{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,13]],"date-time":"2026-10-13T02:36:20Z","timestamp":1791858980767,"version":"4.3.4"},"reference-count":34,"publisher":"Springer Science and Business Media LLC","issue":"10","license":[{"start":{"date-parts":[[2020,5,27]],"date-time":"2020-05-27T00:00:00Z","timestamp":1590537600000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.springer.com\/tdm"},{"start":{"date-parts":[[2020,5,27]],"date-time":"2020-05-27T00:00:00Z","timestamp":1590537600000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/www.springer.com\/tdm"}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["Pediatr Nephrol"],"published-print":{"date-parts":[[2020,10]]},"DOI":"10.1007\/s00467-020-04556-w","type":"journal-article","created":{"date-parts":[[2020,5,27]],"date-time":"2020-05-27T13:02:28Z","timestamp":1590584548000},"page":"1991-1996","update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":11,"title":["Congenital nephrotic syndrome: is early aggressive treatment needed?\u2014No"],"prefix":"10.1007","volume":"35","author":[{"given":"Olivia","family":"Boyer","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Sandra","family":"B\u00e9rody","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2020,5,27]]},"reference":[{"issue":"4","key":"4556_CR1","doi-asserted-by":"publisher","first-page":"575","DOI":"10.1016\/S1097-2765(00)80057-X","volume":"1","author":"M Kestila","year":"1998","unstructured":"Kestila M, Lenkkeri U, Mannikko M, Lamerdin J, McCready P, Putaala H et al (1998) Positionally cloned gene for a novel glomerular protein-nephrin-is mutated in congenital nephrotic syndrome. Mol Cell 1(4):575\u2013582","journal-title":"Mol Cell"},{"issue":"5","key":"4556_CR2","doi-asserted-by":"publisher","first-page":"368","DOI":"10.1002\/humu.1111","volume":"17","author":"O Beltcheva","year":"2001","unstructured":"Beltcheva O, Martin P, Lenkkeri U, Tryggvason K (2001) Mutation spectrum in the nephrin gene (NPHS1) in congenital nephrotic syndrome. Hum Mutat 17(5):368\u2013373","journal-title":"Hum Mutat"},{"issue":"9","key":"4556_CR3","doi-asserted-by":"publisher","first-page":"2837","DOI":"10.1093\/ndt\/gfq434","volume":"25","author":"N Godefroid","year":"2010","unstructured":"Godefroid N, Dahan K (2010) Expanding the clinical spectrum of congenital nephrotic syndrome caused by NPHS1 mutations. Nephrol Dial Transplant 25(9):2837\u20132839","journal-title":"Nephrol Dial Transplant"},{"issue":"11","key":"4556_CR4","doi-asserted-by":"publisher","first-page":"3527","DOI":"10.1093\/ndt\/gfn271","volume":"23","author":"SF Heeringa","year":"2008","unstructured":"Heeringa SF, Vlangos CN, Chernin G, Hinkes B, Gbadegesin R, Liu J et al (2008) Thirteen novel NPHS1 mutations in a large cohort of children with congenital nephrotic syndrome. Nephrol Dial Transplant 23(11):3527\u20133533","journal-title":"Nephrol Dial Transplant"},{"issue":"9","key":"4556_CR5","doi-asserted-by":"publisher","first-page":"2970","DOI":"10.1093\/ndt\/gfq088","volume":"25","author":"DS Schoeb","year":"2010","unstructured":"Schoeb DS, Chernin G, Heeringa SF, Matejas V, Held S, Vega-Warner V et al (2010) Nineteen novel NPHS1 mutations in a worldwide cohort of patients with congenital nephrotic syndrome (CNS). Nephrol Dial Transplant 25(9):2970\u20132976","journal-title":"Nephrol Dial Transplant"},{"issue":"1","key":"4556_CR6","doi-asserted-by":"publisher","first-page":"51","DOI":"10.1086\/302182","volume":"64","author":"U Lenkkeri","year":"1999","unstructured":"Lenkkeri U, Mannikko M, McCready P, Lamerdin J, Gribouval O, Niaudet PM et al (1999) Structure of the gene for congenital nephrotic syndrome of the finnish type (NPHS1) and characterization of mutations. Am J Hum Genet 64(1):51\u201361","journal-title":"Am J Hum Genet"},{"key":"4556_CR7","doi-asserted-by":"publisher","first-page":"178","DOI":"10.1002\/humu.22485","volume":"35","author":"K Bouchireb","year":"2014","unstructured":"Bouchireb K, Boyer O, Gribouval O, Nevo F, Huynh-Cong E, Morini\u00e8re V et al (2014) NPHS2 mutations in steroid-resistant nephrotic syndrome: a mutation update and the associated phenotypic spectrum. Hum Mutat 35:178\u2013186","journal-title":"Hum Mutat"},{"issue":"4","key":"4556_CR8","doi-asserted-by":"publisher","first-page":"379","DOI":"10.1093\/hmg\/11.4.379","volume":"11","author":"A Koziell","year":"2002","unstructured":"Koziell A, Grech V, Hussain S, Lee G, Lenkkeri U, Tryggvason K et al (2002) Genotype\/phenotype correlations of NPHS1 and NPHS2 mutations in nephrotic syndrome advocate a functional inter-relationship in glomerular filtration. Hum Mol Genet 11(4):379\u2013388","journal-title":"Hum Mol Genet"},{"issue":"4","key":"4556_CR9","doi-asserted-by":"publisher","first-page":"349","DOI":"10.1038\/74166","volume":"24","author":"N Boute","year":"2000","unstructured":"Boute N, Gribouval O, Roselli S, Benessy F, Lee H, Fuchshuber A et al (2000) NPHS2, encoding the glomerular protein podocin, is mutated in autosomal recessive steroid-resistant nephrotic syndrome. Nat Genet 24(4):349\u2013354","journal-title":"Nat Genet"},{"issue":"7","key":"4556_CR10","doi-asserted-by":"publisher","first-page":"1209","DOI":"10.1681\/ASN.2009121309","volume":"21","author":"E Machuca","year":"2010","unstructured":"Machuca E, Benoit G, Nevo F, Tete MJ, Gribouval O, Pawtowski A et al (2010) Genotype-phenotype correlations in non-Finnish congenital nephrotic syndrome. J Am Soc Nephrol 21(7):1209\u20131217","journal-title":"J Am Soc Nephrol"},{"issue":"2","key":"4556_CR11","doi-asserted-by":"publisher","first-page":"365","DOI":"10.1681\/ASN.2007040452","volume":"19","author":"B Hinkes","year":"2008","unstructured":"Hinkes B, Vlangos C, Heeringa S, Mucha B, Gbadegesin R, Liu J et al (2008) Specific podocin mutations correlate with age of onset in steroid-resistant nephrotic syndrome. J Am Soc Nephrol 19(2):365\u2013371","journal-title":"J Am Soc Nephrol"},{"issue":"12","key":"4556_CR12","doi-asserted-by":"publisher","first-page":"1397","DOI":"10.1038\/ng1918","volume":"38","author":"B Hinkes","year":"2006","unstructured":"Hinkes B, Wiggins RC, Gbadegesin R, Vlangos CN, Seelow D, Nurnberg G et al (2006) Positional cloning uncovers mutations in PLCE1 responsible for a nephrotic syndrome variant that may be reversible. Nat Genet 38(12):1397\u20131405","journal-title":"Nat Genet"},{"issue":"4","key":"4556_CR13","doi-asserted-by":"publisher","first-page":"e907","DOI":"10.1542\/peds.2006-2164","volume":"119","author":"BG Hinkes","year":"2007","unstructured":"Hinkes BG, Mucha B, Vlangos CN, Gbadegesin R, Liu J, Hasselbacher K et al (2007) Nephrotic syndrome in the first year of life: two thirds of cases are caused by mutations in 4 genes (NPHS1, NPHS2, WT1, and LAMB2). Pediatrics. 119(4):e907\u2013e919","journal-title":"Pediatrics."},{"issue":"4","key":"4556_CR14","doi-asserted-by":"publisher","first-page":"1291","DOI":"10.1093\/ndt\/gfm759","volume":"23","author":"R Gbadegesin","year":"2008","unstructured":"Gbadegesin R, Hinkes BG, Hoskins BE, Vlangos CN, Heeringa SF, Liu J et al (2008) Mutations in PLCE1 are a major cause of isolated diffuse mesangial sclerosis (IDMS). Nephrol Dial Transplant 23(4):1291\u20131297","journal-title":"Nephrol Dial Transplant"},{"issue":"4","key":"4556_CR15","doi-asserted-by":"publisher","first-page":"824","DOI":"10.1086\/301806","volume":"62","author":"C Jeanpierre","year":"1998","unstructured":"Jeanpierre C, Denamur E, Henry I, Cabanis MO, Luce S, C\u00e9cille A et al (1998) Identification of constitutional WT1 mutations, in patients with isolated diffuse mesangial sclerosis, and analysis of genotype\/phenotype correlations by use of a computerized mutation database. Am J Hum Genet 62(4):824\u2013833","journal-title":"Am J Hum Genet"},{"issue":"5","key":"4556_CR16","doi-asserted-by":"publisher","first-page":"344","DOI":"10.1136\/adc.51.5.344","volume":"51","author":"NP Huttunen","year":"1976","unstructured":"Huttunen NP (1976) Congenital nephrotic syndrome of Finnish type. Study of 75 patients. Arch Child 51(5):344\u2013348","journal-title":"Arch Child"},{"issue":"1","key":"4556_CR17","doi-asserted-by":"publisher","first-page":"87","DOI":"10.1007\/BF00858984","volume":"9","author":"C Holmberg","year":"1995","unstructured":"Holmberg C, Antikainen M, Ronnholm K, Ala Houhala M, Jalanko H (1995) Management of congenital nephrotic syndrome of the Finnish type. Pediatr Nephrol 9(1):87\u201393","journal-title":"Pediatr Nephrol"},{"issue":"7817","key":"4556_CR18","doi-asserted-by":"publisher","first-page":"1410","DOI":"10.1016\/S0140-6736(73)91738-8","volume":"1","author":"JR Hoyer","year":"1973","unstructured":"Hoyer JR, Kjellstrand CM, Simmons RL, Naharian JS, Mauer SM, Buselmeier TJ et al (1973) Successful renal transplantation in 3 children with congenital nephrotic syndrome. Lancet. 1(7817):1410\u20131412","journal-title":"Lancet."},{"issue":"5","key":"4556_CR19","doi-asserted-by":"publisher","first-page":"466","DOI":"10.1136\/adc.80.5.466","volume":"80","author":"JM Savage","year":"1999","unstructured":"Savage JM, Jefferson JA, Maxwell AP, Hughes AE, Shanks JH, Gill D (1999) Improved prognosis for congenital nephrotic syndrome of the Finnish type in Irish families. Arch Child 80(5):466\u2013469","journal-title":"Arch Child"},{"issue":"12","key":"4556_CR20","doi-asserted-by":"publisher","first-page":"2317","DOI":"10.1007\/s00467-016-3517-z","volume":"31","author":"T Holtta","year":"2016","unstructured":"Holtta T, Bonthuis M, Van Stralen KJ, Bjerre A, Topaloglu R, Ozaltin F et al (2016) Timing of renal replacement therapy does not influence survival and growth in children with congenital nephrotic syndrome caused by mutations in NPHS1: data from the ESPN\/ERA-EDTA Registry. Pediatr Nephrol 31(12):2317\u20132325","journal-title":"Pediatr Nephrol"},{"key":"4556_CR21","doi-asserted-by":"crossref","unstructured":"Berody S, Heidet L, Gribouval O, Harambat J, Niaudet P, Baudouin V, et al. (2018) Treatment and outcome of congenital nephrotic syndrome. Nephrol Dial Transpl","DOI":"10.1093\/ndt\/gfy015"},{"key":"4556_CR22","doi-asserted-by":"crossref","unstructured":"Dufek S, Holtta T, Trautmann A, Ylinen E, Alpay H, Ariceta G et al (2018) Management of children with congenital nephrotic syndrome: challenging treatment paradigms. Nephrol Dial Transplant 21","DOI":"10.1136\/archdischild-2017-084620.23"},{"issue":"11","key":"4556_CR23","doi-asserted-by":"publisher","first-page":"2045","DOI":"10.1007\/s00467-015-3177-4","volume":"30","author":"BC Reynolds","year":"2015","unstructured":"Reynolds BC, Pickles CW, Lambert HJ, Ognjanovic M, Crosier J, Johnson SA et al (2015) Domiciliary administration of intravenous albumin in congenital nephrotic syndrome. Pediatr Nephrol 30(11):2045\u20132050","journal-title":"Pediatr Nephrol"},{"issue":"9","key":"4556_CR24","doi-asserted-by":"publisher","first-page":"992","DOI":"10.1136\/adc.65.9.992","volume":"65","author":"CR Banton","year":"1990","unstructured":"Banton CR, Thalayasingam B, Coulthard MG (1990) Spontaneous resolution of congenital nephrotic syndrome in a neonate. Arch Dis Child 65(9):992\u2013993","journal-title":"Arch Dis Child"},{"issue":"6","key":"4556_CR25","doi-asserted-by":"publisher","first-page":"752","DOI":"10.1136\/adc.66.6.752-a","volume":"66","author":"G Smith","year":"1991","unstructured":"Smith G, Winterborn M, White RH (1991) Spontaneous resolution of congenital nephrotic syndrome in a neonate. Arch Dis Child 66(6):752\u2013753","journal-title":"Arch Dis Child"},{"issue":"10","key":"4556_CR26","doi-asserted-by":"publisher","first-page":"1897","DOI":"10.1007\/s00467-011-1911-0","volume":"26","author":"JJ Kim","year":"2011","unstructured":"Kim JJ, Clothier J, Sebire NJ, Milford DV, Moghal N, Trompeter RS (2011) Nephrotic syndrome in infancy can spontaneously resolve. Pediatr Nephrol 26(10):1897\u20131901","journal-title":"Pediatr Nephrol"},{"issue":"6","key":"4556_CR27","first-page":"561","volume":"65","author":"D Canalejo Gonzalez","year":"2006","unstructured":"Canalejo Gonzalez D, Gonzalez Rodriguez JD, Navas Lopez VM, Sanchez-Moreno A, Fijo Lopez-Viota J, Martin-Govantes J (2006) Evaluation of therapeutic strategies in congenital nephrotic syndrome of the Finnish type. Pediatr Barc 65(6):561\u2013568","journal-title":"Pediatr Barc"},{"issue":"4","key":"4556_CR28","doi-asserted-by":"publisher","first-page":"549","DOI":"10.1016\/S0022-3476(84)80418-7","volume":"105","author":"JD Mahan","year":"1984","unstructured":"Mahan JD, Mauer SM, Sibley RK, Vernier RL (1984) Congenital nephrotic syndrome: evolution of medical management and results of renal transplantation. J Pediatr 105(4):549\u2013557","journal-title":"J Pediatr"},{"issue":"2","key":"4556_CR29","doi-asserted-by":"publisher","first-page":"148","DOI":"10.1007\/s004670050246","volume":"11","author":"P Ljungberg","year":"1997","unstructured":"Ljungberg P, Holmberg C, Jalanko H (1997) Infections in infants with congenital nephrosis of the Finnish type. Pediatr Nephrol 11(2):148\u2013152","journal-title":"Pediatr Nephrol"},{"key":"4556_CR30","doi-asserted-by":"crossref","unstructured":"Dufek S, Ylinen E, Trautmann A, Alpay H, Ariceta G, Aufricht C, et al. 2018 Infants with congenital nephrotic syndrome have comparable outcomes to infants with other renal diseases. Pediatr Nephrol.","DOI":"10.1007\/s00467-018-4122-0"},{"issue":"8","key":"4556_CR31","doi-asserted-by":"publisher","first-page":"1058","DOI":"10.1007\/s10157-019-01732-7","volume":"23","author":"K Nishi","year":"2019","unstructured":"Nishi K, Inoguchi T, Kamei K, Hamada R, Hataya H, Ogura M et al (2019) Detailed clinical manifestations at onset and prognosis of neonatal-onset Denys-Drash syndrome and congenital nephrotic syndrome of the Finnish type. Clin Exp Nephrol 23(8):1058\u20131065","journal-title":"Clin Exp Nephrol"},{"issue":"10","key":"4556_CR32","doi-asserted-by":"publisher","first-page":"1871","DOI":"10.1681\/ASN.2008010059","volume":"19","author":"A Philippe","year":"2008","unstructured":"Philippe A, Nevo F, Esquivel EL, Reklaityte D, Gribouval O, Tete MJ et al (2008) Nephrin mutations can cause childhood-onset steroid-resistant nephrotic syndrome. J Am Soc Nephrol 19(10):1871\u20131878","journal-title":"J Am Soc Nephrol"},{"issue":"23","key":"4556_CR33","doi-asserted-by":"publisher","first-page":"2637","DOI":"10.1093\/hmg\/10.23.2637","volume":"10","author":"L Liu","year":"2001","unstructured":"Liu L, Done SC, Khoshnoodi J, Bertorello A, Wartiovaara J, Berggren PO et al (2001) Defective nephrin trafficking caused by missense mutations in the NPHS1 gene: insight into the mechanisms of congenital nephrotic syndrome. Hum Mol Genet 10(23):2637\u20132644","journal-title":"Hum Mol Genet"},{"issue":"3","key":"4556_CR34","doi-asserted-by":"publisher","first-page":"972","DOI":"10.1046\/j.1523-1755.2000.00254.x","volume":"58","author":"J Patrakka","year":"2000","unstructured":"Patrakka J, Kestil\u00e4 M, Wartiovaara J, Ruotsalainen V, Tissari P, Lenkkeri U et al (2000) Congenital nephrotic syndrome (NPHS1): features resulting from different mutations in Finnish patients. Kidney Int 58(3):972\u2013980","journal-title":"Kidney Int"}],"container-title":["Pediatric Nephrology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1007\/s00467-020-04556-w.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/link.springer.com\/article\/10.1007\/s00467-020-04556-w\/fulltext.html","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1007\/s00467-020-04556-w.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2021,5,26]],"date-time":"2021-05-26T23:48:03Z","timestamp":1622072883000},"score":1,"resource":{"primary":{"URL":"https:\/\/link.springer.com\/10.1007\/s00467-020-04556-w"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2020,5,27]]},"references-count":34,"journal-issue":{"issue":"10","published-print":{"date-parts":[[2020,10]]}},"alternative-id":["4556"],"URL":"https:\/\/doi.org\/10.1007\/s00467-020-04556-w","relation":{},"ISSN":["0931-041X","1432-198X"],"issn-type":[{"value":"0931-041X","type":"print"},{"value":"1432-198X","type":"electronic"}],"subject":[],"published":{"date-parts":[[2020,5,27]]},"assertion":[{"value":"30 November 2019","order":1,"name":"received","label":"Received","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"25 March 2020","order":2,"name":"revised","label":"Revised","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"27 March 2020","order":3,"name":"accepted","label":"Accepted","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"27 May 2020","order":4,"name":"first_online","label":"First Online","group":{"name":"ArticleHistory","label":"Article History"}}]}}