{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,6,24]],"date-time":"2026-06-24T21:39:43Z","timestamp":1782337183928,"version":"3.54.5"},"reference-count":113,"publisher":"Springer Science and Business Media LLC","issue":"10","license":[{"start":{"date-parts":[[2023,3,8]],"date-time":"2023-03-08T00:00:00Z","timestamp":1678233600000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.springernature.com\/gp\/researchers\/text-and-data-mining"},{"start":{"date-parts":[[2023,3,8]],"date-time":"2023-03-08T00:00:00Z","timestamp":1678233600000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/www.springernature.com\/gp\/researchers\/text-and-data-mining"}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["Clin Rheumatol"],"published-print":{"date-parts":[[2023,10]]},"DOI":"10.1007\/s10067-023-06552-5","type":"journal-article","created":{"date-parts":[[2023,3,8]],"date-time":"2023-03-08T08:03:32Z","timestamp":1678262612000},"page":"2733-2746","update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":6,"title":["Cerebrovascular involvement in systemic childhood vasculitides"],"prefix":"10.1007","volume":"42","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-4925-8948","authenticated-orcid":false,"given":"Martina","family":"Held","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-1092-6491","authenticated-orcid":false,"given":"Mario","family":"Sestan","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-4656-6670","authenticated-orcid":false,"given":"Nastasia","family":"Kifer","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-1728-4260","authenticated-orcid":false,"given":"Marija","family":"Jelusic","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2023,3,8]]},"reference":[{"key":"6552_CR1","doi-asserted-by":"publisher","first-page":"1197","DOI":"10.1016\/S0140-6736(02)11279-7","volume":"360","author":"JM Gardner-Medwin","year":"2002","unstructured":"Gardner-Medwin JM, Dolezalova P, Cummins C, Southwood TR (2002) Incidence of Henoch-Sch\u00f6nlein purpura, Kawasaki disease, and rare vasculitides in children of different ethnic origins. Lancet 360:1197\u2013202. https:\/\/doi.org\/10.1016\/S0140-6736(02)11279-7","journal-title":"Lancet"},{"key":"6552_CR2","doi-asserted-by":"publisher","first-page":"798","DOI":"10.1136\/ard.2009.116657","volume":"69","author":"S Ozen","year":"2010","unstructured":"Ozen S, Pistorio A, Iusan SM et al (2010) EULAR\/PRINTO\/PRES criteria for Henoch-Sch\u00f6nlein purpura, childhood polyarteritis nodosa, childhood Wegener granulomatosis and childhood Takayasu arteritis: Ankara 2008. Part II: final classification criteria. Ann Rheum Dis 69:798\u2013806. https:\/\/doi.org\/10.1136\/ard.2009.116657","journal-title":"Ann Rheum Dis"},{"issue":"1","key":"6552_CR3","doi-asserted-by":"publisher","first-page":"1","DOI":"10.1002\/art.37715","volume":"65","author":"JC Jennette","year":"2013","unstructured":"Jennette JC, Falk RJ, Bacon PA, Basu N, Cid MC, Ferrario F et al (2013) 2012 revised International Chapel Hill consensus conference nomenclature of vasculitides. Arthritis Rheum 65(1):1\u201311. https:\/\/doi.org\/10.1002\/art.37715","journal-title":"Arthritis Rheum"},{"issue":"1","key":"6552_CR4","doi-asserted-by":"publisher","first-page":"33","DOI":"10.1093\/rheumatology\/kev262","volume":"55","author":"N Amiri","year":"2016","unstructured":"Amiri N, De Vera M, Choi HK, Sayre EC, Avina-Zubieta JA (2016) Increased risk of cardiovascular disease in giant cell arteritis: a general population-based study. Rheumatology (Oxford) 55(1):33\u201340. https:\/\/doi.org\/10.1093\/rheumatology\/kev262","journal-title":"Rheumatology (Oxford)"},{"key":"6552_CR5","doi-asserted-by":"publisher","first-page":"227","DOI":"10.1097\/MD.0b013e3181af4518","volume":"88","author":"MA Gonzalez-Gay","year":"2009","unstructured":"Gonzalez-Gay MA, Vazquez-Rodriguez TR, Gomez-Acebo I, Pego-Reigosa R, Lopez-Diaz MJ, Vazquez-Tri\u00f1anes MC, Miranda-Filloy JA, Blanco R, Dierssen T, Gonzalez-Juanatey C, Llorca J (2009) Strokes at time of disease diagnosis in a series of 287 patients with biopsy-proven giant cell arteritis. Medicine 88:227\u2013235. https:\/\/doi.org\/10.1097\/MD.0b013e3181af4518","journal-title":"Medicine"},{"key":"6552_CR6","doi-asserted-by":"publisher","first-page":"3017","DOI":"10.1007\/s00296-013-2814-0","volume":"33","author":"T Zenone","year":"2013","unstructured":"Zenone T, Puget M (2013) Characteristics of cerebrovascular accidents at time of diagnosis in a series of 98 patients with giant cell arteritis. Rheumatol Int 33:3017\u20133023. https:\/\/doi.org\/10.1007\/s00296-013-2814-0","journal-title":"Rheumatol Int"},{"issue":"3","key":"6552_CR7","doi-asserted-by":"publisher","first-page":"504","DOI":"10.1002\/art.41529","volume":"73","author":"R Goel","year":"2021","unstructured":"Goel R, Singh Chandan J, Thayakaran R, Adderley NJ, Nirantharakumar K, Harper L (2021) Cardiovascular and renal morbidity in Takayasu arteritis: a population-based retrospective cohort study from the United Kingdom. Arthritis Rheumatol 73(3):504\u2013511. https:\/\/doi.org\/10.1002\/art.41529","journal-title":"Arthritis Rheumatol"},{"issue":"Suppl 124","key":"6552_CR8","first-page":"91","volume":"38","author":"K Egebjerg","year":"2020","unstructured":"Egebjerg K, Baslund B, Obel N, Faurschou M (2020) Mortality and cardiovascular morbidity among patients diagnosed with Takayasu\u2019s arteritis: a Danish nationwide cohort study. Clin Exp Rheumatol 38(Suppl 124):91\u201394","journal-title":"Clin Exp Rheumatol"},{"issue":"9","key":"6552_CR9","doi-asserted-by":"publisher","first-page":"2308","DOI":"10.1093\/rheumatology\/kez589","volume":"59","author":"ZS Wallace","year":"2020","unstructured":"Wallace ZS, Fu X, Harkness T, Stone JH, Zhang Y, Choi H (2020) All-cause and cause-specific mortality in ANCA-associated vasculitis: overall and according to ANCA type. Rheumatology (Oxford) 59(9):2308\u20132315. https:\/\/doi.org\/10.1093\/rheumatology\/kez589","journal-title":"Rheumatology (Oxford)"},{"issue":"9","key":"6552_CR10","doi-asserted-by":"publisher","first-page":"1566","DOI":"10.1136\/annrheumdis-2016-210942","volume":"76","author":"JA Tan","year":"2017","unstructured":"Tan JA, Dehghan N, Chen W, Xie H, Esdaile JM, Avina-Zubieta JA (2017) Mortality in ANCA-associated vasculitis: a meta-analysis of observational studies. Ann Rheum Dis 76(9):1566\u20131574. https:\/\/doi.org\/10.1136\/annrheumdis-2016-210942","journal-title":"Ann Rheum Dis"},{"key":"6552_CR11","doi-asserted-by":"publisher","first-page":"134","DOI":"10.1016\/j.jaut.2018.09.004","volume":"96","author":"M Mourguet","year":"2019","unstructured":"Mourguet M, Chauveau D, Faguer S, Ruidavets JB, B\u00e9jot Y, Ribes D et al (2019) Increased ischemic stroke, acute coronary artery disease and mortality in patients with granulomatosis with polyangiitis and microscopic polyangiitis. J Autoimmun 96:134\u2013141. https:\/\/doi.org\/10.1016\/j.jaut.2018.09.004","journal-title":"J Autoimmun"},{"issue":"9624","key":"6552_CR12","doi-asserted-by":"publisher","first-page":"1612","DOI":"10.1016\/S0140-6736(08)60694-7","volume":"371","author":"GA Donnan","year":"2008","unstructured":"Donnan GA, Fisher M, Macleod M, Davis SM (2008) Stroke. Lancet 371(9624):1612\u20131623","journal-title":"Lancet"},{"key":"6552_CR13","unstructured":"Eurostat (2019) Causes and occurrence of deaths in the EU. Available at https:\/\/ec.europa.eu\/eurostat\/web\/products-eurostat-news\/-\/ddn-20190716-1"},{"issue":"12 Pt 2","key":"6552_CR14","doi-asserted-by":"publisher","first-page":"e391","DOI":"10.1016\/j.lpm.2016.10.003","volume":"45","author":"Y B\u00e9jot","year":"2016","unstructured":"B\u00e9jot Y, Bailly H, Durier J, Giroud M (2016) Epidemiology of stroke in Europe and trends for the 21st century. Presse Med 45(12 Pt 2):e391\u2013e398","journal-title":"Presse Med"},{"issue":"11","key":"6552_CR15","doi-asserted-by":"publisher","first-page":"1085","DOI":"10.1016\/S1474-4422(10)70251-9","volume":"9","author":"JM Ferro","year":"2010","unstructured":"Ferro JM, Massaro AR, Mas JL (2010) Aethiological diagnosis of ischaemic stroke in young adults. Lancet Neurol 9(11):1085\u20131096. https:\/\/doi.org\/10.1016\/S1474-4422(10)70251-9","journal-title":"Lancet Neurol"},{"issue":"4","key":"6552_CR16","doi-asserted-by":"publisher","first-page":"1195","DOI":"10.1161\/STROKEAHA.108.529883","volume":"40","author":"J Putaala","year":"2009","unstructured":"Putaala J, Metso AJ, Metso TM, Konkola N, Kraemer Y, Haapaniemi E, Kaste M, Tatlisumak T (2009) Analysis of 1008 consecutive patients aged 15 to 49 with first-ever ischemic stroke: the Helsinki young stroke registry. Stroke 40(4):1195\u20131203. https:\/\/doi.org\/10.1161\/STROKEAHA.108.529883","journal-title":"Stroke"},{"key":"6552_CR17","first-page":"335","volume":"141","author":"CO Savage","year":"1992","unstructured":"Savage CO, Pottinger BE, Gaskin G, Pusey CD, Pearson JD (1992) Autoantibodies developing to myeloperoxidase and proteinase 3 in systemic vasculitis stimulate neutrophil cytotoxicity toward cultured endothelial cells. Am J Pathol 141:335\u2013342","journal-title":"Am J Pathol"},{"key":"6552_CR18","doi-asserted-by":"publisher","first-page":"362","DOI":"10.1046\/j.1365-2249.1999.00799.x","volume":"115","author":"M De Bandt","year":"1999","unstructured":"De Bandt M, Meyer O, Dacosta L, Elbim C, Pasquier C (1999) Anti-proteinase-3 (PR3) antibodies (c-ANCA) recognize various targets on the human umbilical vein endothelial cell (HUVEC) membrane. Clin Exp Immunol 115:362\u2013368. https:\/\/doi.org\/10.1046\/j.1365-2249.1999.00799.x","journal-title":"Clin Exp Immunol"},{"issue":"4","key":"6552_CR19","first-page":"433","volume":"17","author":"AC Muller Kobold","year":"1999","unstructured":"Muller Kobold AC, van Wijk RT, Franssen CF, Molema G, Kallenberg CG, Tervaert JW (1999) In vitro up-regulation of E-selectin and induction of interleukin-6 in endothelial cells by autoantibodies in Wegener\u2019s granulomatosis and microscopic polyangiitis. Clin Exp Rheumatol 17(4):433\u2013440","journal-title":"Clin Exp Rheumatol"},{"issue":"2","key":"6552_CR20","doi-asserted-by":"publisher","first-page":"231","DOI":"10.1083\/jcb.200606027","volume":"176","author":"TA Fuchs","year":"2007","unstructured":"Fuchs TA, Abed U, Goosman C, Hurwitz R, Schulze I, Wahn V, Weinrauch Y, Brinkmann V, Zychlinsky A (2007) Novel cell death program leads to neutrophil extracellular traps. J Cell Biol 176(2):231\u2013241. https:\/\/doi.org\/10.1083\/jcb.200606027","journal-title":"J Cell Biol"},{"issue":"6","key":"6552_CR21","doi-asserted-by":"publisher","first-page":"623","DOI":"10.1038\/nm.1959","volume":"15","author":"K Kessenbrock","year":"2009","unstructured":"Kessenbrock K, Krumbholz M, Schonermarck U, Back W, Gross WL, Werb Z, Gr\u00f6ne HJ, Brinkmann V, Jenne DE (2009) Netting neutrophils in autoimmune small vessel vasculitis. Nat Med 15(6):623\u2013625. https:\/\/doi.org\/10.1038\/nm.1959","journal-title":"Nat Med"},{"key":"6552_CR22","doi-asserted-by":"publisher","first-page":"668974","DOI":"10.3389\/fimmu.2021.668974","volume":"12","author":"XQ Chen","year":"2021","unstructured":"Chen XQ, Tu L, Zou JS, Zhu SQ, Zhao YJ, Qin YH (2021) The Involvement of neutrophil extracellular traps in disease activity associated with IgA vasculitis. Front Immunol 12:668974","journal-title":"Front Immunol"},{"issue":"6","key":"6552_CR23","doi-asserted-by":"publisher","first-page":"998","DOI":"10.1038\/s41390-019-0710-3","volume":"87","author":"Y Yoshida","year":"2020","unstructured":"Yoshida Y, Takeshita S, Kawamura Y, Kanai T, Tsujita Y, Nonoyama S (2020) Enhanced formation of neutrophil extracellular traps in Kawasaki disease. Pediatr Res 87(6):998\u20131004. https:\/\/doi.org\/10.1038\/s41390-019-0710-3","journal-title":"Pediatr Res"},{"issue":"9","key":"6552_CR24","doi-asserted-by":"publisher","first-page":"1274","DOI":"10.1136\/annrheumdis-2018-214335","volume":"78","author":"A LeJoncour","year":"2019","unstructured":"LeJoncour A, Martos R, Loyau S, Lelay N, Dossier A, Cazes A (2019) Critical role of neutrophil extracellular traps (NETs) in patients with Behcet\u2019s disease. Ann Rheum Dis 78(9):1274\u20131282. https:\/\/doi.org\/10.1136\/annrheumdis-2018-214335","journal-title":"Ann Rheum Dis"},{"issue":"21","key":"6552_CR25","doi-asserted-by":"publisher","first-page":"8674","DOI":"10.1073\/pnas.1301059110","volume":"110","author":"K Martinod","year":"2013","unstructured":"Martinod K, Demers M, Fuchs TA, Wong SL, Brill A, Gallant M, Hu J, Wang Y, Wagner DD (2013) Neutrophil histone modification by peptidylarginine deiminase 4 is critical for deep vein thrombosis in mice. Proc Natl Acad Sci 110(21):8674\u20138679. https:\/\/doi.org\/10.1073\/pnas.1301059110","journal-title":"Proc Natl Acad Sci"},{"key":"6552_CR26","doi-asserted-by":"publisher","first-page":"143","DOI":"10.1016\/j.jdermsci.2018.08.010","volume":"92","author":"R Safi","year":"2018","unstructured":"Safi R, Kallas R, Bardawil T, Mehanna CJ, Abbas O, Hamam R, Uthman I, Kibbi AG, Nassar D (2018) Neutrophils contribute to vasculitis by increased release of neutrophil extracellular traps in Beh\u00e7et\u2019s disease. J Dermatol Sci 92:143\u2013150. https:\/\/doi.org\/10.1016\/j.jdermsci.2018.08.010","journal-title":"J Dermatol Sci"},{"issue":"3","key":"6552_CR27","doi-asserted-by":"publisher","first-page":"927","DOI":"10.1002\/art.20199","volume":"50","author":"PA Brogan","year":"2004","unstructured":"Brogan PA, Shah V, Brachet C, Harnden A, Mant D, Klein N, Dillon MJ (2004) Endothelial and platelets microparticles in vasculitis in the young. Arthritis Rheum 50(3):927\u2013936. https:\/\/doi.org\/10.1002\/art.20199","journal-title":"Arthritis Rheum"},{"key":"6552_CR28","doi-asserted-by":"publisher","first-page":"536","DOI":"10.1046\/j.1365-2249.2003.02091.x","volume":"131","author":"K Nakatani","year":"2003","unstructured":"Nakatani K, Takeshita S, Tsujimoto H, Kawamura Y, Tokutomi T, Sekine I (2003) Circulating endothelial cells in Kawasaki disease. Clin Exp Immunol 131:536\u2013540. https:\/\/doi.org\/10.1046\/j.1365-2249.2003.02091.x","journal-title":"Clin Exp Immunol"},{"issue":"12","key":"6552_CR29","doi-asserted-by":"publisher","first-page":"1595","DOI":"10.1007\/s00296-010-1528-9","volume":"31","author":"I Dursun","year":"2011","unstructured":"Dursun I, D\u00fcs\u00fcnsel R, Poyrazoglu HM, Gunduz Z, Patiroglu T, Ulger H, Gurgoze MK (2011) Circulating endothelial microparticles in children with Henoch-Sch\u00f6nlein purpura; preliminary results. Rheumatol Int 31(12):1595\u20131600. https:\/\/doi.org\/10.1007\/s00296-010-1528-9","journal-title":"Rheumatol Int"},{"issue":"1","key":"6552_CR30","doi-asserted-by":"publisher","first-page":"120","DOI":"10.1016\/j.jacc.2003.08.030","volume":"43","author":"YF Cheung","year":"2004","unstructured":"Cheung YF, Yung TC, Tam SCF, Ho MHK, Chau AKT (2004) Novel and traditional cardiovascular risk factors in children after Kawasaki disease: implications for premature atherosclerosis. J Am Coll Cardiol 43(1):120\u2013124. https:\/\/doi.org\/10.1016\/j.jacc.2003.08.030","journal-title":"J Am Coll Cardiol"},{"issue":"5","key":"6552_CR31","doi-asserted-by":"publisher","first-page":"1095","DOI":"10.1542\/peds.107.5.1095","volume":"107","author":"N Noto","year":"2001","unstructured":"Noto N, Okada T, Yamasuge M, Taniguchi K, Karasawa K, Ayusawa M, Sumitomo N, Harada K (2001) Noninvasive assessment of the early progression of atherosclerosis in adolescents with Kawasaki disease and coronary artery lesions. Pediatrics 107(5):1095\u20131099. https:\/\/doi.org\/10.1542\/peds.107.5.1095","journal-title":"Pediatrics"},{"key":"6552_CR32","doi-asserted-by":"publisher","first-page":"830","DOI":"10.1016\/j.autrev.2010.07.016","volume":"9","author":"S Sitia","year":"2010","unstructured":"Sitia S, Tomasoni L, Atzeni F, Ambrosio G, Cordiano C, Catapano A, Tramontana S, Perticone F, Naccarato P, Camici P, Picano E, Cortigiani L, Bevilacqua M, Milazzo L, Cusi D, Barlassina C, Sarzi-Puttini P, Turiel M (2010) From endothelial dysfunction to atherosclerosis. Autoimmun Rev 9:830\u2013834. https:\/\/doi.org\/10.1016\/j.autrev.2010.07.016","journal-title":"Autoimmun Rev"},{"key":"6552_CR33","doi-asserted-by":"publisher","first-page":"551","DOI":"10.1002\/art.1780400322","volume":"40","author":"N Del Papa","year":"1997","unstructured":"Del Papa N, Guidali L, Sala A, Buccellati C, Khamashta MA, Ichikawa K, Koike T, Balestrieri G, Tincani A, Hughes GR, Meroni PL (1997) Endothelial cells as target for antiphospholipid antibodies. Human polyclonal and monoclonal anti-beta 2-glycoprotein I antibodies react in vitro with endothelial cells through adherent beta 2-glycoprotein I and induce endothelial activation. Arthritis Rheum 40:551\u2013561. https:\/\/doi.org\/10.1002\/art.1780400322","journal-title":"Arthritis Rheum"},{"issue":"1","key":"6552_CR34","doi-asserted-by":"publisher","first-page":"84","DOI":"10.1161\/ATVBAHA.107.154807","volume":"28","author":"M van Leeuwen","year":"2008","unstructured":"van Leeuwen M, Gijbels MJ, Duijvestijn A, Smook M, van de Gaar MJ, Heeringa P, de Winther MPJ, Cohen Tervaert JW (2008) Accumulation of myeloperoxidase positive neutrophils in atherosclerotic lesions in LDLR\u2013\/\u2013 mice. Arterioscler Thromb Vasc Biol 28(1):84\u201389. https:\/\/doi.org\/10.1161\/ATVBAHA.107.154807","journal-title":"Arterioscler Thromb Vasc Biol"},{"issue":"3","key":"6552_CR35","doi-asserted-by":"publisher","first-page":"754","DOI":"10.1161\/STROKEAHA.117.019896","volume":"49","author":"C Ducroux","year":"2008","unstructured":"Ducroux C, Di Meglio L, Loyau S, Delbosc S, Boisseau W, Deschildre C et al (2008) Thrombus neutrophil extracellular traps content impair tPA-induced thrombolysis in acute ischemic stroke. Stroke 49(3):754\u2013757. https:\/\/doi.org\/10.1161\/STROKEAHA.117.019896","journal-title":"Stroke"},{"issue":"2","key":"6552_CR36","doi-asserted-by":"publisher","first-page":"223","DOI":"10.1002\/ana.24993","volume":"82","author":"E Laridan","year":"2017","unstructured":"Laridan E, Denorme F, Desender L, Fran\u00e7ois O, Andersson T, Deckmyn H, Vanhoorelbeke K, De Meyer SF (2017) Neutrophil extracellular traps in ischemic stroke thrombi. Ann Neurol 82(2):223\u2013232. https:\/\/doi.org\/10.1002\/ana.24993","journal-title":"Ann Neurol"},{"issue":"1","key":"6552_CR37","doi-asserted-by":"publisher","first-page":"202","DOI":"10.1161\/01.str.25.1.202","volume":"25","author":"Y Okada","year":"1994","unstructured":"Okada Y, Copeland BR, Mori E, Tung MM, Thoms WS, del Zoppo GJ (1994) P-Selectin and intercellular adhesion molecule-1 expression after brain ischemia reperfusion. Stroke 25(1):202\u2013211. https:\/\/doi.org\/10.1161\/01.str.25.1.202","journal-title":"Stroke"},{"issue":"6","key":"6552_CR38","doi-asserted-by":"publisher","first-page":"1126","DOI":"10.1097\/00004647-199611000-00006","volume":"16","author":"RL Zhang","year":"1996","unstructured":"Zhang RL, Chopp M, Zhang ZG, Phillips ML, Rosenbloom CL, Cruz R, Manning A (1996) E-selectin in focal cerebral ischemia and reperfusion in the rat. J Cereb Blood Flow Metab 16(6):1126\u20131136. https:\/\/doi.org\/10.1097\/00004647-199611000-00006","journal-title":"J Cereb Blood Flow Metab"},{"issue":"1\u20132","key":"6552_CR39","doi-asserted-by":"publisher","first-page":"61","DOI":"10.1016\/0169-328x(94)90074-4","volume":"26","author":"X Wang","year":"1994","unstructured":"Wang X, Siren AL, Liu Y, Yue TL, Barone FC, Feuerstein GZ (1994) Upregulation of intercellular adhesion molecule 1 (ICAM-1) on brain microvascular endothelial cells in rat ischemic cortex. Brain Res Mol Brain Res 26(1\u20132):61\u201368. https:\/\/doi.org\/10.1016\/0169-328x(94)90074-4","journal-title":"Brain Res Mol Brain Res"},{"issue":"2","key":"6552_CR40","doi-asserted-by":"publisher","first-page":"212","DOI":"10.1006\/jsre.2002.6552","volume":"108","author":"D Myers","year":"2002","unstructured":"Myers D, Farris D, Hawley A, Wrobleski S, Chapman A, Stoolman L, Knibbs R, Strieter R, Wakefield T (2002) Selectins influence thrombosis in a mouse model of experimental deep vein thrombosis. J Surg Res 108(2):212\u2013221. https:\/\/doi.org\/10.1006\/jsre.2002.6552","journal-title":"J Surg Res"},{"issue":"4","key":"6552_CR41","doi-asserted-by":"publisher","first-page":"295","DOI":"10.1016\/0049-3848(93)90138-e","volume":"72","author":"YJ Lee","year":"1993","unstructured":"Lee YJ, Jy W, Horstman LL, Janania J, Reyes Y, Kelley RE, Ahn YS (1993) Elevated platelet microparticles in transient ischemic attacks, lacunar infarcts, and multiinfarct dementias. Thromb Res 72(4):295\u2013304. https:\/\/doi.org\/10.1016\/0049-3848(93)90138-e","journal-title":"Thromb Res"},{"key":"6552_CR42","doi-asserted-by":"publisher","first-page":"19","DOI":"10.1016\/j.thromres.2017.03.025","volume":"154","author":"Z He","year":"2017","unstructured":"He Z, Tang Y, Qin C (2017) Increased circulating leukocyte-derived microparticles in ischemic cerebrovascular disease. Thromb Res 154:19\u201325. https:\/\/doi.org\/10.1016\/j.thromres.2017.03.025","journal-title":"Thromb Res"},{"issue":"1","key":"6552_CR43","doi-asserted-by":"publisher","first-page":"9","DOI":"10.1159\/000495942","volume":"9","author":"N Kandiyil","year":"2019","unstructured":"Kandiyil N, MacSweeney ST, Heptinstall S, May J, Fox SC, Auer DP (2019) Circulating microparticles in patients with symptomatic carotid disease are related to embolic plaque activity and recent cerebral ischaemia. Cerebrovasc Dis Extra 9(1):9\u201318. https:\/\/doi.org\/10.1159\/000495942","journal-title":"Cerebrovasc Dis Extra"},{"issue":"8","key":"6552_CR44","doi-asserted-by":"publisher","first-page":"1863","DOI":"10.1161\/01.str.31.8.1863","volume":"31","author":"M Slevin","year":"2000","unstructured":"Slevin M, Krupinski J, Slowik A, Kumar P, Szczudlik A, GaffneyJ, (2000) Serial measurement of vascular endothelial growth factor and transforming growth factor-beta1 in serum of patient with acute ischemic stroke. Stroke 31(8):1863\u20131870. https:\/\/doi.org\/10.1161\/01.str.31.8.1863","journal-title":"Stroke"},{"issue":"1","key":"6552_CR45","doi-asserted-by":"publisher","first-page":"31","DOI":"10.1186\/s13075-018-1790-x","volume":"21","author":"L Fan","year":"2019","unstructured":"Fan L, Zhang H, Cai J, Yang L, Liu B, Wei D, Yu J, Fan J, Song L, Ma W, Zhou X, Wu H, Lou Y (2019) Clinical course and prognostic factors of childhood Takayasu\u2019s arteritis: over 15-year comprehensive analysis of 101 patients. Arthritis Res Ther 21(1):31. https:\/\/doi.org\/10.1186\/s13075-018-1790-x","journal-title":"Arthritis Res Ther"},{"key":"6552_CR46","doi-asserted-by":"publisher","DOI":"10.1007\/s00296-022-05238-6","author":"M Held","year":"2022","unstructured":"Held M, Sestan M, Jelusic M (2022) Obesity as a comorbidity in children and adolescents with autoimmune rheumatic diseases. Rheumatol Int. https:\/\/doi.org\/10.1007\/s00296-022-05238-6","journal-title":"Rheumatol Int"},{"issue":"11","key":"6552_CR47","doi-asserted-by":"publisher","first-page":"919","DOI":"10.7326\/0003-4819-120-11-199406010-00004","volume":"120","author":"GS Kerr","year":"1994","unstructured":"Kerr GS, Hallahan CW, Giordano J, Leavitt RY, Fauci AS, Rottem M, Hoffman GS (1994) Takayasu arteritis. Ann Intern Med 120(11):919\u2013929. https:\/\/doi.org\/10.7326\/0003-4819-120-11-199406010-00004","journal-title":"Ann Intern Med"},{"key":"6552_CR48","doi-asserted-by":"publisher","first-page":"1806","DOI":"10.1093\/rheumatology\/keq167","volume":"49","author":"J Brunner","year":"2010","unstructured":"Brunner J, Feldman BM, Tyrrell PN, Kuemmerle-Deschner JB, Zimmerhackl LB, Gassner I, Benseler SM (2010) Takayasu arteritis in children and adolescents. Rheumatology (Oxford) 49:1806\u20131814. https:\/\/doi.org\/10.1093\/rheumatology\/keq167","journal-title":"Rheumatology (Oxford)"},{"key":"6552_CR49","doi-asserted-by":"publisher","first-page":"315","DOI":"10.1002\/art.40690","volume":"71","author":"FA Aeschlimann","year":"2019","unstructured":"Aeschlimann FA, Barra L, Alsolaimani R, Benseler SM, Hebert D, Khalidi N, Laxer RM, Noone D, Pagnoux C, Twilt M, Yeung RSM (2019) Presentation and disease course of childhood-onset versus adult-onset Takayasu arteritis. Arthritis Rheumatol 71:315\u2013323. https:\/\/doi.org\/10.1002\/art.40690","journal-title":"Arthritis Rheumatol"},{"key":"6552_CR50","doi-asserted-by":"publisher","first-page":"21","DOI":"10.1186\/1546-0096-12-21","volume":"12","author":"HS Szugye","year":"2014","unstructured":"Szugye HS, Zeft AS, Spalding SJ (2014) Takayasu arteritis in the paediatric population: a contemporary United States-based single center cohort. Pediatr Rheumatol Online J 12:21. https:\/\/doi.org\/10.1186\/1546-0096-12-21","journal-title":"Pediatr Rheumatol Online J"},{"issue":"8","key":"6552_CR51","doi-asserted-by":"publisher","first-page":"642","DOI":"10.1177\/0883073821991287","volume":"36","author":"HE S\u00f6nmez","year":"2021","unstructured":"S\u00f6nmez HE, Demir F, \u00d6zdel S, G\u00fcl Karada\u011f \u015e, Ba\u011flan E, B\u00fclb\u00fcl M, \u00c7akan M, Aktay Ayaz N, S\u00f6zeri B (2021) Neuroimaging of children with Takayasu arteritis. J Child Neurol 36(8):642\u2013647. https:\/\/doi.org\/10.1177\/0883073821991287","journal-title":"J Child Neurol"},{"key":"6552_CR52","doi-asserted-by":"publisher","first-page":"1183","DOI":"10.3899\/jrheum.131117","volume":"41","author":"R Goel","year":"2014","unstructured":"Goel R, Kumar TS, Danda D, Joseph G, Jeyaseelan V, Surin AK, Bacon P (2014) Childhood-onset Takayasu arteritis-experience from a tertiary care center in South India. J Rheumatol 41:1183\u20131189. https:\/\/doi.org\/10.3899\/jrheum.131117","journal-title":"J Rheumatol"},{"issue":"5","key":"6552_CR53","doi-asserted-by":"publisher","first-page":"2246","DOI":"10.1093\/rheumatology\/keaa569","volume":"60","author":"D Danda","year":"2021","unstructured":"Danda D, Goel R, Joseph G, Kumar ST, Nair A, Ravindran R, Jeyaseelen L, Merkel PA, Grayson PC (2021) Clinical course of 602 patients with Takayasu\u2019s arteritis: comparison between childhood-onset versus adult onset disease. Rheumatology (Oxford) 60(5):2246\u20132255. https:\/\/doi.org\/10.1093\/rheumatology\/keaa569","journal-title":"Rheumatology (Oxford)"},{"key":"6552_CR54","doi-asserted-by":"publisher","first-page":"506","DOI":"10.3109\/03009741003742730","volume":"39","author":"LH Jales-Neto","year":"2010","unstructured":"Jales-Neto LH, Levy-Neto M, Bonfa E, de Carvalho JF, Pereira RMR (2010) Juvenile-onset Takayasu arteritis: peculiar vascular involvement and more refractory disease. Scand J Rheumatol 39:506\u2013510. https:\/\/doi.org\/10.3109\/03009741003742730","journal-title":"Scand J Rheumatol"},{"issue":"1","key":"6552_CR55","doi-asserted-by":"publisher","first-page":"36","DOI":"10.1186\/s13075-015-0545-1","volume":"17","author":"D Eleftheriou","year":"2015","unstructured":"Eleftheriou D, Varnier G, Dolezalova P, McMahon AM, Al-Obaidi M, Brogan PA (2015) Takayasu arteritis in childhood: retrospective experience from a tertiary referral centre in the United Kingdom. Arthritis Res Ther 17(1):36. https:\/\/doi.org\/10.1186\/s13075-015-0545-1","journal-title":"Arthritis Res Ther"},{"issue":"3","key":"6552_CR56","doi-asserted-by":"publisher","first-page":"211","DOI":"10.3109\/03009742.2014.964305","volume":"44","author":"NP Jordan","year":"2015","unstructured":"Jordan NP, Bezanahary H, D\u2019Cruz DP (2015) Increased risk of vascular complications in Takayasu\u2019s arteritis patients with positive lupus anticoagulant. Scand J Rheumatol 44(3):211\u2013214. https:\/\/doi.org\/10.3109\/03009742.2014.964305","journal-title":"Scand J Rheumatol"},{"issue":"3","key":"6552_CR57","doi-asserted-by":"publisher","first-page":"295","DOI":"10.1016\/S0104-4230(11)70062-8","volume":"57","author":"NR Alves","year":"1992","unstructured":"Alves NR, Magalh\u00e3es CM, Almeida Rde F, Santos RC, Gandolfi L, Pratesi R (1992) Prospective study of Kawasaki disease complications: review of 115 cases. Rev Assoc Med Bras 57(3):295\u2013300","journal-title":"Rev Assoc Med Bras"},{"issue":"9","key":"6552_CR58","doi-asserted-by":"publisher","first-page":"2476","DOI":"10.1002\/art.38024","volume":"65","author":"D Eleftheriou","year":"2013","unstructured":"Eleftheriou D, Dillon MJ, Tullus K, Marks SD, Pilkington CA, Roebuck DJ, Klein NJ, Brogan PA (2013) Systemic polyarteritis nodosa in the young: a single-center experience over thirty-two years. Arthritis Rheum 65(9):2476\u20132485. https:\/\/doi.org\/10.1002\/art.38024","journal-title":"Arthritis Rheum"},{"issue":"3 Suppl 82","key":"6552_CR59","first-page":"134","volume":"32","author":"F Falcini","year":"2014","unstructured":"Falcini F, La Torre F, Vittadello F, Rigante D, Martini G, Corona F et al (2014) Clinical overview and outcome in a cohort of children with polyarteritis nodosa. Clin Exp Rheumatol 32(3 Suppl 82):134\u2013137","journal-title":"Clin Exp Rheumatol"},{"key":"6552_CR60","doi-asserted-by":"publisher","first-page":"18","DOI":"10.1186\/1750-1172-8-18","volume":"8","author":"P Mora","year":"2013","unstructured":"Mora P, Menozzi C, Orsoni JG, Rubino P, Ruffini L, Carta A (2013) Neuro-Behcet\u2019s disease in childhood: a focus on the neuro-ophthalmological features. Orphanet J Rare Dis 8:18. https:\/\/doi.org\/10.1186\/1750-1172-8-18","journal-title":"Orphanet J Rare Dis"},{"issue":"1","key":"6552_CR61","doi-asserted-by":"publisher","first-page":"61","DOI":"10.1186\/s12969-020-00452-7","volume":"18","author":"X Liu","year":"2020","unstructured":"Liu X, Zhou K, Hua Y, Wu M, Liu L, Shao S, Wang C (2020) Neurological involvement in Kawasaki disease: a retrospective study. Pediatr Rheumatol Online J 18(1):61. https:\/\/doi.org\/10.1186\/s12969-020-00452-7","journal-title":"Pediatr Rheumatol Online J"},{"issue":"4","key":"6552_CR62","doi-asserted-by":"publisher","first-page":"517","DOI":"10.1016\/j.jpeds.2004.06.046","volume":"145","author":"S Ozen","year":"2004","unstructured":"Ozen S, Anton J, Arisoy N, Bakkaloglu A, Besbas N, Brogan P et al (2004) Juvenile polyarteritis: results of a multicenter survey of 110 children. J Pediatr 145(4):517\u2013522. https:\/\/doi.org\/10.1016\/j.jpeds.2004.06.046","journal-title":"J Pediatr"},{"issue":"3","key":"6552_CR63","doi-asserted-by":"publisher","first-page":"167","DOI":"10.1016\/j.pediatrneurol.2012.05.024","volume":"47","author":"A Liu","year":"2012","unstructured":"Liu A, Zhang H (2012) Detection of antiphospholipid antibody in children with Henoch-Sch\u00f6nlein purpura and central nervous system involvement. Pediatr Neurol 47(3):167\u2013170. https:\/\/doi.org\/10.1016\/j.pediatrneurol.2012.05.024","journal-title":"Pediatr Neurol"},{"issue":"3","key":"6552_CR64","doi-asserted-by":"publisher","first-page":"339","DOI":"10.1111\/j.1651-2227.1991.tb11859.x","volume":"80","author":"JR Ostergaard","year":"1991","unstructured":"Ostergaard JR, Storm K (1991) Neurologic manifestations of Sch\u00f6nlein-Henoch purpura. Acta Paediatr Scand 80(3):339\u2013342. https:\/\/doi.org\/10.1111\/j.1651-2227.1991.tb11859.x","journal-title":"Acta Paediatr Scand"},{"issue":"8","key":"6552_CR65","first-page":"1588","volume":"40","author":"R T\u00fct\u00fcnc\u00fc Toker","year":"2022","unstructured":"T\u00fct\u00fcnc\u00fc Toker R, Bodur M, Bican Demir A, Okan MS (2022) Neuro-Beh\u00e7et is a rare disease but should be considered in all kinds of neurological findings, even in childhood. Clin Exp Rheumatol 40(8):1588\u20131592","journal-title":"Clin Exp Rheumatol"},{"issue":"4","key":"6552_CR66","doi-asserted-by":"publisher","first-page":"721","DOI":"10.1016\/s0022-3476(98)70368-3","volume":"132","author":"I Kon\u00e9-Paut","year":"1998","unstructured":"Kon\u00e9-Paut I, Yurdakul S, Bahabri SA, Shafae N, Ozen S, Ozdogan H, Ozdogan H, Bernard JL (1998) Clinical features of Beh\u00e7et\u2019s disease in children: an international study of 86 cases. J Pediatr 132(4):721\u2013725. https:\/\/doi.org\/10.1016\/s0022-3476(98)70368-3","journal-title":"J Pediatr"},{"issue":"12","key":"6552_CR67","doi-asserted-by":"publisher","first-page":"3087","DOI":"10.1007\/s00296-012-2595-x","volume":"33","author":"M Jelusic","year":"2013","unstructured":"Jelusic M, Vikic-Topic M, Batinic D, Milosevic D, Malenica B, Malcic I (2013) Polyarteritis nodosa in Croatian children: a retrospective study over the last 20 years. Rheumatol Int 33(12):3087\u20133090. https:\/\/doi.org\/10.1007\/s00296-012-2595-x","journal-title":"Rheumatol Int"},{"key":"6552_CR68","doi-asserted-by":"publisher","unstructured":"Shah S, Hata J (2021) A rare and severe presentation of Henoch-Sch\u00f6nlein purpura in an adolescent with crescentic glomerulonephritis, arrhythmia, acute gastrointestinal bleed, and neurological complications. Cureus 29;13(3):e14169. https:\/\/doi.org\/10.7759\/cureus.14169.","DOI":"10.7759\/cureus.14169"},{"issue":"1","key":"6552_CR69","doi-asserted-by":"publisher","first-page":"107","DOI":"10.1016\/j.pjnns.2017.11.006","volume":"52","author":"H Arslan","year":"2018","unstructured":"Arslan H, Yavuz A, Arslan A, Aycan A (2018) Posterior reversible encephalopathy syndrome in IgA vasculitis: neuroimaging of a 14-year-old child. Neurol Neurochir Pol 52(1):107\u2013111","journal-title":"Neurol Neurochir Pol"},{"issue":"6","key":"6552_CR70","first-page":"147","volume":"121","author":"S Demir","year":"2019","unstructured":"Demir S, Acari C, Basaran O, Sag E, Oguz KK, Bilginer Y, \u00dcnsal SE, Ozen S (2019) Paediatric Behcet\u2019s disease with sinus venous thrombosis: experience from three centres from Turkey. Clin Exp Rheumatol 121(6):147\u2013151","journal-title":"Clin Exp Rheumatol"},{"issue":"12","key":"6552_CR71","doi-asserted-by":"publisher","first-page":"1139","DOI":"10.1007\/s004670100048","volume":"16","author":"A Bulun","year":"2001","unstructured":"Bulun A, Topaloglu R, Duzova A, Saatci I, Besbas N, Bakkaloglu A (2001) Ataxia and peripheral neuropathy: rare manifestations in Henoch-Sch\u00f6nlein purpura. Pediatr Nephrol 16(12):1139\u20131141. https:\/\/doi.org\/10.1007\/s004670100048","journal-title":"Pediatr Nephrol"},{"issue":"1","key":"6552_CR72","doi-asserted-by":"publisher","first-page":"81","DOI":"10.1186\/s13052-016-0291-2","volume":"42","author":"M Marsili","year":"2016","unstructured":"Marsili M, Marzetti V, Lucantoni M, Lapergola G, Gattorno M, Chiarelli F, Breda L (2016) Autoimmune sensorineural hearing loss as presenting manifestation of paediatric Beh\u00e7et disease responding to adalimumab: a case report. Ital J Pediatr 42(1):81. https:\/\/doi.org\/10.1186\/s13052-016-0291-2","journal-title":"Ital J Pediatr"},{"issue":"18","key":"6552_CR73","doi-asserted-by":"publisher","first-page":"1963","DOI":"10.2169\/internalmedicine.50.5572","volume":"50","author":"O Ogawa","year":"2011","unstructured":"Ogawa O, Watanabe R, Shimizu H, Masani F (2011) Hypertensive crisis in young woman with Takayasu arteritis. Intern Med 50(18):1963\u20131970. https:\/\/doi.org\/10.2169\/internalmedicine.50.5572","journal-title":"Intern Med"},{"issue":"17","key":"6552_CR74","doi-asserted-by":"publisher","first-page":"2747","DOI":"10.1161\/01.CIR.0000145143.19711.78","volume":"110","author":"JW Newburger","year":"2004","unstructured":"Newburger JW, Takahashi M, Gerber MA, Gewitz MH, Tani LY, Burns JC et al (2004) Diagnosis, treatment, and long-term management of Kawasaki disease: a statement for health professionals from the Committee on rheumatic fever, endocarditis and Kawasaki disease, Council on cardiovascular disease in the young. American Heart Association. Circulation 110(17):2747\u20132771. https:\/\/doi.org\/10.1161\/01.CIR.0000145143.19711.78","journal-title":"American Heart Association. Circulation"},{"issue":"4","key":"6552_CR75","doi-asserted-by":"publisher","first-page":"397","DOI":"10.1111\/ped.13809","volume":"61","author":"N Makino","year":"2019","unstructured":"Makino N, Nakamura Y, Yashiro M, Kosami K, Matsubara Y, Ae R, Aoyama Y, Yanagawa H (2019) The Nationwide epidemiologic survey of Kawasaki disease in Japan, 2015\u20132016. Pediatr Int 61(4):397\u2013403. https:\/\/doi.org\/10.1111\/ped.13809","journal-title":"Pediatr Int"},{"issue":"4","key":"6552_CR76","doi-asserted-by":"publisher","first-page":"295","DOI":"10.1016\/j.pediatrneurol.2012.05.022","volume":"47","author":"T Okanishi","year":"2012","unstructured":"Okanishi T, Enoki H (2012) Transient subcortical high-signal lesions in Kawasaki syndrome. Pediatr Neurol\u00a0 47(4):295\u2013298","journal-title":"Pediatr Neurol\u00a0"},{"issue":"1","key":"6552_CR77","doi-asserted-by":"publisher","first-page":"103","DOI":"10.1017\/s1047951103000179","volume":"13","author":"K Suda","year":"2003","unstructured":"Suda K, Matsumura M, Ohta S (2003) Kawasaki disease complicated by cerebral infarction. Cardiol Young 13(1):103\u2013105. https:\/\/doi.org\/10.1017\/s1047951103000179","journal-title":"Cardiol Young"},{"key":"6552_CR78","doi-asserted-by":"publisher","first-page":"235","DOI":"10.1016\/0887-8994(92)90077-c","volume":"883","author":"S Fujiwara","year":"1992","unstructured":"Fujiwara S, Yamano T, Hattori M, Fujiseki Y, Shimada, (1992) Asymptomatic cerebral infarction in Kawasaki disease. Pediatr Neurol 883:235\u2013236. https:\/\/doi.org\/10.1016\/0887-8994(92)90077-c","journal-title":"Pediatr Neurol"},{"issue":"2","key":"6552_CR79","doi-asserted-by":"publisher","first-page":"79","DOI":"10.1053\/ejpn.2001.0469","volume":"5","author":"NM Bailie","year":"2001","unstructured":"Bailie NM, Hensey OJ, Ryan S, Allcut D, King MD (2001) Bilateral subdural collections-an unusual feature of possible Kawasaki disease. Eur J Paediatr Neurol 5(2):79\u201381. https:\/\/doi.org\/10.1053\/ejpn.2001.0469","journal-title":"Eur J Paediatr Neurol"},{"issue":"1","key":"6552_CR80","doi-asserted-by":"publisher","first-page":"30","DOI":"10.1016\/j.braindev.2005.04.003","volume":"28","author":"J Muneuchi","year":"2006","unstructured":"Muneuchi J, Kusuhara K, Kanaya Y, Ohno T, Furuno K, Kira R, Mihara F, Hara T (2006) Magnetic resonance studies of brain lesions in patients with Kawasaki disease. Brain Dev 28(1):30\u201333. https:\/\/doi.org\/10.1016\/j.braindev.2005.04.003","journal-title":"Brain Dev"},{"issue":"2","key":"6552_CR81","doi-asserted-by":"publisher","first-page":"150","DOI":"10.3171\/2010.5.PEDS1012","volume":"6","author":"JH Ahn","year":"2010","unstructured":"Ahn JH, Phi JH, Kang HS, Wang KC, Cho BK, Lee JY, Kim GB, Kim SK (2010) A ruptured middle cerebral artery aneurysm in a 13-month old boy with Kawasaki disease. J Neurosurg Pediatr 6(2):150\u2013153. https:\/\/doi.org\/10.3171\/2010.5.PEDS1012","journal-title":"J Neurosurg Pediatr"},{"issue":"7","key":"6552_CR82","doi-asserted-by":"publisher","first-page":"1320","DOI":"10.1161\/01.str.29.7.1320","volume":"29","author":"T Ichiyama","year":"1998","unstructured":"Ichiyama T, Nishikawa M, Hayashi T, Koga M, Tashiro N, Furukawa S (1998) Cerebral hypoperfusion during acute Kawasaki disease. Stroke 29(7):1320\u20131321. https:\/\/doi.org\/10.1161\/01.str.29.7.1320","journal-title":"Stroke"},{"issue":"1","key":"6552_CR83","doi-asserted-by":"publisher","first-page":"43","DOI":"10.1136\/adc.2006.096628","volume":"92","author":"YF Cheung","year":"2007","unstructured":"Cheung YF, Wong SJ, Ho MH (2007) Relationship between carotid intima-media thickness and arterial stiffness in children after Kawasaki disease. Arch Dis Child 92(1):43\u201347. https:\/\/doi.org\/10.1136\/adc.2006.096628","journal-title":"Arch Dis Child"},{"key":"6552_CR84","doi-asserted-by":"publisher","DOI":"10.1038\/s41390-022-02273-8","author":"JJY Lee","year":"2022","unstructured":"Lee JJY, Feldman BM, McCrindle BW, Li P, Yeung RS, Widdifield, (2022) Evaluating the time-varying risk of hypertension, cardiac events, and mortality following Kawasaki disease diagnosis. Pediatr Res. https:\/\/doi.org\/10.1038\/s41390-022-02273-8","journal-title":"Pediatr Res"},{"issue":"4","key":"6552_CR85","doi-asserted-by":"publisher","first-page":"1256","DOI":"10.1161\/STROKEAHA","volume":"53","author":"CH Lin","year":"2022","unstructured":"Lin CH, Li JN, Lee IC, Chou IC, Lin WD, Lin MC, Hong SY (2022) Kawasaki disease may increase the risk of subsequent cerebrovascular disease. Stroke 53(4):1256\u20131262. https:\/\/doi.org\/10.1161\/STROKEAHA","journal-title":"Stroke"},{"key":"6552_CR86","doi-asserted-by":"publisher","first-page":"629902","DOI":"10.3389\/fimmu.2021.629902","volume":"12","author":"SS Ahn","year":"2021","unstructured":"Ahn SS, Han M, Yoo J, Park YB, Jung I, Lee SW (2021) Risk of stroke in systemic necrotizing vasculitis: a nationwide study using National Claims database. Front Immunol 12:629902","journal-title":"Front Immunol"},{"issue":"1","key":"6552_CR87","doi-asserted-by":"publisher","first-page":"117","DOI":"10.3899\/jrheum.181384","volume":"47","author":"S Ozen","year":"2020","unstructured":"Ozen S, Batu ED, Ta\u015fkiran EZ, \u00d6zkara HA, \u00dcnal \u015e, G\u00fcleray N et al (2020) A monogenic disease with a variety of phenotypes: deficiency of adenosine deaminase 2. J Rheumatol 47(1):117\u2013125. https:\/\/doi.org\/10.3899\/jrheum.181384","journal-title":"J Rheumatol"},{"issue":"10","key":"6552_CR88","doi-asserted-by":"publisher","first-page":"1648","DOI":"10.1136\/annrheumdis-2016-210802","volume":"76","author":"R Caorsi","year":"2017","unstructured":"Caorsi R, Penco F, Grossi A, Insalaco A, Omenetti A, Alessio M et al (2017) ADA2 deficiency (DADA2) as an unrecognized cause of early onset polyarteritis nodosa and stroke: a multicentre national study. Ann Rheum Dis 76(10):1648\u20131656. https:\/\/doi.org\/10.1136\/annrheumdis-2016-210802","journal-title":"Ann Rheum Dis"},{"key":"6552_CR89","doi-asserted-by":"publisher","first-page":"811473","DOI":"10.3389\/fimmu.2021.811473","volume":"12","author":"KS Barron","year":"2022","unstructured":"Barron KS, Aksentijevich I, Deuitch NT, Stone DL, Hoffmann P, Videgar-Laird R et al (2022) The spectrum of the deficiency of adenosine deaminase 2: an observational analysis of a 60 patient cohort. Front Immunol 12:811473","journal-title":"Front Immunol"},{"issue":"9","key":"6552_CR90","doi-asserted-by":"publisher","first-page":"4373","DOI":"10.1093\/rheumatology\/keaa837","volume":"60","author":"S Cooray","year":"2021","unstructured":"Cooray S, Omyinmi E, Hong Y, Papadopoulou C, Harper L, Al-Abadi E et al (2021) Anti-tumor necrosis factor treatment for the prevention of ischaemic events in patients with deficiency of adenosine deaminase 2 (DADA2). Rheumatology (Oxford) 60(9):4373\u20134378","journal-title":"Rheumatology (Oxford)"},{"issue":"8","key":"6552_CR91","doi-asserted-by":"publisher","first-page":"1358","DOI":"10.1093\/rheumatology\/kex158","volume":"56","author":"M Piram","year":"2017","unstructured":"Piram M, Maldini C, Biscardi S, De Suremain N, Orzechowski C, Georget E, Regnard D, Kon\u00e9-Paut I, Mahr A (2017) Incidence of IgA vasculitis in children estimated by four-source capture-recapture analysis: a population-based study. Rheumatology 56(8):1358\u20131366. https:\/\/doi.org\/10.1093\/rheumatology\/kex158","journal-title":"Rheumatology"},{"issue":"5","key":"6552_CR92","doi-asserted-by":"publisher","first-page":"610","DOI":"10.1136\/annrheumdis-2020-218649","volume":"80","author":"M Sapina","year":"2021","unstructured":"Sapina M, Frkovic M, Sestan M, Srsen S, Ovuka A, Batnozic Varga M, Kramaric K, Brdaric D, Milas K, Gagro A, Jelusic M (2021) Geospatial clustering of childhood IgA vasculitis and IgA vasculitis-associated vasculitis. Ann Rheum Dis 80(5):610\u2013616. https:\/\/doi.org\/10.1136\/annrheumdis-2020-218649","journal-title":"Ann Rheum Dis"},{"key":"6552_CR93","doi-asserted-by":"publisher","first-page":"1759720X2110248","DOI":"10.1177\/1759720X211024828","volume":"13","author":"M Sestan","year":"2021","unstructured":"Sestan M, Kifer N, Frkovic M, Sapina S, Srsen S, Batnozic Varga M et al (2021) Gastrointestinal involvement and its association with the risk for nephritis in IgA vasculitis. Ther Adv Musculoskelet Dis 13:1759720X211024828. https:\/\/doi.org\/10.1177\/1759720X211024828","journal-title":"Ther Adv Musculoskelet Dis"},{"key":"6552_CR94","doi-asserted-by":"publisher","DOI":"10.1007\/s40620-022-01545-0","author":"N Kifer","year":"2022","unstructured":"Kifer N, Bulimbasic S, Sestan M, Held M, Kifer D, Srsen S et al (2022) Semiquantitative classification (SQC) and Oxford classifications predict poor renal outcome better than The International Study of Kidney Disease in Children (ISKDC) and Haas in patients with IgAV nephritis: a multicenter study. J Nephrol. https:\/\/doi.org\/10.1007\/s40620-022-01545-0","journal-title":"J Nephrol"},{"issue":"12","key":"6552_CR95","doi-asserted-by":"publisher","first-page":"1524","DOI":"10.1093\/rheumatology\/kep282","volume":"48","author":"L Garzoni","year":"2009","unstructured":"Garzoni L, Vanoni F, Rizzi M, Simonetti GD, Goeggel Simonetti B, Ramelli GP, Bianchetti MG (2009) Nervous system dysfunction in Henoch-Schonlein syndrome: systematic review of the literature. Rheumatology (Oxford) 48(12):1524\u20131529. https:\/\/doi.org\/10.1093\/rheumatology\/kep282","journal-title":"Rheumatology (Oxford)"},{"issue":"9","key":"6552_CR96","doi-asserted-by":"publisher","first-page":"1379","DOI":"10.1212\/wnl.55.9.1379","volume":"55","author":"DK Sokol","year":"2000","unstructured":"Sokol DK, McIntyre JA, Short RA, Gutt J, Wagenknecht DR, Biller J, Garg B (2000) Henoch-Sch\u00f6nlein purpura and stroke: antiphosphatidylethanolamine antibody in CSF and serum. Neurology 55(9):1379\u20131381. https:\/\/doi.org\/10.1212\/wnl.55.9.1379","journal-title":"Neurology"},{"key":"6552_CR97","doi-asserted-by":"publisher","first-page":"1166","DOI":"10.3389\/fneur.2018.01166","volume":"9","author":"Y Zheng","year":"2019","unstructured":"Zheng Y, Zhang Y, Cai M, Lai N, Chen Z, Ding M (2019) Central nervous system involvement in ANCA-associated vasculitis: what neurologists need to know. Front Neurol 9:1166. https:\/\/doi.org\/10.3389\/fneur.2018.01166","journal-title":"Front Neurol"},{"issue":"7","key":"6552_CR98","doi-asserted-by":"publisher","first-page":"1043","DOI":"10.2215\/CJN.19181220","volume":"16","author":"M Calatroni","year":"2021","unstructured":"Calatroni M, Consonni F, Allinovi M, Bettiol A, Jawa N, Fiasella S et al (2021) Prognostic factors and long-term outcome with ANCA-associated kidney vasculitis in childhood. Clin J Am Soc Nephrol 16(7):1043\u20131051. https:\/\/doi.org\/10.2215\/CJN.19181220","journal-title":"Clin J Am Soc Nephrol"},{"issue":"9","key":"6552_CR99","doi-asserted-by":"publisher","first-page":"754","DOI":"10.1007\/s00467-002-0914-2","volume":"17","author":"VM Belostotsky","year":"2002","unstructured":"Belostotsky VM, Shah V, Dillon MJ (2002) Clinical features in 17 paediatric patients with Wegener granulomatosis. Pediatr Nephrol 17(9):754\u2013761. https:\/\/doi.org\/10.1007\/s00467-002-0914-2","journal-title":"Pediatr Nephrol"},{"key":"6552_CR100","doi-asserted-by":"publisher","first-page":"2514","DOI":"10.1002\/art.39729","volume":"68","author":"DA Cabral","year":"2016","unstructured":"Cabral DA, Canter DL, Muscal E, Nanda K, Wahezi DM, Spalding SJ et al (2016) Comparing presenting clinical features in 48 children with microscopic polyangiitis to 183 children who have granulomatosis with polyangiitis (Wegener\u2019s): an ARChiVe cohort study. Arthritis Rheumatol 68:2514\u20132526. https:\/\/doi.org\/10.1002\/art.39729","journal-title":"Arthritis Rheumatol"},{"issue":"12","key":"6552_CR101","doi-asserted-by":"publisher","first-page":"1640","DOI":"10.1002\/ppul.24089","volume":"53","author":"A Fina","year":"2018","unstructured":"Fina A, Dubus JC, Tran A, Derelle J, Reix P, Fayon M et al (2018) Eosinophilic granulomatosis with polyangiitis in children: data from the French RespiRare\u00ae cohort. Pediatr Pulmonol 53(12):1640\u20131650. https:\/\/doi.org\/10.1002\/ppul.24089","journal-title":"Pediatr Pulmonol"},{"key":"6552_CR102","doi-asserted-by":"publisher","first-page":"929","DOI":"10.3899\/jrheum.120808","volume":"4086","author":"S Gendelman","year":"2013","unstructured":"Gendelman S, Zeft A, Spalding SJ (2013) Childhood-onset eosinophilic granulomatosis with polyangiitis (formerly Churg-Strauss syndrome): a contemporary single-center cohort. J Rheumatol 4086:929\u2013935","journal-title":"J Rheumatol"},{"issue":"8","key":"6552_CR103","doi-asserted-by":"publisher","first-page":"1712","DOI":"10.3899\/jrheum.131300","volume":"41","author":"L Sun","year":"2014","unstructured":"Sun L, Wang H, Jiang X, Mo Y, Yue Z, Huang L, Liu T (2014) Clinical and pathological features of microscopic polyangiitis in 20 children. J Rheumatol 41(8):1712\u20131719. https:\/\/doi.org\/10.3899\/jrheum.131300","journal-title":"J Rheumatol"},{"issue":"8","key":"6552_CR104","doi-asserted-by":"publisher","first-page":"NP1-4","DOI":"10.1177\/0883073813488661","volume":"29","author":"E Iglesias","year":"2014","unstructured":"Iglesias E, Eleftheriou D, Mankad K, Prabhakar P, Brogan PA (2014) Microscopic polyangiitis presenting with hemorrhagic stroke. J Child Neurol 29(8):NP1-4. https:\/\/doi.org\/10.1177\/0883073813488661","journal-title":"J Child Neurol"},{"key":"6552_CR105","doi-asserted-by":"publisher","first-page":"958","DOI":"10.1136\/annrheumdis-2015-208491","volume":"75","author":"I Kon\u00e9-Paut","year":"2016","unstructured":"Kon\u00e9-Paut I, Shahram F, Darce-Bello M, Cantarini L, Cimaz R, Gattorno M et al (2016) Consensus classification criteria for paediatric Beh\u00e7et\u2019s disease from a prospective observational cohort: PEDBD. Ann Rheum Dis 75:958\u2013964. https:\/\/doi.org\/10.1136\/annrheumdis-2015-208491","journal-title":"Ann Rheum Dis"},{"issue":"6","key":"6552_CR106","first-page":"119","volume":"108","author":"ED Batu","year":"2017","unstructured":"Batu ED, S\u00f6nmez HE, S\u00f6zeri B, Aviel YB, Bilginer Y, Ozen S (2017) The performance of different classification criteria in paediatric Beh\u00e7et\u2019s disease. Clin Exp Rheumatol 108(6):119\u2013123","journal-title":"Clin Exp Rheumatol"},{"issue":"9","key":"6552_CR107","doi-asserted-by":"publisher","first-page":"1662","DOI":"10.1007\/s00415-013-7209-3","volume":"261","author":"S Kalra","year":"2014","unstructured":"Kalra S, Silman A, Akman-Demir G, Bohlega S, Borhani-Haghighi A, Constantinescu CS et al (2014) Diagnosis and management of neuro-Beh\u00e7et\u2019s disease: international consensus recommendations. J Neurol 261(9):1662\u20131676. https:\/\/doi.org\/10.1007\/s00415-013-7209-3","journal-title":"J Neurol"},{"issue":"5","key":"6552_CR108","doi-asserted-by":"publisher","first-page":"228","DOI":"10.1055\/s-0030-1269909","volume":"41","author":"J Metreau-Vastel","year":"2010","unstructured":"Metreau-Vastel J, Mikaeloff Y, Tardieu M, Kon\u00e9-Paut I, Tran TA (2010) Neurological involvement in paediatric Beh\u00e7et\u2019s disease. Neuropaediatrics 41(5):228\u2013234. https:\/\/doi.org\/10.1055\/s-0030-1269909","journal-title":"Neuropaediatrics"},{"issue":"9","key":"6552_CR109","doi-asserted-by":"publisher","first-page":"2806","DOI":"10.1002\/art.27568","volume":"62","author":"D Saadoun","year":"2010","unstructured":"Saadoun D, Wechsler B, Desseaux K, Thi Huong DL, Amoura Z, Resche-Rigon M, Cacoub P (2010) Mortality in Beh\u00e7et\u2019s disease. Arthritis Rheum 62(9):2806\u20132812. https:\/\/doi.org\/10.1002\/art.27568","journal-title":"Arthritis Rheum"},{"issue":"8","key":"6552_CR110","first-page":"e13778","volume":"52","author":"KW Chuang","year":"2022","unstructured":"Chuang KW, Chang HC (2022) Risk of ischaemic heart diseases and stroke in Beh\u00e7et disease: a systematic review and meta-analysis. Ur J Clin Invest 52(8)","journal-title":"Ur J Clin Invest"},{"issue":"4","key":"6552_CR111","doi-asserted-by":"publisher","first-page":"672","DOI":"10.1093\/rheumatology\/key344","volume":"58","author":"N de Graeff","year":"2019","unstructured":"de Graeff N, Groot N, Ozen S, Eleftheriou D, Avcin T, Bader-Meunier B et al (2019) European consensus-based recommendations for the diagnosis and treatment of Kawasaki disease - the SHARE initiative. Rheumatology (Oxford) 58(4):672\u2013682. https:\/\/doi.org\/10.1093\/rheumatology\/key344","journal-title":"Rheumatology (Oxford)"},{"issue":"9","key":"6552_CR112","doi-asserted-by":"publisher","first-page":"1607","DOI":"10.1093\/rheumatology\/kez041","volume":"58","author":"S Ozen","year":"2019","unstructured":"Ozen S, Marks SD, Brogan P, Groot N, de Graeff N, Avcin T et al (2019) European consensus-based recommendations for diagnosis and treatment of immunoglobulin A vasculitis\u2014the SHARE initiative. Rheumatology (Oxford) 58(9):1607\u20131616. https:\/\/doi.org\/10.1093\/rheumatology\/kez041","journal-title":"Rheumatology (Oxford)"},{"issue":"4","key":"6552_CR113","doi-asserted-by":"publisher","first-page":"919","DOI":"10.1093\/rheumatology\/keaa057","volume":"59","author":"N de Graeff","year":"2020","unstructured":"de Graeff N, Groot N, Brogan P, Ozen S, Avcin T, Bader-Meunier B et al (2020) European consensus-based recommendations for the diagnosis and treatment of rare paediatric vasculitides\u2014the SHARE initiative. Rheumatology (Oxford) 59(4):919. https:\/\/doi.org\/10.1093\/rheumatology\/keaa057","journal-title":"Rheumatology (Oxford)"}],"container-title":["Clinical Rheumatology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1007\/s10067-023-06552-5.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/link.springer.com\/article\/10.1007\/s10067-023-06552-5\/fulltext.html","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1007\/s10067-023-06552-5.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,11,13]],"date-time":"2023-11-13T14:06:21Z","timestamp":1699884381000},"score":1,"resource":{"primary":{"URL":"https:\/\/link.springer.com\/10.1007\/s10067-023-06552-5"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2023,3,8]]},"references-count":113,"journal-issue":{"issue":"10","published-print":{"date-parts":[[2023,10]]}},"alternative-id":["6552"],"URL":"https:\/\/doi.org\/10.1007\/s10067-023-06552-5","relation":{},"ISSN":["0770-3198","1434-9949"],"issn-type":[{"value":"0770-3198","type":"print"},{"value":"1434-9949","type":"electronic"}],"subject":[],"published":{"date-parts":[[2023,3,8]]},"assertion":[{"value":"7 December 2022","order":1,"name":"received","label":"Received","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"2 February 2023","order":2,"name":"revised","label":"Revised","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"15 February 2023","order":3,"name":"accepted","label":"Accepted","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"8 March 2023","order":4,"name":"first_online","label":"First Online","group":{"name":"ArticleHistory","label":"Article History"}},{"order":1,"name":"Ethics","group":{"name":"EthicsHeading","label":"Declarations"}},{"value":"The manuscript does not contain clinical studies or patient data.","order":2,"name":"Ethics","group":{"name":"EthicsHeading","label":"Ethical approval"}},{"value":"Not applicable.","order":3,"name":"Ethics","group":{"name":"EthicsHeading","label":"Consent to participate"}},{"value":"Not applicable.","order":4,"name":"Ethics","group":{"name":"EthicsHeading","label":"Consent for publication"}},{"value":"None.","order":5,"name":"Ethics","group":{"name":"EthicsHeading","label":"Disclosures"}},{"value":"No part of this review is copied or published elsewhere in whole or in part in any languages.","order":6,"name":"Ethics","group":{"name":"EthicsHeading","label":"Disclaimer"}}]}}