{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,15]],"date-time":"2026-09-15T03:09:49Z","timestamp":1789441789003,"version":"build-2803163510"},"reference-count":16,"publisher":"Springer Science and Business Media LLC","issue":"7","license":[{"start":{"date-parts":[[2008,6,27]],"date-time":"2008-06-27T00:00:00Z","timestamp":1214524800000},"content-version":"tdm","delay-in-days":0,"URL":"http:\/\/www.springer.com\/tdm"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["J Neurol"],"published-print":{"date-parts":[[2008,7]]},"DOI":"10.1007\/s00415-008-0779-9","type":"journal-article","created":{"date-parts":[[2008,6,21]],"date-time":"2008-06-21T18:38:06Z","timestamp":1214073486000},"page":"974-979","source":"Crossref","is-referenced-by-count":15,"title":["Is screening for urinary porphobilinogen useful among patients with acute polyneuropathy or encephalopathy?"],"prefix":"10.1007","volume":"255","author":[{"given":"E.","family":"Pischik","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"V.","family":"Kazakov","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"R.","family":"Kauppinen","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2008,6,27]]},"reference":[{"key":"779_CR1","doi-asserted-by":"crossref","first-page":"983","DOI":"10.1007\/s00415-005-0721-3","volume":"252","author":"Ahle","year":"2005","unstructured":"Ahle G, Wierzba S, Haupts M, Konig M, Gehlen W (2005) Acute left hemispheric syndrome with cortical lesions in a patient with secondary porphyrinuria. J Neurol 252:983\u2013984","journal-title":"J Neurol"},{"key":"779_CR2","doi-asserted-by":"crossref","first-page":"57","DOI":"10.1055\/s-2007-1007141","volume":"18","author":"Bonkovsky","year":"1998","unstructured":"Bonkovsky HL, Barnard GF (1998) Diagnosis of porphyric syndromes: a practical approach in the era of molecular biology. Semin Liver Dis 18:57\u201365","journal-title":"Semin Liver Dis"},{"key":"779_CR3","doi-asserted-by":"crossref","first-page":"586","DOI":"10.1002\/art.1780400329","volume":"40","author":"Cohen","year":"1997","unstructured":"Cohen PL, Hadler NM, Starkenburg R (1997) Acute intermittent porphyria presenting as acute muscle pain, fever, and weakness. Arthritis Rheum 40:586\u2013587","journal-title":"Arthritis Rheum"},{"key":"779_CR4","doi-asserted-by":"crossref","first-page":"319","DOI":"10.1136\/jnnp.62.4.319","volume":"62","author":"Crimlisk","year":"1997","unstructured":"Crimlisk HL (1997) The little imitator \u2013 porphyria: a neuropsychiatric disorder. J Neurol Neurosurg Psychiatry 62:319\u2013328","journal-title":"J Neurol Neurosurg Psychiatry"},{"key":"779_CR5","doi-asserted-by":"crossref","first-page":"693","DOI":"10.1111\/j.1468-1331.2004.00876.x","volume":"11","author":"Engelhardt","year":"2004","unstructured":"Engelhardt K, Trinka E, Franz G, Unterberger I, Spiegel M, Beer R, Pfausler B, Kampfl A, Schmutzhard E (2004) Refractory status epilepticus due to acute hepatic porphyria in a pregnant woman: induced abortion as the sole therapeutic option? Eur J Neurol 11:693\u2013697","journal-title":"Eur J Neurol"},{"key":"779_CR6","first-page":"668","volume":"84","author":"Goren","year":"1991","unstructured":"Goren MB, Chen C (1991) Acute intermittent porphyria with atypical neuropathy. South Med J 84:668\u2013669","journal-title":"South Med J"},{"key":"779_CR7","doi-asserted-by":"crossref","first-page":"1891","DOI":"10.1093\/clinchem\/48.11.1891","volume":"48","author":"Kauppinen","year":"2002","unstructured":"Kauppinen R, von und zu Fraunberg M (2002) Molecular and biochemical studies of acute intermittent porphyria in 196 patients and their families. Clin Chem 48:1891\u20131900","journal-title":"Clin Chem"},{"key":"779_CR8","doi-asserted-by":"crossref","first-page":"93","DOI":"10.1002\/bmc.1130010208","volume":"1","author":"Li","year":"1986","unstructured":"Li F, Lim CK, Peters TJ (1986) Analysis of urine and faecal porphyrins by HPLC coupled to an advanced automated sample processor. Biomed Chromatogr 1:93\u201394","journal-title":"Biomed Chromatogr"},{"key":"779_CR9","doi-asserted-by":"crossref","first-page":"1325","DOI":"10.1007\/s00415-002-0797-y","volume":"249","author":"Oberndorfer","year":"2002","unstructured":"Oberndorfer S, Hitzenberger P, Gruber W, Seidel J, Urbanits S, Doss M, Grisold W (2002) Secondary coproporphyrinuria in a patient with the full clinical picture of a hereditary acute hepatic porphyria. A misleading clinical and biochemical course. J Neurol 249:1325\u20131326","journal-title":"J Neurol"},{"key":"779_CR10","doi-asserted-by":"crossref","first-page":"1538","DOI":"10.1007\/s00415-004-0584-z","volume":"251","author":"Pischik","year":"2004","unstructured":"Pischik E, Bulyanitsa A, Kazakov V, Kauppinen R (2004) Clinical features predictive of a poor prognosis in acute porphyria. J Neurol 251:1538\u20131541","journal-title":"J Neurol"},{"key":"779_CR11","first-page":"307","volume":"38","author":"Ridley","year":"1969","unstructured":"Ridley A (1969) The neuropathy of acute intermittent porphyria. QJM 38:307\u2013333","journal-title":"QJM"},{"key":"779_CR12","unstructured":"Rimington C (1958) Quantitative determination of porphobilinogen and porphyrin in urine and faeces. Assoc Clin Path Broadsheet No. 21"},{"key":"779_CR13","doi-asserted-by":"crossref","first-page":"287","DOI":"10.1016\/0303-8467(90)90036-5","volume":"92","author":"Tan","year":"1990","unstructured":"Tan E, Kansu T, Zileli T (1990) Severe ptosis without ophthalmoplegia due to porphyric neuropathy. Clin Neurol Neurosurg 92:287\u2013288","journal-title":"Clin Neurol Neurosurg"},{"key":"779_CR14","doi-asserted-by":"crossref","first-page":"732","DOI":"10.1002\/mus.20510","volume":"33","author":"Thomson","year":"2006","unstructured":"Thomson RM, Parry GJ (2006) Neuropathies associated with excessive exposure to lead. Muscle Nerve 33:732\u2013741","journal-title":"Muscle Nerve"},{"key":"779_CR15","doi-asserted-by":"crossref","first-page":"35","DOI":"10.1097\/01.md.0000152455.38510.af","volume":"84","author":"von und zu Fraunberg","year":"2005","unstructured":"von und zu Fraunberg M, Pischik E, Udd L, Kauppinen R (2005) Clinical and biochemical characteristics and genotype-phenotype correlation in 143 Finnish and Russian patients with acute intermittent porphyria. Medicine 84:35\u201347","journal-title":"Medicine"},{"key":"779_CR16","doi-asserted-by":"crossref","first-page":"119","DOI":"10.1159\/000062990","volume":"48","author":"Yen","year":"2002","unstructured":"Yen PS, Chen CJ, Lui CC, Wai YY, Wan YL (2002) Diffusion-weighted magnetic resonance imaging of porphyric encephalopathy: a case report. Eur Neurol 48:119\u2013121","journal-title":"Eur Neurol"}],"container-title":["Journal of Neurology"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1007\/s00415-008-0779-9.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/link.springer.com\/article\/10.1007\/s00415-008-0779-9\/fulltext.html","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1007\/s00415-008-0779-9","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2020,5,6]],"date-time":"2020-05-06T14:33:59Z","timestamp":1588775639000},"score":1,"resource":{"primary":{"URL":"http:\/\/link.springer.com\/10.1007\/s00415-008-0779-9"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2008,6,27]]},"references-count":16,"journal-issue":{"issue":"7","published-print":{"date-parts":[[2008,7]]}},"alternative-id":["779"],"URL":"https:\/\/doi.org\/10.1007\/s00415-008-0779-9","relation":{},"ISSN":["0340-5354","1432-1459"],"issn-type":[{"value":"0340-5354","type":"print"},{"value":"1432-1459","type":"electronic"}],"subject":[],"published":{"date-parts":[[2008,6,27]]}}}