{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,11,3]],"date-time":"2026-11-03T09:04:06Z","timestamp":1793696646584,"version":"4.5.1"},"reference-count":88,"publisher":"Springer Science and Business Media LLC","issue":"1","license":[{"start":{"date-parts":[[2020,10,20]],"date-time":"2020-10-20T00:00:00Z","timestamp":1603152000000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0"},{"start":{"date-parts":[[2020,10,20]],"date-time":"2020-10-20T00:00:00Z","timestamp":1603152000000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0"}],"funder":[{"DOI":"10.13039\/100014808","name":"Fondation Vaincre Alzheimer","doi-asserted-by":"publisher","award":["# FR18-035"],"award-info":[{"award-number":["# FR18-035"]}],"id":[{"id":"10.13039\/100014808","id-type":"DOI","asserted-by":"publisher"}]},{"name":"LABEX DISTALZ"},{"DOI":"10.13039\/501100001807","name":"FAPESP","doi-asserted-by":"crossref","award":["#2018\/14289-6"],"award-info":[{"award-number":["#2018\/14289-6"]}],"id":[{"id":"10.13039\/501100001807","id-type":"DOI","asserted-by":"crossref"}]}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["Acta Neuropathol"],"published-print":{"date-parts":[[2021,1]]},"abstract":"<jats:title>Abstract<\/jats:title>\n                  <jats:p>Several lines of recent evidence indicate that the amyloid precursor protein-derived C-terminal fragments (APP-CTFs) could correspond to an etiological trigger of Alzheimer\u2019s disease (AD) pathology. Altered mitochondrial homeostasis is considered an early event in AD development. However, the specific contribution of APP-CTFs to mitochondrial structure, function, and mitophagy defects remains to be established. Here, we demonstrate in neuroblastoma SH-SY5Y cells expressing either APP Swedish mutations, or the \u03b2-secretase-derived APP-CTF fragment (C99) combined with \u03b2- and \u03b3-secretase inhibition, that APP-CTFs accumulation independently of A\u03b2 triggers excessive mitochondrial morphology alteration (i.e., size alteration and cristae disorganization) associated with enhanced mitochondrial reactive oxygen species production. APP-CTFs accumulation also elicit basal mitophagy failure illustrated by enhanced conversion of LC3, accumulation of LC3-I and\/or LC3-II, non-degradation of SQSTM1\/p62, inconsistent Parkin and PINK1 recruitment to mitochondria, enhanced levels of membrane and matrix mitochondrial proteins, and deficient fusion of mitochondria with lysosomes. We confirm the contribution of APP-CTFs accumulation to morphological mitochondria alteration and impaired basal mitophagy in vivo in young 3xTgAD transgenic mice treated with \u03b3-secretase inhibitor as well as in adeno-associated-virus-C99 injected mice. Comparison of aged 2xTgAD and 3xTgAD mice indicates that, besides APP-CTFs, an additional contribution of A\u03b2 to late-stage mitophagy activation occurs. Importantly, we report on mitochondrial accumulation of APP-CTFs in human post-mortem sporadic AD brains correlating with mitophagy failure molecular signature. Since defective mitochondria homeostasis plays a pivotal role in AD pathogenesis, targeting mitochondrial dysfunctions and\/or mitophagy by counteracting early APP-CTFs accumulation may represent relevant therapeutic interventions in AD.<\/jats:p>","DOI":"10.1007\/s00401-020-02234-7","type":"journal-article","created":{"date-parts":[[2020,10,20]],"date-time":"2020-10-20T11:02:36Z","timestamp":1603191756000},"page":"39-65","update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":248,"title":["Accumulation of\u00a0amyloid precursor protein C-terminal fragments triggers mitochondrial structure, function, and mitophagy defects in Alzheimer\u2019s disease models and human brains"],"prefix":"10.1007","volume":"141","author":[{"given":"Loan","family":"Vaillant-Beuchot","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Arnaud","family":"Mary","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Rapha\u00eblle","family":"Pardossi-Piquard","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Alexandre","family":"Bourgeois","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Inger","family":"Lauritzen","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Fanny","family":"Eysert","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Paula Fernanda","family":"Kinoshita","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Julie","family":"Cazareth","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"C\u00e9line","family":"Badot","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Konstantina","family":"Fragaki","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Renaud","family":"Bussiere","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"C\u00e9cile","family":"Martin","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Rosanna","family":"Mary","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Charlotte","family":"Bauer","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Sophie","family":"Pagnotta","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"V\u00e9ronique","family":"Paquis-Flucklinger","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Val\u00e9rie","family":"Bu\u00e9e-Scherrer","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Luc","family":"Bu\u00e9e","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Sandra","family":"Lacas-Gervais","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Fr\u00e9d\u00e9ric","family":"Checler","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-1498-7187","authenticated-orcid":false,"given":"Mounia","family":"Chami","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2020,10,20]]},"reference":[{"key":"2234_CR1","doi-asserted-by":"publisher","first-page":"1127","DOI":"10.1038\/embor.2013.168","volume":"14","author":"GF Allen","year":"2013","unstructured":"Allen GF, Toth R, James J, Ganley IG (2013) Loss of iron triggers PINK1\/Parkin-independent mitophagy. EMBO Rep 14:1127\u20131135. https:\/\/doi.org\/10.1038\/embor.2013.168","journal-title":"EMBO Rep"},{"key":"2234_CR2","doi-asserted-by":"publisher","first-page":"626","DOI":"10.1177\/1073858407303536","volume":"13","author":"HK Anandatheerthavarada","year":"2007","unstructured":"Anandatheerthavarada HK, Devi L (2007) Amyloid precursor protein and mitochondrial dysfunction in Alzheimer's disease. Neuroscientist 13:626\u2013638. https:\/\/doi.org\/10.1177\/1073858407303536","journal-title":"Neuroscientist"},{"key":"2234_CR3","doi-asserted-by":"publisher","first-page":"343","DOI":"10.1177\/1073858407303536","volume":"18","author":"HK Anandatheerthavarada","year":"2007","unstructured":"Anandatheerthavarada HK, Devi L (2007) Mitochondrial translocation of amyloid precursor protein and its cleaved products: relevance to mitochondrial dysfunction in Alzheimer's disease. Rev Neurosci 18:343\u2013354.\u00a0https:\/\/doi.org\/10.1177\/1073858407303536","journal-title":"Rev Neurosci"},{"key":"2234_CR4","doi-asserted-by":"publisher","first-page":"4106","DOI":"10.1038\/emboj.2012.202","volume":"31","author":"E Area-Gomez","year":"2012","unstructured":"Area-Gomez E, Del Carmen Lara Castillo M, Tambini MD, Guardia-Laguarta C, de Groof AJ, Madra M et al (2012) Upregulated function of mitochondria-associated ER membranes in Alzheimer disease. EMBO J 31:4106\u20134123. https:\/\/doi.org\/10.1038\/emboj.2012.202","journal-title":"EMBO J"},{"key":"2234_CR5","doi-asserted-by":"publisher","first-page":"3720","DOI":"10.1096\/fj.11-182154","volume":"25","author":"M Asai","year":"2011","unstructured":"Asai M, Yagishita S, Iwata N, Saido TC, Ishiura S, Maruyama K (2011) An alternative metabolic pathway of amyloid precursor protein C-terminal fragments via cathepsin B in a human neuroglioma model. FASEB J 25:3720\u20133730. https:\/\/doi.org\/10.1096\/fj.11-182154","journal-title":"FASEB J"},{"key":"2234_CR6","doi-asserted-by":"publisher","first-page":"150","DOI":"10.1016\/s0169-328x(99)00014-5","volume":"66","author":"J Berger-Sweeney","year":"1999","unstructured":"Berger-Sweeney J, McPhie DL, Arters JA, Greenan J, Oster-Granite ML, Neve RL (1999) Impairments in learning and memory accompanied by neurodegeneration in mice transgenic for the carboxyl-terminus of the amyloid precursor protein. Brain Res Mol Brain Res 66:150\u2013162. https:\/\/doi.org\/10.1016\/s0169-328x(99)00014-5","journal-title":"Brain Res Mol Brain Res"},{"key":"2234_CR7","doi-asserted-by":"publisher","first-page":"10405","DOI":"10.1523\/JNEUROSCI.2288-09.2009","volume":"29","author":"T Bittner","year":"2009","unstructured":"Bittner T, Fuhrmann M, Burgold S, Jung CK, Volbracht C, Steiner H et al (2009) Gamma-secretase inhibition reduces spine density in vivo via an amyloid precursor protein-dependent pathway. J Neurosci 29:10405\u201310409. https:\/\/doi.org\/10.1523\/JNEUROSCI.2288-09.2009","journal-title":"J Neurosci"},{"key":"2234_CR8","doi-asserted-by":"publisher","first-page":"298","DOI":"10.1016\/j.mito.2013.03.008","volume":"13","author":"A Bobba","year":"2013","unstructured":"Bobba A, Amadoro G, Valenti D, Corsetti V, Lassandro R, Atlante A (2013) Mitochondrial respiratory chain Complexes I and IV are impaired by beta-amyloid via direct interaction and through Complex I-dependent ROS production, respectively. Mitochondrion 13:298\u2013311. https:\/\/doi.org\/10.1016\/j.mito.2013.03.008","journal-title":"Mitochondrion"},{"key":"2234_CR9","doi-asserted-by":"publisher","first-page":"213","DOI":"10.1111\/j.1365-2818.2006.01706.x","volume":"224","author":"S Bolte","year":"2006","unstructured":"Bolte S, Cordelieres FP (2006) A guided tour into subcellular colocalization analysis in light microscopy. J Microsc 224:213\u2013232. https:\/\/doi.org\/10.1111\/j.1365-2818.2006.01706.x","journal-title":"J Microsc"},{"key":"2234_CR10","doi-asserted-by":"publisher","first-page":"27","DOI":"10.1016\/j.bbr.2010.01.013","volume":"209","author":"WC Boon","year":"2010","unstructured":"Boon WC, van den Buuse M, Wegener N, Martin S, Chua HK, Bush AI et al (2010) Behavioural phenotype of APPC100.V717F transgenic mice over-expressing a mutant Abeta-bearing fragment is associated with reduced NMDA receptor density. Behav Brain Res 209:27\u201335. https:\/\/doi.org\/10.1016\/j.bbr.2010.01.013","journal-title":"Behav Brain Res"},{"key":"2234_CR11","doi-asserted-by":"publisher","first-page":"21","DOI":"10.1016\/j.neurobiolaging.2018.06.038","volume":"71","author":"A Bourgeois","year":"2018","unstructured":"Bourgeois A, Lauritzen I, Lorivel T, Bauer C, Checler F, Pardossi-Piquard R (2018) Intraneuronal accumulation of C99 contributes to synaptic alterations, apathy-like behavior, and spatial learning deficits in 3xTgAD and 2xTgAD mice. Neurobiol Aging 71:21\u201331. https:\/\/doi.org\/10.1016\/j.neurobiolaging.2018.06.038","journal-title":"Neurobiol Aging"},{"key":"2234_CR12","doi-asserted-by":"publisher","first-page":"3206","DOI":"10.1093\/hmg\/ddp258","volume":"18","author":"MP Burns","year":"2009","unstructured":"Burns MP, Zhang L, Rebeck GW, Querfurth HW, Moussa CE (2009) Parkin promotes intracellular Abeta1-42 clearance. Hum Mol Genet 18:3206\u20133216. https:\/\/doi.org\/10.1093\/hmg\/ddp258","journal-title":"Hum Mol Genet"},{"key":"2234_CR13","doi-asserted-by":"publisher","first-page":"10153","DOI":"10.1074\/jbc.M116.743070","volume":"292","author":"R Bussiere","year":"2017","unstructured":"Bussiere R, Lacampagne A, Reiken S, Liu X, Scheuerman V, Zalk R et al (2017) Amyloid beta production is regulated by beta2-adrenergic signaling-mediated post-translational modifications of the ryanodine receptor. J Biol Chem 292:10153\u201310168. https:\/\/doi.org\/10.1074\/jbc.M116.743070","journal-title":"J Biol Chem"},{"key":"2234_CR14","doi-asserted-by":"publisher","first-page":"1431","DOI":"10.1046\/j.1471-4159.1995.65041431.x","volume":"65","author":"F Checler","year":"1995","unstructured":"Checler F (1995) Processing of the beta-amyloid precursor protein and its regulation in Alzheimer's disease. J Neurochem 65:1431\u20131444. https:\/\/doi.org\/10.1046\/j.1471-4159.1995.65041431.x\u00a0","journal-title":"J Neurochem"},{"issue":"Suppl 2","key":"2234_CR15","doi-asserted-by":"publisher","first-page":"S569","DOI":"10.3233\/JAD-2010-100357","volume":"20","author":"JX Chen","year":"2010","unstructured":"Chen JX, Yan SS (2010) Role of mitochondrial amyloid-beta in Alzheimer's disease. J Alzheimers Dis 20(Suppl 2):S569\u2013578. https:\/\/doi.org\/10.3233\/JAD-2010-100357","journal-title":"J Alzheimers Dis"},{"key":"2234_CR16","doi-asserted-by":"publisher","first-page":"116","DOI":"10.1016\/j.brainres.2009.09.014","volume":"1301","author":"DZ Christensen","year":"2009","unstructured":"Christensen DZ, Bayer TA, Wirths O (2009) Formic acid is essential for immunohistochemical detection of aggregated intraneuronal Abeta peptides in mouse models of Alzheimer's disease. Brain Res 1301:116\u2013125. https:\/\/doi.org\/10.1016\/j.brainres.2009.09.014","journal-title":"Brain Res"},{"key":"2234_CR17","doi-asserted-by":"publisher","DOI":"10.15252\/embj.201899360","author":"N Cummins","year":"2019","unstructured":"Cummins N, Tweedie A, Zuryn S, Bertran-Gonzalez J, Gotz J (2019) Disease-associated tau impairs mitophagy by inhibiting Parkin translocation to mitochondria. EMBO J. https:\/\/doi.org\/10.15252\/embj.201899360","journal-title":"EMBO J"},{"key":"2234_CR18","doi-asserted-by":"publisher","first-page":"24065","DOI":"10.1074\/jbc.M002413200","volume":"275","author":"CA da Costa","year":"2000","unstructured":"da Costa CA, Ancolio K, Checler F (2000) Wild-type but not Parkinson's disease-related ala-53 \u2192 Thr mutant alpha-synuclein protects neuronal cells from apoptotic stimuli. J Biol Chem 275:24065\u201324069. https:\/\/doi.org\/10.1074\/jbc.M002413200","journal-title":"J Biol Chem"},{"key":"2234_CR19","doi-asserted-by":"publisher","first-page":"603","DOI":"10.1016\/j.cell.2015.12.056","volume":"164","author":"B De Strooper","year":"2016","unstructured":"De Strooper B, Karran E (2016) The cellular phase of Alzheimer's disease. Cell 164:603\u2013615. https:\/\/doi.org\/10.1016\/j.cell.2015.12.056","journal-title":"Cell"},{"key":"2234_CR20","doi-asserted-by":"publisher","first-page":"1549","DOI":"10.3233\/JAD-160953","volume":"55","author":"D Del Prete","year":"2017","unstructured":"Del Prete D, Suski JM, Oules B, Debayle D, Gay AS, Lacas-Gervais S et al (2017) Localization and processing of the amyloid-beta protein precursor in mitochondria-associated membranes. J Alzheimers Dis 55:1549\u20131570. https:\/\/doi.org\/10.3233\/JAD-160953","journal-title":"J Alzheimers Dis"},{"key":"2234_CR21","doi-asserted-by":"publisher","first-page":"417","DOI":"10.1016\/j.nbd.2011.09.001","volume":"45","author":"L Devi","year":"2012","unstructured":"Devi L, Ohno M (2012) Mitochondrial dysfunction and accumulation of the beta-secretase-cleaved C-terminal fragment of APP in Alzheimer's disease transgenic mice. Neurobiol Dis 45:417\u2013424. https:\/\/doi.org\/10.1016\/j.nbd.2011.09.001","journal-title":"Neurobiol Dis"},{"key":"2234_CR22","doi-asserted-by":"publisher","first-page":"353","DOI":"10.1016\/S0076-6879(03)61019-0","volume":"361","author":"MR Duchen","year":"2003","unstructured":"Duchen MR, Surin A, Jacobson J (2003) Imaging mitochondrial function in intact cells. Methods Enzymol 361:353\u2013389","journal-title":"Methods Enzymol"},{"key":"2234_CR23","doi-asserted-by":"publisher","first-page":"15419","DOI":"10.1074\/jbc.R118.003999","volume":"293","author":"J Dunys","year":"2018","unstructured":"Dunys J, Valverde A, Checler F (2018) Are N- and C-terminally truncated Abeta species key pathological triggers in Alzheimer's disease? J Biol Chem 293:15419\u201315428. https:\/\/doi.org\/10.1074\/jbc.R118.003999","journal-title":"J Biol Chem"},{"key":"2234_CR24","doi-asserted-by":"publisher","first-page":"75","DOI":"10.3233\/JAD-180337","volume":"66","author":"TL Emmerzaal","year":"2018","unstructured":"Emmerzaal TL, Rodenburg RJ, Tanila H, Verweij V, Kiliaan AJ, Kozicz T (2018) Age-dependent decrease of mitochondrial complex II activity in a familial mouse model for Alzheimer's disease. J Alzheimers Dis 66:75\u201382. https:\/\/doi.org\/10.3233\/JAD-180337","journal-title":"J Alzheimers Dis"},{"key":"2234_CR25","doi-asserted-by":"publisher","first-page":"386","DOI":"10.1002\/jnr.10745","volume":"74","author":"G Evin","year":"2003","unstructured":"Evin G, Zhu A, Holsinger RM, Masters CL, Li QX (2003) Proteolytic processing of the Alzheimer's disease amyloid precursor protein in brain and platelets. J Neurosci Res 74:386\u2013392. https:\/\/doi.org\/10.1002\/jnr.10745","journal-title":"J Neurosci Res"},{"key":"2234_CR26","doi-asserted-by":"publisher","first-page":"5243","DOI":"10.1242\/jcs.02633","volume":"118","author":"JM Falcon-Perez","year":"2005","unstructured":"Falcon-Perez JM, Nazarian R, Sabatti C, Dell'Angelica EC (2005) Distribution and dynamics of Lamp1-containing endocytic organelles in fibroblasts deficient in BLOC-3. J Cell Sci 118:5243\u20135255. https:\/\/doi.org\/10.1242\/jcs.02633","journal-title":"J Cell Sci"},{"key":"2234_CR27","doi-asserted-by":"publisher","first-page":"2044","DOI":"10.1080\/15548627.2019.1596489","volume":"15","author":"C Fedeli","year":"2019","unstructured":"Fedeli C, Filadi R, Rossi A, Mammucari C, Pizzo P (2019) PSEN2 (presenilin 2) mutants linked to familial Alzheimer disease impair autophagy by altering Ca(2+) homeostasis. Autophagy 15:2044\u20132062. https:\/\/doi.org\/10.1080\/15548627.2019.1596489","journal-title":"Autophagy"},{"key":"2234_CR28","doi-asserted-by":"publisher","first-page":"202","DOI":"10.1016\/j.neuint.2017.02.007","volume":"109","author":"EM Fivenson","year":"2017","unstructured":"Fivenson EM, Lautrup S, Sun N, Scheibye-Knudsen M, Stevnsner T et al (2017) Mitophagy in neurodegeneration and aging. Neurochem Int 109:202\u2013209. https:\/\/doi.org\/10.1016\/j.neuint.2017.02.007","journal-title":"Neurochem Int"},{"key":"2234_CR29","doi-asserted-by":"publisher","first-page":"145","DOI":"10.3233\/JAD-2012-112186","volume":"30","author":"B Flammang","year":"2012","unstructured":"Flammang B, Pardossi-Piquard R, Sevalle J, Debayle D, Dabert-Gay AS, Thevenet A et al (2012) Evidence that the amyloid-beta protein precursor intracellular domain, AICD, derives from beta-secretase-generated C-terminal fragment. J Alzheimers Dis 30:145\u2013153. https:\/\/doi.org\/10.3233\/JAD-2012-112186","journal-title":"J Alzheimers Dis"},{"key":"2234_CR30","doi-asserted-by":"publisher","first-page":"109","DOI":"10.1016\/j.mcn.2019.06.009","volume":"98","author":"PJ Flannery","year":"2019","unstructured":"Flannery PJ, Trushina E (2019) Mitochondrial dynamics and transport in Alzheimer's disease. Mol Cell Neurosci 98:109\u2013120. https:\/\/doi.org\/10.1016\/j.mcn.2019.06.009","journal-title":"Mol Cell Neurosci"},{"key":"2234_CR31","doi-asserted-by":"publisher","DOI":"10.1016\/j.biopsych.2017.04.011","author":"T Goiran","year":"2017","unstructured":"Goiran T, Duplan E, Chami M, Bourgeois A, El Manaa W, Rouland L et al (2017) Beta-amyloid precursor protein intracellular domain controls mitochondrial function by modulating phosphatase and tensin homolog-induced kinase 1 transcription in cells and in Alzheimer mice models. Biol Psychiatry. https:\/\/doi.org\/10.1016\/j.biopsych.2017.04.011","journal-title":"Biol Psychiatry"},{"key":"2234_CR32","doi-asserted-by":"publisher","first-page":"873","DOI":"10.1038\/s41418-017-0016-0","volume":"25","author":"T Goiran","year":"2018","unstructured":"Goiran T, Duplan E, Rouland L, El Manaa W, Lauritzen I, Dunys J et al (2018) Nuclear p53-mediated repression of autophagy involves PINK1 transcriptional down-regulation. Cell Death Differ 25:873\u2013884. https:\/\/doi.org\/10.1038\/s41418-017-0016-0","journal-title":"Cell Death Differ"},{"key":"2234_CR33","doi-asserted-by":"publisher","first-page":"2446","DOI":"10.1096\/fj.201600713R","volume":"31","author":"AE Gonzalez","year":"2017","unstructured":"Gonzalez AE, Munoz VC, Cavieres VA, Bustamante HA, Cornejo VH, Januario YC et al (2017) Autophagosomes cooperate in the degradation of intracellular C-terminal fragments of thesoso amyloid precursor protein via the MVB\/lysosomal pathway. FASEB J 31:2446\u20132459. https:\/\/doi.org\/10.1096\/fj.201600713R","journal-title":"FASEB J"},{"key":"2234_CR34","doi-asserted-by":"publisher","first-page":"1574","DOI":"10.1016\/j.neurobiolaging.2007.12.005","volume":"30","author":"S Hauptmann","year":"2009","unstructured":"Hauptmann S, Scherping I, Drose S, Brandt U, Schulz KL, Jendrach M et al (2009) Mitochondrial dysfunction: an early event in Alzheimer pathology accumulates with age in AD transgenic mice. Neurobiol Aging 30:1574\u20131586. https:\/\/doi.org\/10.1016\/j.neurobiolaging.2007.12.005","journal-title":"Neurobiol Aging"},{"key":"2234_CR35","doi-asserted-by":"publisher","first-page":"17356","DOI":"10.18632\/oncotarget.7861","volume":"7","author":"Y Hu","year":"2016","unstructured":"Hu Y, Li XC, Wang ZH, Luo Y, Zhang X, Liu XP et al (2016) Tau accumulation impairs mitophagy via increasing mitochondrial membrane potential and reducing mitochondrial Parkin. Oncotarget 7:17356\u201317368. https:\/\/doi.org\/10.18632\/oncotarget.7861","journal-title":"Oncotarget"},{"issue":"3647\u20133660","key":"2234_CR36","doi-asserted-by":"publisher","first-page":"e3642","DOI":"10.1016\/j.celrep.2018.11.095","volume":"25","author":"COY Hung","year":"2018","unstructured":"Hung COY, Livesey FJ (2018) Altered gamma-secretase processing of APP disrupts lysosome and autophagosome function in monogenic Alzheimer's disease. Cell Rep 25(3647\u20133660):e3642. https:\/\/doi.org\/10.1016\/j.celrep.2018.11.095","journal-title":"Cell Rep"},{"key":"2234_CR37","doi-asserted-by":"publisher","first-page":"104","DOI":"10.1016\/j.pneurobio.2018.05.001","volume":"168","author":"M Jazvinscak Jembrek","year":"2018","unstructured":"Jazvinscak Jembrek M, Slade N, Hof PR, Simic G (2018) The interactions of p53 with tau and Ass as potential therapeutic targets for Alzheimer's disease. Prog Neurobiol 168:104\u2013127. https:\/\/doi.org\/10.1016\/j.pneurobio.2018.05.001","journal-title":"Prog Neurobiol"},{"key":"2234_CR38","doi-asserted-by":"publisher","first-page":"5255","DOI":"10.1523\/JNEUROSCI.0578-19.2019","volume":"39","author":"Y Jiang","year":"2019","unstructured":"Jiang Y, Sato Y, Im E, Berg M, Bordi M, Darji S et al (2019) Lysosomal dysfunction in down syndrome is APP-dependent and mediated by APP-betaCTF (C99). J Neurosci 39:5255\u20135268. https:\/\/doi.org\/10.1523\/JNEUROSCI.0578-19.2019","journal-title":"J Neurosci"},{"key":"2234_CR39","doi-asserted-by":"publisher","first-page":"981","DOI":"10.1038\/mp.2016.189","volume":"22","author":"G Kaur","year":"2017","unstructured":"Kaur G, Pawlik M, Gandy SE, Ehrlich ME, Smiley JF, Levy E (2017) Lysosomal dysfunction in the brain of a mouse model with intraneuronal accumulation of carboxyl terminal fragments of the amyloid precursor protein. Mol Psychiatry 22:981\u2013989. https:\/\/doi.org\/10.1038\/mp.2016.189","journal-title":"Mol Psychiatry"},{"key":"2234_CR40","doi-asserted-by":"publisher","first-page":"1810","DOI":"10.1007\/pl00000661","volume":"57","author":"SH Kim","year":"2000","unstructured":"Kim SH, Vlkolinsky R, Cairns N, Lubec G (2000) Decreased levels of complex III core protein 1 and complex V beta chain in brains from patients with Alzheimer's disease and Down syndrome. Cell Mol Life Sci 57:1810\u20131816. https:\/\/doi.org\/10.1007\/pl00000661","journal-title":"Cell Mol Life Sci"},{"key":"2234_CR41","doi-asserted-by":"publisher","first-page":"1022","DOI":"10.1016\/j.neuron.2019.11.010","volume":"104","author":"D Kwart","year":"2019","unstructured":"Kwart D, Gregg A, Scheckel C, Murphy EA, Paquet D, Duffield M et al (2019) A Large panel of isogenic APP and PSEN1 mutant human iPSC neurons reveals shared endosomal abnormalities mediated by APP beta-CTFs, not abeta. Neuron 104:1022. https:\/\/doi.org\/10.1016\/j.neuron.2019.11.010","journal-title":"Neuron"},{"key":"2234_CR42","doi-asserted-by":"publisher","first-page":"35","DOI":"10.1186\/s40035-019-0176-6","volume":"8","author":"I Lauritzen","year":"2019","unstructured":"Lauritzen I, Becot A, Bourgeois A, Pardossi-Piquard R, Biferi MG, Barkats M et al (2019) Targeting gamma-secretase triggers the selective enrichment of oligomeric APP-CTFs in brain extracellular vesicles from Alzheimer cell and mouse models. Transl Neurodegener 8:35. https:\/\/doi.org\/10.1186\/s40035-019-0176-6","journal-title":"Transl Neurodegener"},{"key":"2234_CR43","doi-asserted-by":"publisher","first-page":"16243","DOI":"10.1523\/JNEUROSCI.2775-12.2012","volume":"32","author":"I Lauritzen","year":"2012","unstructured":"Lauritzen I, Pardossi-Piquard R, Bauer C, Brigham E, Abraham JD, Ranaldi S et al (2012) The beta-secretase-derived C-terminal fragment of betaAPP, C99, but not abeta, is a key contributor to early intraneuronal lesions in triple-transgenic mouse hippocampus. J Neurosci 32:16243\u201316255. https:\/\/doi.org\/10.1523\/JNEUROSCI.2775-12.2012","journal-title":"J Neurosci"},{"key":"2234_CR44","doi-asserted-by":"publisher","first-page":"453","DOI":"10.2174\/1567205016666190325092841","volume":"16","author":"I Lauritzen","year":"2019","unstructured":"Lauritzen I, Pardossi-Piquard R, Bourgeois A, Becot A, Checler F (2019) Does intraneuronal accumulation of carboxyl-terminal fragments of the amyloid precursor protein trigger early neurotoxicity in Alzheimer's disease? Curr Alzheimer Res 16:453\u2013457. https:\/\/doi.org\/10.2174\/1567205016666190325092841","journal-title":"Curr Alzheimer Res"},{"key":"2234_CR45","doi-asserted-by":"publisher","first-page":"257","DOI":"10.1007\/s00401-016-1577-6","volume":"132","author":"I Lauritzen","year":"2016","unstructured":"Lauritzen I, Pardossi-Piquard R, Bourgeois A, Pagnotta S, Biferi MG, Barkats M et al (2016) Intraneuronal aggregation of the beta-CTF fragment of APP (C99) induces Abeta-independent lysosomal-autophagic pathology. Acta Neuropathol 132:257\u2013276. https:\/\/doi.org\/10.1007\/s00401-016-1577-6","journal-title":"Acta Neuropathol"},{"key":"2234_CR46","doi-asserted-by":"publisher","first-page":"186","DOI":"10.1007\/s12035-012-8307-4","volume":"46","author":"K Leuner","year":"2012","unstructured":"Leuner K, Muller WE, Reichert AS (2012) From mitochondrial dysfunction to amyloid beta formation: novel insights into the pathogenesis of Alzheimer's disease. Mol Neurobiol 46:186\u2013193. https:\/\/doi.org\/10.1007\/s12035-012-8307-4","journal-title":"Mol Neurobiol"},{"key":"2234_CR47","doi-asserted-by":"publisher","first-page":"231","DOI":"10.3233\/JAD-2012-121141","volume":"33","author":"I Lonskaya","year":"2013","unstructured":"Lonskaya I, Shekoyan AR, Hebron ML, Desforges N, Algarzae NK, Moussa CE (2013) Diminished parkin solubility and co-localization with intraneuronal amyloid-beta are associated with autophagic defects in Alzheimer's disease. J Alzheimers Dis 33:231\u2013247. https:\/\/doi.org\/10.3233\/JAD-2012-121141","journal-title":"J Alzheimers Dis"},{"key":"2234_CR48","doi-asserted-by":"publisher","first-page":"448","DOI":"10.1126\/science.1091230","volume":"304","author":"JW Lustbader","year":"2004","unstructured":"Lustbader JW, Cirilli M, Lin C, Xu HW, Takuma K, Wang N et al (2004) ABAD directly links Abeta to mitochondrial toxicity in Alzheimer's disease. Science 304:448\u2013452.\u00a0https:\/\/doi.org\/10.1126\/science.1091230","journal-title":"Science"},{"key":"2234_CR49","doi-asserted-by":"publisher","first-page":"2495","DOI":"10.1093\/hmg\/ddr139","volume":"20","author":"M Manczak","year":"2011","unstructured":"Manczak M, Calkins MJ, Reddy PH (2011) Impaired mitochondrial dynamics and abnormal interaction of amyloid beta with mitochondrial protein Drp1 in neurons from patients with Alzheimer's disease: implications for neuronal damage. Hum Mol Genet 20:2495\u20132509. https:\/\/doi.org\/10.1093\/hmg\/ddr139","journal-title":"Hum Mol Genet"},{"key":"2234_CR50","doi-asserted-by":"publisher","first-page":"1332","DOI":"10.1093\/hmg\/ddy042","volume":"27","author":"M Manczak","year":"2018","unstructured":"Manczak M, Kandimalla R, Yin X, Reddy PH (2018) Hippocampal mutant APP and amyloid beta-induced cognitive decline, dendritic spine loss, defective autophagy, mitophagy and mitochondrial abnormalities in a mouse model of Alzheimer's disease. Hum Mol Genet 27:1332\u20131342. https:\/\/doi.org\/10.1093\/hmg\/ddy042","journal-title":"Hum Mol Genet"},{"key":"2234_CR51","doi-asserted-by":"publisher","first-page":"792","DOI":"10.1093\/hmg\/ddv616","volume":"25","author":"P Martin-Maestro","year":"2016","unstructured":"Martin-Maestro P, Gargini R, Perry G, Avila J, Garcia-Escudero V (2016) PARK2 enhancement is able to compensate mitophagy alterations found in sporadic Alzheimer's disease. Hum Mol Genet 25:792\u2013806. https:\/\/doi.org\/10.1093\/hmg\/ddv616","journal-title":"Hum Mol Genet"},{"key":"2234_CR52","doi-asserted-by":"publisher","first-page":"2037","DOI":"10.1523\/JNEUROSCI.4264-11.2012","volume":"32","author":"Y Mitani","year":"2012","unstructured":"Mitani Y, Yarimizu J, Saita K, Uchino H, Akashiba H, Shitaka Y et al (2012) Differential effects between gamma-secretase inhibitors and modulators on cognitive function in amyloid precursor protein-transgenic and nontransgenic mice. J Neurosci 32:2037\u20132050. https:\/\/doi.org\/10.1523\/JNEUROSCI.4264-11.2012","journal-title":"J Neurosci"},{"key":"2234_CR53","doi-asserted-by":"publisher","first-page":"121","DOI":"10.3389\/fncel.2018.00121","volume":"12","author":"S Mondragon-Rodriguez","year":"2018","unstructured":"Mondragon-Rodriguez S, Gu N, Manseau F, Williams S (2018) Alzheimer's transgenic model is characterized by very early brain network alterations and beta-CTF fragment accumulation: reversal by beta-secretase inhibition. Front Cell Neurosci 12:121. https:\/\/doi.org\/10.3389\/fncel.2018.00121","journal-title":"Front Cell Neurosci"},{"key":"2234_CR54","doi-asserted-by":"publisher","first-page":"500","DOI":"10.1038\/387500a0","volume":"387","author":"J Nalbantoglu","year":"1997","unstructured":"Nalbantoglu J, Tirado-Santiago G, Lahsaini A, Poirier J, Goncalves O, Verge G et al (1997) Impaired learning and LTP in mice expressing the carboxy terminus of the Alzheimer amyloid precursor protein. Nature 387:500\u2013505. https:\/\/doi.org\/10.1038\/387500a0","journal-title":"Nature"},{"key":"2234_CR55","doi-asserted-by":"publisher","first-page":"1","DOI":"10.1007\/s00401-014-1347-2","volume":"129","author":"HS Nhan","year":"2015","unstructured":"Nhan HS, Chiang K, Koo EH (2015) The multifaceted nature of amyloid precursor protein and its proteolytic fragments: friends and foes. Acta Neuropathol 129:1\u201319. https:\/\/doi.org\/10.1007\/s00401-014-1347-2","journal-title":"Acta Neuropathol"},{"key":"2234_CR56","doi-asserted-by":"publisher","first-page":"409","DOI":"10.1016\/S0896-6273(03)00434-3","volume":"39","author":"S Oddo","year":"2003","unstructured":"Oddo S, Caccamo A, Shepherd JD, Murphy MP, Golde TE, Kayed R et al (2003) Triple-transgenic model of Alzheimer's disease with plaques and tangles: intracellular A\u03b2 and synaptic dysfunction. Neuron 39:409\u2013421.\u00a0https:\/\/doi.org\/10.1016\/S0896-6273(03)00434-3","journal-title":"Neuron"},{"key":"2234_CR57","doi-asserted-by":"publisher","first-page":"711","DOI":"10.1016\/j.beem.2012.05.003","volume":"26","author":"LD Osellame","year":"2012","unstructured":"Osellame LD, Blacker TS, Duchen MR (2012) Cellular and molecular mechanisms of mitochondrial function. Best Pract Res Clin Endocrinol Metab 26:711\u2013723. https:\/\/doi.org\/10.1016\/j.beem.2012.05.003","journal-title":"Best Pract Res Clin Endocrinol Metab"},{"key":"2234_CR58","doi-asserted-by":"publisher","first-page":"6732","DOI":"10.1523\/JNEUROSCI.16-21-06732.1996","volume":"16","author":"ML Oster-Granite","year":"1996","unstructured":"Oster-Granite ML, McPhie DL, Greenan J, Neve RL (1996) Age-dependent neuronal and synaptic degeneration in mice transgenic for the C terminus of the amyloid precursor protein. J Neurosci 16:6732\u20136741","journal-title":"J Neurosci"},{"key":"2234_CR59","doi-asserted-by":"publisher","first-page":"11820","DOI":"10.1523\/JNEUROSCI.0875-12.2012","volume":"32","author":"B Oules","year":"2012","unstructured":"Oules B, Del Prete D, Greco B, Zhang X, Lauritzen I, Sevalle J et al (2012) Ryanodine receptor blockade reduces amyloid-beta load and memory impairments in Tg2576 mouse model of Alzheimer disease. J Neurosci 32:11820\u201311834. https:\/\/doi.org\/10.1523\/JNEUROSCI.0875-12.2012","journal-title":"J Neurosci"},{"key":"2234_CR60","doi-asserted-by":"publisher","first-page":"925050","DOI":"10.4061\/2011\/925050","volume":"2011","author":"L Pagani","year":"2011","unstructured":"Pagani L, Eckert A (2011) Amyloid-Beta interaction with mitochondria. Int J Alzheimers Dis 2011:925050. https:\/\/doi.org\/10.4061\/2011\/925050","journal-title":"Int J Alzheimers Dis"},{"key":"2234_CR61","doi-asserted-by":"publisher","first-page":"78","DOI":"10.1096\/fj.10-157230","volume":"25","author":"PF Pavlov","year":"2011","unstructured":"Pavlov PF, Wiehager B, Sakai J, Frykman S, Behbahani H, Winblad B et al (2011) Mitochondrial gamma-secretase participates in the metabolism of mitochondria-associated amyloid precursor protein. FASEB J 25:78\u201388. https:\/\/doi.org\/10.1096\/fj.10-157230","journal-title":"FASEB J"},{"key":"2234_CR62","doi-asserted-by":"publisher","first-page":"201","DOI":"10.1007\/s00401-012-1062-9","volume":"125","author":"M Pera","year":"2013","unstructured":"Pera M, Alcolea D, Sanchez-Valle R, Guardia-Laguarta C, Colom-Cadena M, Badiola N et al (2013) Distinct patterns of APP processing in the CNS in autosomal-dominant and sporadic Alzheimer disease. Acta Neuropathol 125:201\u2013213. https:\/\/doi.org\/10.1007\/s00401-012-1062-9","journal-title":"Acta Neuropathol"},{"key":"2234_CR63","doi-asserted-by":"publisher","first-page":"3356","DOI":"10.15252\/embj.201796797","volume":"36","author":"M Pera","year":"2017","unstructured":"Pera M, Larrea D, Guardia-Laguarta C, Montesinos J, Velasco KR, Agrawal RR et al (2017) Increased localization of APP-C99 in mitochondria-associated ER membranes causes mitochondrial dysfunction in Alzheimer disease. EMBO J 36:3356\u20133371. https:\/\/doi.org\/10.15252\/embj.201796797","journal-title":"EMBO J"},{"key":"2234_CR64","doi-asserted-by":"publisher","first-page":"R170","DOI":"10.1016\/j.cub.2018.01.004","volume":"28","author":"S Pickles","year":"2018","unstructured":"Pickles S, Vigie P, Youle RJ (2018) Mitophagy and quality control mechanisms in mitochondrial maintenance. Curr Biol 28:R170\u2013R185. https:\/\/doi.org\/10.1016\/j.cub.2018.01.004","journal-title":"Curr Biol"},{"key":"2234_CR65","doi-asserted-by":"publisher","first-page":"22","DOI":"10.1186\/s40478-016-0292-9","volume":"4","author":"A Piras","year":"2016","unstructured":"Piras A, Collin L, Gruninger F, Graff C, Ronnback A (2016) Autophagic and lysosomal defects in human tauopathies: analysis of post-mortem brain from patients with familial Alzheimer disease, corticobasal degeneration and progressive supranuclear palsy. Acta Neuropathol Commun 4:22. https:\/\/doi.org\/10.1186\/s40478-016-0292-9","journal-title":"Acta Neuropathol Commun"},{"key":"2234_CR66","doi-asserted-by":"publisher","first-page":"273","DOI":"10.1016\/j.jalz.2019.09.002","volume":"16","author":"MV Pulina","year":"2020","unstructured":"Pulina MV, Hopkins M, Haroutunian V, Greengard P, Bustos V (2020) C99 selectively accumulates in vulnerable neurons in Alzheimer's disease. Alzheimers Dement 16:273\u2013282. https:\/\/doi.org\/10.1016\/j.jalz.2019.09.002","journal-title":"Alzheimers Dement"},{"key":"2234_CR67","doi-asserted-by":"publisher","first-page":"1463","DOI":"10.1096\/fj.00-0724fje","volume":"15","author":"JC Rah","year":"2001","unstructured":"Rah JC, Kim HS, Kim SS, Bach JH, Kim YS, Park CH et al (2001) Effects of carboxyl-terminal fragment of Alzheimer's amyloid precursor protein and amyloid beta-peptide on the production of cytokines and nitric oxide in glial cells. FASEB J 15:1463\u20131465. https:\/\/doi.org\/10.1096\/fj.00-0724fje","journal-title":"FASEB J"},{"key":"2234_CR68","doi-asserted-by":"publisher","first-page":"45","DOI":"10.1016\/j.molmed.2007.12.002","volume":"14","author":"PH Reddy","year":"2008","unstructured":"Reddy PH, Beal MF (2008) Amyloid beta, mitochondrial dysfunction and synaptic damage: implications for cognitive decline in aging and Alzheimer's disease. Trends Mol Med 14:45\u201353. https:\/\/doi.org\/10.1016\/j.molmed.2007.12.002","journal-title":"Trends Mol Med"},{"key":"2234_CR69","doi-asserted-by":"publisher","first-page":"2502","DOI":"10.1093\/hmg\/ddy154","volume":"27","author":"PH Reddy","year":"2018","unstructured":"Reddy PH, Yin X, Manczak M, Kumar S, Pradeepkiran JA, Vijayan M et al (2018) Mutant APP and amyloid beta-induced defective autophagy, mitophagy, mitochondrial structural and functional changes and synaptic damage in hippocampal neurons from Alzheimer's disease. Hum Mol Genet 27:2502\u20132516. https:\/\/doi.org\/10.1093\/hmg\/ddy154","journal-title":"Hum Mol Genet"},{"key":"2234_CR70","doi-asserted-by":"publisher","first-page":"15038","DOI":"10.1073\/pnas.0601945103","volume":"103","author":"KM Robinson","year":"2006","unstructured":"Robinson KM, Janes MS, Pehar M, Monette JS, Ross MF, Hagen TM et al (2006) Selective fluorescent imaging of superoxide in vivo using ethidium-based probes. Proc Natl Acad Sci USA 103:15038\u201315043. https:\/\/doi.org\/10.1073\/pnas.0601945103","journal-title":"Proc Natl Acad Sci USA"},{"key":"2234_CR71","doi-asserted-by":"publisher","DOI":"10.7554\/eLife.17896","author":"R Rojansky","year":"2016","unstructured":"Rojansky R, Cha MY, Chan DC (2016) Elimination of paternal mitochondria in mouse embryos occurs through autophagic degradation dependent on PARKIN and MUL1. Elife. https:\/\/doi.org\/10.7554\/eLife.17896","journal-title":"Elife"},{"key":"2234_CR72","doi-asserted-by":"publisher","first-page":"149","DOI":"10.1016\/j.conb.2019.02.001","volume":"57","author":"MJ Rossi","year":"2019","unstructured":"Rossi MJ, Pekkurnaz G (2019) Powerhouse of the mind: mitochondrial plasticity at the synapse. Curr Opin Neurobiol 57:149\u2013155. https:\/\/doi.org\/10.1016\/j.conb.2019.02.001","journal-title":"Curr Opin Neurobiol"},{"key":"2234_CR73","doi-asserted-by":"publisher","first-page":"35","DOI":"10.1016\/0009-8981(94)90055-8","volume":"228","author":"P Rustin","year":"1994","unstructured":"Rustin P, Chretien D, Bourgeron T, Gerard B, Rotig A, Saudubray JM et al (1994) Biochemical and molecular investigations in respiratory chain deficiencies. Clin Chim Acta 228:35\u201351. https:\/\/doi.org\/10.1016\/0009-8981(94)90055-8","journal-title":"Clin Chim Acta"},{"key":"2234_CR74","doi-asserted-by":"publisher","first-page":"369","DOI":"10.3233\/JAD-132543","volume":"43","author":"B Schreiner","year":"2015","unstructured":"Schreiner B, Hedskog L, Wiehager B, Ankarcrona M (2015) Amyloid-beta peptides are generated in mitochondria-associated endoplasmic reticulum membranes. J Alzheimers Dis 43:369\u2013374. https:\/\/doi.org\/10.3233\/JAD-132543","journal-title":"J Alzheimers Dis"},{"key":"2234_CR75","doi-asserted-by":"publisher","first-page":"158","DOI":"10.1016\/j.molcel.2012.09.025","volume":"48","author":"LA Sena","year":"2012","unstructured":"Sena LA, Chandel NS (2012) Physiological roles of mitochondrial reactive oxygen species. Mol Cell 48:158\u2013167. https:\/\/doi.org\/10.1016\/j.molcel.2012.09.025","journal-title":"Mol Cell"},{"key":"2234_CR76","doi-asserted-by":"publisher","first-page":"187","DOI":"10.1038\/nature25143","volume":"552","author":"V Sorrentino","year":"2017","unstructured":"Sorrentino V, Romani M, Mouchiroud L, Beck JS, Zhang H, D'Amico D et al (2017) Enhancing mitochondrial proteostasis reduces amyloid-beta proteotoxicity. Nature 552:187\u2013193. https:\/\/doi.org\/10.1038\/nature25143","journal-title":"Nature"},{"key":"2234_CR77","doi-asserted-by":"publisher","first-page":"19","DOI":"10.1186\/1750-1326-7-19","volume":"7","author":"R Tamayev","year":"2012","unstructured":"Tamayev R, D'Adamio L (2012) Inhibition of gamma-secretase worsens memory deficits in a genetically congruous mouse model of Danish dementia. Mol Neurodegener 7:19. https:\/\/doi.org\/10.1186\/1750-1326-7-19","journal-title":"Mol Neurodegener"},{"key":"2234_CR78","doi-asserted-by":"publisher","first-page":"311","DOI":"10.1016\/j.biopsych.2017.08.010","volume":"83","author":"CH van Dyck","year":"2018","unstructured":"van Dyck CH (2018) Anti-amyloid-beta monoclonal antibodies for Alzheimer's disease: pitfalls and promise. Biol Psychiatry 83:311\u2013319. https:\/\/doi.org\/10.1016\/j.biopsych.2017.08.010","journal-title":"Biol Psychiatry"},{"key":"2234_CR79","doi-asserted-by":"publisher","first-page":"19318","DOI":"10.1073\/pnas.0804871105","volume":"105","author":"X Wang","year":"2008","unstructured":"Wang X, Su B, Siedlak SL, Moreira PI, Fujioka H, Wang Y et al (2008) Amyloid-beta overproduction causes abnormal mitochondrial dynamics via differential modulation of mitochondrial fission\/fusion proteins. Proc Natl Acad Sci USA 105:19318\u201319323. https:\/\/doi.org\/10.1073\/pnas.0804871105","journal-title":"Proc Natl Acad Sci USA"},{"key":"2234_CR80","doi-asserted-by":"publisher","first-page":"1240","DOI":"10.1016\/j.bbadis.2013.10.015","volume":"1842","author":"X Wang","year":"2014","unstructured":"Wang X, Wang W, Li L, Perry G, Lee HG, Zhu X (2014) Oxidative stress and mitochondrial dysfunction in Alzheimer's disease. Biochim Biophys Acta 1842:1240\u20131247. https:\/\/doi.org\/10.1016\/j.bbadis.2013.10.015","journal-title":"Biochim Biophys Acta"},{"key":"2234_CR81","doi-asserted-by":"publisher","first-page":"22244","DOI":"10.1038\/srep22244","volume":"6","author":"Y Wang","year":"2016","unstructured":"Wang Y, Wu F, Pan H, Zheng W, Feng C, Wang Y et al (2016) Lost region in amyloid precursor protein (APP) through TALEN-mediated genome editing alters mitochondrial morphology. Sci Rep 6:22244. https:\/\/doi.org\/10.1038\/srep22244","journal-title":"Sci Rep"},{"key":"2234_CR82","doi-asserted-by":"publisher","first-page":"71","DOI":"10.1016\/j.brainresbull.2016.08.009","volume":"133","author":"HM Wilkins","year":"2017","unstructured":"Wilkins HM, Swerdlow RH (2017) Amyloid precursor protein processing and bioenergetics. Brain Res Bull 133:71\u201379. https:\/\/doi.org\/10.1016\/j.brainresbull.2016.08.009","journal-title":"Brain Res Bull"},{"key":"2234_CR83","doi-asserted-by":"publisher","first-page":"222","DOI":"10.1097\/WNR.0000000000000739","volume":"28","author":"LL Xu","year":"2017","unstructured":"Xu LL, Shen Y, Wang X, Wei LF, Wang P, Yang H et al (2017) Mitochondrial dynamics changes with age in an APPsw\/PS1dE9 mouse model of Alzheimer's disease. NeuroReport 28:222\u2013228. https:\/\/doi.org\/10.1097\/WNR.0000000000000739","journal-title":"NeuroReport"},{"key":"2234_CR84","doi-asserted-by":"publisher","first-page":"2028","DOI":"10.1080\/15548627.2017.1379633","volume":"13","author":"C Yang","year":"2017","unstructured":"Yang C, Cai CZ, Song JX, Tan JQ, Durairajan SSK, Iyaswamy A et al (2017) NRBF2 is involved in the autophagic degradation process of APP-CTFs in Alzheimer disease models. Autophagy 13:2028\u20132040. https:\/\/doi.org\/10.1080\/15548627.2017.1379633","journal-title":"Autophagy"},{"key":"2234_CR85","doi-asserted-by":"publisher","first-page":"417","DOI":"10.1126\/science.2474201","volume":"245","author":"BA Yankner","year":"1989","unstructured":"Yankner BA, Dawes LR, Fisher S, Villa-Komaroff L, Oster-Granite ML, Neve RL (1989) Neurotoxicity of a fragment of the amyloid precursor associated with Alzheimer's disease. Science 245:417\u2013420. https:\/\/doi.org\/10.1126\/science.2474201","journal-title":"Science"},{"key":"2234_CR86","doi-asserted-by":"publisher","first-page":"2938","DOI":"10.1093\/hmg\/ddv056","volume":"24","author":"X Ye","year":"2015","unstructured":"Ye X, Sun X, Starovoytov V, Cai Q (2015) Parkin-mediated mitophagy in mutant hAPP neurons and Alzheimer's disease patient brains. Hum Mol Genet 24:2938\u20132951. https:\/\/doi.org\/10.1093\/hmg\/ddv056","journal-title":"Hum Mol Genet"},{"key":"2234_CR87","doi-asserted-by":"publisher","first-page":"18","DOI":"10.14348\/molcells.2018.2277","volume":"41","author":"SM Yoo","year":"2018","unstructured":"Yoo SM, Jung YK (2018) A molecular approach to mitophagy and mitochondrial dynamics. Mol Cells 41:18\u201326. https:\/\/doi.org\/10.14348\/molcells.2018.2277","journal-title":"Mol Cells"},{"key":"2234_CR88","doi-asserted-by":"publisher","first-page":"18725","DOI":"10.1038\/srep18725","volume":"6","author":"L Zhang","year":"2016","unstructured":"Zhang L, Trushin S, Christensen TA, Bachmeier BV, Gateno B, Schroeder A et al (2016) Altered brain energetics induces mitochondrial fission arrest in Alzheimer's disease. Sci Rep 6:18725. https:\/\/doi.org\/10.1038\/srep18725","journal-title":"Sci Rep"}],"container-title":["Acta Neuropathologica"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1007\/s00401-020-02234-7.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/link.springer.com\/article\/10.1007\/s00401-020-02234-7\/fulltext.html","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1007\/s00401-020-02234-7.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2021,10,20]],"date-time":"2021-10-20T08:09:53Z","timestamp":1634717393000},"score":1,"resource":{"primary":{"URL":"https:\/\/link.springer.com\/10.1007\/s00401-020-02234-7"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2020,10,20]]},"references-count":88,"journal-issue":{"issue":"1","published-print":{"date-parts":[[2021,1]]}},"alternative-id":["2234"],"URL":"https:\/\/doi.org\/10.1007\/s00401-020-02234-7","relation":{},"ISSN":["0001-6322","1432-0533"],"issn-type":[{"value":"0001-6322","type":"print"},{"value":"1432-0533","type":"electronic"}],"subject":[],"published":{"date-parts":[[2020,10,20]]},"assertion":[{"value":"9 June 2020","order":1,"name":"received","label":"Received","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"3 September 2020","order":2,"name":"revised","label":"Revised","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"1 October 2020","order":3,"name":"accepted","label":"Accepted","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"20 October 2020","order":4,"name":"first_online","label":"First Online","group":{"name":"ArticleHistory","label":"Article History"}},{"order":1,"name":"Ethics","group":{"name":"EthicsHeading","label":"Compliance with ethical standards"}},{"value":"Authors declare no conflict of interest.","order":2,"name":"Ethics","group":{"name":"EthicsHeading","label":"Conflict of interest"}},{"value":"All applicable international, national, and\/or institutional guidelines for the care and use of animals were followed. All procedures performed in studies involving animals were in accordance with the ethical standards of the institution or practice at which the studies were conducted. In vivo experiments were performed in accordance with the guidelines established by the European community council (Directive of November 24th, 1986), and approved by Nice university Animal care and use Committee, and the National Council on animal care of the Ministry of Health (Project n\u00b0: APAFIS#20495-201904231352370). All procedures performed in studies involving human participants were in accordance with the ethical standards of the institutional and\/or national research committee and with the 1964 Helsinki declaration and its later amendments or comparable ethical studies. Brain samples were obtained from the Brain Bank \u201cNeuroCEB\u201d run by a consortium of Patients Associations: ARSEP (association for research on multiple sclerosis), CSC (cerebellar ataxias), and France Parkinson. The consents were signed by the patients themselves or their next of kin in their name, in accordance with the French Bioethical (agreement AC-2013-1887). Cases were anonymized, but information was provided regarding sex, age at death, and neuropathology (Suppl.Table 1, online resource).","order":3,"name":"Ethics","group":{"name":"EthicsHeading","label":"Ethical approval"}},{"value":"Informed consent for tissue donation for research is obtained by the brain banks under their approval procedures.","order":4,"name":"Ethics","group":{"name":"EthicsHeading","label":"Informed consent"}}]}}