{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,7,3]],"date-time":"2025-07-03T13:33:12Z","timestamp":1751549592203},"reference-count":9,"publisher":"Springer Science and Business Media LLC","issue":"3","license":[{"start":{"date-parts":[[2016,12,2]],"date-time":"2016-12-02T00:00:00Z","timestamp":1480636800000},"content-version":"unspecified","delay-in-days":0,"URL":"http:\/\/www.springer.com\/tdm"}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["Neurol Sci"],"published-print":{"date-parts":[[2017,3]]},"DOI":"10.1007\/s10072-016-2788-2","type":"journal-article","created":{"date-parts":[[2016,12,2]],"date-time":"2016-12-02T04:16:49Z","timestamp":1480652209000},"page":"445-450","update-policy":"http:\/\/dx.doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":6,"title":["Association between brain structural anomalies, electroencephalogram and history of seizures in Mucopolysaccharidosis type II (Hunter syndrome)"],"prefix":"10.1007","volume":"38","author":[{"given":"Ram\u00f3n Ernesto","family":"Jim\u00e9nez-Arredondo","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Aniel Jessica Leticia","family":"Brambila-Tapia","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Francisco Miguel","family":"Mercado-Silva","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Martha","family":"Ortiz-Aranda","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ver\u00f3nica","family":"Benites-Godinez","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Graciela","family":"Olmos-Garc\u00eda-de-ALBA","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Luis Eduardo","family":"Figuera","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"297","published-online":{"date-parts":[[2016,12,2]]},"reference":[{"key":"2788_CR1","doi-asserted-by":"crossref","first-page":"1319","DOI":"10.3174\/ajnr.A2032","volume":"31","author":"Z Fan","year":"2010","unstructured":"Fan Z, Styner M, Muenzer J, Poe M, Escolar M (2010) Correlation of automated volumetric analysis of brain MR imaging with cognitive impairment in a natural history study of mucopolysaccharidosis II. AJNR Am J Neuroradiol 31:1319\u20131323","journal-title":"AJNR Am J Neuroradiol"},{"key":"2788_CR2","doi-asserted-by":"crossref","first-page":"71","DOI":"10.1111\/j.1651-2227.2007.00213.x","volume":"96","author":"R Froissart","year":"2007","unstructured":"Froissart R, Da Silva IM, Maire I (2007) Mucopolysaccharidosis type II: an update on mutation spectrum. Acta Paediatr 96:71\u201377","journal-title":"Acta Paediatr"},{"key":"2788_CR3","doi-asserted-by":"crossref","first-page":"e1258","DOI":"10.1542\/peds.2010-1274","volume":"127","author":"JB Holt","year":"2011","unstructured":"Holt JB, Poe MD, Escolar LM (2011) Natural progression of neurological disease in mucopolysaccharidosis type II. Pediatrics 127:e1258\u2013e1265","journal-title":"Pediatrics"},{"key":"2788_CR4","doi-asserted-by":"crossref","first-page":"162","DOI":"10.1590\/S1676-26492010000400008","volume":"16","author":"RM Lago-Albuquerque","year":"2010","unstructured":"Lago-Albuquerque RM, Noronha-Liberalesso PB, Schmitz-Ferreira ML, Klagenberg KF, Jurkiewicz AL, Zeigelboim BS (2010) Aspectos Electrencefalogr\u00e1ficos em Criancas com Mucopolissacaridose. J Epilepsy Clin Neurophysiol 16:162\u2013166","journal-title":"J Epilepsy Clin Neurophysiol"},{"key":"2788_CR5","doi-asserted-by":"crossref","first-page":"665","DOI":"10.1007\/s00234-004-1215-1","volume":"46","author":"MG Matheus","year":"2004","unstructured":"Matheus MG, Castillo M, Smith JK, Armao D, Towle D, Muenzer J (2004) Brain MRI findings in patients with mucopolysaccharidosis types I and II and mild clinical presentation. Neuroradiology 46:665\u2013672","journal-title":"Neuroradiology"},{"key":"2788_CR6","doi-asserted-by":"crossref","first-page":"4871","DOI":"10.1093\/hmg\/ddq420","volume":"19","author":"VA Polito","year":"2010","unstructured":"Polito VA, Abbondante S, Polishchuk RS, Nusco E, Salvia R, Cosma MP (2010) Correction of CNS defects in the MPSII mouse model via systemic enzyme replacement therapy. Hum Mol Genet 19:4871\u20134885","journal-title":"Hum Mol Genet"},{"key":"2788_CR7","doi-asserted-by":"crossref","first-page":"333","DOI":"10.1016\/S0074-7742(02)49020-4","volume":"49","author":"ME Ross","year":"2002","unstructured":"Ross ME (2002) Brain malformations, epilepsy, and infantile spasms. Int Rev Neurobiol 49:333\u2013352","journal-title":"Int Rev Neurobiol"},{"key":"2788_CR8","doi-asserted-by":"crossref","first-page":"1029","DOI":"10.3174\/ajnr.A0510","volume":"28","author":"L Vedolin","year":"2007","unstructured":"Vedolin L, Schwartz IV, Komlos M, Schuch A, Puga AC, Pinto LL et al (2007) Correlation of MR imaging and MR spectroscopy findings with cognitive impairment in mucopolysaccharidosis II. AJNR Am J Neuroradiol 28:1029\u20131033","journal-title":"AJNR Am J Neuroradiol"},{"key":"2788_CR9","doi-asserted-by":"crossref","first-page":"267","DOI":"10.1007\/s00431-007-0635-4","volume":"167","author":"JE Wraith","year":"2008","unstructured":"Wraith JE, Scarpa M, Beck M, Bodamer OA, De Meirleir L, Guffon N et al (2008) Mucopolysaccharidosis type II (Hunter syndrome): a clinical review and recommendations for treatment in the era of enzyme replacement therapy. Eur J Pediatr 167:267\u2013277","journal-title":"Eur J Pediatr"}],"container-title":["Neurological Sciences"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1007\/s10072-016-2788-2.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/link.springer.com\/article\/10.1007\/s10072-016-2788-2\/fulltext.html","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1007\/s10072-016-2788-2.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2017,6,25]],"date-time":"2017-06-25T01:07:03Z","timestamp":1498352823000},"score":1,"resource":{"primary":{"URL":"http:\/\/link.springer.com\/10.1007\/s10072-016-2788-2"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2016,12,2]]},"references-count":9,"journal-issue":{"issue":"3","published-print":{"date-parts":[[2017,3]]}},"alternative-id":["2788"],"URL":"https:\/\/doi.org\/10.1007\/s10072-016-2788-2","relation":{},"ISSN":["1590-1874","1590-3478"],"issn-type":[{"value":"1590-1874","type":"print"},{"value":"1590-3478","type":"electronic"}],"subject":[],"published":{"date-parts":[[2016,12,2]]}}}