{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,23]],"date-time":"2026-09-23T21:37:33Z","timestamp":1790199453356,"version":"4.1.0"},"reference-count":89,"publisher":"Springer Science and Business Media LLC","issue":"4","license":[{"start":{"date-parts":[[2007,6,25]],"date-time":"2007-06-25T00:00:00Z","timestamp":1182729600000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.springer.com\/tdm"},{"start":{"date-parts":[[2007,6,25]],"date-time":"2007-06-25T00:00:00Z","timestamp":1182729600000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/www.springer.com\/tdm"}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["J Bone Miner Metab"],"published-print":{"date-parts":[[2007,7]]},"DOI":"10.1007\/s00774-007-0750-3","type":"journal-article","created":{"date-parts":[[2007,6,25]],"date-time":"2007-06-25T10:01:46Z","timestamp":1182765706000},"page":"211-218","update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":24,"title":["Animal models of osteogenesis imperfecta and related syndromes"],"prefix":"10.1007","volume":"25","author":[{"given":"Agn\u00e8s S.","family":"Kamoun-Goldrat","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Martine F.","family":"Le Merrer","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2007,6,25]]},"reference":[{"key":"750_CR1","doi-asserted-by":"publisher","first-page":"1377","DOI":"10.1016\/S0140-6736(04)16051-0","volume":"363","author":"F Rauch","year":"2004","journal-title":"Lancet"},{"key":"750_CR2","doi-asserted-by":"publisher","first-page":"101","DOI":"10.1136\/jmg.16.2.101","volume":"16","author":"DO Sillence","year":"1979","journal-title":"J Med Genet"},{"key":"750_CR3","doi-asserted-by":"publisher","first-page":"627","DOI":"10.1136\/jcp.49.8.627","volume":"49","author":"SJ McAllion","year":"1996","journal-title":"J Clin Pathol"},{"key":"750_CR4","doi-asserted-by":"crossref","first-page":"351","DOI":"10.1136\/bmj.312.7027.351","volume":"312","author":"CR Paterson","year":"1996","journal-title":"BMJ"},{"key":"750_CR5","doi-asserted-by":"publisher","first-page":"1650","DOI":"10.1359\/jbmr.2000.15.9.1650","volume":"15","author":"FH Glorieux","year":"2000","journal-title":"J Bone Miner Res"},{"key":"750_CR6","doi-asserted-by":"publisher","first-page":"30","DOI":"10.1359\/jbmr.2002.17.1.30","volume":"17","author":"FH Glorieux","year":"2002","journal-title":"J Bone Miner Res"},{"key":"750_CR7","doi-asserted-by":"crossref","first-page":"12","DOI":"10.1016\/S8756-3282(02)00790-1","volume":"31","author":"LM Ward","year":"2002","journal-title":"Bone (NY)"},{"key":"750_CR8","doi-asserted-by":"publisher","first-page":"76","DOI":"10.1016\/S0022-3476(87)80292-5","volume":"110","author":"DE Cole","year":"1987","journal-title":"J Pediatr"},{"key":"750_CR9","doi-asserted-by":"publisher","first-page":"117","DOI":"10.1007\/s002470050309","volume":"28","author":"MF Blacksin","year":"1998","journal-title":"Pediatr Radiol"},{"key":"750_CR10","doi-asserted-by":"publisher","first-page":"23","DOI":"10.1136\/jmg.39.1.23","volume":"39","author":"JM Pace","year":"2002","journal-title":"J Med Genet"},{"key":"750_CR11","first-page":"95","volume":"14","author":"M Buyse","year":"1978","journal-title":"Birth Defects Orig Artic Ser"},{"key":"750_CR12","doi-asserted-by":"publisher","first-page":"263","DOI":"10.1111\/j.1399-0004.1986.tb00823.x","volume":"29","author":"P Beighton","year":"1986","journal-title":"Clin Genet"},{"key":"750_CR13","first-page":"224","volume":"76","author":"J Capoen","year":"1993","journal-title":"J Belge Radiol"},{"key":"750_CR14","doi-asserted-by":"publisher","first-page":"16","DOI":"10.1186\/1471-2431-4-16","volume":"4","author":"H Plotkin","year":"2004","journal-title":"BMC Pediatr"},{"key":"750_CR15","doi-asserted-by":"publisher","first-page":"1504","DOI":"10.1073\/pnas.81.5.1504","volume":"81","author":"K Harbers","year":"1984","journal-title":"Proc Natl Acad Sci U S A"},{"key":"750_CR16","doi-asserted-by":"publisher","first-page":"315","DOI":"10.1038\/304315a0","volume":"304","author":"A Schnieke","year":"1983","journal-title":"Nature (Lond)"},{"key":"750_CR17","doi-asserted-by":"publisher","first-page":"597","DOI":"10.1016\/0092-8674(84)90514-2","volume":"38","author":"J Lohler","year":"1984","journal-title":"Cell"},{"key":"750_CR18","doi-asserted-by":"publisher","first-page":"454","DOI":"10.1111\/j.1432-1033.1969.tb19631.x","volume":"7","author":"C Tkocz","year":"1969","journal-title":"Eur J Biochem"},{"key":"750_CR19","doi-asserted-by":"publisher","first-page":"209","DOI":"10.1016\/0092-8674(83)90511-1","volume":"32","author":"R Jaenisch","year":"1983","journal-title":"Cell"},{"key":"750_CR20","doi-asserted-by":"publisher","first-page":"7145","DOI":"10.1073\/pnas.87.18.7145","volume":"87","author":"J Bonadio","year":"1990","journal-title":"Proc Natl Acad Sci U S A"},{"key":"750_CR21","doi-asserted-by":"publisher","first-page":"807","DOI":"10.1016\/0092-8674(89)90795-2","volume":"57","author":"K Kratochwil","year":"1989","journal-title":"Cell"},{"key":"750_CR22","doi-asserted-by":"publisher","first-page":"764","DOI":"10.1073\/pnas.84.3.764","volume":"84","author":"A Schnieke","year":"1987","journal-title":"Proc Natl Acad Sci U S A"},{"key":"750_CR23","doi-asserted-by":"crossref","first-page":"1697","DOI":"10.1172\/JCI116756","volume":"92","author":"J Bonadio","year":"1993","journal-title":"J Clin Invest"},{"key":"750_CR24","doi-asserted-by":"publisher","first-page":"37923","DOI":"10.1074\/jbc.274.53.37923","volume":"274","author":"A Forlino","year":"1999","journal-title":"J Biol Chem"},{"key":"750_CR25","doi-asserted-by":"publisher","first-page":"1701","DOI":"10.1073\/pnas.90.5.1701","volume":"90","author":"SD Chipman","year":"1993","journal-title":"Proc Natl Acad Sci U S A"},{"key":"750_CR26","doi-asserted-by":"crossref","first-page":"1039","DOI":"10.1016\/j.bone.2005.03.004","volume":"36","author":"GE Lopez Franco","year":"2005","journal-title":"Bone (NY)"},{"key":"750_CR27","doi-asserted-by":"crossref","first-page":"453","DOI":"10.1016\/S8756-3282(01)00594-4","volume":"29","author":"B Grabner","year":"2001","journal-title":"Bone (NY)"},{"key":"750_CR28","doi-asserted-by":"crossref","first-page":"40","DOI":"10.1172\/JCI119519","volume":"100","author":"K Misof","year":"1997","journal-title":"J Clin Invest"},{"key":"750_CR29","doi-asserted-by":"publisher","first-page":"172","DOI":"10.1007\/s002239900412","volume":"62","author":"DJ McBride Jr","year":"1998","journal-title":"Calcif Tissue Int"},{"key":"750_CR30","doi-asserted-by":"crossref","first-page":"189","DOI":"10.3109\/03008209909005282","volume":"40","author":"SS Mehta","year":"1999","journal-title":"Connect Tissue Res"},{"key":"750_CR31","doi-asserted-by":"publisher","first-page":"264","DOI":"10.1359\/jbmr.1999.14.2.264","volume":"14","author":"NP Camacho","year":"1999","journal-title":"J Bone Miner Res"},{"key":"750_CR32","doi-asserted-by":"publisher","first-page":"807","DOI":"10.1006\/jmbi.2001.4682","volume":"309","author":"N Kuznetsova","year":"2001","journal-title":"J Mol Biol"},{"issue":"suppl 1","key":"750_CR33","doi-asserted-by":"crossref","first-page":"202","DOI":"10.1080\/03008200390181663","volume":"44","author":"TJ Sims","year":"2003","journal-title":"Connect Tissue Res"},{"key":"750_CR34","doi-asserted-by":"publisher","first-page":"604","DOI":"10.1007\/s00223-002-1038-1","volume":"72","author":"NP Camacho","year":"2003","journal-title":"Calcif Tissue Int"},{"key":"750_CR35","doi-asserted-by":"crossref","first-page":"396","DOI":"10.1172\/JCI118428","volume":"97","author":"P Fratzl","year":"1996","journal-title":"J Clin Invest"},{"key":"750_CR36","doi-asserted-by":"crossref","first-page":"575","DOI":"10.1016\/S8756-3282(96)00305-5","volume":"19","author":"J Saban","year":"1996","journal-title":"Bone (NY)"},{"key":"750_CR37","doi-asserted-by":"crossref","first-page":"663","DOI":"10.1161\/01.RES.87.8.663","volume":"87","author":"SM Weis","year":"2000","journal-title":"Circ Res"},{"key":"750_CR38","doi-asserted-by":"publisher","first-page":"383","DOI":"10.1046\/j.1523-1755.2002.00451.x","volume":"62","author":"CL Phillips","year":"2002","journal-title":"Kidney Int"},{"key":"750_CR39","doi-asserted-by":"publisher","first-page":"451","DOI":"10.1016\/j.matbio.2005.07.001","volume":"24","author":"BJ Pfeiffer","year":"2005","journal-title":"Matrix Biol"},{"key":"750_CR40","doi-asserted-by":"crossref","first-page":"268","DOI":"10.1016\/S8756-3282(02)00974-2","volume":"32","author":"KD Evans","year":"2003","journal-title":"Bone (NY)"},{"key":"750_CR41","doi-asserted-by":"crossref","first-page":"660","DOI":"10.1203\/00006450-200211000-00010","volume":"52","author":"EA McCarthy","year":"2002","journal-title":"Pediatr Res"},{"key":"750_CR42","doi-asserted-by":"publisher","first-page":"94","DOI":"10.1007\/s002230010045","volume":"69","author":"NP Camacho","year":"2001","journal-title":"Calcif Tissue Int"},{"key":"750_CR43","doi-asserted-by":"publisher","first-page":"987","DOI":"10.1359\/JBMR.050108","volume":"20","author":"D King","year":"2005","journal-title":"J Bone Miner Res"},{"key":"750_CR44","doi-asserted-by":"publisher","first-page":"321","DOI":"10.1038\/sj.gt.3300839","volume":"6","author":"M Oyama","year":"1999","journal-title":"Gene Ther"},{"key":"750_CR45","doi-asserted-by":"publisher","first-page":"84","DOI":"10.1002\/jcb.1209","volume":"83","author":"C Niyibizi","year":"2001","journal-title":"J Cell Biochem"},{"key":"750_CR46","doi-asserted-by":"publisher","first-page":"614","DOI":"10.1359\/JBMR.040111","volume":"19","author":"KM Kozloff","year":"2004","journal-title":"J Bone Miner Res"},{"key":"750_CR47","doi-asserted-by":"publisher","first-page":"101","DOI":"10.1016\/j.matbio.2004.03.002","volume":"23","author":"NV Kuznetsova","year":"2004","journal-title":"Matrix Biol"},{"key":"750_CR48","doi-asserted-by":"publisher","first-page":"131","DOI":"10.1038\/332131a0","volume":"332","author":"A Stacey","year":"1988","journal-title":"Nature (Lond)"},{"key":"750_CR49","doi-asserted-by":"crossref","first-page":"23373","DOI":"10.1016\/S0021-9258(18)54506-3","volume":"266","author":"JS Khillan","year":"1991","journal-title":"J Biol Chem"},{"key":"750_CR50","doi-asserted-by":"crossref","first-page":"611","DOI":"10.1016\/8756-3282(94)90308-5","volume":"15","author":"JP Cassella","year":"1994","journal-title":"Bone (NY)"},{"key":"750_CR51","doi-asserted-by":"crossref","first-page":"709","DOI":"10.1172\/JCI116252","volume":"91","author":"R Pereira","year":"1993","journal-title":"J Clin Invest"},{"key":"750_CR52","doi-asserted-by":"crossref","first-page":"1765","DOI":"10.1172\/JCI117161","volume":"93","author":"R Pereira","year":"1994","journal-title":"J Clin Invest"},{"key":"750_CR53","doi-asserted-by":"publisher","first-page":"1837","DOI":"10.1002\/jbmr.5650101202","volume":"10","author":"RF Pereira","year":"1995","journal-title":"J Bone Miner Res"},{"key":"750_CR54","first-page":"108","volume":"53","author":"JP Cassella","year":"1996","journal-title":"Br J Biomed Sci"},{"key":"750_CR55","doi-asserted-by":"crossref","first-page":"183","DOI":"10.2460\/javma.1997.211.02.183","volume":"211","author":"BG Campbell","year":"1997","journal-title":"J Am Vet Med Assoc"},{"key":"750_CR56","doi-asserted-by":"publisher","first-page":"37","DOI":"10.1006\/abbi.2000.2099","volume":"384","author":"BG Campbell","year":"2000","journal-title":"Arch Biochem Biophys"},{"key":"750_CR57","doi-asserted-by":"publisher","first-page":"1147","DOI":"10.1359\/jbmr.2001.16.6.1147","volume":"16","author":"BG Campbell","year":"2001","journal-title":"J Bone Miner Res"},{"key":"750_CR58","first-page":"1047","volume":"69","author":"JR Holmes","year":"1957","journal-title":"Vet Rec"},{"key":"750_CR59","first-page":"936","volume":"7","author":"E Lettow","year":"1960","journal-title":"Zentbl Vetmed"},{"key":"750_CR60","first-page":"92","volume":"54","author":"V Schmidt","year":"1967","journal-title":"Wien Tierarztl Monschr"},{"key":"750_CR61","doi-asserted-by":"publisher","first-page":"64","DOI":"10.1016\/S0012-1606(03)00399-3","volume":"264","author":"P Jagadeeswaran","year":"2003","journal-title":"Dev Biol"},{"key":"750_CR62","first-page":"450","volume":"130","author":"JW Skaggs","year":"1957","journal-title":"J Am Vet Med Assoc"},{"key":"750_CR63","first-page":"980","volume":"76","author":"JR Holmes","year":"1964","journal-title":"Vet Rec"},{"key":"750_CR64","first-page":"304","volume":"28","author":"PT Jensen","year":"1976","journal-title":"Nord Vet Med"},{"key":"750_CR65","first-page":"2083","volume":"55","author":"C Dell'Orbo","year":"1979","journal-title":"Boll Soc Ital Biol Sper"},{"key":"750_CR66","doi-asserted-by":"crossref","first-page":"9","DOI":"10.1111\/j.1751-0813.1983.tb02799.x","volume":"60","author":"LJ Denholm","year":"1983","journal-title":"Aust Vet J"},{"key":"750_CR67","first-page":"49","volume":"1","author":"SA Horvarth","year":"1986","journal-title":"Av Cienc Vet"},{"key":"750_CR68","doi-asserted-by":"publisher","first-page":"16","DOI":"10.1007\/BF02556589","volume":"38","author":"LW Fisher","year":"1986","journal-title":"Calcif Tissue Int"},{"key":"750_CR69","doi-asserted-by":"publisher","first-page":"282","DOI":"10.1007\/BF02555262","volume":"40","author":"LW Fisher","year":"1987","journal-title":"Calcif Tissue Int"},{"key":"750_CR70","doi-asserted-by":"crossref","first-page":"98","DOI":"10.2460\/javma.1990.197.01.98","volume":"197","author":"LA Cohn","year":"1990","journal-title":"J Am Vet Med Assoc"},{"key":"750_CR71","doi-asserted-by":"crossref","first-page":"112","DOI":"10.1080\/00480169.1992.35712","volume":"40","author":"DG Arthur","year":"1992","journal-title":"N Z Vet J"},{"key":"750_CR72","first-page":"128","volume":"41","author":"JS Agerholm","year":"1994","journal-title":"Zentbl Vetmed A"},{"key":"750_CR73","doi-asserted-by":"publisher","first-page":"75","DOI":"10.1016\/S1091-8531(03)00051-X","volume":"7","author":"DH Lee","year":"2003","journal-title":"J AAPOS"},{"key":"750_CR74","doi-asserted-by":"publisher","first-page":"513","DOI":"10.1016\/S0092-8674(01)00571-2","volume":"107","author":"Y Gong","year":"2001","journal-title":"Cell"},{"key":"750_CR75","doi-asserted-by":"publisher","first-page":"303","DOI":"10.1083\/jcb.200201089","volume":"157","author":"M Kato","year":"2002","journal-title":"J Cell Biol"},{"key":"750_CR76","doi-asserted-by":"publisher","first-page":"707","DOI":"10.1038\/27221","volume":"395","author":"BA Parr","year":"1998","journal-title":"Nature (Lond)"},{"key":"750_CR77","doi-asserted-by":"publisher","first-page":"59","DOI":"10.1146\/annurev.cellbio.14.1.59","volume":"14","author":"A Wodarz","year":"1998","journal-title":"Annu Rev Cell Dev Biol"},{"key":"750_CR78","doi-asserted-by":"publisher","first-page":"405","DOI":"10.1038\/17068","volume":"397","author":"S Vainio","year":"1999","journal-title":"Nature (Lond)"},{"key":"750_CR79","doi-asserted-by":"publisher","first-page":"341","DOI":"10.1016\/S0092-8674(01)00222-7","volume":"104","author":"C Hartmann","year":"2001","journal-title":"Cell"},{"key":"750_CR80","doi-asserted-by":"publisher","first-page":"229","DOI":"10.1073\/pnas.0133792100","volume":"100","author":"T Fujino","year":"2003","journal-title":"Proc Natl Acad Sci U S A"},{"key":"750_CR81","doi-asserted-by":"publisher","first-page":"291","DOI":"10.1016\/j.cell.2006.08.039","volume":"127","author":"R Morello","year":"2006","journal-title":"Cell"},{"key":"750_CR82","doi-asserted-by":"crossref","first-page":"440","DOI":"10.1093\/oxfordjournals.jhered.a109554","volume":"72","author":"JL Guenet","year":"1981","journal-title":"J Hered"},{"key":"750_CR83","doi-asserted-by":"crossref","first-page":"241","DOI":"10.1016\/8756-3282(91)90070-Y","volume":"12","author":"MP Muriel","year":"1991","journal-title":"Bone (NY)"},{"key":"750_CR84","doi-asserted-by":"publisher","first-page":"276","DOI":"10.1002\/ajmg.1320450227","volume":"45","author":"DO Sillence","year":"1993","journal-title":"Am J Med Genet"},{"key":"750_CR85","doi-asserted-by":"publisher","first-page":"803","DOI":"10.1038\/ng1603","volume":"37","author":"I Aubin","year":"2005","journal-title":"Nat Genet"},{"key":"750_CR86","doi-asserted-by":"publisher","first-page":"542","DOI":"10.1007\/s00223-003-0155-9","volume":"74","author":"A Grey","year":"2004","journal-title":"Calcif Tissue Int"},{"key":"750_CR87","doi-asserted-by":"publisher","first-page":"13049","DOI":"10.1073\/pnas.192460799","volume":"99","author":"MO Bergo","year":"2002","journal-title":"Proc Natl Acad Sci U S A"},{"key":"750_CR88","doi-asserted-by":"crossref","first-page":"94","DOI":"10.1038\/ng871","volume":"31","author":"AM Pendas","year":"2002","journal-title":"Nat Genet"},{"key":"750_CR89","doi-asserted-by":"publisher","first-page":"530","DOI":"10.1354\/vp.40-5-530","volume":"40","author":"F Seeliger","year":"2003","journal-title":"Vet Pathol"}],"container-title":["Journal of Bone and Mineral Metabolism"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1007\/s00774-007-0750-3.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/link.springer.com\/article\/10.1007\/s00774-007-0750-3\/fulltext.html","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1007\/s00774-007-0750-3","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"},{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1007\/s00774-007-0750-3.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2024,2,15]],"date-time":"2024-02-15T09:02:24Z","timestamp":1707987744000},"score":1,"resource":{"primary":{"URL":"https:\/\/link.springer.com\/10.1007\/s00774-007-0750-3"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2007,6,25]]},"references-count":89,"journal-issue":{"issue":"4","published-print":{"date-parts":[[2007,7]]}},"alternative-id":["750"],"URL":"https:\/\/doi.org\/10.1007\/s00774-007-0750-3","relation":{},"ISSN":["0914-8779","1435-5604"],"issn-type":[{"value":"0914-8779","type":"print"},{"value":"1435-5604","type":"electronic"}],"subject":[],"published":{"date-parts":[[2007,6,25]]},"assertion":[{"value":"27 October 2006","order":1,"name":"received","label":"Received","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"27 February 2007","order":2,"name":"accepted","label":"Accepted","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"25 June 2007","order":3,"name":"first_online","label":"First Online","group":{"name":"ArticleHistory","label":"Article History"}}]}}