{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,25]],"date-time":"2026-09-25T12:05:37Z","timestamp":1790337937325,"version":"4.1.0"},"reference-count":33,"publisher":"Springer Science and Business Media LLC","issue":"10","license":[{"start":{"date-parts":[[2026,7,19]],"date-time":"2026-07-19T00:00:00Z","timestamp":1784419200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0"},{"start":{"date-parts":[[2026,7,19]],"date-time":"2026-07-19T00:00:00Z","timestamp":1784419200000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0"}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["Eur Arch Otorhinolaryngol"],"published-print":{"date-parts":[[2026,9]]},"abstract":"<jats:title>Abstract<\/jats:title>\n                  <jats:sec>\n                    <jats:title>Introduction<\/jats:title>\n                    <jats:p>The newborn hearing screening (NHS) program in the Netherlands consist of two rounds of otoacoustic emissions (OAE) and a third round of automated auditory brainstem responses (AABR). The program identifies about 200 newborns with sensorineural hearing loss (SNHL) annually, enabling early intervention. Nevertheless, a subgroup of patients passes the NHS but present with SNHL in early childhood.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Purpose<\/jats:title>\n                    <jats:p>\n                      To determine the number of patients diagnosed with SNHL (&lt;\u20095\u00a0years) who initially passed their NHS\n                      <jats:bold>,<\/jats:bold>\n                      and characterize this group in terms of patient demographics, NHS results, hearing loss (HL) characteristics and etiology of, to identify opportunities for earlier detection.\n                    <\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Methods<\/jats:title>\n                    <jats:p>A retrospective descriptive study was conducted on patients (&lt;\u20095\u00a0years) seen between 2014 and 2024, passed their NHS and had SNHL with an unknown cause, for which they underwent etiological diagnostics.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Results<\/jats:title>\n                    <jats:p>119 patients with 205 ears were included. Three-fourth of patients had an abnormal speech and language development (SLD). A relatively large number of ears passed in the third AABR round (36%). HL characteristics were highly variable. An etiological diagnosis was found in 74 patients (62%), most commonly a genetic cause (40%) or a cochleovestibular malformation (18%).<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Conclusions<\/jats:title>\n                    <jats:p>We estimate that in the Netherlands approximately 50 patients per year present with SNHL (&lt;\u20095\u00a0years) after\u00a0passing their NHS, of which the majority manifest abnormal SLD. Highly variable HL characteristics and etiology make it difficult to identify them. Nevertheless, a possibility for earlier detection is a second screening for specific subgroups. No evidence of false negatives during NHS was found.<\/jats:p>\n                  <\/jats:sec>","DOI":"10.1007\/s00405-026-10435-1","type":"journal-article","created":{"date-parts":[[2026,7,19]],"date-time":"2026-07-19T15:49:53Z","timestamp":1784476193000},"page":"6391-6402","update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":0,"title":["Sensorineural hearing loss in early childhood after passing newborn hearing screening"],"prefix":"10.1007","volume":"283","author":[{"ORCID":"https:\/\/orcid.org\/0009-0000-2381-6430","authenticated-orcid":false,"given":"I. E. C.","family":"Smetsers","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"N.","family":"Uilenburg","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"R. J. 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