{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,2,21]],"date-time":"2025-02-21T13:14:17Z","timestamp":1740143657657,"version":"3.37.3"},"reference-count":21,"publisher":"Springer Science and Business Media LLC","issue":"4","license":[{"start":{"date-parts":[[2020,8,4]],"date-time":"2020-08-04T00:00:00Z","timestamp":1596499200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.springer.com\/tdm"},{"start":{"date-parts":[[2020,8,4]],"date-time":"2020-08-04T00:00:00Z","timestamp":1596499200000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/www.springer.com\/tdm"}],"funder":[{"DOI":"10.13039\/501100001691","name":"Japan Society for the Promotion of Science KAKENHI","doi-asserted-by":"crossref","award":["17K08764"],"award-info":[{"award-number":["17K08764"]}],"id":[{"id":"10.13039\/501100001691","id-type":"DOI","asserted-by":"crossref"}]},{"name":"Grant-in-Aid for Clinical Research from Miyazaki University Hospital","award":["2019"],"award-info":[{"award-number":["2019"]}]}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["Brain Tumor Pathol"],"published-print":{"date-parts":[[2020,10]]},"DOI":"10.1007\/s10014-020-00376-w","type":"journal-article","created":{"date-parts":[[2020,8,4]],"date-time":"2020-08-04T20:02:22Z","timestamp":1596571342000},"page":"159-164","update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":1,"title":["RELA fusion-positive ependymoma accompanied by extensive desmoplasia: a case report"],"prefix":"10.1007","volume":"37","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-9350-777X","authenticated-orcid":false,"given":"Tsuyoshi","family":"Fukushima","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Takashi","family":"Ueda","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Junko","family":"Hirato","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Hiroaki","family":"Kataoka","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"297","published-online":{"date-parts":[[2020,8,4]]},"reference":[{"key":"376_CR1","unstructured":"Louis DN, Ohgaki H, Wiestler OD, et al (2016) WHO classification of tumours of the central nervous system, revised 4th eds. International Agency for Research on Cancer (IARC), Lyon, pp 106\u2013114"},{"key":"376_CR2","doi-asserted-by":"publisher","first-page":"844","DOI":"10.1001\/archneurpsyc.1935.02250220148014","volume":"34","author":"RP Mackay","year":"1935","unstructured":"Mackay RP (1935) Ependymoblastoma in the fourth ventricle, with new bone formation. Arch Neur Psych 34:844\u2013853","journal-title":"Arch Neur Psych"},{"key":"376_CR3","doi-asserted-by":"publisher","first-page":"421","DOI":"10.1007\/s004010050819","volume":"95","author":"H Takahashi","year":"1998","unstructured":"Takahashi H, Goto J, Emura I et al (1998) Lipidized (foamy) tumor cells in a spinal cord ependymoma with collagenous metaplasia. Acta Neuropathol 95:421\u2013425","journal-title":"Acta Neuropathol"},{"key":"376_CR4","first-page":"186","volume":"19","author":"K Yoshida","year":"2000","unstructured":"Yoshida K, Sato K, Kubota T et al (2000) Supratentorial desmoplastic ependymoma with giant ependymal rosettes. Clin Neuropathol 19:186\u2013191","journal-title":"Clin Neuropathol"},{"key":"376_CR5","doi-asserted-by":"publisher","first-page":"159","DOI":"10.1007\/BF00717041","volume":"47","author":"M Soeur","year":"1979","unstructured":"Soeur M, Monseu G, Ketelbant P et al (1979) Intramedullary ependymoma producing collagen. A clinical and pathological study. Acta Neuropathol 47:159\u2013160","journal-title":"Acta Neuropathol"},{"key":"376_CR6","doi-asserted-by":"publisher","first-page":"165","DOI":"10.1111\/j.1440-1789.2007.00837.x","volume":"28","author":"V Parafeynikov","year":"2008","unstructured":"Parafeynikov V, Boaz JC, Bonnin JM (2008) Clear-cell ependymoma: A report of intracortical tumor with significant desmoplasia. Neuropathology 28:165\u2013170","journal-title":"Neuropathology"},{"key":"376_CR7","first-page":"354873","volume":"2013","author":"AE Elsharkawy","year":"2013","unstructured":"Elsharkawy AE, Abuamona R, Bergmann M et al (2013) Cortical anaplastic ependymoma with significant desmoplasia: a case report and literature review. Case Rep Oncol Med 2013:354873","journal-title":"Case Rep Oncol Med"},{"key":"376_CR8","doi-asserted-by":"publisher","first-page":"451","DOI":"10.1038\/nature13109","volume":"506","author":"M Parker","year":"2014","unstructured":"Parker M, Mohankumar KM, Punchihewa C et al (2014) C11orf95\u2013RELA fusions drive oncogenic NF-kB signalling in ependymoma. Nature 506:451\u2013455","journal-title":"Nature"},{"key":"376_CR9","unstructured":"Louis DN, Ohgaki H, Wiestler OD, et al (2007) WHO classification of tumours of the central nervous system, 4th eds. International Agency for Research on Cancer (IARC), Lyon, pp 74\u201380"},{"key":"376_CR10","doi-asserted-by":"publisher","first-page":"666","DOI":"10.1007\/BF00294308","volume":"86","author":"F Aydin","year":"1993","unstructured":"Aydin F, Ghatak NR, Salvant J et al (1993) Desmoplastic cerebral astrocytoma of infancy. A case report with immunohistochemical, ultrastructural and proliferation studies. Acta Neuropathol 86:666\u2013670","journal-title":"Acta Neuropathol"},{"key":"376_CR11","doi-asserted-by":"publisher","first-page":"1577","DOI":"10.1007\/s00381-016-3126-y","volume":"32","author":"F Bianchi","year":"2016","unstructured":"Bianchi F, Tamburrini G (2016) Supratentorial tumors typical of the infantile age: desmoplastic infantile ganglioglioma (DIG) and astrocytoma (DIA). A review Childs Nerv Syst 32:1577\u20131585","journal-title":"A review Childs Nerv Syst"},{"key":"376_CR12","doi-asserted-by":"publisher","first-page":"2177","DOI":"10.1007\/s00381-011-1587-6","volume":"27","author":"JH Phi","year":"2011","unstructured":"Phi JH, Koh EJ, Kim S-K et al (2011) Desmoplastic infantile astrocytoma: recurrence with malignant transformation into glioblastoma: a case report. Childs Nerv Syst 27:2177\u20132188","journal-title":"Childs Nerv Syst"},{"key":"376_CR13","doi-asserted-by":"publisher","first-page":"699","DOI":"10.1097\/PAS.0b013e318158234e","volume":"32","author":"FJ Rodriguez","year":"2008","unstructured":"Rodriguez FJ, Scheithauer BW, Perry A et al (2008) Ependymal tumors with sarcomatous change (\u2018\u2018ependymosarcoma\u2019\u2019): a clinicopathologic and molecular cytogenetic study. Am J Surg Pathol 32:699\u2013709","journal-title":"Am J Surg Pathol"},{"key":"376_CR14","doi-asserted-by":"publisher","first-page":"425","DOI":"10.1016\/S0002-9440(10)64746-3","volume":"156","author":"RM Reis","year":"2000","unstructured":"Reis RM, K\u00f6n\u00fc-Lebleblicioglu D, Lopes JM et al (2000) Genetic profile of gliosarcomas. Am J Pathol 156:425\u2013432","journal-title":"Am J Pathol"},{"key":"376_CR15","doi-asserted-by":"publisher","first-page":"321","DOI":"10.1007\/s004010000259","volume":"101","author":"C Walker","year":"2001","unstructured":"Walker C, Joyce KA, Thompson-Hehir J (2001) Characterization of molecular alterations in microdissected archival gliomas. Acta Neuropathol 101:321\u2013333","journal-title":"Acta Neuropathol"},{"key":"376_CR16","doi-asserted-by":"crossref","first-page":"1674","DOI":"10.1097\/PAS.0000000000001342","volume":"43","author":"L Wang","year":"2019","unstructured":"Wang L, Liu L, Li H, Wang P et al (2019) RELA Fusion in Supratentorial extraventricular ependymomas: a morphologic, immunohistochemical, and molecular study of 43 Cases. Am J Surg Pathol 43:1674\u20131681","journal-title":"Am J Surg Pathol"},{"key":"376_CR17","doi-asserted-by":"publisher","first-page":"84","DOI":"10.1093\/carcin\/bgr262","volume":"33","author":"H Sch\u00e4fer","year":"2012","unstructured":"Sch\u00e4fer H, Geismann C, Heneweer C et al (2012) Myofibroblast-induced tumorigenicity of pancreatic ductal epithelial cells is L1CAM dependent. Carcinogenesis 33:84\u201393","journal-title":"Carcinogenesis"},{"key":"376_CR18","doi-asserted-by":"publisher","first-page":"919","DOI":"10.1093\/neuonc\/now025","volume":"18","author":"D Figarella-Branger","year":"2016","unstructured":"Figarella-Branger D, Lechapt-Zalcman E, Tabouret E et al (2016) Supratentorial clear cell ependymomas with branching capillaries demonstrate characteristic clinicopathological features and pathological activation of nuclear factor-kappaB signaling. Neuro Oncol 18:919\u2013927","journal-title":"Neuro Oncol"},{"key":"376_CR19","doi-asserted-by":"publisher","first-page":"168","DOI":"10.1016\/j.jocn.2019.02.001","volume":"63","author":"KR Hamilton","year":"2019","unstructured":"Hamilton KR, Lee SS, Urquhart JC et al (2019) A systematic review of outcome in intramedullary ependymoma and astrocytoma. J Clin Neurosci 63:168\u2013175","journal-title":"J Clin Neurosci"},{"key":"376_CR20","doi-asserted-by":"publisher","first-page":"445","DOI":"10.1093\/neuonc\/nox166","volume":"20","author":"R Ruda","year":"2018","unstructured":"Ruda R, Reifenberger G, Frappaz D et al (2018) EANO guidelines for the diagnosis and treatment of ependymal tumor. Neuro Oncol 20:445\u2013456","journal-title":"Neuro Oncol"},{"key":"376_CR21","doi-asserted-by":"publisher","first-page":"921","DOI":"10.1093\/neuonc\/not038","volume":"15","author":"SH Lee","year":"2013","unstructured":"Lee SH, Chung CK, Kim CH et al (2013) Long-term outcomes of surgical resection with or without adjuvant radiation therapy for treatment of spinal ependymoma: a retrospective multicenter study by the Korea Spinal Oncology Research Group. Neuro Oncol 15:921\u2013929","journal-title":"Neuro Oncol"}],"container-title":["Brain Tumor Pathology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1007\/s10014-020-00376-w.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/link.springer.com\/article\/10.1007\/s10014-020-00376-w\/fulltext.html","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1007\/s10014-020-00376-w.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2021,8,3]],"date-time":"2021-08-03T23:14:09Z","timestamp":1628032449000},"score":1,"resource":{"primary":{"URL":"https:\/\/link.springer.com\/10.1007\/s10014-020-00376-w"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2020,8,4]]},"references-count":21,"journal-issue":{"issue":"4","published-print":{"date-parts":[[2020,10]]}},"alternative-id":["376"],"URL":"https:\/\/doi.org\/10.1007\/s10014-020-00376-w","relation":{},"ISSN":["1433-7398","1861-387X"],"issn-type":[{"type":"print","value":"1433-7398"},{"type":"electronic","value":"1861-387X"}],"subject":[],"published":{"date-parts":[[2020,8,4]]},"assertion":[{"value":"26 March 2020","order":1,"name":"received","label":"Received","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"27 July 2020","order":2,"name":"accepted","label":"Accepted","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"4 August 2020","order":3,"name":"first_online","label":"First Online","group":{"name":"ArticleHistory","label":"Article History"}},{"order":1,"name":"Ethics","group":{"name":"EthicsHeading","label":"Compliance with ethical standard"}},{"value":"The authors declare that they have no conflict of interest.","order":2,"name":"Ethics","group":{"name":"EthicsHeading","label":"Conflict of interest"}}]}}