{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2023,9,16]],"date-time":"2023-09-16T11:10:35Z","timestamp":1694862635271},"reference-count":0,"publisher":"Wiley","issue":"5","license":[{"start":{"date-parts":[[2006,8,5]],"date-time":"2006-08-05T00:00:00Z","timestamp":1154736000000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["J of Inher Metab Disea"],"published-print":{"date-parts":[[2006,10]]},"abstract":"<jats:title>Summary<\/jats:title><jats:p>Hepatosplenomegaly is one of the cardinal signs of Hunter disease; however, portal hypertension has not been described. We report portal hypertension in an adult Hunter patient with the attenuated phenotype.<\/jats:p>","DOI":"10.1007\/s10545-006-0308-x","type":"journal-article","created":{"date-parts":[[2006,8,5]],"date-time":"2006-08-05T03:24:59Z","timestamp":1154748299000},"page":"686-686","source":"Crossref","is-referenced-by-count":0,"title":["Portal hypertension in a patient with Hunter disease"],"prefix":"10.1002","volume":"29","author":[{"given":"Tomomi","family":"Kato","sequence":"first","affiliation":[{"name":"Medical Education Development Center Gifu University Graduate School of Medicine Gifu Japan"},{"name":"Department of Pediatrics Gifu University Graduate School of Medicine Gifu Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Koji","family":"Isogai","sequence":"additional","affiliation":[{"name":"Department of Pediatrics Gifu University Graduate School of Medicine Gifu Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Koji","family":"Orii","sequence":"additional","affiliation":[{"name":"Department of Pediatrics Gifu University Graduate School of Medicine Gifu Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Izumi","family":"Kuratsubo","sequence":"additional","affiliation":[{"name":"Department of Pediatrics Gifu University Graduate School of Medicine Gifu Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Naomi","family":"Kondo","sequence":"additional","affiliation":[{"name":"Department of Pediatrics Gifu University Graduate School of Medicine Gifu Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Tadao","family":"Orii","sequence":"additional","affiliation":[{"name":"Chubu Gakuin University Seki Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Yasuyuki","family":"Suzuki","sequence":"additional","affiliation":[{"name":"Medical Education Development Center Gifu University Graduate School of Medicine Gifu Japan"},{"name":"Department of Pediatrics Gifu University Graduate School of Medicine Gifu Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[2006,8,5]]},"container-title":["Journal of Inherited Metabolic Disease"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1007\/s10545-006-0308-x","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1007\/s10545-006-0308-x","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,9,15]],"date-time":"2023-09-15T12:51:12Z","timestamp":1694782272000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1007\/s10545-006-0308-x"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2006,8,5]]},"references-count":0,"journal-issue":{"issue":"5","published-print":{"date-parts":[[2006,10]]}},"alternative-id":["10.1007\/s10545-006-0308-x"],"URL":"https:\/\/doi.org\/10.1007\/s10545-006-0308-x","archive":["Portico"],"relation":{},"ISSN":["0141-8955","1573-2665"],"issn-type":[{"value":"0141-8955","type":"print"},{"value":"1573-2665","type":"electronic"}],"subject":[],"published":{"date-parts":[[2006,8,5]]}}}