{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,11,6]],"date-time":"2025-11-06T19:52:10Z","timestamp":1762458730956},"reference-count":31,"publisher":"Wiley","issue":"S1","license":[{"start":{"date-parts":[[2009,6,7]],"date-time":"2009-06-07T00:00:00Z","timestamp":1244332800000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["J of Inher Metab Disea"],"published-print":{"date-parts":[[2009,12]]},"abstract":"<jats:title>Summary<\/jats:title><jats:p><jats:italic>Background<\/jats:italic>: Ochronosis is a very rare disorder with an incidence of 2 to 5 per million live births. It is a genetic disorder with autosomal recessive inheritance. It is characterized by dark brown pigmentation of cartilage, capsules of joints and other soft tissues. Ochronosis usually presents as ochronotic arthropathy and spondylosis. <jats:italic>Purpose<\/jats:italic>: This article describes a very rare presentation of scoliosis and fracture of the neck of the femur in a patient with ochronosis. <jats:italic>Methods<\/jats:italic>: A 65\u2010year\u2010old woman with left\u2010sided scoliosis presented to us following a fall with fracture of the neck of the femur on the left side. Radiological examination and biochemical study of urine were consistent with ochronosis. <jats:italic>Procedure and results<\/jats:italic>: We have treated the patient by excision arthroplasty. <jats:italic>Conclusion<\/jats:italic>: We report a case of scoliosis, fracture of the neck of the femur and ochronosis occurring together in a patient.<\/jats:p>","DOI":"10.1007\/s10545-009-1172-2","type":"journal-article","created":{"date-parts":[[2009,6,6]],"date-time":"2009-06-06T07:58:08Z","timestamp":1244275088000},"page":"215-220","source":"Crossref","is-referenced-by-count":3,"title":["Black hip, fracture neck of femur and scoliosis: A case of ochronosis"],"prefix":"10.1002","volume":"32","author":[{"given":"B.","family":"Zacharia","sequence":"first","affiliation":[{"name":"Government Medical College Calicut India"},{"name":"Department of Orthopaedics Government Medical College Calicut, Calicut P.O. Calicut\u20108 Calicut 687308 India"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"J.","family":"Chundarathil","sequence":"additional","affiliation":[{"name":"Government Medical College Thrissur India"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"V.","family":"Ramakrishnan","sequence":"additional","affiliation":[{"name":"Government Medical College Thrissur India"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"R. M.","family":"Krishnankutty","sequence":"additional","affiliation":[{"name":"Government Medical College Calicut India"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"R.","family":"Veluthedath","sequence":"additional","affiliation":[{"name":"Government Medical College Calicut India"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"K.","family":"Puthezhath","sequence":"additional","affiliation":[{"name":"Government Medical College Calicut India"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"I.","family":"Varughese","sequence":"additional","affiliation":[{"name":"Government Medical College Calicut India"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[2009,6,7]]},"reference":[{"key":"e_1_2_7_2_1","doi-asserted-by":"publisher","DOI":"10.1016\/S0929-693X(00)80194-3"},{"key":"e_1_2_7_3_1","doi-asserted-by":"publisher","DOI":"10.1046\/j.1365-2796.2003.01145.x"},{"key":"e_1_2_7_4_1","doi-asserted-by":"publisher","DOI":"10.1007\/s10067-006-0390-3"},{"key":"e_1_2_7_5_1","doi-asserted-by":"publisher","DOI":"10.1007\/s00296-007-0456-9"},{"key":"e_1_2_7_6_1","doi-asserted-by":"publisher","DOI":"10.1111\/j.1365-4632.2005.02346.x"},{"issue":"3","key":"e_1_2_7_7_1","first-page":"258","article-title":"Case of exogenetic ochronosis from carbolic acid compresses","volume":"32","author":"Brogren N","year":"1952","journal-title":"Acta Derm Venereol"},{"key":"e_1_2_7_8_1","doi-asserted-by":"publisher","DOI":"10.1016\/S0190-9622(86)70178-3"},{"issue":"11","key":"e_1_2_7_9_1","first-page":"854","article-title":"Ocular ochronosis from alkaptonuria","volume":"62","author":"Carlson DM","year":"1991","journal-title":"J Am Optom Assoc"},{"key":"e_1_2_7_10_1","doi-asserted-by":"publisher","DOI":"10.1016\/S0190-9622(08)81922-6"},{"key":"e_1_2_7_11_1","doi-asserted-by":"publisher","DOI":"10.1001\/archopht.122.7.1060"},{"issue":"11","key":"e_1_2_7_12_1","first-page":"583","article-title":"[Ochronosis: a case report with multisystemic affectation, including pericardium]","volume":"19","author":"Cobos Soler FJ","year":"2002","journal-title":"An Med Interna"},{"issue":"1","key":"e_1_2_7_13_1","first-page":"41","article-title":"Alkaptonuric ochronosis: a case report","volume":"73","author":"Collins E","year":"2005","journal-title":"AANA J"},{"issue":"1","key":"e_1_2_7_14_1","first-page":"87","article-title":"Ochronosis and alkaptonuria: report of a new case with calcified aortic valve stenosis","volume":"45","author":"Dereymaeker L","year":"1990","journal-title":"Acta Cardiol"},{"issue":"5","key":"e_1_2_7_15_1","first-page":"249","article-title":"[Biomechanical studies on the pathogenesis of ochronotic arthropathy]","volume":"43","author":"Eberle P","year":"1984","journal-title":"Z Rheumatol"},{"key":"e_1_2_7_16_1","doi-asserted-by":"publisher","DOI":"10.1016\/0046-8177(89)90200-1"},{"issue":"4","key":"e_1_2_7_17_1","first-page":"273","article-title":"[HLA\u2010B27 antigen and alkaptonuria]","volume":"44","author":"Gaucher A","year":"1977","journal-title":"Rev Rhum Mal Osteoartic"},{"key":"e_1_2_7_18_1","doi-asserted-by":"publisher","DOI":"10.1007\/s002640050325"},{"key":"e_1_2_7_19_1","doi-asserted-by":"publisher","DOI":"10.1006\/geno.1994.1003"},{"key":"e_1_2_7_20_1","doi-asserted-by":"publisher","DOI":"10.1007\/BF02081762"},{"key":"e_1_2_7_21_1","doi-asserted-by":"publisher","DOI":"10.1007\/BF00347328"},{"key":"e_1_2_7_22_1","doi-asserted-by":"publisher","DOI":"10.1302\/0301-620X.85B6.13662"},{"key":"e_1_2_7_23_1","doi-asserted-by":"publisher","DOI":"10.2106\/00004623-196547070-00013"},{"issue":"5","key":"e_1_2_7_24_1","first-page":"476","article-title":"[Ochronotic arthropathy in alkaptonuria. 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