Brain"},{"key":"236_CR43","doi-asserted-by":"publisher","first-page":"1343","DOI":"10.2353\/ajpath.2006.060438","volume":"169","author":"DM Sampathu","year":"2006","unstructured":"Sampathu DM, Neumann M, Kwong LK, Chou TT, Micsenyi M, Truax A, Bruce J, Grossman M, Trojanowski JQ, Lee VM (2006) Pathological heterogeneity of frontotemporal lobar degeneration with ubiquitin-positive inclusions delineated by ubiquitin immunohistochemistry and novel monoclonal antibodies. Am J Pathol 169:1343\u20131352","journal-title":"Am J Pathol"},{"key":"236_CR44","doi-asserted-by":"publisher","first-page":"501","DOI":"10.1007\/s00401-005-1079-4","volume":"110","author":"J Shi","year":"2005","unstructured":"Shi J, Shaw CL, Du Plessis D, Richardson AM, Bailey KL, Julien C, Stopford C, Thompson J, Varma A, Craufurd D, Tian J, Pickering-Brown S, Neary D, Snowden JS, Mann DM (2005) Histopathological changes underlying frontotemporal lobar degeneration with clinicopathological correlation. Acta Neuropathol (Berl) 110:501\u2013512","journal-title":"Acta Neuropathol (Berl)"},{"key":"236_CR45","volume-title":"Fronto-temporal lobar degeneration: fronto-temporal dementia, progressive aphasia, semantic dementia","author":"JS Snowden","year":"1996","unstructured":"Snowden JS, Neary D, Mann DMA (1996) Fronto-temporal lobar degeneration: fronto-temporal dementia, progressive aphasia, semantic dementia. Churchill-Livingstone, London"},{"key":"236_CR46","doi-asserted-by":"crossref","first-page":"167","DOI":"10.1155\/1989\/124043","volume":"2","author":"JS Snowden","year":"1989","unstructured":"Snowden JS, Goulding PJ, Neary D (1989) Semantic dementia: a form of circumscribed cerebral atrophy. Behav Neurol 2:167\u2013182","journal-title":"Behav Neurol"},{"key":"236_CR47","doi-asserted-by":"publisher","first-page":"860","DOI":"10.1093\/brain\/awh099","volume":"127","author":"JS Snowden","year":"2004","unstructured":"Snowden JS, Thompson JC, Neary D (2004) Knowledge of famous faces and names in semantic dementia. Brain 127:860\u2013872","journal-title":"Brain"},{"key":"236_CR48","doi-asserted-by":"publisher","first-page":"1337","DOI":"10.1136\/jnnp.2003.028498","volume":"75","author":"JS Snowden","year":"2004","unstructured":"Snowden JS, Neary D, Mann DM (2004) Autopsy proven sporadic frontotemporal dementia due to microvacuolar-type histology, with onset at 21 years of age. J Neurol Neurosurg Psychiatry 75:1337\u20131339","journal-title":"J Neurol Neurosurg Psychiatry"},{"key":"236_CR49","doi-asserted-by":"publisher","first-page":"3091","DOI":"10.1093\/brain\/awl267","volume":"129","author":"JS Snowden","year":"2006","unstructured":"Snowden JS, Pickering-Brown SM, Mackenzie IR, Richardson AMT, Varma A, Neary D, Mann DMA (2006) Progranulin gene mutations associated with frontotemporal dementia and progressive non-fluent aphasia. Brain 129:3091\u20133102","journal-title":"Brain"},{"key":"236_CR50","doi-asserted-by":"publisher","first-page":"323","DOI":"10.1136\/jnnp.70.3.323","volume":"70","author":"JS Snowden","year":"2001","unstructured":"Snowden JS, Bathgate D, Varma A, Blackshaw A, Gibbons ZC, Neary D (2001) Distinct behavioural profiles in frontotemporal dementia and semantic dementia. J Neurol Neurosurg Psychiatry 70:323\u2013332","journal-title":"J Neurol Neurosurg Psychiatry"},{"key":"236_CR51","doi-asserted-by":"crossref","unstructured":"Stopford CL, Snowden JS, Thompson JC, Neary D (2007) Variability in cognitive presentation of Alzheimer\u2019s disease. Cortex, in press","DOI":"10.1016\/j.cortex.2005.11.002"},{"key":"236_CR52","doi-asserted-by":"publisher","first-page":"261","DOI":"10.1159\/000077150","volume":"17","author":"JC Van Swieten","year":"2004","unstructured":"Van Swieten JC, Rosso SM, van Herpen E, Kamphorst W, Ravid R, Heutink P (2004) Phenotypic variation in frontotemporal dementia and parkinsonism linked to chromosome 17. Dement Geriatr Cogn Disord 17:261\u2013264","journal-title":"Dement Geriatr Cogn Disord"}],"container-title":["Acta Neuropathologica"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1007\/s00401-007-0236-3.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/link.springer.com\/article\/10.1007\/s00401-007-0236-3\/fulltext.html","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1007\/s00401-007-0236-3","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"},{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1007\/s00401-007-0236-3.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2022,5,15]],"date-time":"2022-05-15T12:19:56Z","timestamp":1652617196000},"score":1,"resource":{"primary":{"URL":"https:\/\/link.springer.com\/10.1007\/s00401-007-0236-3"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2007,6,14]]},"references-count":52,"journal-issue":{"issue":"1","published-print":{"date-parts":[[2007,7]]}},"alternative-id":["236"],"URL":"https:\/\/doi.org\/10.1007\/s00401-007-0236-3","relation":{},"ISSN":["0001-6322","1432-0533"],"issn-type":[{"value":"0001-6322","type":"print"},{"value":"1432-0533","type":"electronic"}],"subject":[],"published":{"date-parts":[[2007,6,14]]},"assertion":[{"value":"8 May 2007","order":1,"name":"received","label":"Received","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"8 May 2007","order":2,"name":"revised","label":"Revised","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"8 May 2007","order":3,"name":"accepted","label":"Accepted","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"14 June 2007","order":4,"name":"first_online","label":"First Online","group":{"name":"ArticleHistory","label":"Article History"}}]}}