{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,10]],"date-time":"2026-09-10T16:11:47Z","timestamp":1789056707472,"version":"build-2803163510"},"reference-count":5,"publisher":"Springer Science and Business Media LLC","issue":"3","license":[{"start":{"date-parts":[[2026,8,10]],"date-time":"2026-08-10T00:00:00Z","timestamp":1786320000000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0"},{"start":{"date-parts":[[2026,8,10]],"date-time":"2026-08-10T00:00:00Z","timestamp":1786320000000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/creativecommons.org\/licenses\/by\/4.0"}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["J Artif Organs"],"published-print":{"date-parts":[[2026,9]]},"abstract":"<jats:title>Abstract<\/jats:title>\n                  <jats:p>A 4-year-old boy with a diagnosis of right-sided heterotaxy syndrome was transferred to our hospital under the extracorporeal membrane oxygenation (ECMO). He had undergone an extracardiac total cavopulmonary connection (TCPC) with a fenestration. Approximately 6\u00a0months after the TCPC procedure, common atrioventricular valve regurgitation worsened and persisted despite multiple valve repair procedures. ECMO support was initiated 318\u00a0days after the TCPC procedure for progressive heart failure and multiple organ dysfunction. Although ECMO was initially discontinued after transient improvement, recurrent circulatory failure necessitated reinitiation, and the patient remained ECMO-dependent thereafter. We implanted a Berlin Heart EXCOR\u00ae Pediatric ventricular assist device. In the operation, the fenestration of the TCPC conduit was closed. An expanded polytetrafluoroethylene conduit for the arterial cannula was anastomosed to the ascending aorta in an end-to-side fashion. The apex of the left-sided ventricle was incised, followed by the meticulous resection of residual ventricular septal tissue to obtain effective venting from both ventricles. An inflow cannula was anastomosed to the coring site. Ventricular assist support was initiated without complications. On the postoperative day 433, intracerebral hemorrhage was abruptly developed, necessitating management in the intensive care unit. Two hematoma evacuation procedures of decompressing surgery for intracerebral hemorrhage were required. Despite these interventions, the patient ultimately died on postoperative day 488. The autopsy confirmed that the residual ventricular septum-like tissue had been almost completely resected and that the inflow cannula tip was positioned away from any muscular structures, suggesting that the resection enabled effective ventricular drainage without obstruction or suction.<\/jats:p>","DOI":"10.1007\/s10047-026-01586-3","type":"journal-article","created":{"date-parts":[[2026,8,10]],"date-time":"2026-08-10T16:46:54Z","timestamp":1786380414000},"update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":0,"title":["Berlin heart EXCOR\u00ae implantation for Fontan failure in right-sided heterotaxy with ventricular septal protuberance: autopsy case report"],"prefix":"10.1007","volume":"29","author":[{"ORCID":"https:\/\/orcid.org\/0009-0004-0876-7449","authenticated-orcid":false,"given":"Hiroshi","family":"Sakamoto","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Shunji","family":"Uchita","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Kazuki","family":"Tanimoto","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Masaki","family":"Taira","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mayumi","family":"Kamada","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Hironori","family":"Izutani","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2026,8,10]]},"reference":[{"key":"1586_CR1","doi-asserted-by":"publisher","first-page":"74","DOI":"10.1053\/j.optechstcvs.2020.04.003","volume":"25","author":"I Adachi","year":"2020","unstructured":"Adachi I. Ventricular assist device implantation for single ventricle. Oper Tech Thorac Cardiovasc Surg. 2020;25:74\u201384.","journal-title":"Oper Tech Thorac Cardiovasc Surg"},{"key":"1586_CR2","doi-asserted-by":"publisher","first-page":"365","DOI":"10.1016\/j.pcad.2018.09.005","volume":"61","author":"WA Kay","year":"2018","unstructured":"Kay WA, Moe T, Suter B, et al. Long term consequences of the Fontan procedure and how to manage them. Prog Cardiovasc Dis. 2018;61:365\u201376.","journal-title":"Prog Cardiovasc Dis"},{"key":"1586_CR3","doi-asserted-by":"crossref","unstructured":"Weinstein S, Bello R, Pizarro C, et al. The use of the Berlin Heart EXCOR in patients with functional single ventricle. J Thorac Cardiovasc Surg 2014;147:697\u2013704; discussion 704\u20135.","DOI":"10.1016\/j.jtcvs.2013.10.030"},{"key":"1586_CR4","doi-asserted-by":"publisher","first-page":"368","DOI":"10.1016\/j.healun.2021.01.011","volume":"40","author":"A Cedars","year":"2021","unstructured":"Cedars A, Kutty S, Danford D, et al. Systemic ventricular assist device support in Fontan patients: a report by ACTION. J Heart Lung Transplant. 2021;40:368\u201376.","journal-title":"J Heart Lung Transplant"},{"key":"1586_CR5","doi-asserted-by":"publisher","first-page":"E193","DOI":"10.1111\/petr.12607","volume":"19","author":"I Halaweish","year":"2015","unstructured":"Halaweish I, Ohye RG, Si MS. Berlin heart ventricular assist device as a long-term bridge to transplantation in a Fontan patient with failing single ventricle. Pediatr Transplant. 2015;19:E193\u20135.","journal-title":"Pediatr Transplant"}],"container-title":["Journal of Artificial Organs"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1007\/s10047-026-01586-3.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/link.springer.com\/article\/10.1007\/s10047-026-01586-3","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1007\/s10047-026-01586-3.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2026,9,10]],"date-time":"2026-09-10T16:03:16Z","timestamp":1789056196000},"score":1,"resource":{"primary":{"URL":"https:\/\/link.springer.com\/10.1007\/s10047-026-01586-3"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2026,8,10]]},"references-count":5,"journal-issue":{"issue":"3","published-print":{"date-parts":[[2026,9]]}},"alternative-id":["1586"],"URL":"https:\/\/doi.org\/10.1007\/s10047-026-01586-3","relation":{},"ISSN":["1434-7229","1619-0904"],"issn-type":[{"value":"1434-7229","type":"print"},{"value":"1619-0904","type":"electronic"}],"subject":[],"published":{"date-parts":[[2026,8,10]]},"assertion":[{"value":"14 May 2026","order":1,"name":"received","label":"Received","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"3 August 2026","order":2,"name":"accepted","label":"Accepted","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"10 August 2026","order":3,"name":"first_online","label":"First Online","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"The authors declare that they have no conflict of interest.","order":1,"name":"Ethics","label":"Conflict of interest","group":{"name":"EthicsHeading","label":"Declarations"}},{"value":"Written informed consent was obtained from the patient\u2019s parents for publication of this case report and any accompanying images. This case report did not require approval by the Institutional Review Board of our institution, in accordance with the institutional policy for case reports.","order":2,"name":"Ethics","label":"Ethical approval","group":{"name":"EthicsHeading","label":"Declarations"}}],"article-number":"55"}}