{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,3,17]],"date-time":"2026-03-17T22:28:18Z","timestamp":1773786498668,"version":"3.50.1"},"reference-count":23,"publisher":"Wiley","issue":"2","license":[{"start":{"date-parts":[[2011,9,7]],"date-time":"2011-09-07T00:00:00Z","timestamp":1315353600000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["J of Inher Metab Disea"],"published-print":{"date-parts":[[2012,3]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>We present a review of our experience and pregnancy outcome in patients with GSD III managed by our centre. Between 1997 and 2010 there were 15 pregnancies in seven women with GSD III. Four women had GSD IIIb (nine pregnancies) and three GSD IIIa (six pregnancies). There was a successful outcome in all 15 pregnancies with delivery of 15 liveborn infants. Four infants were of low birthweight (&lt;2nd centile) but all have developed normally apart from one with behavioural\/psychiatric problems. Three women had pre\u2010existing cardiomyopathy prior to pregnancy. One of these women had deterioration of her cardiomyopathy during pregnancy and again in the post\u2010partum period. Women with GSD III do not seem to have any issues with fertility. Overall the outcome of pregnancy for both mother and child is good. Care needs to be taken to avoid maternal hypoglycemia which may be associated with intrauterine growth restriction and low birth weight. Cardiac function should be monitored carefully particularly in those with pre\u2010existing cardiomyopathy.<\/jats:p>","DOI":"10.1007\/s10545-011-9384-7","type":"journal-article","created":{"date-parts":[[2011,9,6]],"date-time":"2011-09-06T16:44:01Z","timestamp":1315327441000},"page":"245-251","source":"Crossref","is-referenced-by-count":27,"title":["Pregnancy and its management in women with GSD type III \u2010 a single centre experience"],"prefix":"10.1002","volume":"35","author":[{"given":"Radha","family":"Ramachandran","sequence":"first","affiliation":[{"name":"Charles Dent Metabolic Unit National Hospital for Neurology and Neurosurgery Internal Mailbox 92 Queen Square London WC1N 3BG UK"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Yehani","family":"Wedatilake","sequence":"additional","affiliation":[{"name":"Charles Dent Metabolic Unit National Hospital for Neurology and Neurosurgery Internal Mailbox 92 Queen Square London WC1N 3BG UK"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Caroline","family":"Coats","sequence":"additional","affiliation":[{"name":"The Heart Hospital 16 \u2010 18 Westmoreland Street London W1G 8PH UK"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Fiona","family":"Walker","sequence":"additional","affiliation":[{"name":"The Heart Hospital 16 \u2010 18 Westmoreland Street London W1G 8PH UK"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Perry","family":"Elliott","sequence":"additional","affiliation":[{"name":"The Heart Hospital 16 \u2010 18 Westmoreland Street London W1G 8PH UK"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Philip J","family":"Lee","sequence":"additional","affiliation":[{"name":"Charles Dent Metabolic Unit National Hospital for Neurology and Neurosurgery Internal Mailbox 92 Queen Square London WC1N 3BG UK"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Robin H","family":"Lachmann","sequence":"additional","affiliation":[{"name":"Charles Dent Metabolic Unit National Hospital for Neurology and Neurosurgery Internal Mailbox 92 Queen Square London WC1N 3BG UK"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Elaine","family":"Murphy","sequence":"additional","affiliation":[{"name":"Charles Dent Metabolic Unit National Hospital for Neurology and Neurosurgery Internal Mailbox 92 Queen Square London WC1N 3BG UK"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[2011,9,7]]},"reference":[{"key":"e_1_2_6_2_1","doi-asserted-by":"publisher","DOI":"10.1111\/j.1479-828X.2006.00549.x"},{"key":"e_1_2_6_3_1","doi-asserted-by":"publisher","DOI":"10.1093\/ajcn\/71.5.1256s"},{"key":"e_1_2_6_4_1","doi-asserted-by":"crossref","unstructured":"DagliAI ZoriRT McCuneH IvsicT MaisenbacherMK WeinsteinDA(2009)Reversal of glycogen storage disease type IIIa\u2010related cardiomyopathy with modification of diet.J Inherit Metab Dis.","DOI":"10.1007\/s10545-009-1088-x"},{"key":"e_1_2_6_5_1","doi-asserted-by":"crossref","unstructured":"Dagli AI LeePJ CorreiaCE RodriguezC BhattacharyaK SteinkraussL StanleyCA WeinsteinDA(2010)Pregnancy in glycogen storage disease type Ib: gestational care and report of first successful deliveries.J Inherit Metab Dis.","DOI":"10.1007\/s10545-010-9054-1"},{"key":"e_1_2_6_6_1","doi-asserted-by":"publisher","DOI":"10.1016\/0026-0495(90)90075-N"},{"key":"e_1_2_6_7_1","doi-asserted-by":"publisher","DOI":"10.1097\/00006254-199412011-00001"},{"key":"e_1_2_6_8_1","doi-asserted-by":"publisher","DOI":"10.1016\/0002-8223(93)92246-T"},{"key":"e_1_2_6_9_1","doi-asserted-by":"publisher","DOI":"10.1113\/jphysiol.2006.105072"},{"issue":"6","key":"e_1_2_6_10_1","first-page":"E704","article-title":"Effects of glucose and insulin on fetal glucose oxidation and oxygen consumption","volume":"256","author":"Hay WW","year":"1989","journal-title":"Am J Physiol"},{"key":"e_1_2_6_11_1","doi-asserted-by":"publisher","DOI":"10.1172\/JCI109314"},{"key":"e_1_2_6_12_1","doi-asserted-by":"crossref","unstructured":"KrulSP van derSmagtJJ van denBergMP SollieKM PieperPG vanSpaendonck\u2010ZwartsKY(2011)Systematic review of pregnancy in women with inherited cardiomyopathies.Eur J Heart Fail.","DOI":"10.1093\/eurjhf\/hfr040"},{"key":"e_1_2_6_13_1","doi-asserted-by":"publisher","DOI":"10.1007\/s10545-005-0252-1"},{"key":"e_1_2_6_14_1","doi-asserted-by":"publisher","DOI":"10.1111\/j.1365-2265.1995.tb02686.x"},{"key":"e_1_2_6_15_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.ejogrb.2004.04.010"},{"key":"e_1_2_6_16_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.ajog.2007.11.050"},{"key":"e_1_2_6_17_1","doi-asserted-by":"publisher","DOI":"10.1111\/j.1471-0528.1998.tb10186.x"},{"key":"e_1_2_6_18_1","doi-asserted-by":"publisher","DOI":"10.1159\/000240677"},{"key":"e_1_2_6_19_1","doi-asserted-by":"publisher","DOI":"10.1093\/humupd\/6.6.578"},{"key":"e_1_2_6_20_1","doi-asserted-by":"publisher","DOI":"10.1056\/NEJM199109263251303"},{"key":"e_1_2_6_21_1","doi-asserted-by":"publisher","DOI":"10.1093\/aje\/154.6.514"},{"key":"e_1_2_6_22_1","doi-asserted-by":"publisher","DOI":"10.1161\/hc3001.093437"},{"key":"e_1_2_6_23_1","doi-asserted-by":"publisher","DOI":"10.1034\/j.1600-0676.2000.020002186.x"},{"key":"e_1_2_6_24_1","doi-asserted-by":"publisher","DOI":"10.1136\/hrt.2006.095240"}],"container-title":["Journal of Inherited Metabolic Disease"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1007\/s10545-011-9384-7","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/full-xml\/10.1007\/s10545-011-9384-7","content-type":"application\/xml","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1007\/s10545-011-9384-7","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,9,15]],"date-time":"2023-09-15T22:04:09Z","timestamp":1694815449000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1007\/s10545-011-9384-7"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2011,9,7]]},"references-count":23,"journal-issue":{"issue":"2","published-print":{"date-parts":[[2012,3]]}},"alternative-id":["10.1007\/s10545-011-9384-7"],"URL":"https:\/\/doi.org\/10.1007\/s10545-011-9384-7","archive":["Portico"],"relation":{},"ISSN":["0141-8955","1573-2665"],"issn-type":[{"value":"0141-8955","type":"print"},{"value":"1573-2665","type":"electronic"}],"subject":[],"published":{"date-parts":[[2011,9,7]]}}}