{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,11,30]],"date-time":"2025-11-30T08:46:35Z","timestamp":1764492395150},"reference-count":18,"publisher":"Wiley","issue":"3","license":[{"start":{"date-parts":[[2012,2,18]],"date-time":"2012-02-18T00:00:00Z","timestamp":1329523200000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["J of Inher Metab Disea"],"published-print":{"date-parts":[[2012,5]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>We describe a new neuroradiologic picture observed during metabolic decompensation in two maple syrup urine disease (MSUD) patients that resembles Wernicke encephalopathy (WE). Clinical observations and the review of the literature regarding WE and MSUD pathophysiology prompted us to hypothesize a pathogenic link between these two disorders. Based on these findings, clinicians and neuroradiologists should be aware of MSUD as a possible predisposing factor of WE in children.<\/jats:p>","DOI":"10.1007\/s10545-012-9456-3","type":"journal-article","created":{"date-parts":[[2012,2,17]],"date-time":"2012-02-17T08:20:15Z","timestamp":1329466815000},"page":"413-417","source":"Crossref","is-referenced-by-count":10,"title":["Wernicke\u2010like encephalopathy during classic maple syrup urine disease decompensation"],"prefix":"10.1002","volume":"35","author":[{"given":"R.","family":"Manara","sequence":"first","affiliation":[{"name":"Division of Neuroradiology University Hospital of Padua Padua Italy"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"M.","family":"Del Rizzo","sequence":"additional","affiliation":[{"name":"Division of Metabolic Diseases, Department of Paediatrics University Hospital of Padua Via Giustiniani 3 Padua 35128 Italy"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"A. 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