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Thymoma is a rare tumor of the thymus. Autoimmune diseases and paraneoplastic syndromes such as myasthenia gravis, pure red blood cell aplasia, and systemic lupus erythematosus, although relatively uncommon, have been described in association with thymomas. Rare cases of post-thymectomy autoimmune related diseases, including systemic lupus erythematosus and pure red cell aplasia, have been reported in the literature. Here, we present the case of a 65-year-old male who developed systemic lupus erythematosus 2\u00a0years after thymectomy in the setting of thymoma-associated pure red cell aplasia.<\/jats:p>","DOI":"10.1007\/s10067-020-05061-z","type":"journal-article","created":{"date-parts":[[2020,4,10]],"date-time":"2020-04-10T07:02:28Z","timestamp":1586502148000},"page":"2227-2234","update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":26,"title":["A tale of autoimmunity: thymoma, thymectomy, and systemic lupus erythematosus"],"prefix":"10.1007","volume":"39","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-1483-2241","authenticated-orcid":false,"given":"Arash","family":"Mollaeian","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Christopher","family":"Haas","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2020,4,10]]},"reference":[{"issue":"1","key":"5061_CR1","doi-asserted-by":"publisher","first-page":"82","DOI":"10.1016\/j.autrev.2015.09.005","volume":"15","author":"C Bernard","year":"2016","unstructured":"Bernard C, Frih H, Pasquet F, Kerever S, Jamilloux Y, Tronc F, Guibert B, Isaac S, Devouassoux M, Chalabreysse L, Broussolle C, Petiot P, Girard N, S\u00e8ve P (2016) Thymoma associated with autoimmune diseases: 85 cases and literature review. 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