{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,4,13]],"date-time":"2026-04-13T02:00:00Z","timestamp":1776045600383,"version":"3.50.1"},"reference-count":12,"publisher":"Springer Science and Business Media LLC","issue":"1","license":[{"start":{"date-parts":[[2017,10,18]],"date-time":"2017-10-18T00:00:00Z","timestamp":1508284800000},"content-version":"unspecified","delay-in-days":0,"URL":"http:\/\/www.springer.com\/tdm"}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["Neurol Sci"],"published-print":{"date-parts":[[2018,1]]},"DOI":"10.1007\/s10072-017-3156-6","type":"journal-article","created":{"date-parts":[[2017,10,18]],"date-time":"2017-10-18T07:11:50Z","timestamp":1508310710000},"page":"149-152","update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":12,"title":["Peripheral markers of autophagy in polyglutamine diseases"],"prefix":"10.1007","volume":"39","author":[{"given":"Giorgia","family":"Puorro","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Angela","family":"Marsili","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Francesca","family":"Sapone","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Chiara","family":"Pane","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Anna","family":"De Rosa","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Silvio","family":"Peluso","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Giuseppe","family":"De Michele","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Alessandro","family":"Filla","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-1323-6317","authenticated-orcid":false,"given":"Francesco","family":"Sacc\u00e0","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"297","published-online":{"date-parts":[[2017,10,18]]},"reference":[{"key":"3156_CR1","doi-asserted-by":"crossref","first-page":"247","DOI":"10.1038\/nrg2748","volume":"11","author":"AR Spada La","year":"2010","unstructured":"La Spada AR, Taylor JP (2010) Repeat expansion disease: progress and puzzles in disease pathogenesis. Nat Rev Genet 11:247\u2013258","journal-title":"Nat Rev Genet"},{"key":"3156_CR2","doi-asserted-by":"crossref","first-page":"1485","DOI":"10.1093\/hmg\/ddg175","volume":"12","author":"DP Huynh","year":"2003","unstructured":"Huynh DP, Yang HT, Vakharia H, Nguyen D, Pulst SM (2003) Expansion of the polyQ repeat in ataxin-2 alters its Golgi localization, disrupts the Golgi complex and causes cell death. Hum Mol Genet 12:1485\u20131496","journal-title":"Hum Mol Genet"},{"key":"3156_CR3","doi-asserted-by":"crossref","first-page":"1335","DOI":"10.1242\/dmm.017368","volume":"7","author":"H Brandstaetter","year":"2014","unstructured":"Brandstaetter H, Kruppa AJ, Buss F (2014) Huntingtin is required for ER-to-Golgi transport and for secretory vesicle fusion at the plasma membrane. Dis Model Mech 7:1335\u20131340","journal-title":"Dis Model Mech"},{"key":"3156_CR4","doi-asserted-by":"crossref","first-page":"424","DOI":"10.5483\/BMBRep.2016.49.8.081","volume":"49","author":"YK Lee","year":"2016","unstructured":"Lee YK, Lee JA (2016) Role of the mammalian ATG8\/LC3 family in autophagy: differential and compensatory roles in the spatiotemporal regulation of autophagy. BMB Rep 49:424\u2013430","journal-title":"BMB Rep"},{"key":"3156_CR5","doi-asserted-by":"crossref","first-page":"4672","DOI":"10.1111\/febs.13540","volume":"282","author":"Y Katsuragi","year":"2015","unstructured":"Katsuragi Y, Ichimura Y, Komatsu M (2015) p62\/SQSTM1 functions as a signaling hub and an autophagy adaptor. FEBS J 282:4672\u20134678","journal-title":"FEBS J"},{"key":"3156_CR6","doi-asserted-by":"crossref","first-page":"486","DOI":"10.1212\/01.wnl.0000324863.76290.19","volume":"71","author":"T Schmitz-H\u00fcbsch","year":"2008","unstructured":"Schmitz-H\u00fcbsch T, Giunti P, Stephenson DA et al (2008) SCA functional index: a useful compound performance measure for spinocerebellar ataxia. Neurology 71:486\u2013492","journal-title":"Neurology"},{"key":"3156_CR7","doi-asserted-by":"crossref","first-page":"136","DOI":"10.1002\/mds.870110204","volume":"11","author":"Huntington Study group","year":"1996","unstructured":"Huntington Study group (1996) Unified Huntington\u2019s disease rating scale: reliability and-consistency. Mov Disord 11:136\u2013142","journal-title":"Mov Disord"},{"key":"3156_CR8","doi-asserted-by":"crossref","first-page":"1116","DOI":"10.1007\/s00415-012-6770-5","volume":"260","author":"F Sacc\u00e0","year":"2013","unstructured":"Sacc\u00e0 F, Marsili A, Puorro G et al (2013) Clinical use of frataxin measurement in a patient with a novel deletion in the FXN gene. J Neurol 260:1116\u20131121","journal-title":"J Neurol"},{"key":"3156_CR9","doi-asserted-by":"crossref","first-page":"44","DOI":"10.1038\/79162","volume":"26","author":"DP Huynh","year":"2000","unstructured":"Huynh DP, Figueroa K, Hoang N, Pulst SM (2000) Nuclear localization or inclusion body formation of ataxin-2 are not necessary for SCA2 pathogenesis in mouse or human. Nat Genet 26:44\u201350","journal-title":"Nat Genet"},{"key":"3156_CR10","doi-asserted-by":"crossref","first-page":"858","DOI":"10.1080\/15548627.2015.1039219","volume":"11","author":"YN Rui","year":"2015","unstructured":"Rui YN, Xu Z, Patel B, Cuervo AM, Zhang SHTT (2015) Huntingtin in selective autophagy and Huntington disease: a foe or a friend within? Autophagy 11:858\u2013860","journal-title":"Autophagy"},{"key":"3156_CR11","doi-asserted-by":"crossref","first-page":"1613","DOI":"10.1080\/15548627.2017.1336278","volume":"13","author":"A Ashkenazi","year":"2017","unstructured":"Ashkenazi A, Bento CF, Ricketts T et al (2017) Polyglutamine tracts regulate autophagy. Autophagy 13:1613\u20131614","journal-title":"Autophagy"},{"key":"3156_CR12","doi-asserted-by":"crossref","first-page":"170","DOI":"10.1093\/hmg\/ddm294","volume":"17","author":"S Sarkar","year":"2008","unstructured":"Sarkar S, Krishna G, Imarisio S, Saiki S, O'Kane CJ, Rubinsztein DCA (2008) Rational mechanism for combination treatment of Huntington\u2019s disease using lithium and rapamycin. Hum Mol Genet 17:170\u2013178","journal-title":"Hum Mol Genet"}],"updated-by":[{"DOI":"10.1007\/s10072-017-3193-1","type":"correction","label":"Correction","source":"publisher","updated":{"date-parts":[[2017,11,17]],"date-time":"2017-11-17T00:00:00Z","timestamp":1510876800000}}],"container-title":["Neurological Sciences"],"original-title":[],"language":"en","link":[{"URL":"http:\/\/link.springer.com\/article\/10.1007\/s10072-017-3156-6\/fulltext.html","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1007\/s10072-017-3156-6.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/link.springer.com\/content\/pdf\/10.1007\/s10072-017-3156-6.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2018,1,16]],"date-time":"2018-01-16T23:33:59Z","timestamp":1516145639000},"score":1,"resource":{"primary":{"URL":"http:\/\/link.springer.com\/10.1007\/s10072-017-3156-6"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2017,10,18]]},"references-count":12,"journal-issue":{"issue":"1","published-print":{"date-parts":[[2018,1]]}},"alternative-id":["3156"],"URL":"https:\/\/doi.org\/10.1007\/s10072-017-3156-6","relation":{"correction":[{"id-type":"doi","id":"10.1007\/s10072-017-3193-1","asserted-by":"object"}]},"ISSN":["1590-1874","1590-3478"],"issn-type":[{"value":"1590-1874","type":"print"},{"value":"1590-3478","type":"electronic"}],"subject":[],"published":{"date-parts":[[2017,10,18]]}}}