{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,18]],"date-time":"2026-09-18T20:45:01Z","timestamp":1789764301234,"version":"4.0.1"},"reference-count":11,"publisher":"Springer Science and Business Media LLC","issue":"5","license":[{"start":{"date-parts":[[2022,2,24]],"date-time":"2022-02-24T00:00:00Z","timestamp":1645660800000},"content-version":"tdm","delay-in-days":0,"URL":"https:\/\/www.springer.com\/tdm"},{"start":{"date-parts":[[2022,2,24]],"date-time":"2022-02-24T00:00:00Z","timestamp":1645660800000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/www.springer.com\/tdm"}],"content-domain":{"domain":["link.springer.com"],"crossmark-restriction":false},"short-container-title":["Neurol Sci"],"published-print":{"date-parts":[[2022,5]]},"DOI":"10.1007\/s10072-022-05962-8","type":"journal-article","created":{"date-parts":[[2022,2,24]],"date-time":"2022-02-24T05:41:22Z","timestamp":1645681282000},"page":"3423-3425","update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":5,"title":["Spinocerebellar ataxia type 3: response to levodopa infusion in two cases"],"prefix":"10.1007","volume":"43","author":[{"ORCID":"https:\/\/orcid.org\/0000-0001-6493-3158","authenticated-orcid":false,"given":"Javier","family":"Miranda","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Esther","family":"Cubo","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2022,2,24]]},"reference":[{"key":"5962_CR1","doi-asserted-by":"crossref","unstructured":"Tuite PJ, Rogaeva EA, St George-Hysop PH, Lang AE (1995) Dopa-responsive Parkinsonism phenotype of Machado-Joseph disease: confirmation of 14q CAG expansion. Ann Neurol 684\u2013687","DOI":"10.1002\/ana.410380422"},{"key":"5962_CR2","unstructured":"Paulson H (2015) Spinocerebellar ataxia type 3 (SCA3). GeneReviews\u00ae; 3"},{"key":"5962_CR3","doi-asserted-by":"crossref","unstructured":"Durr A, Stevanin G, Cancel G, Duyckaerts C, Abbas N, Didierjean O, et al (1996) Spinocerebellar ataxia 3 and Machado-Joseph disease: clinical, molecular, and neuropathological features. Ann Neurol 490\u2013499","DOI":"10.1002\/ana.410390411"},{"key":"5962_CR4","doi-asserted-by":"crossref","unstructured":"Yamada M, Hayashi S, Takahashi H, Tsuji S (2001) Involvement of the cerebral cortex and autonomic ganglia in Machado-Joseph disease. Acta Neuropathol 101(22):140\u2013144","DOI":"10.1007\/s004010000277"},{"issue":"1","key":"5962_CR5","doi-asserted-by":"publisher","first-page":"8","DOI":"10.1111\/jnc.14541","volume":"148","author":"CA Matos","year":"2019","unstructured":"Matos CA, de Almeida LP, N\u00f3brega C (2019) Machado-Joseph disease\/spinocerebellar ataxia type 3: lessons from disease pathogenesis and clues into therapy. J Neurochem 148(1):8\u201328","journal-title":"J Neurochem"},{"issue":"13","key":"5962_CR6","doi-asserted-by":"publisher","first-page":"729","DOI":"10.1056\/NEJM197709292971318","volume":"297","author":"FC Romanul","year":"1977","unstructured":"Romanul FC, Fowler HL, Radvany J, Feldman RG, Feingold M (1977) Azorean disease of the nervous system. N Engl J Med 297(13):729\u2013730","journal-title":"N Engl J Med"},{"issue":"2","key":"5962_CR7","doi-asserted-by":"publisher","first-page":"219","DOI":"10.1002\/mds.10322","volume":"18","author":"C Buhmann","year":"2003","unstructured":"Buhmann C, Bussopulos A, Oechsner M (2003) Dopaminergic response in parkinsonian phenotype of Machado-Joseph disease. Mov Disord 18(2):219\u2013221","journal-title":"Mov Disord"},{"issue":"2","key":"5962_CR8","doi-asserted-by":"publisher","first-page":"308","DOI":"10.1007\/s00415-010-5724-z","volume":"258","author":"E Cubo","year":"2011","unstructured":"Cubo E, L\u00f3pez MD, Ceberio JI, Alfonso IL, Martinez BM, Berciano J et al (2011) Striatal dopamine function in a family with multiple SCA-3 phenotypes. J Neurol 258(2):308\u2013310","journal-title":"J Neurol"},{"issue":"6","key":"5962_CR9","doi-asserted-by":"publisher","first-page":"369","DOI":"10.1016\/j.parkreldis.2004.03.009","volume":"10","author":"CS Lu","year":"2004","unstructured":"Lu CS, Chang HC, Kuo PC, Liu YL, Wu WS, Weng YH et al (2004) The parkinsonian phenotype of spinocerebellar ataxia type 3 in a Taiwanese family. Parkinsonism Relat Disord 10(6):369\u2013373","journal-title":"Parkinsonism Relat Disord"},{"issue":"5","key":"5962_CR10","doi-asserted-by":"publisher","first-page":"374","DOI":"10.1016\/j.parkreldis.2008.09.005","volume":"15","author":"MP Socal","year":"2009","unstructured":"Socal MP, Emmel VE, Rieder CRM, Hilbig A, Saraiva-Pereira ML, Jardim LB (2009) Parkinsonism and related disorders intrafamilial variability of Parkinson phenotype in SCAs: novel cases due to SCA2 and SCA3 expansions. Parkinsonism Relat Disord 15(5):374\u2013378","journal-title":"Parkinsonism Relat Disord"},{"issue":"6","key":"5962_CR11","doi-asserted-by":"publisher","first-page":"800","DOI":"10.1212\/WNL.55.6.800","volume":"55","author":"K Gwinn-Hardy","year":"2000","unstructured":"Gwinn-Hardy K, Chen JY, Liu HC, Liu TY, Boss M, Seltzer W, Adam A, Singleton A, Koroshetz W, Waters C, Hardy J, Farrer M (2000) Spinocerebellar ataxia type 2 with parkinsonism in ethnic Chinese. Neurology 55(6):800\u2013805","journal-title":"Neurology"}],"container-title":["Neurological Sciences"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1007\/s10072-022-05962-8.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/link.springer.com\/article\/10.1007\/s10072-022-05962-8\/fulltext.html","content-type":"text\/html","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/link.springer.com\/content\/pdf\/10.1007\/s10072-022-05962-8.pdf","content-type":"application\/pdf","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2022,4,20]],"date-time":"2022-04-20T09:18:30Z","timestamp":1650446310000},"score":1,"resource":{"primary":{"URL":"https:\/\/link.springer.com\/10.1007\/s10072-022-05962-8"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2022,2,24]]},"references-count":11,"journal-issue":{"issue":"5","published-print":{"date-parts":[[2022,5]]}},"alternative-id":["5962"],"URL":"https:\/\/doi.org\/10.1007\/s10072-022-05962-8","relation":{},"ISSN":["1590-1874","1590-3478"],"issn-type":[{"value":"1590-1874","type":"print"},{"value":"1590-3478","type":"electronic"}],"subject":[],"published":{"date-parts":[[2022,2,24]]},"assertion":[{"value":"17 March 2021","order":1,"name":"received","label":"Received","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"17 February 2022","order":2,"name":"accepted","label":"Accepted","group":{"name":"ArticleHistory","label":"Article History"}},{"value":"24 February 2022","order":3,"name":"first_online","label":"First Online","group":{"name":"ArticleHistory","label":"Article History"}},{"order":1,"name":"Ethics","group":{"name":"EthicsHeading","label":"Declarations"}},{"value":"The authors confirm that the approval of an institutional review board was not required for this work. We claim that informed consent was obtained from the patient shown in the videos. We confirm that we have read the journal\u2019s position on ethical publication issues and affirm that this work is consistent with those guidelines.","order":2,"name":"Ethics","group":{"name":"EthicsHeading","label":"Ethics approval and consent to participate"}},{"value":"The authors declare no competing interests.","order":3,"name":"Ethics","group":{"name":"EthicsHeading","label":"Conflict of interest"}}]}}