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Multiple deficiency of oxidative phosphorylation was found in the patient's liver. We suggest that patients with B<jats:sub>12<\/jats:sub>\u2010sensitive methylmalonic aciduria who have a milder clinical course should be carefully monitored for long\u2010term complications.<\/jats:p>","DOI":"10.1007\/s10545-009-1023-1","type":"journal-article","created":{"date-parts":[[2009,3,10]],"date-time":"2009-03-10T11:13:21Z","timestamp":1236683601000},"page":"159-162","source":"Crossref","is-referenced-by-count":14,"title":["Multiple OXPHOS deficiency in the liver of a patient with CblA methylmalonic aciduria sensitive to vitamin B<sub>12<\/sub>"],"prefix":"10.1002","volume":"32","author":[{"given":"V.","family":"Valayannopoulos","sequence":"first","affiliation":[{"name":"Reference Center for Inherited Metabolic Disorders H\u00f4pital Necker\u2010Enfants Malades and Universit\u00e9 Paris Descartes 149 rue de S\u00e8vres Paris cedex 15 75743 France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"L.","family":"Hubert","sequence":"additional","affiliation":[{"name":"INSERM\u2010U781 H\u00f4pital Necker\u2010Enfants Malades Paris France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"J. 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