{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,26]],"date-time":"2026-08-26T17:21:11Z","timestamp":1787764871299,"version":"build-2784847793"},"reference-count":15,"publisher":"SAGE Publications","issue":"6","license":[{"start":{"date-parts":[[2004,11,1]],"date-time":"2004-11-01T00:00:00Z","timestamp":1099267200000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/journals.sagepub.com\/page\/policies\/text-and-data-mining-license"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Pediatr Dev Pathol"],"published-print":{"date-parts":[[2004,11]]},"abstract":"<jats:p> Congenital pulmonary airway malformation, or congenital cystic adenomatoid malformation, is postulated to be a disorder of pulmonary airway morphogenesis and encompasses 5 different types with distinct levels or stages of tracheobronchial development. We present a unique case of type 2 congenital pulmonary airway malformation with a previously undocumented combination of multiple extrapulmonary anomalies, featuring ipsilateral multicystic renal dysgenesis, contralateral renal agenesis, and ovarian germ cell hypoplasia, diagnosed in a 19-week gestational age fetus by autopsy. Epithelial cells comprising the pulmonary lesions were positive for thyroid transcription factor-1, surfactant protein-B, and cytokeratin-7 but negative for cytokeratin-20 immunostainings, with the pattern seen in normal terminal bronchioles. Chromosomal analysis showed a normal female karyotype, despite a high estimated risk for Down syndrome suggested by the low maternal serum \u03b1-fetoprotein level. <\/jats:p>","DOI":"10.1007\/s10024-004-1007-y","type":"journal-article","created":{"date-parts":[[2004,11,5]],"date-time":"2004-11-05T22:35:07Z","timestamp":1099694107000},"page":"661-666","source":"Crossref","is-referenced-by-count":20,"title":["Congenital Pulmonary Airway Malformation (Congenital Cystic Adenomatoid Malformation) with Multiple Extrapulmonary Anomalies: Autopsy Report of a Fetus at 19 Weeks of Gestation"],"prefix":"10.1177","volume":"7","author":[{"given":"Truc T.","family":"Pham","sequence":"first","affiliation":[{"name":"Department of Pathology, University of California San Diego, School of Medicine, San Diego, 200 West Arbor Drive, San Diego, CA 92103-8720, USA"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Kurt","family":"Benirschke","sequence":"additional","affiliation":[{"name":"Department of Pathology, University of California San Diego, School of Medicine, San Diego, 200 West Arbor Drive, San Diego, CA 92103-8720, USA"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Eliezer","family":"Masliah","sequence":"additional","affiliation":[{"name":"Department of Pathology, University of California San Diego, School of Medicine, San Diego, 200 West Arbor Drive, San Diego, CA 92103-8720, USA"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"J. 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