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Patients are characterized by the classic triad of congenital ichthyosiform erythroderma, a hair shaft abnormality termed trichorrhexis invaginata and atopic diathesis. These children require meticulous fluid and salt control from the first day of life to prevent kidney damage due to the defective skin barrier.<\/jats:p>","DOI":"10.1007\/s00467-025-06821-2","type":"journal-article","created":{"date-parts":[[2025,6,5]],"date-time":"2025-06-05T02:24:45Z","timestamp":1749090285000},"page":"3391-3393","update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":0,"title":["Bilateral renal vein thrombosis in a preterm with Netherton syndrome"],"prefix":"10.1007","volume":"40","author":[{"ORCID":"https:\/\/orcid.org\/0009-0000-8472-1670","authenticated-orcid":false,"given":"Ana","family":"Roche-Gomez","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Diana","family":"Voskanyan","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Joanna","family":"\u015aladowska-Koz\u0142owska","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Giulia","family":"Bassanese","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Claus Peter","family":"Schmitt","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"297","published-online":{"date-parts":[[2025,6,5]]},"reference":[{"key":"6821_CR1","doi-asserted-by":"publisher","first-page":"693","DOI":"10.1111\/j.1365-4632.2005.02637.x","volume":"45","author":"J Sun","year":"2006","unstructured":"Sun J, Linden K (2006) Netherton syndrome: a case report and review of the literature. 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