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Anti-Ri antibodies (ANNA-2) are typically found in patients with opsoclonus myoclonus syndrome (OMS) and ataxia.<\/jats:p>\n              <\/jats:sec><jats:sec>\n                <jats:title>Case report<\/jats:title>\n                <jats:p>We present an anti-Ri antibody-positive 77-year-old woman with subacute progressive bilateral cranial nerve\u00a0VI palsy, gait disturbance and jaw dystonia. MRI of the brain showed hyperintense signals on T<jats:sub>2<\/jats:sub> bitemporal without contrast enhancement. Cerebrospinal fluid (CSF) examination exhibited mild pleocytosis of 13\u00a0cells\/\u00b5l and positive oligoclonal bands. CSF was overall inconspicuous for a\u00a0malignant or inflammatory etiology. Immunofluorescence analysis revealed anti-Ri antibodies in both serum and CSF. Subsequent diagnostic work up resulted in a\u00a0newly diagnosed ductal carcinoma of the right breast. PNS in this case partially responded to the anti-tumor therapy.<\/jats:p>\n              <\/jats:sec><jats:sec>\n                <jats:title>Conclusion<\/jats:title>\n                <jats:p>This case shows similarities with recently published anti-Ri syndromes, which might form a\u00a0distinct triad within the anti-Ri spectrum.<\/jats:p>\n              <\/jats:sec>","DOI":"10.1007\/s10354-023-01006-8","type":"journal-article","created":{"date-parts":[[2023,3,3]],"date-time":"2023-03-03T10:05:48Z","timestamp":1677837948000},"page":"16-21","update-policy":"https:\/\/doi.org\/10.1007\/springer_crossmark_policy","source":"Crossref","is-referenced-by-count":9,"title":["Anti-Ri paraneoplastic neurological syndrome presenting with bilateral cranial nerve\u00a0VI palsy and jaw dystonia\u2014a\u00a0distinctive syndrome within the anti-Ri spectrum?","Paraneoplastisches neurologisches Anti-Ri-Syndrom mit beidseitiger Parese des VI.\u00a0Hirnnervs und Kieferdystonie\u00a0\u2013 ein abgegrenztes Syndrom innerhalb des Anti-Ri-Spektrums?"],"prefix":"10.1007","volume":"174","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-0773-9006","authenticated-orcid":false,"given":"Elisabeth","family":"Freydl","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Alexander","family":"Tinchon","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Katrin","family":"Blauensteiner","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Stefan","family":"Oberndorfer","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"297","published-online":{"date-parts":[[2023,3,3]]},"reference":[{"key":"1006_CR1","first-page":"2135423","volume":"2019","author":"BM Arneth","year":"2019","unstructured":"Arneth\u00a0BM. 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