{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,23]],"date-time":"2026-08-23T16:30:12Z","timestamp":1787502612851,"version":"build-2736575974"},"reference-count":16,"publisher":"Wiley","issue":"S3","license":[{"start":{"date-parts":[[2010,11,20]],"date-time":"2010-11-20T00:00:00Z","timestamp":1290211200000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["J of Inher Metab Disea"],"published-print":{"date-parts":[[2010,12]]},"abstract":"<jats:title>Abstract<\/jats:title>\n                  <jats:p>Patients with type I glycogen storage disease (GSD) have poor tolerance to fasting, sometimes less than 3 hours during infancy. Even though most patients are able, as they get older, to tolerate a longer fasting period, they are at permanent risk for fast\u2010induced hypoglycaemia, even in adulthood. Kl\u00fcver Bucy syndrome, is characterized by psychic blindness (inability to recognize familiar objects), hypermetamorphosis (strong tendency to react to visual stimulus), increased oral exploration, placidity, indiscriminate hyper\u2010sexuality and change in dietary habits. In this case report, we describe the development of Kl\u00fcver Bucy syndrome in a 28\u2010year\u2010old man with type Ib GSD, following prolonged and severe hypoglycaemia triggered by a common respiratory infection.<\/jats:p>","DOI":"10.1007\/s10545-010-9243-y","type":"journal-article","created":{"date-parts":[[2010,11,19]],"date-time":"2010-11-19T04:07:33Z","timestamp":1290139653000},"page":"477-480","source":"Crossref","is-referenced-by-count":4,"title":["Kl\u00fcver Bucy syndrome following hypoglycaemic coma in a patient with glycogen storage disease type Ib"],"prefix":"10.1002","volume":"33","author":[{"given":"Alix Mollet","family":"Boudjemline","sequence":"first","affiliation":[{"name":"APHP, Service de P\u00e9diatrie H\u00f4pital Antoine B\u00e9cl\u00e8re Clamart France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Arnaud","family":"Isapof","sequence":"additional","affiliation":[{"name":"APHP, Service de P\u00e9diatrie H\u00f4pital Antoine B\u00e9cl\u00e8re Clamart France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jean\u2010Bernard","family":"Witas","sequence":"additional","affiliation":[{"name":"CMPR Centre du Ch\u00e2teau Soisy sur Seine France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Fran\u00e7ois M.","family":"Petit","sequence":"additional","affiliation":[{"name":"APHP, Laboratoire de biochimie et biologie mol\u00e9culaire H\u00f4pital Antoine B\u00e9cl\u00e8re Clamart France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Vincent","family":"Gajdos","sequence":"additional","affiliation":[{"name":"APHP, Service de P\u00e9diatrie H\u00f4pital Antoine B\u00e9cl\u00e8re Clamart France"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Philippe","family":"Labrune","sequence":"additional","affiliation":[{"name":"APHP, Service de P\u00e9diatrie H\u00f4pital Antoine B\u00e9cl\u00e8re Clamart France"},{"name":"Univ\u2010Paris Sud, UFR Kremlin Bic\u00eatre Clamart 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